Published in Eur J Pediatr on April 01, 1989
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Cystatin C--a new marker of glomerular filtration rate in children independent of age and height. Pediatrics (1998) 2.50
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Sulphur-containing "perfumes" attract flower-visiting bats. J Comp Physiol A (2000) 1.76
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Aromatic L-amino acid decarboxylase deficiency: an extrapyramidal movement disorder with oculogyric crises. Eur J Paediatr Neurol (1997) 1.54
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Endogenous renal transport of free amino acids in infancy and childhood. Pediatrics (1968) 1.42
Glutaryl-coenzyme A dehydrogenase deficiency: a distinct encephalopathy. Pediatrics (1991) 1.41
Long-term outcome in 134 patients with galactosaemia. Eur J Pediatr (1993) 1.39
Low-dose subcutaneous recombinant interleukin-2 in advanced human malignancy: a phase II outpatient study. Mol Biother (1990) 1.37
TPA-induced differentiation and adhesion of U937 cells: changes in ultrastructure, cytoskeletal organization and expression of cell surface antigens. Eur J Cell Biol (1989) 1.32
The DiGeorge syndrome. I. Clinical evaluation and course of partial and complete forms of the syndrome. Eur J Pediatr (1988) 1.27
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Progressive familial intrahepatic cholestasis: partial biliary diversion normalizes serum lipids and improves growth in noncirrhotic patients. Am J Gastroenterol (2000) 1.19
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Macrophage cytotoxicity: interleukin 1 as a mediator of tumor cytostasis. J Immunol (1986) 1.13
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Visualization of a covalent intermediate between microsomal epoxide hydrolase, but not cholesterol epoxide hydrolase, and their substrates. Eur J Biochem (1997) 1.12
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A subset of human cells isolated and characterized by monoclonal antibodies. Eur J Immunol (1981) 1.06
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Nifedipine aggravates cyclosporine A-induced gingival hyperplasia. Pediatr Nephrol (1994) 1.04
A molecular approach to dominance in hypophosphatasia. Hum Genet (2001) 1.04
Isolation and characterization of an ornithine-containing lipid from Paracoccus denitrificans. Eur J Biochem (1980) 1.03
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The treatment of minimal change nephrotic syndrome (lipoid nephrosis): cooperative studies of the Arbeitsgemeinschaft für Pädiatrische Nephrologie (APN). Klin Padiatr (1982) 1.00
Neuroblastoma screening: arguments from retrospective analysis of three German neuroblastoma trials. Am J Pediatr Hematol Oncol (1991) 0.96
Oxalate elimination via hemodialysis or peritoneal dialysis in children with chronic renal failure. Pediatr Nephrol (1996) 0.95
[An isolated defect of the tubular cystine reabsorption in a family with idiopathic hypoparathyroidism]. Klin Wochenschr (1967) 0.94
Acute interstitial nephritis in childhood. Eur J Pediatr (1984) 0.93
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Clinical course of hypophosphatemic rickets in 23 adults. Clin Nephrol (1996) 0.91
Steroid resistant nephrotic syndrome associated with spondyloepiphyseal dysplasia, transient ischemic attacks and lymphopenia. Clin Nephrol (1995) 0.91
Divergent expression of HLA-DC/MB, -DR, and -SB region products on normal and pathological tissues as detected by monoclonal antibodies. Immunobiology (1985) 0.90
Survival time in cystinosis. A collaborative study. Proc Eur Dial Transplant Assoc (1983) 0.90
Somatic growth after kidney transplantation. Beneficial effect of cyclosporine in comparison with conventional immunosuppression. Am J Dis Child (1987) 0.89
Treatment of inherited metabolic disorders by liver transplantation. J Inherit Metab Dis (1991) 0.88
Exercise capacity and blood pressure response in children and adolescents after renal transplantation. Acta Paediatr (1994) 0.88
Dosage of Cyclosporin A in children with renal transplants. Clin Nephrol (1984) 0.88
Quantitation of up to 12 estrogens in 1-50 l of pregnancy urine. J Steroid Biochem (1973) 0.88
Growth and pubertal development in nephropathic cystinosis. Eur J Pediatr (1993) 0.87
Stereochemistry of hydrolysis of adenosine 3':5'-cyclic phosphorothioate by the cyclic phosphodiesterase from beef heart. J Biol Chem (1979) 0.87
Association of spondylo-epiphyseal dysplasia with nephrotic syndrome. Pediatr Nephrol (1990) 0.87
Complete absence of tubular glucose reabsorption: a new type of renal glucosuria (type 0). Clin Nephrol (1987) 0.86
Characterization of human TUR leukemia cells: continued cell cycle progression in the presence of phorbol ester is associated with resistance to apoptosis. Eur J Cell Biol (1994) 0.86
Recurrent haemolytic uraemic syndrome in a boy with focal and segmental glomerulosclerosis. Eur J Pediatr (1992) 0.86
The renal transport of amino acids in untreated infants with phenylketonuria. Acta Paediatr Scand (1970) 0.86
End stage renal failure: 14 years' experience of dialysis and renal transplantation. Arch Dis Child (1988) 0.85
Severe congenital hyperthyroidism caused by a germ-line neo mutation in the extracellular portion of the thyrotropin receptor. J Clin Endocrinol Metab (1998) 0.85
Practical aspects in the use of cyclosporin in paediatric nephrology. Pediatr Nephrol (1991) 0.85
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Maximal tubular reabsorption of glucose in infants and children. Acta Paediatr Scand (1972) 0.84
Low-dose interleukin-2 in combination with interferon-alpha effectively modulates biological response in vivo. Acta Haematol (1993) 0.84
Sensitive in vivo assay of the phenylalanine hydroxylating system with a small intravenous dose of heptadeutero L-phenylalanine using high pressure liquid chromatography and capillary gas chromatography/mass fragmentography. Clin Chim Acta (1979) 0.84
Cystatin C and creatinine after successful kidney transplantation in children. Clin Nephrol (1999) 0.84
Mass fragmentographic determination of myocardial free fatty acids. J Mol Cell Cardiol (1982) 0.84
Facts and artefacts in mevalonic aciduria: development of a stable isotope dilution GCMS assay for mevalonic acid and its application to physiological fluids, tissue samples, prenatal diagnosis and carrier detection. Clin Chim Acta (1991) 0.84
Distal myopathy in nephropathic cystinosis. Pediatr Nephrol (2000) 0.83
Identification of mutations in the ALD-gene of 20 families with adrenoleukodystrophy/adrenomyeloneuropathy. Hum Genet (1996) 0.83
End-stage renal failure in children younger than 6 years: renal transplantation is the therapy of choice. Eur J Pediatr (1998) 0.83
Liver transplantation in children. Z Kinderchir (1983) 0.83
Intrathecal IgA synthesis in X-linked cerebral adrenoleukodystrophy. J Child Neurol (1997) 0.83
Analysis of mast cells in rheumatoid arthritis and osteoarthritis by an avidin-peroxidase staining. Virchows Arch B Cell Pathol Incl Mol Pathol (1984) 0.83
Glucocorticoid receptors in sheep brain tissues during development. Am J Physiol (1985) 0.83
Liver transplantation in children: the Hannover experience. Transplant Proc (1987) 0.83
Glyceroltrioleate/glyceroltrierucate therapy in 16 patients with X-chromosomal adrenoleukodystrophy/adrenomyeloneuropathy: effect on clinical, biochemical and neurophysiological parameters. Eur J Pediatr (1995) 0.83
Cyclosporin A in pediatric kidney transplantation and its effect on posttransplantation growth. Nephron (1986) 0.83
Cyclosporin A in paediatric kidney transplantation. Pediatr Nephrol (1987) 0.83
Regulation of the mitochondrial ATP-synthase in human fibroblasts. Clin Chim Acta (1994) 0.82
Proteinuria, hematuria, and leukocyturia in children with mixed urinary and intestinal schistosomiasis. Kidney Int (1985) 0.82
Cerebral adrenoleukodystrophy (ALD) in only one of monozygotic twins with an identical ALD genotype. Ann Neurol (1996) 0.82
[Adrenomyeloneuropathy. A frequent cause of Addison's disease]. Dtsch Med Wochenschr (1994) 0.82
Expansion of peripheral blood natural killer cells correlates with clinical outcome in cancer patients receiving recombinant subcutaneous interleukin-2 and interferon-alpha-2. Tumour Biol (1993) 0.82
Renal function after kidney transplantation in children. A comparison of conventional immunosuppression with cyclosporine. Transplantation (1987) 0.82
The role of lipoproteins in the degradation of platelet-activating factor. Thromb Res (1986) 0.82
Carbohydrate and fatty acid metabolism of cultured adult cardiac myocytes. Am J Physiol (1986) 0.82
Evaluation of catecholamine metabolites, mIBG scan, and bone marrow cytology as response markers in stage 4 neuroblastoma. Med Pediatr Oncol (2001) 0.82
[Kidney transplantation in children at Hannover from 1970 to 1977 (author's transl)]. Dtsch Med Wochenschr (1979) 0.82
Determination of oxalate excretion in spot urines of healthy children by ion chromatography. Eur J Clin Chem Clin Biochem (1994) 0.81
[Influence of a fat-free diet on the content and synthesis of arachidonic acid in the feto-placental unit of the rat]. Acta Biol Med Ger (1977) 0.81