Published in Pediatr Res on May 01, 1973
Combined methylmalonic acidemia and homocystinuria, cblC type. II. Complications, pathophysiology, and outcomes. J Inherit Metab Dis (2011) 1.06
Methionine metabolism in human pregnancy. Am J Clin Nutr (2009) 1.01
Betaine rescue of an animal model with methylenetetrahydrofolate reductase deficiency. Biochem J (2004) 0.92
Metabolism of methionine in the newborn infant: response to the parenteral and enteral administration of nutrients. Pediatr Res (2008) 0.83
Studies on N5-methyltetrahydrofolate-homocystein methyltransferase in normal and leukemia leukocytes. J Clin Invest (1975) 0.75
Maternal Folate Status and the BHMT c.716G>A Polymorphism Affect the Betaine Dimethylglycine Pathway during Pregnancy. Nutrients (2016) 0.75
Milk protein quantity and quality in low-birthweight infants: I. Metabolic responses and effects on growth. Pediatrics (1976) 1.70
Plasma lipids and apolipoproteins in breastfed and formula-fed Swedish infants. Acta Paediatr (1999) 1.58
Development of mammalian sulfur metabolism: absence of cystathionase in human fetal tissues. Pediatr Res (1972) 1.54
Inhibition of pyridoxal enzymes by L-canaline. Biochim Biophys Acta (1971) 1.50
Absence of cystathionase in human fetal liver: is cystine essential? Science (1970) 1.48
Metabolism of L- 35 S-methionine in vitamin B 6 deficiency: observations on cystathioninuria. Biochem Med (1970) 1.40
Taurine: biological update. Annu Rev Biochem (1986) 1.27
Aluminum-induced neurofibrillary changes in axons and dendrites. Acta Neuropathol (1984) 1.18
Pyridoxine-dependency in homocystinuria. Lancet (1968) 1.16
Methionine intolerance: a possible risk factor for coronary artery disease. J Am Coll Cardiol (1985) 1.14
Intensive care of small premature infants. I. Clinical findings and results of treatment. Acta Paediatr Scand (1970) 1.13
Milk protein quantity and quality in low-birth-weight infants. III. Effects on sulfur amino acids in plasma and urine. J Pediatr (1977) 1.12
Homocystinuria due to cystathionine synthase deficiency: enzymatic and ultrastructural studies. J Pediatr (1974) 1.10
Hypermethioninemia associated with methionine adenosyltransferase deficiency: clinical, morphologic, and biochemical observations on four patients. J Pediatr (1981) 1.10
Taurine in metabolism. Annu Rev Nutr (1981) 1.04
Development of alcohol dehydrogenase activity in the human liver. Pediatr Res (1967) 1.04
Nutritional proteins in milk and the protein requirement of normal infants. Pediatrics (1985) 1.02
Methionine adenosyltransferase deficiency: new enzymatic defect associated with hypermethioninemia. Science (1974) 1.02
A comparative study of the tapetum, retina and skull of the ferret, dog and cat. Lab Anim Sci (1985) 1.01
Induction of cystathionase in human foetal liver. Biochem J (1974) 1.01
Taurine and other free amino acids in milk of man and other mammals. Early Hum Dev (1978) 1.01
Ornithine-ketoacid aminotransferase in human liver with reference to patients with hyperornithinaemia and familial protein intolerance. Clin Chim Acta (1969) 1.01
Ornithine carbamoyltransferase deficiency in an adult male patient: significance of hepatic ultrastructure in clinical diagnosis. Pediatrics (1983) 1.01
Metabolism of steroid and amino acid moieties of conjugated bile acids in man. 3. Cholyltaurine (taurocholic acid). J Clin Invest (1973) 1.00
Activities of lipase and trypsin in duodenal juice of infants small for gestational age. J Pediatr Gastroenterol Nutr (1991) 1.00
The mechanism of the inhibition of dehydrogenases by salicylate. J Pharm Pharmacol (1967) 0.99
Taurine ameliorates chronic streptozocin-induced diabetic nephropathy in rats. Am J Physiol (1995) 0.99
Aluminum chloride induced neurofibrillary changes in the developing rabbit a chronic animal model. Ann Neurol (1980) 0.98
Fetal tissue amino acid concentrations in argininosuccinic aciduria and in "maternal homocystinuria". Clin Chim Acta (1979) 0.98
A procedure for the quantitative analysis of the sulphur amino acids of rat tissues. Biochem J (1967) 0.96
Hereditary hyperphosphatasia. Studies of three siblings. Am J Med (1969) 0.95
Taurine: an essential nutrient for the cat. J Nutr (1978) 0.94
The role of taurine in infant nutrition. Adv Exp Med Biol (1998) 0.94
Significance of hypermethionaemia in acute tyrosinosis. Lancet (1968) 0.94
Milk protein quantity and quality in low-birth-weight infants: II. Effects on selected aliphatic amino acids in plasma and urine. Pediatrics (1977) 0.94
Argininosuccinic aciduria: prenatal studies in a family at risk. Am J Hum Genet (1979) 0.94
Taurine deficiency in the developing cat: persistence of the cerebellar external granule cell layer. J Neurosci Res (1985) 0.94
Milk protein quantity and quality in low-birth-weight infants. IV. Effects on tyrosine and phenylalanine in plasma and urine. J Pediatr (1977) 0.94
Taurine in the brain and liver of the developing human and monkey. J Neurochem (1975) 0.93
Development of urea-synthesizing enzymes in human liver. Acta Paediatr Scand (1968) 0.93
Development of some enzymes involved in gluconeogenesis in human liver. Ann Med Exp Biol Fenn (1969) 0.92
Higher concentrations of serum transferrin receptor in children than in adults. Am J Clin Nutr (1999) 0.91
Biochemical observations on so-called hereditary tyrosinemia. Pediatr Res (1970) 0.91
Protein intake of premature infants: a reply. J Pediatr (1977) 0.91
Methioninemia and myopathy: a new disorder. Ann Neurol (1981) 0.91
Cystathionase: immunochemical evidence for absence from human fetal liver. Pediatr Res (1972) 0.90
Studies on the development of ornithine-keto acid aminotransferase activity in rat liver. Biochem J (1968) 0.89
Individualized protein fortification of human milk for preterm infants: comparison of ultrafiltrated human milk protein and a bovine whey fortifier. J Pediatr Gastroenterol Nutr (1999) 0.88
Cystathionine beta-synthase deficiency: a qualitative abnormality of the deficient enzyme modified by vitamin B6 therapy. Pediatr Res (1977) 0.88
Regulation of tyrosine aminotransferase in foetal rat liver. Biochem J (1980) 0.87
Pentose phosphate pathway metabolism by normal and glucose-6-phosphate dehydrogenase-deficient human red cell haemolysates. Clin Chim Acta (1967) 0.87
Iron-fortified and unfortified cow's milk: effects on iron intakes and iron status in young children. Acta Paediatr (2001) 0.87
The binding of salicylate to plasma proteins in different species. J Pharm Pharmacol (1967) 0.86
Metabolism of [35S]taurine in man. J Nutr (1975) 0.86
A method for measurement of free and bound plasma cyst(e)ine. Anal Biochem (1981) 0.86
Urinary and serum urea as indicators of protein metabolism in very low birthweight infants fed varying human milk protein intakes. Acta Paediatr Scand (1990) 0.86
Vitamin B6-responsive and -unresponsive cystathioninuria: two variant molecular forms. Science (1975) 0.86
Feeding the low-birth-weight infant. III. Diet influences bile acid metabolism. Pediatrics (1983) 0.85
The loss of neuron-specific proteins during the course of Wallerian degeneration of optic and sciatic nerve. J Neurosci (1981) 0.85
Taurine and osmoregulation: taurine is a cerebral osmoprotective molecule in chronic hypernatremic dehydration. Pediatr Res (1988) 0.85
The site of amino acid addition to posttranslationally modified proteins of regenerating rat sciatic nerves. Biochim Biophys Acta (1990) 0.85
Protective effect of taurine, zinc and tocopherol on retinol-induced damage in human lymphoblastoid cells. J Nutr (1984) 0.85
Histochemical localization of zinc in the feline tapetum. Effect of taurine depletion. Histochemistry (1981) 0.84
Homolanthionine synthesis by human liver cystathionase. Biochem Biophys Res Commun (1971) 0.84
Tyrosine aminotransferase activity in human fetal liver. J Dev Physiol (1981) 0.84
Taurine deficiency in the kitten: exchange and turnover of [35S] taurine in brain, retina, and other tissues. J Nutr (1978) 0.84
Protein intake in early infancy: effects on plasma amino acid concentrations, insulin metabolism, and growth. Pediatr Res (1989) 0.84
Vitamin B6 dependency in homocystinuria. Br Med J (1971) 0.83
The distribution of salicylate in mouse tissues after intraperitoneal injection. J Pharm Pharmacol (1968) 0.83
Mitochondrial abnormalities of liver in primary ornithine transcarbamylase deficiency. Pediatr Res (1980) 0.83
Bile salt-stimulated lipase in non-primate milk: longitudinal variation and lipase characteristics in cat and dog milk. Biochim Biophys Acta (1986) 0.83
Enzyme induction in human fetal liver in organ culture. Enzyme (1973) 0.83
Enzymes of urea synthesis in familial protein intolerance with deficient transport of basic amino acids. Acta Paediatr Scand (1967) 0.83
Chronic model of neurofibrillary changes induced in mature rabbits by metallic aluminum. Neurobiol Aging (1982) 0.83
Growth depression in taurine-depleted infant monkeys. J Nutr (1980) 0.82
Feline maternal taurine deficiency: effect on mother and offspring. J Nutr (1986) 0.82
Taurine pool sizes in the rat: effects of vitamin B-6 deficiency and high taurine diet. J Nutr (1973) 0.82
Polyamine biosynthesis in human fetal liver and brain. Pediatr Res (1974) 0.82
Taurine in developing rat brain: transfer of [35S] taurine to pups via the milk. Pediatr Res (1977) 0.82
Taurine attenuates renal disease in chronic puromycin aminonucleoside nephropathy. Am J Physiol (1992) 0.82
Macromolecular absorption in small-for-gestational-age infants. Acta Paediatr (1992) 0.82
Metabolic differences between AGA- and SGA-infants of very low birthweight. I. Relationship to intrauterine growth retardation. Acta Paediatr Scand (1988) 0.81
Ethanol elimination in a mother and her premature twins. Lancet (1971) 0.81
Tapetum disorganization in taurine-depleted cats. Invest Ophthalmol Vis Sci (1979) 0.81
Milk protein quantity and quality in the term infant. II. Effects on acidic and neutral amino acids. Pediatrics (1982) 0.81
Biochemical basis for nutritional management of preterm infants. Pediatrics (1974) 0.81