Published in Eur J Biochem on May 11, 1971
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Effects of palmitoyl CoA on citrate and malate transport by rat liver mitochondria. Proc Natl Acad Sci U S A (1972) 0.92
Lipogenesis from ketone bodies in rat brain. Evidence for conversion of acetoacetate into acetyl-coenzyme A in the cytosol. Biochem J (1976) 0.90
Stimulation of ammonia production and excretion in the rabbit by inorganic phosphate. Study of control mechanisms. J Clin Invest (1976) 0.89
Inhibitors of the mitochondrial citrate transport protein: validation of the role of substrate binding residues and discovery of the first purely competitive inhibitor. Mol Pharmacol (2009) 0.88
The yeast mitochondrial citrate transport protein: molecular determinants of its substrate specificity. J Biol Chem (2010) 0.82
Isolation and characterization of the tricarboxylate transporter from pea mitochondria. Plant Physiol (1992) 0.82
The reduction of diamide by rat liver mitochondria and the role of glutathione. Biochem J (1978) 0.77
Determining clinically important differences in health status measures: a general approach with illustration to the Health Utilities Index Mark II. Pharmacoeconomics (1999) 4.86
Development of a brief measure to assess quality of life in obesity. Obes Res (2001) 3.92
Lactic acidemia and bradyarrhythmia in a child sedated with propofol. Crit Care Med (1998) 3.71
Characteristics of isolated and purified preparations of the outer and inner membranes of mitochondria. Ann N Y Acad Sci (1966) 3.64
Approaches to DNA mutagenesis: an overview. Anal Biochem (1997) 3.09
Mitochondria, oxygen free radicals, disease and ageing. Trends Biochem Sci (2000) 3.04
A bovine albumin peptide as a possible trigger of insulin-dependent diabetes mellitus. N Engl J Med (1992) 2.86
The inhibition of malate, tricarboxylate and oxoglutarate entry into mitochondria by 2-n-butylmalonate. Biochem Biophys Res Commun (1967) 2.64
Quality of life and obesity. Obes Rev (2001) 2.63
Heteroplasmic mtDNA mutation (T----G) at 8993 can cause Leigh disease when the percentage of abnormal mtDNA is high. Am J Hum Genet (1992) 2.41
The control of fatty acid and triglyceride synthesis in rat epididymal adipose tissue. Roles of coenzyme A derivatives, citrate and L-glycerol 3-phosphate. Biochem J (1968) 2.37
Postoperative hyponatremia despite near-isotonic saline infusion: a phenomenon of desalination. Ann Intern Med (1997) 2.33
Tendon to bone healing: differences in biomechanical, structural, and compositional properties due to a range of activity levels. J Biomech Eng (2003) 2.28
Mitochondrial complex I deficiency leads to increased production of superoxide radicals and induction of superoxide dismutase. J Clin Invest (1996) 2.20
Encoding of anisotropic diffusion with tetrahedral gradients: a general mathematical diffusion formalism and experimental results. Magn Reson Med (1996) 2.20
Renal tubular acidosis and osteopetrosis with carbonic anhydrase II deficiency: pathogenesis of impaired acidification. Pediatr Nephrol (1997) 2.16
Quantitative analysis of amino acid oxidation and related gluconeogenesis in humans. Physiol Rev (1992) 2.12
Penetration of the mitochondrial membrane by glutamate and aspartate. Biochem Biophys Res Commun (1967) 1.99
Ribosome changes following illumination of dark-grown plants. Biochim Biophys Acta (1968) 1.92
Penetration of the mitochondrial membrane by tricarboxylic acid anions. Biochem Soc Symp (1968) 1.91
The localized expression of extracellular matrix components in healing tendon insertion sites: an in situ hybridization study. J Orthop Res (2002) 1.85
A rapid and reliable DNA preparation method for screening a large number of yeast clones by polymerase chain reaction. Nucleic Acids Res (1995) 1.84
Mutations in the X-linked pyruvate dehydrogenase (E1) alpha subunit gene (PDHA1) in patients with a pyruvate dehydrogenase complex deficiency. Hum Mutat (2000) 1.75
Hypokalaemia and paralysis. QJM (2001) 1.72
Metabolic acidosis in the alcoholic: a pathophysiologic approach. Metabolism (1983) 1.70
The relationship between health-related quality of life and weight loss. Obes Res (2001) 1.68
Hyperglycemia-induced hyponatremia: metabolic considerations in calculation of serum sodium depression. Can Med Assoc J (1975) 1.66
Importance of timing of risk factors for cerebral oedema during therapy for diabetic ketoacidosis. Arch Dis Child (2003) 1.63
The sensitivity of dicarboxylate anion exchange reactions o transport inhibitors in rat-liver mitochondria. Biochim Biophys Acta (1970) 1.62
Mitochondria, oxygen free radicals, and apoptosis. Am J Med Genet (2001) 1.61
Effect of moderate weight loss on health-related quality of life: an analysis of combined data from 4 randomized trials of sibutramine vs placebo. Am J Manag Care (2001) 1.61
Presidential Address: a history of appendicitis. With anecdotes illustrating its importance. Ann Surg (1983) 1.61
Rotator cuff tear arthropathy. J Bone Joint Surg Am (1999) 1.60
Reverse micelles as hosts for proteins and small molecules. Biochim Biophys Acta (1988) 1.58
A biochemically distinct form of cytochrome oxidase (COX) deficiency in the Saguenay-Lac-Saint-Jean region of Quebec. Am J Hum Genet (1993) 1.57
Genetic analysis reveals different functions for the products of the thyroid hormone receptor alpha locus. Mol Cell Biol (2001) 1.54
Cancer in patients receiving dialysis. Br Med J (1980) 1.52
How to select optimal maintenance intravenous fluid therapy. QJM (2003) 1.51
Glue-sniffing and distal renal tubular acidosis: sticking to the facts. J Am Soc Nephrol (1991) 1.50
Acidosis in a patient with cholera: a need to redefine concepts. QJM (2004) 1.47
Anion transporters in plant mitochondria. Plant Physiol (1973) 1.47
An additional role for insulin in the control of fatty acid synthesis independent of glucose transport. Can J Biochem (1970) 1.47
A modified classification of metabolic acidosis: a pathophysiologic approach. Nephron (1992) 1.45
Intrarater and interrater reliability of three isometric dynamometers in assessing shoulder strength. J Shoulder Elbow Surg (1997) 1.45
Sites of ammonia addition to tubular fluid in rats with chronic metabolic acidosis. Kidney Int (1981) 1.45
Treatment of acute hyponatremia: ensuring the excretion of a predictable amount of electrolyte-free water. Crit Care Med (2000) 1.44
Severe hypokalaemia in a Chinese male. QJM (2002) 1.42
Débridement of degenerative, irreparable lesions of the rotator cuff. J Bone Joint Surg Am (1995) 1.41
The genetic heterogeneity of lactic acidosis: occurrence of recognizable inborn errors of metabolism in pediatric population with lactic acidosis. Pediatr Res (1980) 1.41
Clinical, metabolic, and genetic aspects of cytochrome C oxidase deficiency in Saguenay-Lac-Saint-Jean. Am J Hum Genet (1993) 1.40
Isolation and sequence determination of cDNA clones for porcine and human lipoamide dehydrogenase. Homology to other disulfide oxidoreductases. J Biol Chem (1987) 1.40
The patient with a severe degree of metabolic acidosis: a deductive analysis. QJM (2006) 1.39
Evaluation of the Neer system of classification of proximal humeral fractures with computerized tomographic scans and plain radiographs. J Bone Joint Surg Am (1996) 1.38
Open medial subtalar dislocation associated with fracture of the posterior process of the talus. J Orthop Trauma (1996) 1.37
Superoxides from mitochondrial complex III: the role of manganese superoxide dismutase. Free Radic Biol Med (2000) 1.37
Isolation of a full-length complementary DNA coding for human E1 alpha subunit of the pyruvate dehydrogenase complex. J Biol Chem (1988) 1.33
Barth syndrome: clinical observations and genetic linkage studies. Am J Med Genet (1994) 1.31
Periprosthetic humeral fractures: mechanisms of fracture and treatment options. J Shoulder Elbow Surg (1998) 1.31
Studies on the pathogenesis of type I (distal) renal tubular acidosis as revealed by the urinary PCO2 tensions. J Clin Invest (1974) 1.30
An analysis of the reflex systemic vasodilator response elicited by lung inflation in the dog. J Physiol (1968) 1.29
Expression of mtDNA and nDNA encoded respiratory chain proteins in chemically and genetically-derived Rho0 human fibroblasts: a comparison of subunit proteins in normal fibroblasts treated with ethidium bromide and fibroblasts from a patient with mtDNA depletion syndrome. Biochim Biophys Acta (1997) 1.29
Regulation of glycolysis and L-glycerol 3-phosphate concentration in rat epididymal adipose tissue in vitro. Role of phosphofructokinase. Biochem J (1969) 1.27
[3H]biotin-labeled proteins in cultured human skin fibroblasts from patients with pyruvate carboxylase deficiency. J Biol Chem (1983) 1.27
Long durations of immobilization in the rat result in enhanced mechanical properties of the healing supraspinatus tendon insertion site. J Biomech Eng (2007) 1.27
Diphtheria in London and Birmingham, 1975. Public Health (1977) 1.26
Familial Hibernian fever. Q J Med (1982) 1.26
Iron metabolism in the anaemia of chronic renal failure. Effects of dialysis and of parenteral iron. Br Med J (1969) 1.26
Effects of 2-Butylmalonate, 2-Phenylsuccinate, Benzylmalonate, and p-Iodobenzylmalonate on the Oxidation of Substrates by Mung Bean Mitochondria. Plant Physiol (1973) 1.24
Site-specific incorporation of nitroxide spin-labels into internal sites of the TAR RNA; structure-dependent dynamics of RNA by EPR spectroscopy. J Am Chem Soc (2001) 1.23
Agonal phase, ischaemic times, and renal vascular abnormalities and outcome of cadaver kidney transplants. Br Med J (1975) 1.22
A novel syndrome affecting multiple mitochondrial functions, located by microcell-mediated transfer to chromosome 2p14-2p13. Am J Hum Genet (2001) 1.22
Motions of short DNA duplexes: an analysis of DNA dynamics using an EPR-active probe. Biochemistry (1993) 1.20
Factors that control the effect of pH on glycolysis in leukocytes. J Biol Chem (1969) 1.20
Jefferson fractures in children. Case report. J Neurosurg (1983) 1.19
Sequence-dependent dynamics of duplex DNA: the applicability of a dinucleotide model. Biophys J (2002) 1.18
Interfacial membrane docking of cytosolic phospholipase A2 C2 domain using electrostatic potential-modulated spin relaxation magnetic resonance. Proc Natl Acad Sci U S A (1999) 1.18
Transport of reduced nicotinamide-adenine dinucleotide into mitochondria of rat white adipose tissue. Biochem J (1970) 1.17
The transtubular potassium concentration in patients with hypokalemia and hyperkalemia. Am J Kidney Dis (1990) 1.17
Sequence- and structure-dependent DNA base dynamics: synthesis, structure, and dynamics of site and sequence specifically spin-labeled DNA. Biochemistry (1989) 1.16
Analysis of double-helix motions with spin-labeled probes: binding geometry and the limit of torsional elasticity. J Mol Biol (1980) 1.16
The mitochondrial DNA mutation at 8993 associated with NARP slows the rate of ATP synthesis in isolated lymphoblast mitochondria. Biochem Biophys Res Commun (1993) 1.16
Simultaneous detection of mitochondrial respiratory chain activity and reactive oxygen in digitonin-permeabilized cells using flow cytometry. Cytometry (2000) 1.14
Operative treatment of malunion of a fracture of the proximal aspect of the humerus. J Bone Joint Surg Am (1998) 1.14
Insight into the physiological actions of thyroid hormone receptors from genetically modified mice. J Endocrinol (2002) 1.12
Effect of domperidone on the health-related quality of life of patients with symptoms of diabetic gastroparesis. Diabetes Care (1998) 1.12
The effects of graded doses of phenoxybenzamine on the vascular and capsular responses of the isolated, blood-perfused dogs spleen to sympathetic nerve stimulation and catecholamines. Arch Int Pharmacodyn Ther (1969) 1.12
The molecular basis for the two different clinical presentations of classical pyruvate carboxylase deficiency. Am J Hum Genet (1984) 1.12
Formyl-methenyl-methylenetetrahydrofolate synthetase (combined); correlation of enzymic activities with limited proteolytic degradation of the protein from yeast. Biochem Biophys Res Commun (1977) 1.12
A genomewide linkage-disequilibrium scan localizes the Saguenay-Lac-Saint-Jean cytochrome oxidase deficiency to 2p16. Am J Hum Genet (2001) 1.12
Thyroid hormone acts directly on growth plate chondrocytes to promote hypertrophic differentiation and inhibit clonal expansion and cell proliferation. Endocrinology (2000) 1.12
Spontaneous detachment of the deltoid muscle origin. J Shoulder Elbow Surg (1998) 1.11
Defective intramitochondrial NADH oxidation in skin fibroblasts from an infant with fatal neonatal lacticacidemia. Am J Hum Genet (1985) 1.11
Postoperative assessment of shoulder function: a prospective study of full-thickness rotator cuff tears. J Shoulder Elbow Surg (1997) 1.10
Development of a test to evaluate the transtubular potassium concentration gradient in the cortical collecting duct in vivo. Miner Electrolyte Metab (1986) 1.10
3-Mercaptopicolinic acid, a preferential inhibitor of the cytosolic phosphoenolpyruvate carboxykinase. FEBS Lett (1975) 1.10
Structure, functioning, and assembly of the ATP synthase in cells from patients with the T8993G mitochondrial DNA mutation. Comparison with the enzyme in Rho(0) cells completely lacking mtdna. J Biol Chem (2000) 1.09
Using nitroxide spin labels. How to obtain T1e from continuous wave electron paramagnetic resonance spectra at all rotational rates. Biophys J (1993) 1.09