Published in Sci Rep on February 17, 2016
A murine model of early Pseudomonas aeruginosa lung disease with transition to chronic infection. Sci Rep (2016) 0.80
IL-17A impairs host tolerance during airway chronic infection by Pseudomonas aeruginosa. Sci Rep (2016) 0.79
IL-22 exacerbates weight loss in a murine model of chronic pulmonary Pseudomonas aeruginosa infection. J Cyst Fibros (2016) 0.78
Efficacy of the Novel Antibiotic POL7001 in Preclinical Models of Pseudomonas aeruginosa Pneumonia. Antimicrob Agents Chemother (2016) 0.77
The host genetic background defines diverse immune-reactivity and susceptibility to chronic Pseudomonas aeruginosa respiratory infection. Sci Rep (2016) 0.75
Mapping genetic determinants of host susceptibility to Pseudomonas aeruginosa lung infection in mice. BMC Genomics (2016) 0.75
The PAPI-1 pathogenicity island-encoded small RNA PesA influences Pseudomonas aeruginosa virulence and modulates pyocin S3 production. PLoS One (2017) 0.75
Immunoprotective potential of BamA, the outer membrane protein assembly factor, against MDR Acinetobacter baumannii. Sci Rep (2017) 0.75
Efficacy of Rhesus Theta (θ)-Defensin-1 in Experimental Models of Pseudomonas aeruginosa Lung Infection and Inflammation. Antimicrob Agents Chemother (2017) 0.75
Genetic adaptation by Pseudomonas aeruginosa to the airways of cystic fibrosis patients. Proc Natl Acad Sci U S A (2006) 8.85
An animal model for cystic fibrosis made by gene targeting. Science (1992) 5.75
Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice. Nat Med (2004) 5.24
A novel peptide CXCR ligand derived from extracellular matrix degradation during airway inflammation. Nat Med (2006) 5.05
Origins of cystic fibrosis lung disease. N Engl J Med (2015) 2.97
A novel proteolytic cascade generates an extracellular matrix-derived chemoattractant in chronic neutrophilic inflammation. J Immunol (2008) 2.58
Convergent evolution and adaptation of Pseudomonas aeruginosa within patients with cystic fibrosis. Nat Genet (2014) 2.42
Excessive inflammatory response of cystic fibrosis mice to bronchopulmonary infection with Pseudomonas aeruginosa. J Clin Invest (1997) 2.10
Pseudomonas aeruginosa microevolution during cystic fibrosis lung infection establishes clones with adapted virulence. Am J Respir Crit Care Med (2009) 2.08
Cystic fibrosis: a mucosal immunodeficiency syndrome. Nat Med (2012) 2.03
Induced sputum matrix metalloproteinase-9 correlates with lung function and airway inflammation in children with cystic fibrosis. Pediatr Pulmonol (2005) 2.00
Cystic fibrosis mouse models. Am J Respir Cell Mol Biol (2006) 1.98
Airway remodelling and its relationship to inflammation in cystic fibrosis. Thorax (2010) 1.67
Nonmucoid Pseudomonas aeruginosa expresses alginate in the lungs of patients with cystic fibrosis and in a mouse model. J Infect Dis (2005) 1.62
Mouse models of cystic fibrosis: phenotypic analysis and research applications. J Cyst Fibros (2011) 1.61
Characteristic multiorgan pathology of cystic fibrosis in a long-living cystic fibrosis transmembrane regulator knockout murine model. Am J Pathol (2004) 1.54
Lung disease in mice with cystic fibrosis. J Clin Invest (1997) 1.44
Matrix metalloprotease-9 dysregulation in lower airway secretions of cystic fibrosis patients. Am J Physiol Lung Cell Mol Physiol (2007) 1.41
Airway remodelling in children with cystic fibrosis. Thorax (2007) 1.38
Role of Cftr genotype in the response to chronic Pseudomonas aeruginosa lung infection in mice. Am J Physiol Lung Cell Mol Physiol (2004) 1.33
Murine models of acute and chronic lung infection with cystic fibrosis pathogens. Int J Med Microbiol (2010) 1.31
Pseudomonas aeruginosa exploits lipid A and muropeptides modification as a strategy to lower innate immunity during cystic fibrosis lung infection. PLoS One (2009) 1.26
The ENaC-overexpressing mouse as a model of cystic fibrosis lung disease. J Cyst Fibros (2011) 1.20
Cystic fibrosis-niche adaptation of Pseudomonas aeruginosa reduces virulence in multiple infection hosts. PLoS One (2012) 1.20
Differential adaptation of microbial pathogens to airways of patients with cystic fibrosis and chronic obstructive pulmonary disease. FEMS Microbiol Rev (2011) 1.16
Critical modifier role of membrane-cystic fibrosis transmembrane conductance regulator-dependent ceramide signaling in lung injury and emphysema. J Immunol (2010) 1.14
Pseudomonas aeruginosa adaptation in the nasopharyngeal reservoir leads to migration and persistence in the lungs. Nat Commun (2014) 1.13
Role of oxygen availability in CFTR expression and function. Am J Respir Cell Mol Biol (2008) 1.05
Lack of neutrophil elastase reduces inflammation, mucus hypersecretion, and emphysema, but not mucus obstruction, in mice with cystic fibrosis-like lung disease. Am J Respir Crit Care Med (2014) 1.01
Myofibroblast differentiation and enhanced TGF-B signaling in cystic fibrosis lung disease. PLoS One (2013) 0.95
Lung disease modifier genes in cystic fibrosis. Int J Biochem Cell Biol (2014) 0.92
The role of matrix metalloproteinases in cystic fibrosis lung disease. Eur Respir J (2011) 0.91
Clinical findings and lung pathology in children with cystic fibrosis. Am J Respir Crit Care Med (2002) 0.91
Endothelial activation and increased heparan sulfate expression in cystic fibrosis. Am J Respir Crit Care Med (2005) 0.91
Assessing Pseudomonas aeruginosa virulence and the host response using murine models of acute and chronic lung infection. Methods Mol Biol (2014) 0.90
Dampening Host Sensing and Avoiding Recognition in Pseudomonas aeruginosa Pneumonia. J Biomed Biotechnol (2011) 0.88
Modulators of sphingolipid metabolism reduce lung inflammation. Am J Respir Cell Mol Biol (2011) 0.87
Impact of heterozygote CFTR mutations in COPD patients with chronic bronchitis. Respir Res (2014) 0.84
The involvement of glycosaminoglycans in airway disease associated with cystic fibrosis. ScientificWorldJournal (2011) 0.83
Role of elastase in a mouse model of chronic respiratory Pseudomonas aeruginosa infection that mimics diffuse panbronchiolitis. J Med Microbiol (2003) 0.82
Tgf-beta downregulation of distinct chloride channels in cystic fibrosis-affected epithelia. PLoS One (2014) 0.81
An observational study of matrix metalloproteinase (MMP)-9 in cystic fibrosis. J Cyst Fibros (2014) 0.79
Deleterious impact of Pseudomonas aeruginosa on cystic fibrosis transmembrane conductance regulator function and rescue in airway epithelial cells. Eur Respir J (2015) 0.79
Knockout mice offer first animal model for CF. Science (1992) 0.77
Regulation of expression of O6-methylguanine-DNA methyltransferase and the treatment of glioblastoma (Review). Int J Oncol (2015) 0.87
IL-17A impairs host tolerance during airway chronic infection by Pseudomonas aeruginosa. Sci Rep (2016) 0.79
Paratuberculosis in sheep: Histochemical, immunohistochemical and in situ hybridization evidence of in utero and milk transmission. Res Vet Sci (2016) 0.75
Comparison of celioscopy and histological examinations to assess male gonadal health and functionality in adults and immature wild raptors. Theriogenology (2017) 0.75