Published in Biochem J on January 01, 1978
A radiochemical method for the measurement of coproporphyrinogen oxidase and the utilization of substrates other than coproporphyrinogen III by the enzyme from rat liver. Biochem J (1978) 1.58
Structure and function of enzymes in heme biosynthesis. Protein Sci (2010) 1.48
Structural basis of hereditary coproporphyria. Proc Natl Acad Sci U S A (2005) 1.08
Harderoporphyria: a variant hereditary coproporphyria. J Clin Invest (1983) 1.06
Cloning, expression, and biochemical properties of CPOX4, a genetic variant of coproporphyrinogen oxidase that affects susceptibility to mercury toxicity in humans. Toxicol Sci (2009) 0.89
Characterization of mutations in the CPO gene in British patients demonstrates absence of genotype-phenotype correlation and identifies relationship between hereditary coproporphyria and harderoporphyria. Am J Hum Genet (2001) 0.88
Role of aspartate 400, arginine 262, and arginine 401 in the catalytic mechanism of human coproporphyrinogen oxidase. Protein Sci (2007) 0.78
Prokaryotic Heme Biosynthesis: Multiple Pathways to a Common Essential Product. Microbiol Mol Biol Rev (2017) 0.77
H.p.l.c. analysis of di- and tri-carboxylic porphyrins in porphyric patients. Biochem J (1985) 0.75
Mitochondrial coproporphyrinogen oxidase and protoporphyrin formation. J Biol Chem (1961) 5.06
An inherited enzymatic defect in porphyria cutanea tarda: decreased uroporphyrinogen decarboxylase activity. J Clin Invest (1976) 2.83
Macrocyclic intermediates in the biosynthesis of porphyrins. Philos Trans R Soc Lond B Biol Sci (1976) 2.73
Heme biosynthesis in intermittent acute prophyria: decreased hepatic conversion of porphobilinogen to porphyrins and increased delta aminolevulinic acid synthetase activity. Proc Natl Acad Sci U S A (1970) 2.33
The enzymic conversion of coproporphyrinogen 3 into protoporphyrin 9. Biochem J (1964) 1.88
A radiochemical method for the measurement of coproporphyrinogen oxidase and the utilization of substrates other than coproporphyrinogen III by the enzyme from rat liver. Biochem J (1978) 1.58
The role of iron in the pathogenesis of porphyria cutanea tarda. II. Inhibition of uroporphyrinogen decarboxylase. J Clin Invest (1975) 1.45
Protein-bound porphyrins associated with protoporphyrin biosynthesis. Biochem Biophys Res Commun (1961) 1.43
Isolation, structure and synthesis of a tricarboxylic porphyrin from the harderian glands of the rat. FEBS Lett (1970) 1.38
The effect of the porphyrogenic compound, hexachlorobenzene, on the activity of hepatic uroporphyrinogen decarboxylase in the rat. Clin Sci Mol Med (1976) 1.24
Enzymatic formation and cellular regulation of heme synthesis. Semin Hematol (1977) 1.01
High-performance liquid chromatographic analysis of porphyrins in clinical materials. J Chromatogr (1976) 1.00
Conversion of coproporphyrinogen 3 to protoporphyrin IX. Enzyme (1974) 0.94
Formation of uroporphyrinogen IV during the chemical dimerization of 2-aminomethyl-3',3'-carboxymethyl-4,4' (beta-carboxyethyl) dipyrrylmethane. FEBS Lett (1975) 0.86
The later stages of porphyrin biosynthesis. Ann N Y Acad Sci (1975) 0.82
Synthetic and biosynthetic studies of porphyrins. Part 1. Synthesis of the "S-411" porphyrin obtained from meconium. J Chem Soc Perkin 1 (1976) 0.80
Performance of four computer-based diagnostic systems. N Engl J Med (1994) 9.40
Economic stress, coercive family process, and developmental problems of adolescents. Child Dev (1994) 5.45
A family process model of economic hardship and adjustment of early adolescent boys. Child Dev (1992) 4.32
Pubertal transition, stressful life events, and the emergence of gender differences in adolescent depressive symptoms. Dev Psychol (2001) 3.79
Variability in automatic activation as an unobtrusive measure of racial attitudes: a bona fide pipeline? J Pers Soc Psychol (1995) 3.14
Competence in early adult romantic relationships: a developmental perspective on family influences. J Pers Soc Psychol (2000) 2.87
Macrocyclic intermediates in the biosynthesis of porphyrins. Philos Trans R Soc Lond B Biol Sci (1976) 2.73
Are religious grandparents more involved grandparents? J Gerontol B Psychol Sci Soc Sci (1999) 2.36
Molecular epidemiology of erythropoietic protoporphyria in the U.K. Br J Dermatol (2010) 2.15
Couple resilience to economic pressure. J Pers Soc Psychol (1999) 2.09
Coming of age too early: pubertal influences on girls' vulnerability to psychological distress. Child Dev (1996) 2.08
Trial of strategy for reducing the use of laboratory tests. Br Med J (Clin Res Ed) (1986) 1.82
Erythropoietic protoporphyria in the U.K.: clinical features and effect on quality of life. Br J Dermatol (2006) 1.77
Increased frequency of the haemochromatosis Cys282Tyr mutation in sporadic porphyria cutanea tarda. Lancet (1997) 1.69
Pathways of economic influence on adolescent adjustment. Am J Community Psychol (1999) 1.69
A radiochemical method for the measurement of coproporphyrinogen oxidase and the utilization of substrates other than coproporphyrinogen III by the enzyme from rat liver. Biochem J (1978) 1.58
Inhibition by -amanitin of simian virus 40-specific ribonucleic acid synthesis in nuclei of infected monkey cells. J Virol (1972) 1.56
The prophyrins of normal human urine, with a comparison of the excretion pattern in porphyria cutanea tarda. Int J Biochem (1980) 1.54
Relationships among performance scores of four diagnostic decision support systems. J Am Med Inform Assoc (1996) 1.53
Continuities and consequences of interactional styles across the life course. J Pers (1989) 1.52
Linking family hardship to children's lives. Child Dev (1985) 1.52
ACP Best Practice No 165: front line tests for the investigation of suspected porphyria. J Clin Pathol (2001) 1.50
Parent-adolescent reciprocity in negative affect and its relation to early adult social development. Dev Psychol (2001) 1.49
The efficacy of a serum screening service for neural-tube defects: the South Wales experience. Lancet (1983) 1.49
Brain death in the pediatric intensive care unit. A clinical definition. Am J Dis Child (1983) 1.48
Comparison of effects of transcutaneous electrical nerve stimulation of auricular, somatic, and the combination of auricular and somatic acupuncture points on experimental pain threshold. Phys Ther (1989) 1.42
A further cohort study of workers employed at a factory manufacturing chemicals for the rubber industry, with special reference to the chemicals 2-mercaptobenzothiazole (MBT), aniline, phenyl-beta-naphthylamine and o-toluidine. Occup Environ Med (2000) 1.40
Decreased activity of hepatic uroporphyrinogen decarboxylase in sporadic porphyria cutanea tarda. N Engl J Med (1978) 1.39
A MspI polymorphism for the human porphobilinogen deaminase gene. Nucleic Acids Res (1987) 1.37
Porphyrin metabolism in porphyria cutanea tarda. Semin Hematol (1977) 1.35
Can we afford screening for neural tube defects? The South Wales experience. Br Med J (Clin Res Ed) (1985) 1.34
Past and future of the mitotic spindle as an oncology target. Curr Opin Pharmacol (2001) 1.31
A 50-year prospective study of the psychological sequelae of World War II combat. Am J Psychiatry (1995) 1.29
The porphyrias: a review. J Clin Pathol (1972) 1.28
Evidence that the coproporphyrinogen oxidase activity of rat liver is situated in the intermembrane space of mitochondria. Biochem J (1978) 1.26
Continuing medical education using clinical algorithms. A controlled-trial assessment of effect on neonatal care. Am J Dis Child (1986) 1.26
Husband and wife differences in response to undesirable life events. J Health Soc Behav (1993) 1.24
Differentiation of porphyria cutanea tarda symptomatica from other types of porphyria by measurement of isocoproporphyrin in faeces. J Clin Pathol (1975) 1.24
The effect of the porphyrogenic compound, hexachlorobenzene, on the activity of hepatic uroporphyrinogen decarboxylase in the rat. Clin Sci Mol Med (1976) 1.24
The intergenerational transmission of health-risk behaviors: adolescent lifestyles and gender moderating effects. J Health Soc Behav (1999) 1.23
Sputum sol-phase proteins and elastase activity in patients with cystic fibrosis. Eur J Respir Dis (1984) 1.22
Manipulation of distinct NFkappaB proteins alters interleukin-1beta-induced human rheumatoid synovial fibroblast prostaglandin E2 formation. J Biol Chem (1996) 1.20
Acute mercury vapor poisoning. Fatality in an infant. Am J Dis Child (1981) 1.19
Investigation of the subcellular location of the tetrapyrrole-biosynthesis enzyme coproporphyrinogen oxidase in higher plants. Biochem J (1993) 1.18
DNA polymorphism of human porphobilinogen deaminase gene in acute intermittent porphyria. Lancet (1987) 1.17
Appearance and education in marriage mobility. Am Sociol Rev (1969) 1.16
Family history and the life course. J Fam Hist (1977) 1.15
Hepatoerythropoietic porphyria: a new uroporphyrinogen decarboxylase defect or homozygous porphyria cutanea tarda? Lancet (1981) 1.12
Lymphocyte monovalent cation metabolism: cell volume, cation content and cation transport. J Cell Physiol (1972) 1.11
Pyrroles and related compounds. XX. Syntheses of coproporphyrins. J Chem Soc Perkin 1 (1972) 1.11
Immunoreactive uroporphyrinogen decarboxylase in the liver in porphyria cutanea tarda. Lancet (1985) 1.11
Purification of uroporphyrinogen decarboxylase from human erythrocytes. Immunochemical evidence for a single protein with decarboxylase activity in human erythrocytes and liver. Biochem J (1983) 1.11
Identification of two types of porphyria cutanea tarda by measurement of erythrocyte uroporphyrinogen decarboxylase. Clin Sci (Lond) (1980) 1.09
Worklives and longevity: insights from a life course perspective. J Health Soc Behav (1993) 1.09
The primary enzyme defect in hereditary coproporphyria. Lancet (1976) 1.08
Conversion of liver haem into N-substituted porphyrins or green pigments. Nature of the substituent at the pyrrole nitrogen atom. FEBS Lett (1980) 1.08
Mutations in the hemochromatosis gene, porphyria cutanea tarda, and iron overload. Hepatology (1998) 1.04
Isocoproporphyrin: nuclear-magnetic-resonance-and mass-spectral methods for the determination of porphyrin structure. Biochem J (1973) 1.04
N-methylporphyrins. Ann N Y Acad Sci (1973) 1.03
Structural isomerism and chirality of N-monosubstituted protoporphyrins. FEBS Lett (1982) 1.03
Role of neutrophils in the deposition of platelets during acute inflammation. Lab Invest (1983) 1.02
Synthetic and biosynthetic studies of porphyrins, Part V. Evidence for an alternative pathway in the biosynthesis of haem. Int J Biochem (1980) 1.01
Immunoreactive uroporphyrinogen decarboxylase is unchanged in porphyria caused by TCDD and hexachlorobenzene. Biochem Biophys Res Commun (1982) 1.00
High-performance liquid chromatographic analysis of porphyrins in clinical materials. J Chromatogr (1976) 1.00
Intergenerational continuity of parental rejection and depressed affect. J Pers Soc Psychol (1992) 0.99
The metabolism of porphyrins of the isocoproporphyrin series. Enzyme (1974) 0.98
Decreased activity of uroporphyrinogen decarboxylase caused by 2,4,5,3',4'-pentabromobiphenyl in chick embryo hepatocyte cultures. Difference in activity in intact or homogenized cells. FEBS Lett (1983) 0.98
A mortality study of workers in a factory manufacturing chlorinated toluenes. Ann Occup Hyg (1983) 0.97
Acute intermittent porphyria caused by a C----T mutation that produces a stop codon in the porphobilinogen deaminase gene. Hum Genet (1990) 0.97
Immunoreactive uroporphyrinogen decarboxylase in porphyria cutanea tarda. Lancet (1983) 0.96
Measurement of uroporphyrinogen decarboxylase using porphyrinogens prepared by chemical reduction. Enzyme (1982) 0.96
Economic hardship and marital relations in the 1930s. Am Sociol Rev (1983) 0.95
The porphyrias: clinical chemistry, diagnosis and methodology. Clin Haematol (1980) 0.94
Recent developments in porphyrin chemistry. Biochem Soc Symp (1968) 0.94
Conversion of coproporphyrinogen 3 to protoporphyrin IX. Enzyme (1974) 0.94
Amputation: energy cost of ambulation. Arch Phys Med Rehabil (1979) 0.93
Molecular species of the urobilins. Nature (1966) 0.93
Variegate porphyria in Western Europe: identification of PPOX gene mutations in 104 families, extent of allelic heterogeneity, and absence of correlation between phenotype and type of mutation. Am J Hum Genet (1999) 0.93
Late presentation of erythropoietic protoporphyria: case report and genetic analysis of family members. Br J Dermatol (2007) 0.93
Incubation of 5-aminolaevulinate with erythrocyte haemolysates from normal and protein-deficient guinea pigs [proceedings]. Biochem Soc Trans (1979) 0.93
Mini and micro plating of phalangeal and metacarpal fractures: a biomechanical study. J Hand Surg Am (1995) 0.93
Management of acute and cutaneous porphyrias. Int J Clin Pract (2002) 0.92
Enzymatic defects in porphyria: an overview. Semin Liver Dis (1982) 0.92
Small intestinal submucosa: utilization as a wound dressing in full-thickness rodent wounds. Ann Plast Surg (1995) 0.92
Matrilineal advantage in grandchild-grandparent relations. Gerontologist (2000) 0.92
Life satisfaction in old age: linking social psychology and history. Psychol Aging (1986) 0.92
Effect of helium-neon laser auriculotherapy on experimental pain threshold. Phys Ther (1990) 0.91
Relationships among the MCAT reading subtest, Nelson-Denny Reading Test, and medical school achievement. J Med Educ (1985) 0.91
Autosomal recessive erythropoietic protoporphyria in the United Kingdom: prevalence and relationship to liver disease. J Med Genet (2004) 0.91
18F-labeled benzamides for studying the dopamine D2 receptor with positron emission tomography. J Med Chem (1993) 0.91
Histiocytosis X with benign intracranial hypertension. Dev Med Child Neurol (1975) 0.91
Balance performance and step width in noninstitutionalized, elderly, female fallers and nonfallers. Phys Ther (1989) 0.90