Published in Am J Dis Child on October 01, 1986
Cellular bicarbonate protects rat duodenal mucosa from acid-induced injury. J Clin Invest (2001) 1.07
Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. The Pulmozyme Study Group. N Engl J Med (1994) 7.98
A cluster of cystic fibrosis mutations in the first nucleotide-binding fold of the cystic fibrosis conductance regulator protein. Nature (1990) 5.42
Innovative communicable disease reporting. HSMHA Health Rep (1971) 4.67
Eosinophilic esophagitis attributed to gastroesophageal reflux: improvement with an amino acid-based formula. Gastroenterology (1995) 4.24
Evaluation of the culture of safety: survey of clinicians and managers in an academic medical center. Qual Saf Health Care (2003) 3.86
Feeding of Bifidobacterium bifidum and Streptococcus thermophilus to infants in hospital for prevention of diarrhoea and shedding of rotavirus. Lancet (1994) 3.62
Use of CT scans in selection of patients for pectus excavatum surgery: a preliminary report. J Pediatr Surg (1987) 2.46
Two patients with cystic fibrosis, nonsense mutations in each cystic fibrosis gene, and mild pulmonary disease. N Engl J Med (1990) 2.37
A statewide mass measles immunization program. JAMA (1967) 1.99
Comparison of the clinical manifestations of cystic fibrosis in black and white patients. J Pediatr (1998) 1.97
Dermatitis as a presenting sign of cystic fibrosis. Arch Dermatol (1992) 1.96
Role of pH in production of hydrogen from carbohydrates by colonic bacterial flora. Studies in vivo and in vitro. J Clin Invest (1981) 1.93
Identification of common cystic fibrosis mutations in African-Americans with cystic fibrosis increases the detection rate to 75%. Am J Hum Genet (1997) 1.84
Analysis of DNA polymorphism haplotypes linked to the cystic fibrosis locus in North American black and Caucasian families supports the existence of multiple mutations of the cystic fibrosis gene. Am J Hum Genet (1989) 1.81
Intestinal malrotation in children: tutorial on radiographic diagnosis in difficult cases. Radiology (1996) 1.80
Salmonellosis in infants and children. J Pediatr (1967) 1.80
Sucrose malabsorption in children: noninvasive diagnosis by interval breath hydrogen determination. J Pediatr (1978) 1.78
Risk of persistent growth impairment after alternate-day prednisone treatment in children with cystic fibrosis. N Engl J Med (2000) 1.78
A multicenter study of alternate-day prednisone therapy in patients with cystic fibrosis. Cystic Fibrosis Foundation Prednisone Trial Group. J Pediatr (1995) 1.75
Assessment of methacholine-induced airway constriction by ultrafast high-resolution computed tomography. J Appl Physiol (1985) (1993) 1.65
Severe deficiency of cystic fibrosis transmembrane conductance regulator messenger RNA carrying nonsense mutations R553X and W1316X in respiratory epithelial cells of patients with cystic fibrosis. J Clin Invest (1991) 1.56
Macroamylasemia in patients with celiac disease. Am J Gastroenterol (2001) 1.54
Radiographic patterns of intestinal malrotation in children. Radiographics (1996) 1.54
A controlled trial of long-term bronchodilator therapy in cystic fibrosis. Chest (1991) 1.52
Behavioral assessment and treatment of pediatric feeding disorders. J Dev Behav Pediatr (1994) 1.50
Pneumonia and septicemia due to Pseudomonas cepacia in a patient with cystic fibrosis. Johns Hopkins Med J (1980) 1.47
Glycoproteins as substrates for production of hydrogen and methane by colonic bacterial flora. Gastroenterology (1982) 1.44
Breath hydrogen testing as a physiology laboratory exercise for medical students. Am J Physiol (1992) 1.40
Complications of smallpox vaccination United States 1963. II. Results obtained by four statewide surveys. Pediatrics (1967) 1.34
Skeletal changes of copper deficiency in infants receiving prolonged total parenteral nutrition. J Pediatr (1978) 1.28
Cystic fibrosis patients bearing both the common missense mutation Gly----Asp at codon 551 and the delta F508 mutation are clinically indistinguishable from delta F508 homozygotes, except for decreased risk of meconium ileus. Am J Hum Genet (1992) 1.22
Diagnosis and differentiation of fat malabsorption in children using 13C-labeled lipids: trioctanoin, triolein, and palmitic acid breath tests. Gastroenterology (1982) 1.22
CFTR nonsense mutations G542X and W1282X associated with severe reduction of CFTR mRNA in nasal epithelial cells. Hum Mol Genet (1992) 1.19
Pediatric feeding disorders. J Clin Gastroenterol (2000) 1.17
Analysis of four diverse population groups indicates that a subset of cystic fibrosis mutations occur in common among Caucasians. Am J Hum Genet (1992) 1.17
Fasting breath hydrogen concentration: normal values and clinical application. Gastroenterology (1984) 1.17
Incidence of distal intestinal obstruction syndrome in cystic fibrosis. J Pediatr Gastroenterol Nutr (1983) 1.10
A double-blind controlled trial of anti-Pseudomonas chemotherapy of acute respiratory exacerbations in patients with cystic fibrosis. J Pediatr (1981) 1.09
Pulmonary tuberculosis in children. Semin Roentgenol (1993) 1.06
Mycobacterium avium complex in a patient with cystic fibrosis: disease vs. colonization. Pediatr Infect Dis J (1989) 1.06
Passive smoking among children with chronic respiratory disease. J Asthma (1992) 1.06
Images in clinical medicine. Pulmonary Langerhans'-cell granulomatosis (histiocytosis X). N Engl J Med (2000) 1.05
Pulmonary manifestations of juvenile laryngotracheal papillomatosis. AJR Am J Roentgenol (1985) 1.03
Factors involved in treatment failures following oral penicillin therapy of streptococcal pharyngitis. J Pediatr (1968) 1.02
Mucosal function and breath hydrogen excretion: comparative studies in the clinical evaluation of children with nonspecific abdominal complaints. Pediatrics (1981) 1.02
Lethal chylothoraces due to superior vena caval thrombosis in infants. AJR Am J Roentgenol (1981) 1.01
Incidence of meconium abnormalities in newborn infants with cystic fibrosis. Am J Dis Child (1980) 0.99
Accuracy of throat cultures processed in physicians' offices. J Pediatr (1970) 0.98
Effect of breastfeeding support from different sources on mothers' decisions to breastfeed. J Hum Lact (1994) 0.97
Prenatal care and drug use in pregnant women. Drug Alcohol Depend (1993) 0.97
Pharyngoesophageal interrelationships: observations and working concepts. Gastrointest Radiol (1985) 0.96
Noninvasive evaluation of ventricular function in cystic fibrosis. J Pediatr (1979) 0.95
Differences in expression of cystic fibrosis in blacks and whites. Am J Dis Child (1991) 0.95
Cystic fibrosis: diagnostic considerations. Johns Hopkins Med J (1982) 0.95
Computed tomography of gastrointestinal inflammation after bone marrow transplantation. AJR Am J Roentgenol (1986) 0.95
The cause of rectal prolapse in children. Am J Dis Child (1988) 0.93
Congenital surfactant protein B deficiency--emphasis on imaging. Pediatr Radiol (2001) 0.93
Longitudinal assessment of growth in children born to mothers with human immunodeficiency virus infection. Arch Pediatr Adolesc Med (1995) 0.92
Life-threatening airway obstruction as a complication to the management of mediastinal masses in children. J Pediatr Surg (1985) 0.92
Neonatal intussusception. Report of 12 cases. Radiology (1977) 0.91
Homogeneity of bronchopulmonary distribution of 99mTc aerosol in normal subjects and in cystic fibrosis patients. Chest (1989) 0.88
Gastritis associated with Gastrospirillum hominis in children. Comparison with Helicobacter pylori and review of the literature. Mod Pathol (1993) 0.87
Gastrointestinal dysfunction and disaccharide intolerance in children infected with human immunodeficiency virus. J Pediatr (1991) 0.87
Successful intestinal transplantation for microvillus inclusion disease. Gastroenterology (1994) 0.87
Metastatic calcification in cystic fibrosis. A report of two cases. Radiology (1970) 0.87
Current concepts in lactose malabsorption and intolerance. Annu Rev Nutr (1989) 0.87
Misdiagnosis of cystic fibrosis. Need for continuing follow-up and reevaluation. Clin Pediatr (Phila) (1987) 0.87
Duodenitis in children: correlation of radiologic findings with endoscopic and pathologic findings. Radiology (1998) 0.86
Differential pathology of nasal polyps in cystic fibrosis and atopy. Lab Invest (1979) 0.86
Identification of a novel nonsense mutation (L88X) in exon 3 of the cystic fibrosis transmembrane conductance regulator gene in a native Korean cystic fibrosis chromosome. Hum Mutat (1992) 0.86
Gastrointestinal inflammation after bone marrow transplantation: graft-versus-host disease or opportunistic infection? AJR Am J Roentgenol (1988) 0.85
Nutritional consequences of bowel segments in the lower urinary tract. J Urol (1989) 0.85
Cystic fibrosis. Problems encountered with sweat testing. JAMA (1978) 0.85
Airway hyperreactivity in cystic fibrosis. Clinical correlates and possible effects on the course of the disease. Chest (1988) 0.84
Endotracheal tube displacement in the newborn infant. J Pediatr (1976) 0.84
Are fathers prepared to encourage their partners to breast feed? A study about fathers' knowledge of breast feeding. Acta Paediatr (1994) 0.84
N-type anorectal malformations. J Pediatr Surg (1978) 0.84
Influence of frequent and long-term bean consumption on colonic function and fermentation. Am J Clin Nutr (1985) 0.84
Effect of enteral tube feeding on growth of children with symptomatic human immunodeficiency virus infection. J Pediatr Gastroenterol Nutr (1994) 0.83
Alveolar rupture as an independent predictor of bronchopulmonary dysplasia. Crit Care Med (1978) 0.83
Effect of milks inoculated with Lactobacillus acidophilus or a yogurt starter culture in lactose-maldigesting children. J Dairy Sci (1995) 0.83
Chronic fructose intoxication after infancy in children with hereditary fructose intolerance. A cause of growth retardation. N Engl J Med (1983) 0.83
Pneumatosis intestinalis in children after allogeneic bone marrow transplantation. Pediatr Radiol (1987) 0.83
Use of oral contraceptives in women with cystic fibrosis. Chest (1984) 0.83
Utility of breath ethane as a noninvasive biomarker of vitamin E status in children. Pediatr Res (1991) 0.82
Diagnosis of cystic fibrosis during adolescence. J Adolesc Health Care (1986) 0.82
Effect of yogurt on symptoms and kinetics of hydrogen production in lactose-malabsorbing children. Am J Clin Nutr (1995) 0.82
Radiologic examination of the swallowing impaired child. Dysphagia (1989) 0.82
Facial cosmetics have little effect on attractiveness judgments compared with identity. Perception (2015) 0.82
Gynecomastia as a presenting sign of fibrolamellar carcinoma of the liver. Pediatrics (1988) 0.82
Bronchial diseases and lung aeration in children. J Thorac Imaging (2001) 0.82
Infant health care utilization predicted by pattern of prenatal care. Pediatrics (1993) 0.82
Effect of rhDNase on airflow obstruction and mucociliary clearance in cystic fibrosis. Am J Respir Crit Care Med (1996) 0.82
ABH secretor status in cystic fibrosis--a negative report. Eur J Respir Dis (1985) 0.81
Air trapping in children: evaluation with dynamic lung densitometry with spiral CT. Radiology (1998) 0.81
Breath tests in pediatric gastrointestinal disorders: new diagnostic opportunities. Pediatrics (1978) 0.81
Chronic nonspecific inflammatory bowel disease of the cecum and proximal colon in children with grossly normal-appearing colonic mucosa: diagnosis by colonoscopic biopsies. Pediatrics (1987) 0.80
Lysozyme activity in cystic fibrosis. Pediatr Res (1982) 0.80
Bile acid metabolism in infants and children. Clin Gastroenterol (1977) 0.80
Diagnostic delay in Duchenne s muscular dystrophy and cystic fibrosis. JAMA (1982) 0.80