PubRank

Aurora Pujol

Author PubWeight™ 36.19‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 General aspects and neuropathology of X-linked adrenoleukodystrophy. Brain Pathol 2010 1.41
2 The evolutionary origin of peroxisomes: an ER-peroxisome connection. Mol Biol Evol 2006 1.39
3 Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy. Ann Neurol 2011 1.31
4 Early oxidative damage underlying neurodegeneration in X-adrenoleukodystrophy. Hum Mol Genet 2008 1.27
5 Current and future pharmacological treatment strategies in X-linked adrenoleukodystrophy. Brain Pathol 2010 1.27
6 PeroxisomeDB 2.0: an integrative view of the global peroxisomal metabolome. Nucleic Acids Res 2009 1.24
7 Pathomechanisms underlying X-adrenoleukodystrophy: a three-hit hypothesis. Brain Pathol 2010 1.20
8 PeroxisomeDB: a database for the peroxisomal proteome, functional genomics and disease. Nucleic Acids Res 2006 1.08
9 A key role for the peroxisomal ABCD2 transporter in fatty acid homeostasis. Am J Physiol Endocrinol Metab 2008 1.07
10 Inactivation of the peroxisomal ABCD2 transporter in the mouse leads to late-onset ataxia involving mitochondria, Golgi and endoplasmic reticulum damage. Hum Mol Genet 2005 1.06
11 Valproic acid induces antioxidant effects in X-linked adrenoleukodystrophy. Hum Mol Genet 2010 1.03
12 Oxidative stress underlying axonal degeneration in adrenoleukodystrophy: a paradigm for multifactorial neurodegenerative diseases? Biochim Biophys Acta 2012 0.99
13 Mouse liver PMP70 and ALDP: homomeric interactions prevail in vivo. Biochim Biophys Acta 2004 0.98
14 ABCD2 is abundant in adipose tissue and opposes the accumulation of dietary erucic acid (C22:1) in fat. J Lipid Res 2010 0.96
15 Oxidative stress modulates mitochondrial failure and cyclophilin D function in X-linked adrenoleukodystrophy. Brain 2012 0.92
16 Functional genomic analysis unravels a metabolic-inflammatory interplay in adrenoleukodystrophy. Hum Mol Genet 2011 0.91
17 Neuroinflammatory signals in Alzheimer disease and APP/PS1 transgenic mice: correlations with plaques, tangles, and oligomeric species. J Neuropathol Exp Neurol 2015 0.90
18 Steroid hormones control circadian Elovl3 expression in mouse liver. Endocrinology 2008 0.90
19 Oxidative damage compromises energy metabolism in the axonal degeneration mouse model of X-adrenoleukodystrophy. Antioxid Redox Signal 2011 0.90
20 Amyloid generation and dysfunctional immunoproteasome activation with disease progression in animal model of familial Alzheimer's disease. Brain Pathol 2012 0.89
21 Pioglitazone halts axonal degeneration in a mouse model of X-linked adrenoleukodystrophy. Brain 2013 0.89
22 The role of peroxisomal ABC transporters in the mouse adrenal gland: the loss of Abcd2 (ALDR), Not Abcd1 (ALD), causes oxidative damage. Lab Invest 2007 0.88
23 Functional genomics reveals dysregulation of cortical olfactory receptors in Parkinson disease: novel putative chemoreceptors in the human brain. J Neuropathol Exp Neurol 2013 0.87
24 Mitochondrial dysfunction in central nervous system white matter disorders. Glia 2014 0.87
25 PGC-1α overexpression exacerbates β-amyloid and tau deposition in a transgenic mouse model of Alzheimer's disease. FASEB J 2014 0.86
26 Bezafibrate lowers very long-chain fatty acids in X-linked adrenoleukodystrophy fibroblasts by inhibiting fatty acid elongation. J Inherit Metab Dis 2012 0.86
27 Bezafibrate administration improves behavioral deficits and tau pathology in P301S mice. Hum Mol Genet 2012 0.86
28 Histone deacetylase inhibitor upregulates peroxisomal fatty acid oxidation and inhibits apoptotic cell death in abcd1-deficient glial cells. PLoS One 2013 0.83
29 Insulin-like growth factor-1 and neurotrophin-3 gene therapy prevents motor decline in an X-linked adrenoleukodystrophy mouse model. Ann Neurol 2009 0.83
30 The absence of ABCD2 sensitizes mice to disruptions in lipid metabolism by dietary erucic acid. J Lipid Res 2012 0.82
31 Glutathione imbalance in patients with X-linked adrenoleukodystrophy. Mol Genet Metab 2013 0.81
32 Oxidative stress regulates the ubiquitin-proteasome system and immunoproteasome functioning in a mouse model of X-adrenoleukodystrophy. Brain 2013 0.80
33 Staging anti-inflammatory therapy in Alzheimer's disease. Front Aging Neurosci 2010 0.79
34 JNK/ERK/FAK mediate promigratory actions of basic fibroblast growth factor in astrocytes via CCL2 and COX2. Neurosignals 2011 0.79
35 ATP and noradrenaline activate CREB in astrocytes via noncanonical Ca(2+) and cyclic AMP independent pathways. Glia 2012 0.79
36 Phylogenomic evidence for a myxococcal contribution to the mitochondrial fatty acid beta-oxidation. PLoS One 2011 0.78
37 Cyclophilin D as a potential target for antioxidants in neurodegeneration: the X-ALD case. Biol Chem 2013 0.76
38 Autophagy induction halts axonal degeneration in a mouse model of X-adrenoleukodystrophy. Acta Neuropathol 2014 0.75
39 Schilder's disease a heterogenous group of disorders known as X-linked adrenoleukodystrophy. Foreword. Brain Pathol 2010 0.75