Published in Poumon Coeur on January 01, 1969
Familial microcephaly with normal intelligence, immunodeficiency, and risk for lymphoreticular malignancies: a new autosomal recessive disorder. Am J Med Genet (1985) 1.44
Analysis of oxidative phosphorylation complexes in cultured human fibroblasts and amniocytes by blue-native-electrophoresis using mitoplasts isolated with the help of digitonin. Anal Biochem (1995) 1.40
Characterization of a novel 21-kb deletion, CFTRdele2,3(21 kb), in the CFTR gene: a cystic fibrosis mutation of Slavic origin common in Central and East Europe. Hum Genet (2000) 1.37
Beta-adrenergic, cAMP-mediated stimulation of proliferation of brown fat cells in primary culture. Mediation via beta 1 but not via beta 3 adrenoceptors. J Biol Chem (1992) 1.34
Tetramethyl rhodamine methyl ester (TMRM) is suitable for cytofluorometric measurements of mitochondrial membrane potential in cells treated with digitonin. Biosci Rep (1999) 1.17
Synthesis of mitochondrial uncoupling protein in brown adipocytes differentiated in cell culture. J Biol Chem (1990) 0.98
Paraproteinaemia and unusual dys-gamma-globulinaemia in a case of Wiskott-Aldrich syndrome. An immunochemical study. Arch Dis Child (1967) 0.96
A peroral test of pancreatic insufficiency with 4-(N-acetyl-L-tyrosyl)aminobenzoic acid in children with cystic fibrosis. J Pediatr (1979) 0.93
Assembly of mitochondrial ATP synthase in cultured human cells: implications for mitochondrial diseases. Biochim Biophys Acta (1995) 0.92
Occurrence of a specific foetal protein in a primary liver carcinoma. Nature (1966) 0.91
Serum alpha-glutathione S-transferase as a sensitive marker of hepatocellular damage in patients with cystic fibrosis. Physiol Res (2003) 0.90
Insulin-like growth factor-I and insulin-like growth factor-binding protein-3 in cystic fibrosis: a positive effect of antibiotic therapy and hyperalimentation. Acta Paediatr (2001) 0.89
[Macroamylasemia in children]. Cesk Pediatr (1981) 0.88
Distribution of pulmonary blood flow in children with cystic fibrosis. Acta Paediatr Scand (1971) 0.86
Hepatocellular carcinoma in association with a specific fetal alpha-1-globulin, fetoprotein. J Pediatr (1968) 0.85
Ultrastructure of the bronchial epithelium in three children with asthma. Pediatr Pulmonol (1986) 0.84
High number of high-affinity binding sites for (-)-[3H]dihydroalprenolol on isolated hamster brown-fat cells. A study of the beta-adrenergic receptors. Eur J Biochem (1979) 0.84
Antineutrophil cytoplasmic autoantibodies (ANCA) in children with cystic fibrosis. J Autoimmun (1998) 0.83
Low translational efficiency of the F1-ATPase beta-subunit mRNA largely accounts for the decreased ATPase content in brown adipose tissue mitochondria. FEBS Lett (1992) 0.83
Purification and properties of adenosine triphosphatase solubilized from beef heart mitochondria by chloroform. Mol Cell Biochem (1977) 0.83
Alpha 1 antitrypsin deficiency in a child with chronic lung disease. Chest (1973) 0.82
Lung function in children and adolescents with idiopathic interstitial pulmonary fibrosis. Pediatr Pulmonol (1985) 0.81
Is the mitochondrial dicyclohexylcarbodiimide-reactive protein of Mr 33 000 identical with the phosphate transport protein? FEBS Lett (1981) 0.81
[Our experience with mucoviscidosis]. Rev Med Liege (1967) 0.81
Purification and properties of mitochondrial adenosine triphosphatase of hamster brown adipose tissue. Biochim Biophys Acta (1977) 0.81
Multifactorial induction of gene expression and nuclear localization of mouse interleukin 1 alpha. Cytokine (1996) 0.81
Ultrastructure of bronchial epithelium in children with chronic or recurrent respiratory diseases. Eur J Respir Dis (1982) 0.81
Molecular mechanism of uncoupling in brown adipose tissue mitochondria. The non-identity of proton and chloride conducting pathways. FEBS Lett (1984) 0.80
[A new missense mutation of 574C>T in the SURF1 gene--biochemical and molecular genetic study in seven children with Leigh syndrome]. Cas Lek Cesk (2002) 0.79
A simple procedure for isolating adenosine triphosphatase from mitochondria. Biochim Biophys Acta (1977) 0.79
[Changes in serum proteins and ultrastructure of thrombocytes in the Wiskott-Aldrich syndrome]. Cas Lek Cesk (1966) 0.79
Chest physiotherapy and airway obstruction in patients with cystic fibrosis - a negative report. Eur J Respir Dis (1983) 0.79
Adenine nucleotide and phosphate transport systems of mitochondria. Relative location of sulfhydryl groups based on the use of the novel fluorescent probe eosin-5-maleimide. J Biol Chem (1985) 0.79
In vitro hypoxia increases production of matrix metalloproteinases and tryptase in isolated rat lung mast cells. Physiol Res (2007) 0.78
Control of uncoupling protein in brown-fat mitochondria by purine nucleotides. Chemical modification by diazobenzenesulfonate. Eur J Biochem (1987) 0.78
The regulation of glycerol 3-phosphate oxidase of rate brownadipose tissue mitochondria by long-chain free fatty acids. Mol Cell Biochem (1975) 0.78
Effects of short-term and prolonged aerogenic hypoxia on gamma-glutamyl transpeptidase activity in the brain, liver, and biological fluids of young rats. Neurochem Res (1985) 0.78
Gylcerol-3-phosphate shuttle and its function in intermediary metabolism of hamster brown-adipose tissue. Eur J Biochem (1975) 0.78
[Cultivation of cells from amniotic fluid for prenatal diagnosis]. Cesk Pediatr (1974) 0.78
The binding of dicyclohexylcarbodiimide to uncoupling protein in brown adipose tissue mitochondria. FEBS Lett (1982) 0.78
Role of the carboxyl-terminal region of the PVP protein (F0I subunit) in the H+ conduction of F0F1 H+-ATP synthase of bovine heart mitochondria. FEBS Lett (1989) 0.78
Differentiation of dicyclohexylcarbodiimide reactive sites of the ATPase complex bovine heart mitochondria. Biochim Biophys Acta (1981) 0.77
Evaluation of the specific dicyclohexylcarbodiimide binding sites in brown adipose tissue mitochondria. Biochim Biophys Acta (1981) 0.77
[Psychogenic cough]. Cesk Pediatr (1983) 0.77
Adrenergic control of induction of type II iodothyronine 5'-deiodinase activity in cultured mouse brown adipocytes. Biochem J (1993) 0.77
Comparison of the effect of three oral mucolytics on the ultrastructure of the tracheal epithelium in rabbits. Respiration (1985) 0.77
Alkaline pH, membrane potential, and magnesium cations are negative modulators of purine nucleotide inhibition of H+ and Cl- transport through the uncoupling protein of brown adipose tissue mitochondria. J Bioenerg Biomembr (1988) 0.77
[The exogenous surfactant and its effect on the respiratory distress syndrome (RDS)]. Cesk Fysiol (1996) 0.76
Gamma-glutamyl transferase activity in the amniotic fluid of fetuses with chromosomal aberrations and inborn errors of metabolism. Clin Genet (1987) 0.76
Electrophoretic behavior of the H+-ATPase proteolipid from bovine heart mitochondria. J Bioenerg Biomembr (1986) 0.76
Mitochondrial F0F1 H+-ATP synthase. Characterization of F0 components involved in H+ translocation. FEBS Lett (1989) 0.75
Identification of nucleus-encoded F0I protein of bovine heart mitochondrial H+-ATPase as a functional part of the F0 moiety. FEBS Lett (1988) 0.75
Structure and function of the membrane-integral components of the mitochondrial H+-ATPase. J Bioenerg Biomembr (1982) 0.75
[Influence of repeated chronic diseases of respiratory tract on the weight in childhood]. Cesk Pediatr (1971) 0.75
[Possible existence of a selective factor for mucoviscidosis in heterozygotes]. Cesk Pediatr (1970) 0.75
[Experience with diagnosing cystic fibrosis during the past 5 years]. Cesk Pediatr (1983) 0.75
Reaction of goblet cells in the tracheal epithelium to the stimulation with mucolytic agent. Folia Morphol (Praha) (1980) 0.75
[The use N-acetylcysteine in the treatment of mucoviscidosis]. Cesk Pediatr (1966) 0.75
Ultrastructure of the bronchial epithelium in children with cystic fibrosis. Monogr Paediatr (1979) 0.75
Antibiotic treatment of cystic fibrosis. Acta Univ Carol Med (Praha) (1990) 0.75
[Correction of oxygen tension in blood according to temperature and pH and computation of saturation from the standard dissociation curve]. Cas Lek Cesk (1966) 0.75
[The effect of repeated inhalation of 4% Mistabron on the ultrastructure of respiratory tract epithelium]. Cesk Pediatr (1979) 0.75
Summer and winter recondition camps for children with cystic fibrosis. Acta Univ Carol Med (Praha) (1990) 0.75
[Factors inhibiting ciliary movement in the serum of patients with nasal polyps]. Cesk Otolaryngol (1982) 0.75
Cardiomyopathy and changes of skeletal muscles in cystic fibrosis. Acta Univ Carol Med (Praha) (1990) 0.75
[Diffusion capacity of the lungs and its components in interstitial pulmonary fibrosis adolescents]. Cas Lek Cesk (1965) 0.75
Obstruction of the respiratory pathways, its evaluation by methods of functional examination of the lungs and development in patients with cystic fibrosis. Czech Med (1979) 0.75
Ultrastructure of rabbit tracheal epithelium after the inhalation of physiological saline. Folia Morphol (Praha) (1979) 0.75
[The effect of peroral administration of the mucolytic Mucopront on the ultrastructure of the epithelium of the respiratory tract]. Cesk Pediatr (1982) 0.75
[Treatment of cystic fibrosis]. Cesk Pediatr (1982) 0.75
[Incidence and genetics of pancreatic cystic fibrosis]. Cesk Pediatr (1970) 0.75
Care for cystic fibrosis patients in Czechoslovakia. Acta Univ Carol Med (Praha) (1990) 0.75
[Cystic fibrosis (mucoviscidosis) as underlying cause of chronic obstructive pulmonary disease in children]. Cas Lek Cesk (1972) 0.75
Lung transplantation for cystic fibrosis: immune system and autoimmunity. Med Sci Monit (2001) 0.75
Development of non-respiratory components of acid-base equilibrium in 250 normal children aged one month to 15 years. Acta Paediatr Scand (1968) 0.75
[Changes of acid-base equilibrium in chronic respiratory diseases of children]. Bratisl Lek Listy (1970) 0.75
Effect of the inhalation of a surface tension-reducing substance (propylene glycol) on the ultrastructure of epithelium of the respiratory passages in rabbits. Folia Morphol (Praha) (1978) 0.75
[Cystic fibrosis 1946-1982]. Cesk Pediatr (1983) 0.75
[Changes of blood homeostasis during exchange transfusions in newborns. I. Changes in the bicarbonate system]. Cas Lek Cesk (1967) 0.75
[X-ray picture of pulmonary changes in pancreatic cystic fibrosis and their classification. Analysis of 146 cases]. Cesk Pediatr (1979) 0.75
[Use of the classification of pathological findings in the epithelium of large bronchi in various stages of chronic respiratory diseases]. Cesk Pediatr (1982) 0.75
[Hypercapnia in childhood]. Vnitr Lek (1970) 0.75
[Partial pressure of CO2 in blood: comparison between the results of the direct and indirect methods]. Poumon Coeur (1969) 0.75
[Immunoglobulin D in respiratory diseases]. Cesk Pediatr (1978) 0.75
Psychosocial typology of the CF family system. Acta Univ Carol Med (Praha) (1990) 0.75
[pH, PCO2 and nonrespiratory component of the acid-base balance of the arterialized cutaneous blood in 97 healthy children from 3 months to 15 years of age]. Poumon Coeur (1969) 0.75
The supporting weekend's meeting of families with CF children. Acta Univ Carol Med (Praha) (1990) 0.75
[Pathogenesis of cystic fibrosis]. Cesk Pediatr (1982) 0.75
[Prospects of children with mucoviscidosis]. Cesk Pediatr (1967) 0.75
Evaluation of the reliability of hemoglobin determination by copper sulphate densitometry. Acta Univ Carol Med (Praha) (1969) 0.75
[Report on the session of the European Pedriatic Respiration Club at Göteberg and Lysekil June 3-6, 1969]. Cesk Pediatr (1970) 0.75
[Peroral test involving 4-(N-acetyl-L-tyrosyl) aminobenzoic acid in children with mucoviscidosis (author's transl)]. Cas Lek Cesk (1978) 0.75
Genetic variants of transferrin in cystic fibrosis. J Inherit Metab Dis (2008) 0.75
[Modification of the method for detecting serum ciliary-inhibiting factors in patients with mucoviscidosis and their parents]. Cesk Pediatr (1981) 0.75
[Evaluation of three dosage regimens of amikacin using pharmacokinetic models in patients with cystic fibrosis]. Cas Lek Cesk (2004) 0.75
Changes in the values of immunoglobulins and antiprotease activity accompanying the death of children with cystic fibrosis. Acta Univ Carol Med (Praha) (1990) 0.75
Comparison of the effect of aerosols of four mucolytic solutions on the ultrastructure of the tracheal epithelium in rabbits. Respiration (1982) 0.75