Post-translational modifications of CFTR: insight into protein trafficking and cystic fibrosis disease.

The zebrafish Kupffer's vesicle as a model system for the molecular mechanisms by which the lack of Polycystin-2 leads to stimulation of CFTR. Biol Open (2015) 0.82

Solubilizing mutations used to crystallize one CFTR domain attenuate the trafficking and channel defects caused by the major cystic fibrosis mutation. Chem Biol (2008) 1.97

Antibodies for CFTR studies. J Cyst Fibros (2004) 1.06

Rescuing mutant CFTR: a multi-task approach to a better outcome in treating cystic fibrosis. Curr Pharm Des (2013) 1.03

Revertant mutants modify, but do not rescue, the gating defect of the cystic fibrosis mutant G551D-CFTR. J Physiol (2014) 1.00

Unusually common cystic fibrosis mutation in Portugal encodes a misprocessed protein. Biochem Biophys Res Commun (2003) 0.94

Characterization of novel airway submucosal gland cell models for cystic fibrosis studies. Cell Physiol Biochem (2005) 0.91

Deletion of CFTR translation start site reveals functional isoforms of the protein in CF patients. Cell Physiol Biochem (2009) 0.90

Methods for RNA extraction, cDNA preparation and analysis of CFTR transcripts. J Cyst Fibros (2004) 0.89

Contribution of casein kinase 2 and spleen tyrosine kinase to CFTR trafficking and protein kinase A-induced activity. Mol Cell Biol (2011) 0.87

CFTR mutations altering CFTR fragmentation. Biochem J (2013) 0.80

Antagonistic regulation of cystic fibrosis transmembrane conductance regulator cell surface expression by protein kinases WNK4 and spleen tyrosine kinase. Mol Cell Biol (2011) 0.80

Non-PCR methods for the analysis of CFTR transcripts. J Cyst Fibros (2004) 0.78

BAG-1 stabilizes mutant F508del-CFTR in a ubiquitin-like-domain-dependent manner. Cell Physiol Biochem (2012) 0.77

Analysis of genomic CFTR DNA. J Cyst Fibros (2004) 0.75