Rank |
Title |
Journal |
Year |
PubWeight™‹?› |
1
|
Intravenous immune globulin (10% caprylate-chromatography purified) for the treatment of chronic inflammatory demyelinating polyradiculoneuropathy (ICE study): a randomised placebo-controlled trial.
|
Lancet Neurol
|
2008
|
3.59
|
2
|
A clinical prognostic scoring system for Guillain-Barré syndrome.
|
Lancet Neurol
|
2007
|
2.73
|
3
|
The natural course of non-classic Pompe's disease; a review of 225 published cases.
|
J Neurol
|
2005
|
2.39
|
4
|
Residual fatigue in Guillain-Barre syndrome is related to axonal loss.
|
Neurology
|
2013
|
2.01
|
5
|
Immunotherapy for Guillain-Barré syndrome: a systematic review.
|
Brain
|
2007
|
1.87
|
6
|
Pharmacokinetics of intravenous immunoglobulin and outcome in Guillain-Barré syndrome.
|
Ann Neurol
|
2009
|
1.67
|
7
|
Pulsed high-dose dexamethasone versus standard prednisolone treatment for chronic inflammatory demyelinating polyradiculoneuropathy (PREDICT study): a double-blind, randomised, controlled trial.
|
Lancet Neurol
|
2010
|
1.63
|
8
|
Guillain-Barré syndrome subtypes related to Campylobacter infection.
|
J Neurol Neurosurg Psychiatry
|
2011
|
1.62
|
9
|
Serum IgG levels in IV immunoglobulin treated chronic inflammatory demyelinating polyneuropathy.
|
J Neurol Neurosurg Psychiatry
|
2013
|
1.57
|
10
|
TDP-43 pathology in familial frontotemporal dementia and motor neuron disease without Progranulin mutations.
|
Brain
|
2007
|
1.55
|
11
|
Revised normative values for grip strength with the Jamar dynamometer.
|
J Peripher Nerv Syst
|
2011
|
1.48
|
12
|
Increased aortic stiffness and blood pressure in non-classic Pompe disease.
|
J Inherit Metab Dis
|
2014
|
1.44
|
13
|
Intravenous immunoglobulin for Guillain-Barré syndrome.
|
Cochrane Database Syst Rev
|
2014
|
1.40
|
14
|
Morphological changes in muscle tissue of patients with infantile Pompe's disease receiving enzyme replacement therapy.
|
Muscle Nerve
|
2003
|
1.32
|
15
|
High antibody titer in an adult with Pompe disease affects treatment with alglucosidase alfa.
|
Mol Genet Metab
|
2010
|
1.32
|
16
|
Fatigue: an important feature of late-onset Pompe disease.
|
J Neurol
|
2007
|
1.31
|
17
|
Corticosteroids for Guillain-Barré syndrome.
|
Cochrane Database Syst Rev
|
2012
|
1.20
|
18
|
Clinical features and predictors for disease natural progression in adults with Pompe disease: a nationwide prospective observational study.
|
Orphanet J Rare Dis
|
2012
|
1.19
|
19
|
Intravenous immunoglobulin for Guillain-Barré syndrome.
|
Cochrane Database Syst Rev
|
2012
|
1.17
|
20
|
Prediction of respiratory insufficiency in Guillain-Barré syndrome.
|
Ann Neurol
|
2010
|
1.16
|
21
|
Distinguishing acute-onset CIDP from Guillain-Barré syndrome with treatment related fluctuations.
|
Neurology
|
2005
|
1.15
|
22
|
TLR4-mediated sensing of Campylobacter jejuni by dendritic cells is determined by sialylation.
|
J Immunol
|
2010
|
1.14
|
23
|
Upper and extra-motoneuron involvement in early motoneuron disease: a diffusion tensor imaging study.
|
Brain
|
2011
|
1.13
|
24
|
Does a carpal tunnel syndrome predict an underlying disease?
|
J Neurol Neurosurg Psychiatry
|
2006
|
1.06
|
25
|
Diagnostic value of anti-GM1 ganglioside serology and validation of the INCAT-ELISA.
|
J Neurol Sci
|
2005
|
1.06
|
26
|
Impact of enzyme replacement therapy on survival in adults with Pompe disease: results from a prospective international observational study.
|
Orphanet J Rare Dis
|
2013
|
1.04
|
27
|
Effect of enzyme therapy and prognostic factors in 69 adults with Pompe disease: an open-label single-center study.
|
Orphanet J Rare Dis
|
2012
|
1.03
|
28
|
Survival and associated factors in 268 adults with Pompe disease prior to treatment with enzyme replacement therapy.
|
Orphanet J Rare Dis
|
2011
|
1.00
|
29
|
Comparison of weakness progression in inclusion body myositis during treatment with methotrexate or placebo.
|
Ann Neurol
|
2002
|
0.99
|
30
|
IgG Fc N-glycosylation in Guillain-Barré syndrome treated with immunoglobulins.
|
J Proteome Res
|
2014
|
0.98
|
31
|
Intravenous immunoglobulin for Guillain-Barré syndrome.
|
Cochrane Database Syst Rev
|
2010
|
0.96
|
32
|
Immunomodulatory treatment other than corticosteroids, immunoglobulin and plasma exchange for chronic inflammatory demyelinating polyradiculoneuropathy.
|
Cochrane Database Syst Rev
|
2013
|
0.93
|
33
|
Perception of prognostic risk in patients with multiple sclerosis: the relationship with anxiety, depression, and disease-related distress.
|
J Clin Epidemiol
|
2004
|
0.92
|
34
|
The CMAP scan as a tool to monitor disease progression in ALS and PMA.
|
Amyotroph Lateral Scler Frontotemporal Degener
|
2012
|
0.90
|
35
|
Increased aortic stiffness in glycogenosis type 2 (Pompe's disease).
|
Int J Cardiol
|
2006
|
0.90
|
36
|
First experience with enzyme replacement therapy during pregnancy and lactation in Pompe disease.
|
Mol Genet Metab
|
2011
|
0.90
|
37
|
Subclass IgG to motor gangliosides related to infection and clinical course in Guillain-Barré syndrome.
|
J Neuroimmunol
|
2008
|
0.89
|
38
|
Understanding the consequences of chronic inflammatory demyelinating polyradiculoneuropathy from impairments to activity and participation restrictions and reduced quality of life: the ICE study.
|
J Peripher Nerv Syst
|
2010
|
0.89
|
39
|
Functional polymorphisms in LPS receptors CD14 and TLR4 are not associated with disease susceptibility or Campylobacter jejuni infection in Guillain-Barré patients.
|
J Neuroimmunol
|
2004
|
0.88
|
40
|
Mannose-binding lectin contributes to the severity of Guillain-Barré syndrome.
|
J Immunol
|
2006
|
0.87
|
41
|
Anti-GM1 IgG antibodies induce leukocyte effector functions via Fcgamma receptors.
|
Ann Neurol
|
2003
|
0.87
|
42
|
Chronic inflammatory demyelinating polyneuropathy disease activity status: recommendations for clinical research standards and use in clinical practice.
|
J Peripher Nerv Syst
|
2010
|
0.86
|
43
|
Chlamydia pneumoniae and the risk for exacerbation in multiple sclerosis patients.
|
Ann Neurol
|
2003
|
0.86
|
44
|
Origin of ganglioside complex antibodies in Guillain-Barré syndrome.
|
J Neuroimmunol
|
2007
|
0.85
|
45
|
Severity of Guillain-Barré syndrome is associated with Fc gamma Receptor III polymorphisms.
|
J Neuroimmunol
|
2005
|
0.85
|
46
|
Challenges of clinical trial design when there is lack of clinical equipoise: use of a response-conditional crossover design.
|
J Neurol
|
2011
|
0.83
|
47
|
Enzyme replacement therapy and fatigue in adults with Pompe disease.
|
Mol Genet Metab
|
2013
|
0.82
|
48
|
Newer therapeutic options for chronic inflammatory demyelinating polyradiculoneuropathy.
|
Drugs
|
2009
|
0.82
|
49
|
Unmyelinated and myelinated skin nerve damage in Guillain-Barré syndrome: correlation with pain and recovery.
|
Pain
|
2011
|
0.82
|
50
|
The quick motor function test: a new tool to rate clinical severity and motor function in Pompe patients.
|
J Inherit Metab Dis
|
2011
|
0.82
|
51
|
Emerging drugs for Guillain-Barré syndrome.
|
Expert Opin Emerg Drugs
|
2011
|
0.82
|
52
|
Phenotypical variation within 22 families with Pompe disease.
|
Orphanet J Rare Dis
|
2013
|
0.81
|
53
|
Analysing the favourable effects of physical exercise: relationships between physical fitness, fatigue and functioning in Guillain-Barré syndrome and chronic inflammatory demyelinating polyneuropathy.
|
J Rehabil Med
|
2007
|
0.81
|
54
|
Differentiation of hereditary spastic paraparesis from primary lateral sclerosis in sporadic adult-onset upper motor neuron syndromes.
|
Arch Neurol
|
2009
|
0.81
|
55
|
Mortality in Guillain-Barre syndrome.
|
Neurology
|
2013
|
0.81
|
56
|
Genetic polymorphisms of macrophage-mediators in Guillain-Barré syndrome.
|
J Neuroimmunol
|
2007
|
0.81
|
57
|
Effect of glucocorticoid receptor gene polymorphisms in Guillain-Barré syndrome.
|
J Peripher Nerv Syst
|
2009
|
0.81
|
58
|
ANO5 mutations in the Dutch limb girdle muscular dystrophy population.
|
Neuromuscul Disord
|
2013
|
0.81
|
59
|
Corticosteroids for Guillain-Barré syndrome.
|
Cochrane Database Syst Rev
|
2010
|
0.80
|
60
|
Electrophysiology in chronic inflammatory demyelinating polyneuropathy with IGIV.
|
Muscle Nerve
|
2009
|
0.80
|
61
|
AChR deficiency due to epsilon-subunit mutations: two common mutations in the Netherlands.
|
J Neurol
|
2009
|
0.79
|
62
|
Hearing in adults with Pompe disease.
|
J Inherit Metab Dis
|
2011
|
0.79
|
63
|
Susceptibility to Guillain-Barré syndrome is not associated with CD1A and CD1E gene polymorphisms.
|
J Neuroimmunol
|
2008
|
0.78
|
64
|
Recurrences, vaccinations and long-term symptoms in GBS and CIDP.
|
J Peripher Nerv Syst
|
2009
|
0.78
|
65
|
Host factors determine anti-GM1 response following oral challenge of chickens with Guillain-Barré syndrome derived Campylobacter jejuni strain GB11.
|
PLoS One
|
2010
|
0.77
|
66
|
Selective digestive tract decontamination decreases time on ventilator in Guillain-Barré syndrome.
|
Neurocrit Care
|
2011
|
0.77
|
67
|
Fas polymorphisms are associated with the presence of anti-ganglioside antibodies in Guillain-Barre syndrome.
|
J Neuroimmunol
|
2005
|
0.77
|
68
|
Congenital hypomyelinating neuropathy, a long term follow-up study in an affected family.
|
Neuromuscul Disord
|
2007
|
0.76
|
69
|
Screening for antecedent Campylobacter jejuni infections and anti-ganglioside antibodies in idiopathic neuralgic amyotrophy.
|
J Peripher Nerv Syst
|
2011
|
0.76
|
70
|
Improving fatigue assessment in immune-mediated neuropathies: the modified Rasch-built fatigue severity scale.
|
J Peripher Nerv Syst
|
2009
|
0.76
|
71
|
Immunomodulatory treatment other than corticosteroids, immunoglobulin and plasma exchange for chronic inflammatory demyelinating polyradiculoneuropathy.
|
Cochrane Database Syst Rev
|
2010
|
0.76
|
72
|
Screening for anti-ganglioside antibodies in hypocretin-deficient human narcolepsy.
|
Neurosci Lett
|
2003
|
0.76
|
73
|
Pain accompanies pure motor Guillain-Barré syndrome.
|
J Peripher Nerv Syst
|
2008
|
0.75
|
74
|
Presence or absence of cytomegalovirus in cerebrospinal fluid from patients with Guillain-Barré syndrome?
|
J Infect Dis
|
2006
|
0.75
|
75
|
Multifocal motor neuropathy with abrupt onset and spontaneous recovery.
|
J Neurol
|
2007
|
0.75
|
76
|
Determination of pain and response to methylprednisolone in Guillain-Barré syndrome.
|
J Neurol
|
2007
|
0.75
|
77
|
Sensory exam with a quantitative tuning fork: rapid, sensitive and predictive of SNAP amplitude.
|
Neurology
|
2004
|
0.75
|
78
|
Predicting the course of Guillain-Barré syndrome.
|
Lancet Neurol
|
2006
|
0.75
|
79
|
Diagnostic value of anti-GQ1b antibodies in a patient with relapsing dysarthria and ataxia.
|
BMJ Case Rep
|
2009
|
0.75
|
80
|
A case of adult Pompe disease presenting with severe fatigue and selective involvement of type 1 muscle fibers.
|
Neuromuscul Disord
|
2010
|
0.75
|
81
|
Symptoms of activity-induced weakness in peripheral nervous system disorders.
|
J Peripher Nerv Syst
|
2011
|
0.75
|
82
|
Transient hypertrichosis in a patient with Guillain-Barré syndrome.
|
J Peripher Nerv Syst
|
2007
|
0.75
|
83
|
Conduction velocity distribution in neurologically well-recovered but fatigued Guillain-Barré syndrome patients.
|
Muscle Nerve
|
2006
|
0.75
|
84
|
Health-related quality of life in Guillain-Barré syndrome patients: a systematic review.
|
J Peripher Nerv Syst
|
2014
|
0.75
|
85
|
[A woman with polyneuropathy and white nails].
|
Ned Tijdschr Geneeskd
|
2014
|
0.75
|
86
|
Corticosteroids for Guillain-Barré syndrome.
|
Cochrane Database Syst Rev
|
2016
|
0.75
|
87
|
Limb motor nerve dysfunction in Miller Fisher syndrome.
|
J Peripher Nerv Syst
|
2013
|
0.75
|
88
|
Remarkably low fibroblast acid α-glucosidase activity in three adults with Pompe disease.
|
Mol Genet Metab
|
2012
|
0.75
|
89
|
Concurrent myopathy in patients with Graves' orbitopathy.
|
Orbit
|
2009
|
0.75
|
90
|
Individual patients who experienced both Guillain-Barré syndrome and CIDP.
|
J Peripher Nerv Syst
|
2009
|
0.75
|
91
|
Multiplet discharges after electrical stimulation: new evidence for distal excitability changes in motor neuron disease.
|
Amyotroph Lateral Scler
|
2012
|
0.75
|
92
|
Interventions for fatigue in peripheral neuropathy.
|
Cochrane Database Syst Rev
|
2014
|
0.75
|