PubRank

Claire-Anne Gutekunst

Author PubWeight™ 36.24‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Early mitochondrial calcium defects in Huntington's disease are a direct effect of polyglutamines. Nat Neurosci 2002 4.15
2 Selective striatal neuronal loss in a YAC128 mouse model of Huntington disease. Hum Mol Genet 2003 4.07
3 A protein interaction network links GIT1, an enhancer of huntingtin aggregation, to Huntington's disease. Mol Cell 2004 3.26
4 Huntingtin-interacting protein HIP14 is a palmitoyl transferase involved in palmitoylation and trafficking of multiple neuronal proteins. Neuron 2004 3.04
5 Recruitment and activation of caspase-8 by the Huntingtin-interacting protein Hip-1 and a novel partner Hippi. Nat Cell Biol 2002 2.50
6 Caspase cleavage of mutant huntingtin precedes neurodegeneration in Huntington's disease. J Neurosci 2002 2.05
7 Implanted neural electrodes cause chronic, local inflammation that is correlated with local neurodegeneration. J Neural Eng 2009 1.80
8 HIP14, a novel ankyrin domain-containing protein, links huntingtin to intracellular trafficking and endocytosis. Hum Mol Genet 2002 1.79
9 Early phenotypes that presage late-onset neurodegenerative disease allow testing of modifiers in Hdh CAG knock-in mice. Hum Mol Genet 2002 1.67
10 A mutation of beta -actin that alters depolymerization dynamics is associated with autosomal dominant developmental malformations, deafness, and dystonia. Am J Hum Genet 2006 1.20
11 Disruption of the endocytic protein HIP1 results in neurological deficits and decreased AMPA receptor trafficking. EMBO J 2003 1.19
12 A novel transferrin/TfR2-mediated mitochondrial iron transport system is disrupted in Parkinson's disease. Neurobiol Dis 2009 1.11
13 Targeted disruption of Huntingtin-associated protein-1 (Hap1) results in postnatal death due to depressed feeding behavior. Hum Mol Genet 2002 1.10
14 The pivotal role of RhoA GTPase in the molecular signaling of axon growth inhibition after CNS injury and targeted therapeutic strategies. Cell Transplant 2007 0.95
15 Long-term lentiviral-mediated expression of ciliary neurotrophic factor in the striatum of Huntington's disease transgenic mice. Exp Neurol 2004 0.92
16 Inhibition of the Rho signaling pathway improves neurite outgrowth and neuronal differentiation of mouse neural stem cells. Int J Physiol Pathophysiol Pharmacol 2013 0.90
17 Expression by midbrain dopamine neurons of Sema3A and 3F receptors is associated with chemorepulsion in vitro but a mild in vivo phenotype. Mol Cell Neurosci 2010 0.90
18 Aggregation of actin and cofilin in identical twins with juvenile-onset dystonia. Ann Neurol 2002 0.89
19 Anti-inflammatory treatment with acetylsalicylate or rofecoxib is not neuroprotective in Huntington's disease transgenic mice. Neurobiol Dis 2004 0.88
20 Spontaneous and evoked high-frequency oscillations in the tetanus toxin model of epilepsy. Epilepsia 2010 0.84
21 Analyzing neuronal activation with macroelectrode vs. microelectrode array stimulation. Conf Proc IEEE Eng Med Biol Soc 2012 0.78
22 A C. elegans homolog of huntingtin-associated protein 1 is expressed in chemosensory neurons and in a number of other somatic cell types. J Mol Neurosci 2008 0.77