Published in J Inherit Metab Dis on January 01, 1988
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Early referral for intentional rescue PTCA after initiation of thrombolytic therapy in patients admitted to a community hospital because of a large acute myocardial infarction. Am Heart J (1999) 0.99
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Transmission rates, screening methods and costs of MRSA--a systematic literature review related to the prevalence in Germany. Eur J Clin Microbiol Infect Dis (2012) 0.94
Congenital myopathy with excess of thin myofilaments. Neuromuscul Disord (1997) 0.92
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A cysteine 3340 substitution in the dystroglycan-binding domain of dystrophin associated with Duchenne muscular dystrophy, mental retardation and absence of the ERG b-wave. Hum Mol Genet (1996) 0.90
Protracted course of juvenile ceroid lipofuscinosis associated with a novel CLN3 mutation (p.Y199X). Clin Genet (2009) 0.90
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Evaluation of a Diagnostic Encyclopedia Workstation for ovarian pathology. Hum Pathol (1990) 0.88
Diaphragmatic spinal muscular atrophy with respiratory distress is heterogeneous, and one form Is linked to chromosome 11q13-q21. Am J Hum Genet (1999) 0.87
Neurological observations after local irradiation and hyperthermia of rat lumbosacral spinal cord. Int J Radiat Oncol Biol Phys (1995) 0.87
Antioxidative activity of ubiquinol-10 at physiologic concentrations in human low density lipoprotein. Biochim Biophys Acta (1995) 0.87
A method for the acquisition of formalized knowledge in pathology. Methods Inf Med (1990) 0.87
Oxidized LDL-induced leukocyte/endothelium interaction in vivo involves the receptor for platelet-activating factor. Arterioscler Thromb (1993) 0.87
Primary amenorrhoea with hypertension due to 17-hydroxylase deficiency. Therapy with dexamethasone and ethinyloestradiol. Acta Med Scand (1973) 0.87
Deteriorating free radical-trapping capacity and antioxidant status in plasma during bone marrow transplantation. Bone Marrow Transplant (1995) 0.86
[Long-term therapy with nitrates. Relation between dosage and tolerance effect]. Herz (1984) 0.85
Heterozygous myogenic factor 6 mutation associated with myopathy and severe course of Becker muscular dystrophy. Neuromuscul Disord (2000) 0.85
In vitro effects of oxidized low density lipoprotein on CD11b/CD18 and L-selectin presentation on neutrophils and monocytes with relevance for the in vivo situation. Am J Pathol (1995) 0.85
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On the morphology of the transitional zone of the seminiferous tubule and the rete testis in man. Andrologia (1982) 0.84
DNA hybridization and latex agglutination for detection of heat-labile- and shiga-like toxin-producing Escherichia coli in meat. Int J Food Microbiol (1991) 0.84
Dietary fish oil blocks the microcirculatory manifestations of ischemia-reperfusion injury in striated muscle in hamsters. Proc Natl Acad Sci U S A (1991) 0.84
Muscarinic acetylcholine receptor stimulation of biliary epithelial cells and its effect on bile secretion in the isolated perfused liver [corrected]. Hepatology (1997) 0.83
Superoxide-dependent stimulation of leukocyte adhesion by oxidatively modified LDL in vivo. Arterioscler Thromb (1992) 0.83
Treatment of ataxia in isolated vitamin E deficiency caused by alpha-tocopherol transfer protein deficiency. J Pediatr (1999) 0.83
Histamine H1-receptor-mediated cyclic GMP production in guinea-pig lung tissue is an L-arginine-dependent process. Biochem Pharmacol (1991) 0.83
Cystic leukoencephalopathy without megalencephaly: a distinct disease entity in 15 children. Neurology (2005) 0.83
A small in-frame deletion within the protease domain of muscle-specific calpain, p94 causes early-onset limb-girdle muscular dystrophy 2A. Hum Mutat (1998) 0.83
An alcoholic with pleural effusion. Eur Respir J (1990) 0.82
Autoantibodies against CD28 are associated with atopic diseases. Clin Exp Immunol (2006) 0.82
Facing the genetic heterogeneity in neuromuscular disorders: linkage analysis as an economic diagnostic approach towards the molecular diagnosis. Neuromuscul Disord (2005) 0.82
Primary combined saccharase and isomaltase deficiency. Report of two adult siblings of consanguineous parentage. Arch Intern Med (1965) 0.82
Dietary fish oil reduces leukocyte/endothelium interaction following systemic administration of oxidatively modified low density lipoprotein. Circulation (1991) 0.81
Multipoint mapping of the central core disease locus. Genomics (1993) 0.80
Monitoring of ubiquinol-10, ubiquinone-10, carotenoids, and tocopherols in neonatal plasma microsamples using high-performance liquid chromatography with coulometric electrochemical detection. Anal Biochem (1995) 0.80
Hyperthermia, radiation carcinogenesis and the protective potential of vitamin A and N-acetylcysteine. J Cancer Res Clin Oncol (1996) 0.80
Intraduodenal cyst containing bile and stones: "choledochocele" in an accessory bile duct. Report of a case with recurrent pancreatitis. Gastroenterology (1970) 0.80
Decreased binding of HIV-1 and vasoactive intestinal peptide following plasma membrane fluidization of CD4+ cells by phenytoin. Virology (1990) 0.80
[Testing vision in children]. Klin Monbl Augenheilkd (1991) 0.79
MRI of normal or cancerous laryngeal cartilages: histopathologic correlation. Laryngoscope (1987) 0.79
Preferential expression of IgG2b in nose draining cervical lymph nodes and its putative role in mucosal tolerance induction. Allergy (2004) 0.79
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Prevention of pancreatic islet xenograft rejection by dietary vitamin E. Am J Pathol (1997) 0.79
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Low erythrocyte plasmalogen and plasma docosahexaenoic acid (DHA) in juvenile neuronal ceroid-lipofuscinosis (JNCL). J Inherit Metab Dis (1993) 0.79
High incidence of transiently appearing complement-sensitive bone marrow precursor cells in patients with severe aplastic anemia--A possible role of high endogenous IL-2 in their suppression. Acta Haematol (1999) 0.79
Myocardial infarction as a complication of dobutamine stress echocardiography. J Am Soc Echocardiogr (1997) 0.79
Quantitative immunophenotypic characterization, cryopreservation, and enrichment of second- and third-trimester human fetal cord blood hematopoietic stem cells (progenitor cells). Am J Obstet Gynecol (1998) 0.79
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[Effect of 50 mg isosorbide-5-nitrate retard on the stress tolerance of patients with coronary heart disease]. Med Klin (Munich) (1986) 0.78
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[Treatment of decreasing cardiac performance. Therapy using standardized crataegus extract in advanced age]. Fortschr Med (1986) 0.78
[Computed tomographic findings in mitral valve disease]. Rofo (1984) 0.78
High-performance liquid chromatography-coulometric electrochemical detection of ubiquinol 10, ubiquinone 10, carotenoids, and tocopherols in neonatal plasma. Methods Enzymol (1999) 0.78
Multicystic mesothelioma presenting as a pelvic tumour: case report and literature review. Scand J Urol Nephrol (1995) 0.78
Surgical aspects of radiation enteritis of the small bowel. Dis Colon Rectum (1984) 0.78
Increased plasma membrane fluidity and decreased receptor availability of nonmuscle cells in myotonic dystrophy. J Neurol Sci (1989) 0.77
Urinary alpha-tocopherol metabolites in alpha-tocopherol transfer protein-deficient patients. J Lipid Res (2000) 0.77
5-Fluorouracil cardiotoxicity with left ventricular dysfunction under different dosing regimens. Am J Cardiol (1995) 0.77
Dose dependence of tolerance during treatment with mononitrates. Z Kardiol (1983) 0.77
Absorptive and secretory mechanisms in biliary epithelial cells. J Hepatol (1996) 0.76
Serum antibodies to the deleted dystrophin sequence after cardiac transplantation in a patient with Becker's muscular dystrophy. N Engl J Med (1995) 0.76
Ataxia with vitamin E deficiency: biochemical effects of malcompliance with vitamin E therapy. Neurology (2000) 0.76