Published in Ear Hear on February 13, 1986
Wideband acoustic-reflex test in a test battery to predict middle-ear dysfunction. Hear Res (2009) 1.06
The middle ear muscle reflex in the diagnosis of cochlear neuropathy. Hear Res (2015) 0.83
Pressurized Wideband Acoustic Stapedial Reflex Thresholds: Normal Development and Relationships to Auditory Function in Infants. J Assoc Res Otolaryngol (2016) 0.79
AUX1 regulates root gravitropism in Arabidopsis by facilitating auxin uptake within root apical tissues. EMBO J (1999) 4.00
The crystal structure of diphtheria toxin. Nature (1992) 3.80
Comparative anatomy of the aldo-keto reductase superfamily. Biochem J (1997) 3.39
Plasma homocysteine levels and folate status in children with sickle cell anemia. J Pediatr Hematol Oncol (1999) 3.27
PTEN mutation spectrum and genotype-phenotype correlations in Bannayan-Riley-Ruvalcaba syndrome suggest a single entity with Cowden syndrome. Hum Mol Genet (1999) 3.22
Crystal structure of the hemochromatosis protein HFE and characterization of its interaction with transferrin receptor. Cell (1998) 2.80
AXR4 is required for localization of the auxin influx facilitator AUX1. Science (2006) 2.49
The 1993 epidemic of pertussis in Cincinnati. Resurgence of disease in a highly immunized population of children. N Engl J Med (1994) 2.40
The effect of childbirth on pelvic organ mobility. Obstet Gynecol (2003) 2.29
Oligomer formation by 3D domain swapping: a model for protein assembly and misassembly. Adv Protein Chem (1997) 2.17
Antenatal screening in Oxford for fetal neural tube defects. Br J Obstet Gynaecol (1979) 2.06
Long term follow up of newborns tested with the auditory response cradle. Arch Dis Child (1984) 1.91
Fatty acid oxidation disorders: a new class of metabolic diseases. J Pediatr (1992) 1.85
A fetal fatty-acid oxidation disorder as a cause of liver disease in pregnant women. N Engl J Med (1999) 1.79
Predictive value of ultrasound measurement in early pregnancy: a randomized controlled trial. Br J Obstet Gynaecol (1982) 1.78
Acute otitis media caused by Branhamella catarrhalis: biology and therapy. Rev Infect Dis (1987) 1.77
Glutaric aciduria type I: a common cause of episodic encephalopathy and spastic paralysis in the Amish of Lancaster County, Pennsylvania. Am J Med Genet (1991) 1.74
A randomized controlled trial of amoxicillin plus clavulanate compared with cefaclor for treatment of acute otitis media. J Pediatr (1986) 1.72
Bactericidal antibody and susceptibility to otitis media caused by nontypable strains of Haemophilus influenzae. J Pediatr (1980) 1.69
Novel auxin transport inhibitors phenocopy the auxin influx carrier mutation aux1. Plant J (2001) 1.67
Acute fatty liver of pregnancy, hemolysis, elevated liver enzymes, and low platelets syndrome, and long chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency. Am J Gastroenterol (1996) 1.66
Maternal serum-alpha-fetoprotein and low birth-weight. Lancet (1977) 1.64
Emergence of beta-lactamase-producing strains of Branhamella catarrhalis as important agents of acute otitis media. Pediatr Infect Dis (1983) 1.62
Bacterial polysaccharide immune globulin for prophylaxis of acute otitis media in high-risk children. J Pediatr (1993) 1.61
A new syndrome with ethylmalonic aciduria and normal fatty acid oxidation in fibroblasts. J Pediatr (1994) 1.59
Acute phase reactants and risk of bacterial meningitis among febrile infants and children. Ann Emerg Med (1991) 1.54
Persistence of middle-ear effusion after acute otitis media in children. N Engl J Med (1979) 1.50
Use of high-fat formula for premature infants with bronchopulmonary dysplasia: metabolic, pulmonary, and nutritional studies. J Pediatr (1994) 1.50
Synergistic heterozygosity: disease resulting from multiple partial defects in one or more metabolic pathways. Mol Genet Metab (2000) 1.44
Lack of mitochondrial trifunctional protein in mice causes neonatal hypoglycemia and sudden death. J Clin Invest (2001) 1.43
Sjogren's syndrome. A case report with an additional diagnostic aid. Arch Intern Med (1966) 1.43
The increasing incidence of pertussis in Massachusetts adolescents and adults, 1989-1998. J Infect Dis (2000) 1.42
Mutational analysis of the transferrin receptor reveals overlapping HFE and transferrin binding sites. J Mol Biol (2001) 1.41
Comparison of the interactions of transferrin receptor and transferrin receptor 2 with transferrin and the hereditary hemochromatosis protein HFE. J Biol Chem (2000) 1.41
Subclavian cannulation with ultrasound: a novel method. Anaesthesia (2010) 1.39
The molecular basis of pediatric long chain 3-hydroxyacyl-CoA dehydrogenase deficiency associated with maternal acute fatty liver of pregnancy. Proc Natl Acad Sci U S A (1995) 1.38
Do children with recurrent Haemophilus influenzae otitis media become infected with a new organism or reacquire the original strain? J Pediatr (1984) 1.36
Defects of metabolism of fatty acids in the sudden infant death syndrome. Br Med J (Clin Res Ed) (1985) 1.34
Isoelectric focusing of beta-lactamases from sputum and middle ear isolates of Branhamella catarrhalis recovered in the United States. Drugs (1986) 1.26
Trials with the auditory response cradle. 1--Neonatal responses to auditory stimuli. Br J Audiol (1979) 1.25
Congenital and postnatally acquired cytomegalovirus infections: long-term follow-up. J Pediatr (1984) 1.25
Measuring the comparative efficacy of antibacterial agents for acute otitis media: the "Pollyanna phenomenon". J Pediatr (1992) 1.25
Acylcarnitines in fibroblasts of patients with long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency and other fatty acid oxidation disorders. J Inherit Metab Dis (2000) 1.22
Deficiency of medium chain fatty acylcoenzyme A dehydrogenase presenting as the sudden infant death syndrome. Br Med J (Clin Res Ed) (1984) 1.19
Mitochondrial respiratory chain complex I deficiency with clinical and biochemical features of long-chain 3-hydroxyacyl-coenzyme A dehydrogenase deficiency. J Pediatr (2000) 1.18
Transfer and expression of foreign genes in mammalian cells. Biotechniques (2000) 1.18
Anesthesia for laser surgery. Anesth Analg (1983) 1.14
Vitamin A, vitamin E, and lipids in serum of children with cystic fibrosis or congenital heart defects compared with normal children. Am J Clin Nutr (1967) 1.14
The neonatal acoustic reflex. Scand Audiol (1980) 1.13
Course and outcome of otitis media in early infancy: a prospective study. J Pediatr (1984) 1.13
Two alpha subunit donor splice site mutations cause human trifunctional protein deficiency. J Clin Invest (1995) 1.11
The Arabidopsis AUX1 gene: a model system to study mRNA processing in plants. Plant Mol Biol (1998) 1.11
The metabolic autopsy comes of age. Clin Chem (2001) 1.10
Tympanometry in the diagnosis of middle-ear effusion. N Engl J Med (1977) 1.10
Expression of glutamine synthetase genes in roots and nodules of Phaseolus vulgaris following changes in the ammonium supply and infection with various Rhizobium mutants. Plant Mol Biol (1990) 1.09
Evidence for fatty acid oxidation in human placenta, and the relationship of fatty acid oxidation enzyme activities with gestational age. Placenta (2002) 1.09
Trimethoprim-sulfamethoxazole compared with ampicillin in the treatment of acute otitis media. J Pediatr (1980) 1.09
Detection of intrauterine growth retardation by ultrasound: preliminary communication. J R Soc Med (1981) 1.08
Maternal acute fatty liver of pregnancy associated with fetal trifunctional protein deficiency: molecular characterization of a novel maternal mutant allele. Pediatr Res (1996) 1.07
3-Methylcrotonyl-coenzyme A carboxylase deficiency in Amish/Mennonite adults identified by detection of increased acylcarnitines in blood spots of their children. J Pediatr (1998) 1.07
Molecular characterization of L-CPT I deficiency in six patients: insights into function of the native enzyme. J Lipid Res (2001) 1.07
Some problems of alpha-fetoprotein screening. Lancet (1978) 1.06
Clinical and biochemical characterization of short-chain acyl-coenzyme A dehydrogenase deficiency. J Pediatr (1995) 1.05
Objective diagnosis of otitis media in early infancy by tympanometry and ipsilateral acoustic reflex thresholds. J Pediatr (1986) 1.05
Trials with the Auditory Response Cradle. II--The neonatal respiratory response to an auditory stimulus. Br J Audiol (1980) 1.05
3-Methylglutaconic aciduria associated with Pearson syndrome and respiratory chain defects. J Pediatr (1992) 1.04
Cell marking in Arabidopsis thaliana and its application to patch-clamp studies. Plant J (1998) 1.04
Early recurrences of otitis media: reinfection or relapse? J Pediatr (1987) 1.04
Glutaric aciduria type II: biochemical investigation and treatment of a child diagnosed prenatally. J Inherit Metab Dis (1984) 1.03
Chorioamnionitis and colonization of the newborn infant with genital mycoplasmas. N Engl J Med (1975) 1.00
Batten disease: evaluation of CLN3 mutations on protein localization and function. Hum Mol Genet (2000) 1.00
Trials with the auditory response cradle III: head turns and startles as auditory responses in the neonate. Br J Audiol (1980) 1.00
Late-onset holocarboxylase synthetase deficiency. J Inherit Metab Dis (1996) 1.00
Otitis media caused by non-typable, ampicillin-resistant strains of Haemophilus influenzae. J Pediatr (1976) 0.99
The Arabidopsis thaliana/Myzus persicae model system demonstrates that a single gene can influence the interaction between a plant and a sap-feeding insect. Mol Ecol (2006) 0.99
Taccalonolide binding to tubulin imparts microtubule stability and potent in vivo activity. Cancer Res (2013) 0.98
Abnormal myocardial lipid composition in an infant with type II glutaric aciduria. J Lipid Res (1987) 0.98
Inherited long-chain 3-hydroxyacyl-CoA dehydrogenase deficiency and a fetal-maternal interaction cause maternal liver disease and other pregnancy complications. Semin Perinatol (1999) 0.98
The diagnosis and biochemical investigation of a patient with a short chain fatty acid oxidation defect. J Inherit Metab Dis (1985) 0.96
Mathematical modelling of the Aux/IAA negative feedback loop. Bull Math Biol (2010) 0.96
Recent advances in otitis media. Diagnosis and screening. Ann Otol Rhinol Laryngol Suppl (1989) 0.94
Mellituria and postprandial blood sugar curves in dogs after the ingestion of various carbohydrates with the diet. J Nutr (1966) 0.94
Host factors and early therapeutic response in acute otitis media. J Pediatr (1991) 0.94
Structural and functional analysis of cationic transfection lipids: the hydrophobic domain. Gene Ther (1996) 0.93
Middle ear disease in children. Pathogenesis, diagnosis, and management. Pediatr Clin North Am (1974) 0.93
Fibroblast studies documenting a case of peroxisomal 2-methylacyl-CoA racemase deficiency: possible link between racemase deficiency and malabsorption and vitamin K deficiency. Eur J Clin Invest (2001) 0.93
beta-Ketothiolase (2-methylacetoacetyl-coenzyme A thiolase) deficiency: identification of two patients in Israel. J Inherit Metab Dis (1996) 0.93
Mucocele of the cystic duct remnant in eight liver transplant recipients: findings at cholangiography, CT, and US. Radiology (1990) 0.93
Riboflavin-responsive ethylmalonic-adipic aciduria. J Inherit Metab Dis (1985) 0.92
Identification of children requiring radiologic evaluation for urinary infection. Pediatr Infect Dis (1986) 0.92