Published in R I Med J on April 01, 1984
Cognition and anatomy in three variants of primary progressive aphasia. Ann Neurol (2004) 7.07
Neuropsychological syndromes in presenile dementia due to cerebral atrophy. J Neurol Neurosurg Psychiatry (1986) 1.83
A case of progressive aphasia without dementia: "temporal" Pick's disease? J Neurol Neurosurg Psychiatry (1990) 1.42
Single photon emission tomography using 99mTc-HM-PAO in the investigation of dementia. J Neurol Neurosurg Psychiatry (1987) 1.39
Progressive biparietal atrophy: an atypical presentation of Alzheimer's disease. J Neurol Neurosurg Psychiatry (1996) 1.39
Progressive loss of speech output and orofacial dyspraxia associated with frontal lobe hypometabolism. J Neurol Neurosurg Psychiatry (1991) 1.28
Slowly progressive aphasia: three cases with language, memory, CT and PET data. J Neurol Neurosurg Psychiatry (1990) 1.22
Alzheimer's pathology in primary progressive aphasia. Neurobiol Aging (2010) 1.18
Patterns of longitudinal brain atrophy in the logopenic variant of primary progressive aphasia. Brain Lang (2013) 1.02
PET: its clinical role in neurology. J Neurol Neurosurg Psychiatry (1991) 0.98
The corticobasal syndrome-Alzheimer's disease conundrum. Expert Rev Neurother (2011) 0.95
Progressive degeneration of the right temporal lobe studied with positron emission tomography. J Neurol Neurosurg Psychiatry (1990) 0.94
Alzheimer's disease: differences in technetium-99m HMPAO SPECT scan findings between early onset and late onset dementia. J Neurol Neurosurg Psychiatry (2003) 0.82
Dementia presenting with aphasia: clinical characteristics. J Neurol Neurosurg Psychiatry (1991) 0.80
A review on primary progressive aphasia. Neuropsychiatr Dis Treat (2007) 0.76
Progressive aphasia with rapidly progressive dementia in a 49 year old woman. J Neurol Neurosurg Psychiatry (1999) 0.75
A calcineurin-dependent transcriptional pathway controls skeletal muscle fiber type. Genes Dev (1998) 5.14
MEF2 responds to multiple calcium-regulated signals in the control of skeletal muscle fiber type. EMBO J (2000) 3.59
E2F3 activity is regulated during the cell cycle and is required for the induction of S phase. Genes Dev (1998) 3.48
Cytochrome c deficiency causes embryonic lethality and attenuates stress-induced apoptosis. Cell (2000) 3.39
A protein encoded within the Down syndrome critical region is enriched in striated muscles and inhibits calcineurin signaling. J Biol Chem (2000) 3.26
Stimulation of slow skeletal muscle fiber gene expression by calcineurin in vivo. J Biol Chem (2000) 3.19
Independent signals control expression of the calcineurin inhibitory proteins MCIP1 and MCIP2 in striated muscles. Circ Res (2000) 3.04
Myocyte-enriched calcineurin-interacting protein, MCIP1, inhibits cardiac hypertrophy in vivo. Proc Natl Acad Sci U S A (2001) 2.64
Presentation of midgut malrotation in adults. Br Med J (1968) 2.56
Structure of a conjugating enzyme-ubiquitin thiolester intermediate reveals a novel role for the ubiquitin tail. Structure (2001) 2.48
Cdc6 is regulated by E2F and is essential for DNA replication in mammalian cells. Proc Natl Acad Sci U S A (1998) 2.40
Activation of MEF2 by muscle activity is mediated through a calcineurin-dependent pathway. EMBO J (2001) 2.38
Functional heterogeneity of mammalian TATA-box sequences revealed by interaction with a cell-specific enhancer. Nature (1990) 2.27
Evidence for degenerative and regenerative changes in neostriatal spiny neurons in Huntington's disease. Science (1985) 2.23
Calcineurin signaling and muscle remodeling. Cell (2000) 2.22
Regulation of stroke volume during submaximal and maximal upright exercise in normal man. Circ Res (1986) 2.15
The Growth of Various Species of Bacteria and Other Micro-Organisms in Atmospheres Enriched with Oxygen. Biochem J (1911) 2.06
Web sites selling cigarettes: how many are there in the USA and what are their sales practices? Tob Control (2001) 2.06
Acceptors for botulinum neurotoxin reside on motor nerve terminals and mediate its internalization. Nature (1984) 2.02
The fascinating history of bezoars. Med J Aust (1987) 1.96
Dual roles of modulatory calcineurin-interacting protein 1 in cardiac hypertrophy. Proc Natl Acad Sci U S A (2003) 1.84
Physical conditioning augments the fibrinolytic response to venous occlusion in healthy adults. N Engl J Med (1980) 1.81
Mice without myoglobin. Nature (1998) 1.78
Regulation of nuclear and mitochondrial gene expression by contractile activity in skeletal muscle. J Biol Chem (1986) 1.78
Repeat polymorphisms within gene regions: phenotypic and evolutionary implications. Am J Hum Genet (2000) 1.75
Cardiac-specific LIM protein FHL2 modifies the hypertrophic response to beta-adrenergic stimulation. Circulation (2001) 1.74
The Growth of the Bacillus tuberculosis and other Micro-Organisms in Varying Percentages of Oxygen. Biochem J (1909) 1.72
Myogenic stem cell function is impaired in mice lacking the forkhead/winged helix protein MNF. Proc Natl Acad Sci U S A (2000) 1.68
The passage of Florida's Statute on Assisted Reproductive Technology. Obstet Gynecol (1994) 1.66
Remodeling muscles with calcineurin. Bioessays (2000) 1.66
A prospective study of Alzheimer disease in Down syndrome. Arch Neurol (1989) 1.64
Management of Meckel's diverticulum. Br J Surg (1981) 1.61
Increased plasma tumor necrosis factor in severe alcoholic hepatitis. Ann Intern Med (1990) 1.60
Subcellular partitioning of MRP RNA assessed by ultrastructural and biochemical analysis. J Cell Biol (1994) 1.54
Colour Changes produced by two groups of Bacteria upon Caseinogen and certain Amino-acids. Biochem J (1917) 1.53
Lhermitte-Duclos disease (granule cell hypertrophy of the cerebellum) pathological analysis of the first familial cases. J Neuropathol Exp Neurol (1969) 1.53
Mitochondrial gene expression in mammalian striated muscle. Evidence that variation in gene dosage is the major regulatory event. J Biol Chem (1986) 1.51
Cardiovascular and behavioral effects of aerobic exercise training in healthy older men and women. J Gerontol (1989) 1.51
Exercise training in healthy type A middle-aged men: effects on behavioral and cardiovascular responses. Psychosom Med (1988) 1.45
Dietary protein, growth and retention of ascorbic acid in guinea-pigs. Br J Nutr (1972) 1.39
Comparison of high- and low-intensity exercise training early after acute myocardial infarction. Am J Cardiol (1988) 1.39
Induction of stress proteins in cultured myogenic cells. Molecular signals for the activation of heat shock transcription factor during ischemia. J Clin Invest (1992) 1.37
Out-patient letters: requirement and contents. Eff Health Care (1985) 1.37
Activation of the heat shock transcription factor by hypoxia in mammalian cells. Proc Natl Acad Sci U S A (1990) 1.36
Physiological and psychological variables predict compliance to prescribed exercise therapy in patients recovering from myocardial infarction. Psychosom Med (1982) 1.36
Transient expression of a winged-helix protein, MNF-beta, during myogenesis. Mol Cell Biol (1997) 1.36
Cerebro-ocular dysgenesis (Walker-Warburg syndrome): neuropathologic and etiologic analysis. Neurology (1984) 1.36
PR48, a novel regulatory subunit of protein phosphatase 2A, interacts with Cdc6 and modulates DNA replication in human cells. Mol Cell Biol (2000) 1.36
Persistent expression of MNF identifies myogenic stem cells in postnatal muscles. Dev Biol (1997) 1.35
Direct characterization of methanogens in two high-rate anaerobic biological reactors. Appl Environ Microbiol (1988) 1.34
Cardioprotective effects of 70-kDa heat shock protein in transgenic mice. Proc Natl Acad Sci U S A (1996) 1.32
Methods for reducing non-specific antibody binding in enzyme-linked immunosorbent assays. J Immunol Methods (1985) 1.32
Synergistic interactions between heterologous upstream activation elements and specific TATA sequences in a muscle-specific promoter. Mol Cell Biol (1995) 1.32
Morphometric analysis of the prefrontal cortex in Huntington's disease. Neurology (1991) 1.30
Radioiodination of botulinum neurotoxin type A with retention of biological activity and its binding to brain synaptosomes. Eur J Biochem (1983) 1.25
Rupture of spleen at colonoscopy. Br Med J (1979) 1.24
Cloning and characterization of a eukaryotic pantothenate kinase gene (panK) from Aspergillus nidulans. J Biol Chem (1999) 1.24
Exercise responses before and after physical conditioning in patients with severely depressed left ventricular function. Am J Cardiol (1982) 1.23
A 40-kilodalton protein binds specifically to an upstream sequence element essential for muscle-specific transcription of the human myoglobin promoter. Mol Cell Biol (1992) 1.22
Changing strategies in the performance of laparoscopic Nissen fundoplication as a result of experience with 230 operations. Surg Endosc (1995) 1.22
Transport of proteins into chloroplasts. Organization, orientation, and lateral distribution of the plastocyanin processing peptidase in the thylakoid network. J Biol Chem (1988) 1.22
The Golgi rapid method in clinical neuropathology: the morphologic consequences of suboptimal fixation. J Neuropathol Exp Neurol (1978) 1.20
Autism and mental retardation: neuropathologic studies performed in four retarded persons with autistic behavior. Arch Neurol (1980) 1.19
Adaptation of skeletal muscle to increased contractile activity. Expression nuclear genes encoding mitochondrial proteins. J Biol Chem (1987) 1.19
Identification of a muscle-specific enhancer within the 5'-flanking region of the human myoglobin gene. J Biol Chem (1989) 1.19
The cellular pathology of Menkes steely hair syndrome. Neurology (1978) 1.19
Botulinum neurotoxin and dendrotoxin as probes for studies on transmitter release. J Physiol (Paris) (1984) 1.19
The winged-helix/forkhead protein myocyte nuclear factor beta (MNF-beta) forms a co-repressor complex with mammalian sin3B. Biochem J (2000) 1.18
Botulinum neurotoxin type B. Its purification, radioiodination and interaction with rat-brain synaptosomal membranes. Eur J Biochem (1986) 1.17
Age-related changes in the density and morphology of plaques and neurofibrillary tangles in Down syndrome brain. Acta Neuropathol (1989) 1.16
Electrical stimulation of neonatal cardiac myocytes activates the NFAT3 and GATA4 pathways and up-regulates the adenylosuccinate synthetase 1 gene. J Biol Chem (2000) 1.15
Characterization of the glycosylation sites in yeast external invertase. I. N-linked oligosaccharide content of the individual sequons. J Biol Chem (1988) 1.15
Sex-linked hereditary bilateral anophthalmos. Pathologic and radiologic correlation. Arch Ophthalmol (1984) 1.15
Myocyte nuclear factor, a novel winged-helix transcription factor under both developmental and neural regulation in striated myocytes. Mol Cell Biol (1994) 1.15
Effects of GnRH analogues, 'add-back' steroid therapy, antiestrogen and antiprogestins on leiomyoma and myometrial smooth muscle cell growth and transforming growth factor-beta expression. Mol Hum Reprod (2002) 1.13
The cellular pathology of neuronal ceroid-lipofuscinosis. A golgi-electronmicroscopic study. Arch Neurol (1977) 1.10
Skeletal muscle beta-adrenergic receptors: variations due to fiber type and training. Am J Physiol (1984) 1.09
Differential expression of mitochondrial DNA replication factors in mammalian tissues. J Biol Chem (1998) 1.09
Continuous contractile activity induces fiber type specific expression of HSP70 in skeletal muscle. Am J Physiol (1996) 1.08
Mitochondrial biogenesis in striated muscles: rapid induction of citrate synthase mRNA by nerve stimulation. Am J Physiol (1991) 1.07
The Viability of B. tuberculosis (bovinus) on Pasture Land, in Stored Faeces and in Liquid Manure. J Hyg (Lond) (1930) 1.07
Morphological features of Pick's and atypical Alzheimer's disease in Down's syndrome. Acta Neuropathol (1982) 1.07
Malignant monophasic multiple sclerosis or "Marburg's disease". Neurology (1988) 1.07
Postnatal development and plasticity of specialized muscle fiber characteristics in the hindlimb. Dev Genet (1996) 1.07
Vascular biology and invasive cardiology. The streams are beginning to merge. Circulation (1992) 1.06
Sox15 and Fhl3 transcriptionally coactivate Foxk1 and regulate myogenic progenitor cells. EMBO J (2007) 1.05
Relationship between plaques, tangles, and dementia in Down syndrome. Neurology (1980) 1.04
Adaptive mechanisms that preserve cardiac function in mice without myoglobin. Circ Res (2001) 1.04
Physiologic basis for the age-related decline in aerobic work capacity. Am J Cardiol (1986) 1.04
Beta-Adrenergic receptors of human lymphocytes are unaltered by hyperthyroidism. J Clin Endocrinol Metab (1979) 1.04
Golgi and electronmicroscopic studies of spongiform encephalopathy. Neurology (1981) 1.04
Evidence for neuronal degeneration and dendritic plasticity in cortical pyramidal neurons of Huntington's disease: a quantitative Golgi study. Neurology (1993) 1.03
Regulatory elements governing transcription in specialized myofiber subtypes. J Biol Chem (2001) 1.02
Effects of exercise on the Type A (coronary prone) behavior pattern. Psychosom Med (1980) 1.01
Clinical and radiologic remission in reticulum cell sarcoma of the brain. Arch Neurol (1979) 1.01
Differentiation of hemodynamic, humoral and metabolic responses to beta 1- and beta 2-adrenergic stimulation in man using atenolol and propranolol. Circulation (1983) 1.01
Collaborative interactions between MEF-2 and Sp1 in muscle-specific gene regulation. J Cell Biochem (1998) 1.01
Induction of immediate-early genes by angiotensin II and endothelin-1 in adult rat cardiomyocytes. J Hypertens (1993) 1.01
Gradients of transgene expression directed by the human myoglobin promoter in the developing mouse heart. Proc Natl Acad Sci U S A (1993) 1.00