Quantitative Disease Progression Model of Alpha-1 Proteinase Inhibitor Therapy on CT Lung Density in Patients with Alpha-1 Antitrypsin Deficiency.

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🔗 View Article (PMID 28662542)

Published in Br J Clin Pharmacol on June 29, 2017

Authors

M A Tortorici1, James A Rogers2, Oliver Vit3, Martin Bexon3, Robert A Sandhaus4, Jonathan Burdon5, Joanna Chorostowska-Wynimko6, Philip Thompson7, James Stocks8, Noel G McElvaney9, Kenneth R Chapman10, Jonathan M Edelman11

Author Affiliations

1: Clinical Strategy and Development, CSL Behring, King of Prussia, Pennsylvania, United States, PA, 19406.
2: Metrum Research Group LLC, Tariffville, Connecticut, USA.
3: Global Clinical Research and Development, CSL Behring, Bern, Switzerland.
4: Division of Pulmonary, Critical Care and Sleep Medicine, National Jewish Health, Denver, Colorado, USA.
5: Respiratory Medicine, St. Vincent's Hospital, Melbourne, V ictoria, Australia.
6: Department of Genetics and Clinical Immunology, National Institute of Tuberculosis and Lung Diseases, Warsaw, Poland.
7: Molecular Genetics and Inflammation Unit, Institute of Respiratory Health and School of Medicine, University of Western Australia, Perth, Western Australia, Australia.
8: Pulmonary and Critical Care, University of Texas Health Science Center at Tyler, Tyler, Texas, USA.
9: Department of Respiratory Medicine, Beaumont Hospital, Royal College of Surgeons in Ireland, Dublin, Ireland.
10: Department of Medicine, University of Toronto, Toronto, Ontario, Canada.
11: Clinical Strategy and Development, CSL Behring, King of Prussia, Pennsylvania, USA.

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