Published in Lancet on November 22, 1986
Deconstructing sickle cell disease: reappraisal of the role of hemolysis in the development of clinical subphenotypes. Blood Rev (2006) 4.46
The inherited diseases of hemoglobin are an emerging global health burden. Blood (2010) 3.48
Sickle cell disease: old discoveries, new concepts, and future promise. J Clin Invest (2007) 2.47
The natural history of sickle cell disease. Cold Spring Harb Perspect Med (2013) 1.49
The switch from fetal to adult hemoglobin. Cold Spring Harb Perspect Med (2013) 1.47
Protection against malaria morbidity: near-fixation of the alpha-thalassemia gene in a Nepalese population. Am J Hum Genet (1991) 1.28
Current concerns in haematology. 1. Is the painful crisis of sickle cell disease a "steal" syndrome? J Clin Pathol (1990) 1.08
A divergent Artiodactyl MYADM-like repeat is associated with erythrocyte traits and weight of lamb weaned in domestic sheep. PLoS One (2013) 0.94
The screening and morbidity pattern of sickle cell anemia in chhattisgarh. Indian J Hematol Blood Transfus (2014) 0.93
Genetic counselling in tribals in India. Indian J Med Res (2011) 0.89
Morbidity pattern in hospitalized under five children with sickle cell disease. Indian J Med Res (2013) 0.85
Genotypic influence of α-deletions on the phenotype of Indian sickle cell anemia patients. Korean J Hematol (2011) 0.82
Sickle cell disease in India: A perspective. Indian J Med Res (2016) 0.80
Haemoglobinopathies in tribal populations of India. Indian J Med Res (2015) 0.80
Hematological profile of sickle cell disease in central India. Indian J Hematol Blood Transfus (2008) 0.79
Hematological profile of sickle cell disease from South Gujarat, India. Hematol Rep (2012) 0.79
Priapism in Homozygous Sickle Cell Disease: A 40-year Study of the Natural History. West Indian Med J (2015) 0.76
A case series of cholecystectomy in Jamaican sickle cell disease patients - The need for a new strategy. Ann Med Surg (Lond) (2017) 0.75
Evolving locally appropriate models of care for indian sickle cell disease. Indian J Med Res (2016) 0.75
Population and Public Health Implications of Child Health and Reproductive Outcomes Among Carrier Couples of Sickle Cell Disorders in Madhya Pradesh, Central India. Int J MCH AIDS (2014) 0.75
Moritz schiff (1823-1896): a physiologist in exile. Rambam Maimonides Med J (2011) 0.75
Sickle cell disease and pregnancy outcomes: a study of the community-based hospital in a tribal block of Gujarat, India. J Health Popul Nutr (2017) 0.75
A perfect message: RNA surveillance and nonsense-mediated decay. Cell (1999) 7.08
Outbreak of aplastic crises in sickle cell anaemia associated with parvovirus-like agent. Lancet (1981) 4.62
Binary specification of nonsense codons by splicing and cytoplasmic translation. EMBO J (1998) 3.79
Screening cord bloods for detection of sickle cell disease in Jamaica. Clin Chem (1974) 3.44
Early deaths in Jamaican children with sickle cell disease. Br Med J (1978) 3.38
Ocular findings in hemoglobin SC disease in Jamaica. Am J Ophthalmol (1972) 2.97
Relatively benign sickle-cell anaemia in 60 patients aged over 30 in the West Indies. Br Med J (1968) 2.87
Yellow oleander (cerbera thevetia) poisoning with jaundice and renal failure. J Assoc Physicians India (1989) 2.54
The interaction of alpha-thalassemia and homozygous sickle-cell disease. N Engl J Med (1982) 2.52
Ocular findings in homozygous sickle cell anemia in Jamaica. Am J Ophthalmol (1972) 2.44
Is there an acute-phase response in steady-state sickle cell disease? Lancet (1993) 2.35
Prevention of pneumococcal infection in children with homozygous sickle cell disease. Br Med J (Clin Res Ed) (1984) 2.34
Causes of death in sickle-cell disease in Jamaica. Br Med J (Clin Res Ed) (1983) 2.17
The development and use of an antibody capture radioimmunoassay for specific IgM to a human parvovirus-like agent. J Hyg (Lond) (1982) 2.09
Stroke in a cohort of patients with homozygous sickle cell disease. J Pediatr (1992) 2.02
Central retinal artery occlusion without retrobulbar hemorrhage after retrobulbar anesthesia. Am J Ophthalmol (1982) 2.02
Acute splenic sequestration in homozygous sickle cell disease: natural history and management. J Pediatr (1985) 2.02
Behaviour of untreated proliferative sickle retinopathy. Br J Ophthalmol (1980) 2.02
Origin of the beta S-globin gene in blacks: the contribution of recurrent mutation or gene conversion or both. Proc Natl Acad Sci U S A (1984) 2.00
Haemoglobin gene frequencies in the Jamaican population: a study in 100,000 newborns. Br J Haematol (1986) 2.00
Geographical survey of beta S-globin gene haplotypes: evidence for an independent Asian origin of the sickle-cell mutation. Am J Hum Genet (1986) 1.89
Increased efficiency of mRNA 3' end formation: a new genetic mechanism contributing to hereditary thrombophilia. Nat Genet (2001) 1.86
Priapism and impotence in homozygous sickle cell disease. Arch Intern Med (1980) 1.85
G gamma beta+ hereditary persistence of fetal hemoglobin: cosmid cloning and identification of a specific mutation 5' to the G gamma gene. Proc Natl Acad Sci U S A (1984) 1.84
Resting metabolic rate in homozygous sickle cell disease. Am J Clin Nutr (1993) 1.79
Comparison of homozygous sickle cell disease in northern Greece and Jamaica. Lancet (1990) 1.78
Septicemia caused by Salmonella infection: an overlooked complication of sickle cell disease. J Pediatr (1997) 1.76
Irreversibly sickled cells and splenomegaly in sickle-cell anaemia. Br J Haematol (1970) 1.71
Human parvovirus infection in homozygous sickle cell disease. Lancet (1993) 1.71
Neural tube defects in hurricane aftermath. Lancet (1991) 1.69
The prothrombin 20209 C-->T mutation in Jewish-Moroccan Caucasians: molecular analysis of gain-of-function of 3' end processing. J Thromb Haemost (2006) 1.67
The clinical features of sickle-cell- thalassaemia in Jamaica. Br J Haematol (1973) 1.58
The favorable effect of activating NOTCH1 receptor mutations on long-term outcome in T-ALL patients treated on the ALL-BFM 2000 protocol can be separated from FBXW7 loss of function. Leukemia (2010) 1.56
Haematological factors associated with proliferative retinopathy in homozygous sickle cell disease. Br J Ophthalmol (1981) 1.55
Ocular findings in sickle cell thalassemia in Jamaica. Am J Ophthalmol (1972) 1.54
The development of haematological changes in homozygous sickle cell disease: a cohort study from birth to 6 years. Br J Haematol (1981) 1.54
The painful crisis of homozygous sickle cell disease. A study of the risk factors. Arch Intern Med (1987) 1.53
The irreversibly sickled cell; a determinant of haemolysis in sickle cell anaemia. Br J Haematol (1969) 1.52
Acute splenic sequestration and hypersplenism in the first five years in homozygous sickle cell disease. Arch Dis Child (1981) 1.48
Increased renal reflectivity in sickle cell disease: prevalence and characteristics. Clin Radiol (1995) 1.46
Biliary sludge in sickle cell disease. J Pediatr (1996) 1.45
Medroxyprogesterone acetate and homozygous sickle-cell disease. Lancet (1982) 1.43
Splicing and 3' end formation in the definition of nonsense-mediated decay-competent human beta-globin mRNPs. EMBO J (2001) 1.41
Bacteraemia in homozygous sickle cell disease in Africa: is pneumococcal prophylaxis justified? Arch Dis Child (2006) 1.40
Determination of mRNA fate by different RNA polymerase II promoters. Proc Natl Acad Sci U S A (1993) 1.39
An assessment of lung volumes and gas transfer in sickle-cell anaemia. Thorax (1971) 1.38
Fetal haemoglobin in homozygous sickle cell disease. Clin Haematol (1975) 1.35
Observations on the epidemiology of sickle cell disease. Trans R Soc Trop Med Hyg (1981) 1.33
Macular vasculature, visual acuity, and irreversibly sickled cells in homozygous sickle cell disease. Br J Ophthalmol (1982) 1.31
Renal function in patients over 40 with homozygous sickle-cell disease. Br Med J (Clin Res Ed) (1981) 1.30
Post-natal decline of fetal haemoglobin in homozygous sickle cell disease: relationship to parenteral Hb F levels. Br J Haematol (1982) 1.29
The progression of sickle cell eye disease in Jamaica. Doc Ophthalmol (1975) 1.28
alpha-Thalassemia reduces the hemolytic rate in homozygous sickle-cell disease. N Engl J Med (1983) 1.28
Sickle cell retinopathy in Jamaican children: further observations from a cohort study. Br J Ophthalmol (1988) 1.25
The sickle-cell and altitude. Br Med J (1971) 1.25
Sickle cell retinopathy in young children in Jamaica. Br J Ophthalmol (1982) 1.24
Oral zinc sulphate in sickle-cell ulcers. Lancet (1970) 1.24
The clinical features of haemoglobin SC disease in Jamaica. Br J Haematol (1973) 1.23
Haematological factors associated with proliferative retinopathy in sickle cell-haemoglobin C disease. Br J Ophthalmol (1981) 1.23
Retinal and choroidal neovascularization in sickle cell disease. Trans Ophthalmol Soc U K (1980) 1.22
Negro alpha-thalassaemia is caused by deletion of a single alpha-globin gene. Lancet (1979) 1.22
Fetal hemoglobin and clinical severity of homozygous sickle cell disease in early childhood. J Pediatr (1981) 1.21
Haematological factors associated with avascular necrosis of the femoral head in homozygous sickle cell disease. Br J Haematol (1982) 1.21
Leg ulceration in sickle cell anemia. Arch Intern Med (1974) 1.17
Two different forms of homozygous sickle cell disease occur in Saudi Arabia. Br J Haematol (1991) 1.15
Gallstones in sickle cell disease: observations from The Jamaican Cohort study. J Pediatr (2000) 1.15
Nuclear degradation of nonsense mutated beta-globin mRNA: a post-transcriptional mechanism to protect heterozygotes from severe clinical manifestations of beta-thalassemia? Nucleic Acids Res (1995) 1.14
Comparison of sickle cell-beta0 thalassaemia with homozygous sickle cell disease. Br J Haematol (1979) 1.14
Localization of collagen alpha 1(I) gene expression during wound healing by in situ hybridization. J Invest Dermatol (1989) 1.12
Photocoagulation and diathermy in the treatment of proliferative sickle retinopathy. Br J Ophthalmol (1974) 1.10
Climate and painful crisis of sickle-cell disease in Jamaica. Br Med J (1976) 1.10
Sickle cell retinopathy in Jamaican children: a search for prognostic factors. Br J Ophthalmol (1983) 1.10
Photocoagulation in proliferative sickle retinopathy: results of a 5-year study. Br J Ophthalmol (1980) 1.10
Heights, weights, and skeletal age of Jamaican adolescents with sickle cell anaemia. Arch Dis Child (1972) 1.10
Early splenomegaly in homozygous sickle-cell disease: An indicator of susceptibility to infection. Lancet (1978) 1.10
Determinants of nocturnal enuresis in homozygous sickle cell disease. Arch Dis Child (1990) 1.09
Fetal haemoglobin and early manifestations of homozygous sickle cell disease. Arch Dis Child (1992) 1.09
Body habirus of Jamaican adults with sickle cell anemia. South Med J (1972) 1.09
Prepubertal growth and skeletal maturation in children with sickle cell disease. Pediatrics (1986) 1.09
A comparison of erythrocyte characteristics in sickle cell syndromes in Jamaica. Br J Haematol (1972) 1.09
The molecular basis of alpha thalassemia in India. Its interaction with the sickle cell gene. Blood (1988) 1.08