Published in Eur J Pediatr on May 01, 1988
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The alpha-keto acids of branched-chain amino acids: simplified derivatization for physiological samples and complete separation as quinoxalinols by packed column gas chromatography. Anal Biochem (1980) 1.03
Treatment of homozygous protein C deficiency and neonatal purpura fulminans with a purified protein C concentrate. N Engl J Med (1991) 1.02
Identification and quantitation of protein S in human platelets. Blood (1985) 1.02
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Monitoring the bioavailability of FEIBA with a thrombin generation assay. J Thromb Haemost (2003) 1.00
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Treatment of purpura fulminans in meningococcemia with protein C concentrate. J Pediatr (1995) 0.99
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Immunoblotting studies of the molecular forms of protein C in plasma. Thromb Res (1988) 0.97
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Factor VIII inhibitor-bypassing agents act by inducing thrombin generation and can be monitored by a thrombin generation assay. Pathophysiol Haemost Thromb (2003) 0.97
Therapy with a purified plasminogen concentrate in an infant with ligneous conjunctivitis and homozygous plasminogen deficiency. N Engl J Med (1998) 0.96
FEIBA: mode of action. Haemophilia (2004) 0.96
Biochemical, molecular and preclinical characterization of a double-virus-reduced human butyrylcholinesterase preparation designed for clinical use. Vox Sang (2010) 0.96
Hyperprolactinemia as a cause of delayed puberty: successful treatment with bromocriptine. J Clin Endocrinol Metab (1977) 0.95
Success and relapse rate after treatment of cryptorchidism with intranasal LHRH. Acta Paediatr Scand (1985) 0.94
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Successful early dietary intervention avoids obesity in patients with Prader-Willi syndrome: a ten-year follow-up. J Pediatr Endocrinol Metab (2008) 0.92
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Liver involvement in cystic fibrosis. A report of 9 cases. Helv Paediatr Acta (1978) 0.92
Increased risk of diabetes mellitus in beta- thalassemia major due to iron overload. Helv Paediatr Acta (1979) 0.91
Musculoskeletal and functional muscle-bone analysis in children with rheumatic disease using peripheral quantitative computed tomography. Osteoporos Int (2004) 0.90
A new liquid intravenous immunoglobulin with three dedicated virus reduction steps: virus and prion reduction capacity. Vox Sang (2007) 0.90
Increasing incidence of hypoglycemic coma in children with IDDM. Diabetes Care (1991) 0.90
Growth patterns in the first three years of life in children with classical congenital adrenal hyperplasia diagnosed by newborn screening and treated with low doses of hydrocortisone. Horm Res Paediatr (2010) 0.89
Oxandrolone in girls with Turner's syndrome. A pair-matched controlled study up to final height. Acta Paediatr Scand (1984) 0.89
Detection of in vitro and in vivo cleavage of high molecular weight kininogen in human plasma by immunoblotting with monoclonal antibodies. Blood (1986) 0.88
Development of a plasma- and albumin-free recombinant von Willebrand factor. Hamostaseologie (2009) 0.88
Comprehensive analytical strategy for mutation screening in 21-hydroxylase deficiency. Clin Chem (1998) 0.87
The determination of von Willebrand factor activity by collagen binding assay. Haemophilia (1998) 0.87
Thrombin generation assay and other universal tests for monitoring haemophilia therapy. Haemophilia (2004) 0.86
Musculoskeletal analyses of the forearm in young women with Turner syndrome: a study using peripheral quantitative computed tomography. J Clin Endocrinol Metab (2001) 0.86
Toxic psychosis from transdermal scopolamine in a child. Lancet (1986) 0.86
Partnership and sexuality in adult female patients with congenital adrenal hyperplasia. First results of a cross-sectional quality-of-life evaluation. J Steroid Biochem Mol Biol (1993) 0.86
Feminization in a galactosemic girl in the presence of hypergonadotropic hypogonadism. Acta Endocrinol Suppl (Copenh) (1986) 0.85
Growth hormone changes bone geometry and body composition in patients with juvenile idiopathic arthritis requiring glucocorticoid treatment: a controlled study using peripheral quantitative computed tomography. J Clin Endocrinol Metab (2005) 0.85
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Final height and predicted height in boys with untreated constitutional growth delay. Eur J Pediatr (1995) 0.85
In vivo characterization of recombinant von Willebrand factor in dogs with von Willebrand disease. Blood (1997) 0.84
Seizures, psychosis and coma: severe course of hashimoto encephalopathy in a six-year-old girl. Neuropediatrics (2007) 0.84
Factor V enhances the cofactor function of protein S in the APC-mediated inactivation of factor VIII: influence of the factor VR506Q mutation. Thromb Haemost (1996) 0.84
Normalization of markers of coagulation activation with a purified protein C concentrate in adults with homozygous protein C deficiency. Blood (1993) 0.84
Growth pattern of untreated boys with simple virilizing congenital adrenal hyperplasia indicates relative androgen insensitivity during the first six months of life. Horm Res Paediatr (2010) 0.84
Young adults born small for gestational age: is reduced baroreceptor sensitivity a risk factor for hypertension? Clin Cardiol (2006) 0.84
Structural analysis of recombinant von Willebrand factor produced at industrial scale fermentation of transformed CHO cells co-expressing recombinant furin. FEBS Lett (1995) 0.83
Phenotypic expression of murine hemophilia. Thromb Haemost (1999) 0.83
Prostaglandin induced, stress related, phospholipid changes in blood and brain. Physiol Chem Phys (1974) 0.83
Long-chain bases of brain and spinal cord of rabbits. J Neurochem (1967) 0.83
Pertussis toxin sensitive G-proteins are not involved in the mitogenic signaling pathway of insulin-like growth factor-I in normal rat kidney epithelial (NRKE) cells. Regul Pept (1996) 0.83
Modulation of factor VIII-specific memory B cells. Haemophilia (2010) 0.83
The determination of iodine-containing compounds by neutron activation of I-129. Int J Appl Radiat Isot (1966) 0.83
C-reactive protein and IL-6: new marker proteins for the diagnosis of CJD in plasma? Transfusion (2001) 0.83
Serum concentrations of LH and FSH in the healthy newborn. Eur J Endocrinol (2000) 0.83
Quantitative immunoblotting assay of blood coagulation factor XII. Thromb Res (1986) 0.83
Adult height after GH therapy in 188 Ullrich-Turner syndrome patients: results of the German IGLU Follow-up Study 2001. Eur J Endocrinol (2002) 0.83
Endocrine function of the pancreas in cystic fibrosis: evidence for an impaired glucagon and insulin response following arginine infusion. J Pediatr (1974) 0.83
Changes in BMI and management of patients with childhood onset growth hormone deficiency in the transition phase. Exp Clin Endocrinol Diabetes (2012) 0.83
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Effects of human alpha-1-acid glycoprotein on aminonucleoside-induced minimal change nephrosis in rats. Nephron (1999) 0.82
True hermaphroditism in a 46,XY individual, caused by a postzygotic somatic point mutation in the male gonadal sex-determining locus (SRY): molecular genetics and histological findings in a sporadic case. Am J Hum Genet (1993) 0.82
A new type of familial growth hormone deficiency due to a 8.5 kb deletion within the growth hormone gene cluster. Prog Clin Biol Res (1985) 0.82
Vaccine tolerance in steroid substituted patients with congenital adrenal hyperplasia. Eur J Med Res (1997) 0.82
[Diagnostic significance of serum bile acids]. Schweiz Med Wochenschr (1975) 0.82
Optimization, refinement and reduction of murine in vivo experiments to assess therapeutic approaches for haemophilia A. Lab Anim (2010) 0.82
Variation of anti-Fas antibodies in different lots of intravenous immunoglobulin. Vox Sang (2008) 0.82
Strategies for recombinant Furin employment in a biotechnological process: complete target protein precursor cleavage. Cytotechnology (1999) 0.81