Published in Ann N Y Acad Sci on January 01, 1979
X chromosome-linked muscular dystrophy (mdx) in the mouse. Proc Natl Acad Sci U S A (1984) 8.35
The relationship between end-plate size and transmitter release in normal and dystrophic muscles of the mouse. J Physiol (1979) 1.32
Some reminiscences on studies of age-dependent and activity-dependent degeneration of sensory and motor endings in mammalian skeletal muscle. J Anat (2015) 0.75
Characterization of dystrophin in muscle-biopsy specimens from patients with Duchenne's or Becker's muscular dystrophy. N Engl J Med (1988) 5.84
Abnormal dendritic spines in fragile X knockout mice: maturation and pruning deficits. Proc Natl Acad Sci U S A (1997) 4.73
Wallerian degeneration of injured axons and synapses is delayed by a Ube4b/Nmnat chimeric gene. Nat Neurosci (2001) 4.10
Very mild muscular dystrophy associated with the deletion of 46% of dystrophin. Nature (1990) 3.84
Abnormal dendritic spine characteristics in the temporal and visual cortices of patients with fragile-X syndrome: a quantitative examination. Am J Med Genet (2001) 3.77
Studies on tetrodotoxin resistant action potentials in denervated skeletal muscle. Acta Physiol Scand (1971) 2.24
Inhibition of denervation changes in skeletal muscle by blockers of protein synthesis. J Physiol (1972) 2.19
Dystrophin in skeletal muscle. I. Western blot analysis using a monoclonal antibody. J Neurol Sci (1989) 1.87
Improved diagnosis of Becker muscular dystrophy by dystrophin testing. Neurology (1989) 1.81
Mutation detection in the med and medJ alleles of the sodium channel Scn8a. Unusual splicing due to a minor class AT-AC intron. J Biol Chem (1996) 1.71
Further observations on the pathological responses of rat skeletal muscle to toxins isolated from the venom of the Australian tiger snake, Notechis scutatus scutatus. Clin Exp Pharmacol Physiol (1979) 1.66
Heterogeneity of dystrophin expression in patients with Duchenne and Becker muscular dystrophy. Acta Neuropathol (1990) 1.52
The size of motor units during post-natal development of rat lumbrical muscle. J Physiol (1979) 1.52
Tetrodotoxin-resistant action potentials in newborn rat muscle. Nat New Biol (1973) 1.49
Dystrophin in skeletal muscle. II. Immunoreactivity in patients with Xp21 muscular dystrophy. J Neurol Sci (1989) 1.48
An economical, simplified haemagglutination test for mass syphilis screening. J Clin Pathol (1980) 1.43
Ultrastructural localization of dystrophin in human muscle by using gold immunolabelling. Proc R Soc Lond B Biol Sci (1990) 1.38
The clinical, genetic and dystrophin characteristics of Becker muscular dystrophy. II. Correlation of phenotype with genetic and protein abnormalities. J Neurol (1993) 1.37
Expression of myosin isoforms during notexin-induced regeneration of rat soleus muscles. Dev Biol (1990) 1.35
The relationship between end-plate size and transmitter release in normal and dystrophic muscles of the mouse. J Physiol (1979) 1.32
Adenosine-3',5'-monophosphate: intracellular mediator for methyl xanthine stimulation of gastric secretion. Gastroenterology (1969) 1.32
Compartmental neurodegeneration and synaptic plasticity in the Wld(s) mutant mouse. J Physiol (2001) 1.28
The effects of partial denervation at birth on the development of muscle fibres and motor units in rat lumbrical muscle. J Physiol (1980) 1.26
Morphology and physiology of skeletal muscle in aging rodents. Muscle Nerve (1980) 1.24
Animal models: what is their relevance to the pathogenesis of human muscular dystrophy? Br Med Bull (1980) 1.20
Nerve stump length and membrane changes in denervated skeletal muscle. Nat New Biol (1972) 1.18
Effects of an isolated toxin from Australian tiger snake (Notechis scutatus scutatus) venom at the mammalian neuromuscular junction. Br J Pharmacol (1973) 1.17
Mechanical properties of dystrophic mouse muscle. J Neurol Neurosurg Psychiatry (1971) 1.15
Muscle fibre membrane potentials in fast and slow muscles of developing mice. J Physiol (1969) 1.13
Phospholipases in snake venoms and their effects on nerve and muscle. Pharmacol Ther (1985) 1.11
Action of a cobra neurotoxin on denervated rat skeletal muscle. Eur J Pharmacol (1971) 1.10
Endogenous electric field around muscle fibres depends on the Na+-K+ pump. Nature (1980) 1.08
Dystrophin or a "related protein" in Duchenne muscular dystrophy? Acta Neurol Scand (1992) 1.08
Hereditary pancreatitis. A kindred without gross aminoaciduria. Ann Intern Med (1968) 1.06
Nerve terminal damage by beta-bungarotoxin: its clinical significance. Am J Pathol (1999) 1.06
Screening of snake venoms for neurotoxic and myotoxic effects using simple in vitro preparations from rodents and chicks. Toxicon (1994) 1.04
Sprouting of active nerve terminals in partially inactive muscles of the rat. J Physiol (1980) 1.03
A physiological study of chick myotubes grown in tissue culture. J Physiol (1973) 1.03
Long-term results of pectoralis major muscle transposition for infected sternotomy wounds. Ann Surg (1991) 1.02
Transcutaneous immunization with a Vibrio cholerae O1 Ogawa synthetic hexasaccharide conjugate following oral whole-cell cholera vaccination boosts vibriocidal responses and induces protective immunity in mice. Clin Vaccine Immunol (2012) 1.02
A variant in long palate, lung and nasal epithelium clone 1 is associated with cholera in a Bangladeshi population. Genes Immun (2009) 1.01
Cerebellar structure and function in the murine mutant "jolting". J Neurol Sci (1986) 1.01
Neuromuscular transmission at newly formed neuromuscular junctions in the regenerating soleus muscle of the rat. J Physiol (1991) 1.00
Tissue heterogeneity of the FMR1 mutation in a high-functioning male with fragile X syndrome. Am J Med Genet (1999) 1.00
Stimulation of the gastric mucosa by adenosine-3',5'-monophosphate. Fed Proc (1966) 0.99
Programmed axon death, synaptic dysfunction and the ubiquitin proteasome system. Curr Drug Targets CNS Neurol Disord (2004) 0.98
Mechanical and electrophysiological effects of sea anemone (Anemonia sulcata) toxins on rat innervated and denervated skeletal muscle. Br J Pharmacol (1981) 0.98
Use of bronchial provocation with histamine to compare the pharmacodynamics of inhaled albuterol and metaproterenol in patients with asthma. J Allergy Clin Immunol (1987) 0.98
Competition at silent synapses in reinnervated skeletal muscle. Nat Neurosci (2000) 0.97
Motor unit size and synaptic competition in rat lumbrical muscles reinnervated by active and inactive motor axons. J Physiol (1983) 0.95
The effect of lesions in the neural crest on the formation of synaptic connexions in the embryonic chick spinal cord. J Physiol (1982) 0.94
Oxidative damage to muscle protein in Duchenne muscular dystrophy. Neuroreport (1996) 0.94
Immunogold labelling of dystrophin in human muscle, using an antibody to the last 17 amino acids of the C-terminus. Neuromuscul Disord (1991) 0.94
Emetine myopathy in the rat. Br J Pharmacol (1976) 0.94
Competitive mechanisms underlying synapse elimination in the lumbrical muscle of the rat. J Neurobiol (1990) 0.93
Myotoxic activity of the crude venom and the principal neurotoxin, taipoxin, of the Australian taipan, Oxyuranus scutellatus. Br J Pharmacol (1982) 0.93
Inhibition of denervation changes in mammalian skeletal muscle by actinomycin D. J Physiol (1971) 0.92
Some biochemical responses of rat skeletal muscle to a single subcutaneous injection of a toxin (notexin) isolated from the venom of the Australian tiger snake Notechis scutatus scutatus. Clin Exp Pharmacol Physiol (1978) 0.92
Elimination of motor nerve terminals in neonatal mice expressing a gene for slow wallerian degeneration (C57Bl/Wlds). Eur J Neurosci (1997) 0.92
The distribution of desmin and titin in normal and dystrophic human muscle. Acta Neuropathol (1992) 0.92
Early intervention with short courses of prednisone to prevent progression of asthma in ambulatory patients incompletely responsive to bronchodilators. J Pediatr (1987) 0.92
Envenoming bites by kraits: the biological basis of treatment-resistant neuromuscular paralysis. Brain (2005) 0.91
An electrophysiological and morphological study of normal and denervated chicken latissimus dorsi muscles. J Physiol (1975) 0.91
Regeneration of mammalian skeletal muscle following the injection of the snake-venom toxin, taipoxin. Cell Tissue Res (1983) 0.91
The resting membrane potential of fibres of fast and slow twitch muscles in normal and dystrophic mice. J Neurol Sci (1971) 0.91
Myotoxic activity of the toxic phospholipase, notexin, from the venom of the Australian tiger snake. J Neuropathol Exp Neurol (1996) 0.90
Some mechanical and electrical properties of distal hind limb muscles of genetically dystrophic mice (C57BL/6Jdy2j/dy2j). Exp Neurol (1975) 0.90
Persistent polyneuronal innervation in partially denervated rat muscle after reinnervation and recovery from prolonged nerve conduction block. J Neurosci (1995) 0.90
Myelinated nerve fibre counts in the nerves of normal and dystrophic mouse muscle. J Neurol Sci (1972) 0.90
Phospholipase A2 activity of notexin and its role in muscle damage. Toxicon (1981) 0.90
A comparative study of "denervation" in muscles from mice with inherited progressive neuromuscular disorders. Exp Neurol (1974) 0.90
Pharmacological strategies to block rod photoreceptor apoptosis caused by calcium overload: a mechanistic target-site approach to neuroprotection. Eur J Ophthalmol (2003) 0.89
Quantitative enzyme studies in extensor digitorum longus and soleus muscles of rats. Enzymol Biol Clin (Basel) (1970) 0.89
Beta-bungarotoxin-induced depletion of synaptic vesicles at the mammalian neuromuscular junction. Neuropharmacology (2004) 0.89
Neuromuscular effects of Papuan Taipan snake venom. Ann Neurol (1995) 0.88
Co-regulation of synaptic efficacy at stable polyneuronally innervated neuromuscular junctions in reinnervated rat muscle. J Physiol (1999) 0.88
The fate of desmin and titin during the degeneration and regeneration of the soleus muscle of the rat. Acta Neuropathol (1992) 0.88
Repression of inactive motor nerve terminals in partially denervated rat muscle after regeneration of active motor axons. J Physiol (1984) 0.88
Clostridial neurotoxins. J Neurol Neurosurg Psychiatry (2004) 0.87
The fate of dystrophin during the degeneration and regeneration of the soleus muscle of the rat. Acta Neuropathol (1992) 0.86
Taipoxin, a presynaptically active neurotoxin, destroys mammalian skeletal muscle [proceedings]. Br J Pharmacol (1977) 0.86
The expression of vimentin in satellite cells of regenerating skeletal muscle in vivo. Histochem J (1994) 0.86
The effect of temperature on end-plate depolarization of the rat diaphragm produced by suxamethonium and acetylcholine. J Pharm Pharmacol (1968) 0.85
Post-natal development of motor units and muscle fibers in rat lumbrical muscles [proceedings]. J Physiol (1979) 0.85
Proceedings: Histological and histochemical aspects of the effect of notexin on rat skeletal muscle. Br J Pharmacol (1974) 0.84
Preliminary observations of satellite cells in undamaged fibres of the rat soleus muscle assaulted by a snake-venom toxin. Cell Tissue Res (1983) 0.84
Differential susceptibility of human skeletal muscle proteins to free radical induced oxidative damage: a histochemical, immunocytochemical and electron microscopical study in vitro. Acta Neuropathol (1996) 0.84
Energy sources for gastric secretion: substrates. Am J Physiol (1967) 0.84
Absence of calpain 3 in a form of limb-girdle muscular dystrophy (LGMD2A). J Neurol Sci (1997) 0.84
Effects of senescence on chloroplasts of the tobacco leaf. Tissue Cell (1973) 0.84
Progressive denervation of skeletal muscle induced by spinal irradiation in rats. Brain (1977) 0.83
Activation of alpha-latrotoxin receptors in neuromuscular synapses leads to a prolonged splash acetylcholine release. Bull Exp Biol Med (2009) 0.83
Neuronal anti-nuclear antibody in paraneoplastic sensory neuronopathy. J Neurol Sci (1988) 0.83
Pentose phosphate shunt and gastric acid secretion in the rat. Am J Physiol (1972) 0.83
A study of action potential generation in murine dystrophy with reference to "functional denervation". Exp Neurol (1973) 0.83
The uptake of 99mtechnetium diphosphonate into degenerating and regenerating muscle. A correlative histological and biochemical study. J Neurol Sci (1981) 0.83
Polypeptides from snake venoms which act on nerve and muscle. Prog Med Chem (1984) 0.82
Neuromuscular transmission is adequate in identified abnormal dystrophic muscle fibres. Nature (1978) 0.81