Rank |
Title |
Journal |
Year |
PubWeight™‹?› |
1
|
Sildenafil citrate therapy for pulmonary arterial hypertension.
|
N Engl J Med
|
2005
|
9.27
|
2
|
Treatment of pulmonary arterial hypertension.
|
N Engl J Med
|
2004
|
6.88
|
3
|
Pulmonary arterial hypertension in France: results from a national registry.
|
Am J Respir Crit Care Med
|
2006
|
6.06
|
4
|
Survival in patients with idiopathic, familial, and anorexigen-associated pulmonary arterial hypertension in the modern management era.
|
Circulation
|
2010
|
5.87
|
5
|
2015 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension: The Joint Task Force for the Diagnosis and Treatment of Pulmonary Hypertension of the European Society of Cardiology (ESC) and the European Respiratory Society (ERS): Endorsed by: Association for European Paediatric and Congenital Cardiology (AEPC), International Society for Heart and Lung Transplantation (ISHLT).
|
Eur Heart J
|
2015
|
5.24
|
6
|
Macitentan and morbidity and mortality in pulmonary arterial hypertension.
|
N Engl J Med
|
2013
|
4.98
|
7
|
Long-term intravenous epoprostenol infusion in primary pulmonary hypertension: prognostic factors and survival.
|
J Am Coll Cardiol
|
2002
|
4.79
|
8
|
Long-term response to calcium channel blockers in idiopathic pulmonary arterial hypertension.
|
Circulation
|
2005
|
2.98
|
9
|
Pulmonary arterial hypertension in patients treated by dasatinib.
|
Circulation
|
2012
|
2.87
|
10
|
Imatinib mesylate as add-on therapy for pulmonary arterial hypertension: results of the randomized IMPRES study.
|
Circulation
|
2013
|
2.64
|
11
|
Chronic thromboembolic pulmonary hypertension.
|
Circulation
|
2006
|
2.58
|
12
|
Dysregulated renin-angiotensin-aldosterone system contributes to pulmonary arterial hypertension.
|
Am J Respir Crit Care Med
|
2012
|
2.52
|
13
|
Platelet-derived growth factor expression and function in idiopathic pulmonary arterial hypertension.
|
Am J Respir Crit Care Med
|
2008
|
2.48
|
14
|
New formula for predicting mean pulmonary artery pressure using systolic pulmonary artery pressure.
|
Chest
|
2004
|
2.47
|
15
|
Is pulmonary arterial hypertension really a late complication of systemic sclerosis?
|
Chest
|
2009
|
2.40
|
16
|
Long-term outcome with first-line bosentan therapy in idiopathic pulmonary arterial hypertension.
|
Eur Heart J
|
2006
|
2.34
|
17
|
Vascular and right ventricular remodelling in chronic thromboembolic pulmonary hypertension.
|
Eur Respir J
|
2012
|
2.32
|
18
|
Initial Use of Ambrisentan plus Tadalafil in Pulmonary Arterial Hypertension.
|
N Engl J Med
|
2015
|
2.23
|
19
|
CX(3)C chemokine fractalkine in pulmonary arterial hypertension.
|
Am J Respir Crit Care Med
|
2002
|
2.15
|
20
|
C-kit-positive cells accumulate in remodeled vessels of idiopathic pulmonary arterial hypertension.
|
Am J Respir Crit Care Med
|
2011
|
2.12
|
21
|
Prevalence of HIV-related pulmonary arterial hypertension in the current antiretroviral therapy era.
|
Am J Respir Crit Care Med
|
2007
|
2.03
|
22
|
Chronic thromboembolic pulmonary hypertension (CTEPH): results from an international prospective registry.
|
Circulation
|
2011
|
1.92
|
23
|
Severe pulmonary hypertension during pregnancy: mode of delivery and anesthetic management of 15 consecutive cases.
|
Anesthesiology
|
2005
|
1.88
|
24
|
Ambrisentan therapy for pulmonary arterial hypertension.
|
J Am Coll Cardiol
|
2005
|
1.82
|
25
|
Treprostinil, a prostacyclin analogue, in pulmonary arterial hypertension associated with connective tissue disease.
|
Chest
|
2004
|
1.72
|
26
|
Portopulmonary hypertension: survival and prognostic factors.
|
Am J Respir Crit Care Med
|
2008
|
1.71
|
27
|
Effects of the dual endothelin receptor antagonist bosentan in patients with pulmonary arterial hypertension: a 1-year follow-up study.
|
Chest
|
2003
|
1.71
|
28
|
Bosentan for treatment of inoperable chronic thromboembolic pulmonary hypertension: BENEFiT (Bosentan Effects in iNopErable Forms of chronIc Thromboembolic pulmonary hypertension), a randomized, placebo-controlled trial.
|
J Am Coll Cardiol
|
2008
|
1.69
|
29
|
Pulmonary Langerhans cell histiocytosis-associated pulmonary hypertension: clinical characteristics and impact of pulmonary arterial hypertension therapies.
|
Chest
|
2012
|
1.68
|
30
|
Selexipag for the Treatment of Pulmonary Arterial Hypertension.
|
N Engl J Med
|
2015
|
1.62
|
31
|
2015 ESC/ERS Guidelines for the Diagnosis and Treatment of Pulmonary Hypertension.
|
Rev Esp Cardiol (Engl Ed)
|
2016
|
1.61
|
32
|
Intravenous epoprostenol in inoperable chronic thromboembolic pulmonary hypertension.
|
J Heart Lung Transplant
|
2007
|
1.58
|
33
|
Potts shunt in children with idiopathic pulmonary arterial hypertension: long-term results.
|
Ann Thorac Surg
|
2012
|
1.54
|
34
|
IgG from patients with pulmonary arterial hypertension and/or systemic sclerosis binds to vascular smooth muscle cells and induces cell contraction.
|
Ann Rheum Dis
|
2011
|
1.53
|
35
|
Role of endothelium-derived CC chemokine ligand 2 in idiopathic pulmonary arterial hypertension.
|
Am J Respir Crit Care Med
|
2007
|
1.52
|
36
|
Stress Doppler echocardiography in relatives of patients with idiopathic and familial pulmonary arterial hypertension: results of a multicenter European analysis of pulmonary artery pressure response to exercise and hypoxia.
|
Circulation
|
2009
|
1.50
|
37
|
Clinical outcomes of pulmonary arterial hypertension in patients carrying an ACVRL1 (ALK1) mutation.
|
Am J Respir Crit Care Med
|
2010
|
1.50
|
38
|
Characterization of pulmonary arterial hypertension patients walking more than 450 m in 6 min at diagnosis.
|
Chest
|
2010
|
1.48
|
39
|
Prognostic factors for survival in human immunodeficiency virus-associated pulmonary arterial hypertension.
|
Am J Respir Crit Care Med
|
2003
|
1.46
|
40
|
Pre-implantation genetic diagnosis in pulmonary arterial hypertension due to BMPR2 mutation.
|
Eur Respir J
|
2012
|
1.45
|
41
|
Pulmonary veno-occlusive disease: clinical, functional, radiologic, and hemodynamic characteristics and outcome of 24 cases confirmed by histology.
|
Medicine (Baltimore)
|
2008
|
1.43
|
42
|
Fibrous remodeling of the pulmonary venous system in pulmonary arterial hypertension associated with connective tissue diseases.
|
Hum Pathol
|
2007
|
1.42
|
43
|
Pulmonary hypertension: CT of the chest in pulmonary venoocclusive disease.
|
AJR Am J Roentgenol
|
2004
|
1.41
|
44
|
Immunosuppressive therapy in lupus- and mixed connective tissue disease-associated pulmonary arterial hypertension: a retrospective analysis of twenty-three cases.
|
Arthritis Rheum
|
2008
|
1.40
|
45
|
Bosentan for the treatment of human immunodeficiency virus-associated pulmonary arterial hypertension.
|
Am J Respir Crit Care Med
|
2004
|
1.40
|
46
|
Left ventricular ejection time in acute heart failure complicating precapillary pulmonary hypertension.
|
Chest
|
2013
|
1.39
|
47
|
Chemokine RANTES in severe pulmonary arterial hypertension.
|
Am J Respir Crit Care Med
|
2002
|
1.38
|
48
|
Sildenafil for pulmonary arterial hypertension: still waiting for evidence.
|
Am J Respir Crit Care Med
|
2004
|
1.38
|
49
|
Screening for pulmonary arterial hypertension in patients with systemic sclerosis: clinical characteristics at diagnosis and long-term survival.
|
Arthritis Rheum
|
2011
|
1.35
|
50
|
Diagnostic strategy for patients with suspected pulmonary embolism: a prospective multicentre outcome study.
|
Lancet
|
2002
|
1.32
|
51
|
Immunosuppressive therapy in connective tissue diseases-associated pulmonary arterial hypertension.
|
Chest
|
2006
|
1.29
|
52
|
HIV-associated pulmonary arterial hypertension: survival and prognostic factors in the modern therapeutic era.
|
AIDS
|
2010
|
1.27
|
53
|
Absence of influence of gender and BMPR2 mutation type on clinical phenotypes of pulmonary arterial hypertension.
|
Respir Res
|
2010
|
1.19
|
54
|
Pulmonary arterial hypertension.
|
Orphanet J Rare Dis
|
2013
|
1.18
|
55
|
Evaluation of various empirical formulas for estimating mean pulmonary artery pressure by using systolic pulmonary artery pressure in adults.
|
Chest
|
2008
|
1.16
|
56
|
Phosphodiesterase type 5 inhibitors in pulmonary arterial hypertension.
|
Adv Ther
|
2009
|
1.10
|
57
|
Autocrine fibroblast growth factor-2 signaling contributes to altered endothelial phenotype in pulmonary hypertension.
|
Am J Respir Cell Mol Biol
|
2010
|
1.08
|
58
|
Future perspectives for the treatment of pulmonary arterial hypertension.
|
J Am Coll Cardiol
|
2009
|
1.08
|
59
|
Treatment of pulmonary arterial hypertension with targeted therapies.
|
Nat Rev Cardiol
|
2011
|
1.08
|
60
|
Pulmonary veno-occlusive disease: recent progress and current challenges.
|
Respir Med
|
2010
|
1.06
|
61
|
Current and future management of chronic thromboembolic pulmonary hypertension: from diagnosis to treatment responses.
|
Proc Am Thorac Soc
|
2006
|
1.05
|
62
|
Out-of-proportion pulmonary hypertension and heart failure with preserved ejection fraction.
|
Respiration
|
2012
|
1.03
|
63
|
Long-term response to calcium-channel blockers in non-idiopathic pulmonary arterial hypertension.
|
Eur Heart J
|
2010
|
1.01
|
64
|
Severe pulmonary arterial hypertension in type 1 glycogen storage disease.
|
Eur J Pediatr
|
2002
|
1.01
|
65
|
Pulmonary arterial hypertension: a rare complication of primary Sjögren syndrome: report of 9 new cases and review of the literature.
|
Medicine (Baltimore)
|
2007
|
0.97
|
66
|
Pulmonary arterial hypertension in ANCA-associated vasculitis.
|
Sarcoidosis Vasc Diffuse Lung Dis
|
2006
|
0.96
|
67
|
Long-term outcome of systemic sclerosis-associated pulmonary arterial hypertension treated with bosentan as first-line monotherapy followed or not by the addition of prostanoids or sildenafil.
|
Rheumatology (Oxford)
|
2009
|
0.96
|
68
|
Increased oxidative stress and severe arterial remodeling induced by permanent high-flow challenge in experimental pulmonary hypertension.
|
Respir Res
|
2011
|
0.95
|
69
|
Identification of target antigens of antifibroblast antibodies in pulmonary arterial hypertension.
|
Am J Respir Crit Care Med
|
2008
|
0.94
|
70
|
Treatment of pulmonary arterial hypertension with bosentan: from pathophysiology to clinical evidence.
|
Expert Opin Pharmacother
|
2005
|
0.93
|
71
|
Controversies, uncertainties and future research on the treatment of chronic thromboembolic pulmonary hypertension.
|
Proc Am Thorac Soc
|
2006
|
0.93
|
72
|
Diagnostic value of D-dimer in patients with suspected pulmonary embolism: results from a multicentre outcome study.
|
Thromb Res
|
2006
|
0.92
|
73
|
Pulmonary arterial hypertension associated with systemic sclerosis in patients with functional class II dyspnoea: mild symptoms but severe outcome.
|
Rheumatology (Oxford)
|
2010
|
0.92
|
74
|
Systemic sclerosis-related pulmonary hypertension associated with interstitial lung disease: impact of pulmonary arterial hypertension therapies.
|
Arthritis Rheum
|
2011
|
0.91
|
75
|
Long-term outcome of double-lung and heart-lung transplantation for pulmonary hypertension: a comparative retrospective study of 219 patients.
|
Eur J Cardiothorac Surg
|
2010
|
0.91
|
76
|
Targets of anti-endothelial cell antibodies in pulmonary hypertension and scleroderma.
|
Eur Respir J
|
2011
|
0.90
|
77
|
Pulmonary hypertension in patients with neurofibromatosis type I.
|
Medicine (Baltimore)
|
2011
|
0.90
|
78
|
Usefulness of first-line combination therapy with epoprostenol and bosentan in pulmonary arterial hypertension: an observational study.
|
J Heart Lung Transplant
|
2011
|
0.90
|
79
|
Dynamic respiratory mechanics and exertional dyspnoea in pulmonary arterial hypertension.
|
Eur Respir J
|
2012
|
0.90
|
80
|
Idiopathic pulmonary arterial hypertension and pulmonary veno-occlusive disease: similarities and differences.
|
Semin Respir Crit Care Med
|
2009
|
0.90
|
81
|
Clinical worsening in trials of pulmonary arterial hypertension: results and implications.
|
Curr Opin Pulm Med
|
2010
|
0.89
|
82
|
An extreme consequence of splenectomy in dehydrated hereditary stomatocytosis: gradual thrombo-embolic pulmonary hypertension and lung-heart transplantation.
|
Hemoglobin
|
2003
|
0.88
|
83
|
Therapeutic advances in pulmonary arterial hypertension.
|
Ther Adv Respir Dis
|
2008
|
0.88
|
84
|
Human herpes virus 8 in HIV and non-HIV infected patients with pulmonary arterial hypertension in France.
|
AIDS
|
2005
|
0.87
|
85
|
Pharmacokinetic evaluation of sildenafil as a pulmonary hypertension treatment.
|
Expert Opin Drug Metab Toxicol
|
2013
|
0.85
|
86
|
Pulmonary arterial hypertension and its association with HIV infection: an overview.
|
AIDS
|
2008
|
0.85
|
87
|
Pulmonary hypertension in lymphangioleiomyomatosis: characteristics in 20 patients.
|
Eur Respir J
|
2012
|
0.85
|
88
|
Pulmonary hypertension associated with benfluorex exposure.
|
Eur Respir J
|
2012
|
0.85
|
89
|
Characteristics of pulmonary arterial hypertension in affected carriers of a mutation located in the cytoplasmic tail of bone morphogenetic protein receptor type 2.
|
Chest
|
2015
|
0.85
|
90
|
EBUS-TBNA in the differential diagnosis of pulmonary artery sarcoma and thromboembolism.
|
Eur Respir J
|
2012
|
0.85
|
91
|
Therapies for pulmonary arterial hypertension: where are we today, where do we go tomorrow?
|
Eur Respir Rev
|
2013
|
0.84
|
92
|
Pulmonary arterial hypertension in a patient with Cowden syndrome and anorexigen exposure.
|
Chest
|
2011
|
0.84
|
93
|
Evidence for the use of combination targeted therapeutic approaches for the management of pulmonary arterial hypertension.
|
Respir Med
|
2010
|
0.84
|
94
|
Efficacy, safety and pharmacokinetics of bosentan in portopulmonary hypertension.
|
Eur Respir J
|
2012
|
0.83
|
95
|
Hyperplasia of pulmonary artery smooth muscle cells is causally related to overexpression of the serotonin transporter in primary pulmonary hypertension.
|
Chest
|
2002
|
0.83
|
96
|
Primary pulmonary hypertension: Current therapy.
|
Prog Cardiovasc Dis
|
2002
|
0.82
|
97
|
Endothelin receptor antagonists for the treatment of pulmonary arterial hypertension.
|
Expert Opin Pharmacother
|
2011
|
0.82
|
98
|
Perspective on the optimal endpoints for pulmonary arterial hypertension trials.
|
Curr Opin Pulm Med
|
2010
|
0.81
|
99
|
Pulmonary arterial hypertension: bridging the present to the future.
|
Eur Respir Rev
|
2012
|
0.81
|
100
|
N-acetylcysteine improves established monocrotaline-induced pulmonary hypertension in rats.
|
Respir Res
|
2014
|
0.81
|
101
|
Drug Insight: endothelin-receptor antagonists for pulmonary arterial hypertension in systemic rheumatic diseases.
|
Nat Clin Pract Rheumatol
|
2005
|
0.80
|
102
|
[Pulmonary veno-occlusive disease and pulmonary capillary hemangiomatosis].
|
Presse Med
|
2009
|
0.80
|
103
|
The need to move from 6-minute walk distance to outcome trials in pulmonary arterial hypertension.
|
Eur Respir Rev
|
2013
|
0.80
|
104
|
Definition and classification of pulmonary hypertension.
|
Handb Exp Pharmacol
|
2013
|
0.78
|
105
|
Effect of age on the performance of a diagnostic strategy based on clinical probability, spiral computed tomography and venous compression ultrasonography: the ESSEP study.
|
Thromb Haemost
|
2005
|
0.78
|
106
|
Dasatinib induces lung vascular toxicity and predisposes to pulmonary hypertension.
|
J Clin Invest
|
2016
|
0.78
|
107
|
Pulmonary arterial hypertension and HIV infection.
|
Semin Respir Crit Care Med
|
2009
|
0.78
|
108
|
Mediastinal fibrosis mimicking proximal chronic thromboembolic disease.
|
Circulation
|
2012
|
0.78
|
109
|
[Pulmonary arterial hypertension associated with common diseases: connective-tissue diseases, HIV infection and portal hypertension].
|
Rev Prat
|
2008
|
0.78
|
110
|
Factors associated with diagnosis and operability of chronic thromboembolic pulmonary hypertension. A case-control study.
|
Thromb Haemost
|
2013
|
0.78
|
111
|
Pulse wave reflection in pulmonary hypertension.
|
J Am Coll Cardiol
|
2002
|
0.78
|
112
|
Pulmonary Hypertension Complicating Fibrosing Mediastinitis.
|
Medicine (Baltimore)
|
2015
|
0.78
|
113
|
[Pulmonary hypertension associated with systemic sclerosis].
|
Ann Med Interne (Paris)
|
2002
|
0.77
|
114
|
Macitentan and pulmonary arterial hypertension.
|
N Engl J Med
|
2014
|
0.77
|
115
|
Pulmonary veno-occlusive disease: the bête noire of pulmonary hypertension in connective tissue diseases?
|
Presse Med
|
2011
|
0.77
|
116
|
Clinical challenges in pulmonary hypertension: Roger S. Mitchell lecture.
|
Chest
|
2005
|
0.77
|
117
|
Drug-induced pulmonary arterial hypertension: a recent outbreak.
|
Eur Respir Rev
|
2013
|
0.77
|
118
|
[2015 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension].
|
Kardiol Pol
|
2015
|
0.77
|
119
|
Ventilation/perfusion lung scan in pulmonary veno-occlusive disease.
|
Eur Respir J
|
2011
|
0.76
|
120
|
A proof of concept for the detection and classification of pulmonary arterial hypertension through breath analysis with a sensor array.
|
Am J Respir Crit Care Med
|
2013
|
0.76
|
121
|
[Pulmonary arterial hypertension].
|
Rev Prat
|
2008
|
0.76
|
122
|
Pulmonary arterial hypertension in familial hemiplegic migraine with ATP1A2 channelopathy.
|
Eur Respir J
|
2013
|
0.75
|
123
|
Estimating right ventricular stroke work and the pulsatile work fraction in pulmonary hypertension.
|
Chest
|
2013
|
0.75
|
124
|
Pulmonary venoocclusive disease and failure of specific therapy.
|
Chest
|
2009
|
0.75
|
125
|
Vasodilators in patients with chronic obstructive pulmonary disease and pulmonary hypertension: not ready for prime time!
|
Am J Respir Crit Care Med
|
2010
|
0.75
|
126
|
[Treatment of pulmonary arterial hypertension in 2011: what's new since the 2009 ERS/ESC guidelines?].
|
Presse Med
|
2011
|
0.75
|
127
|
[Introduction. Pulmonary arterial hypertension].
|
Presse Med
|
2010
|
0.75
|
128
|
A paradigm shift in pulmonary arterial hypertension management.
|
Eur Respir Rev
|
2013
|
0.75
|
129
|
Editors' perspective and conclusions.
|
AIDS
|
2008
|
0.75
|
130
|
[Eisenmenger syndrome. Role of rare diseases reference centers in the management of pulmonary hypertension in congenital heart diseases].
|
Presse Med
|
2009
|
0.75
|
131
|
[Perspectives on pulmonary vascular diseases].
|
Presse Med
|
2005
|
0.75
|
132
|
Developing a heart score: next steps.
|
Am J Cardiol
|
2012
|
0.75
|
133
|
Clinical pharmacology of endothelin receptor antagonists used in the treatment of pulmonary arterial hypertension.
|
Am J Cardiovasc Drugs
|
2015
|
0.75
|
134
|
[Deep venous thrombosis and pulmonary embolism].
|
Rev Prat
|
2002
|
0.75
|
135
|
Assessing effectiveness of pulmonary arterial hypertension therapies in daily practice.
|
Curr Opin Pulm Med
|
2010
|
0.75
|
136
|
Renal replacement therapy in patients with severe precapillary pulmonary hypertension with acute right heart failure.
|
Respiration
|
2012
|
0.75
|