Published in Neurology on August 01, 1980
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Cerebral plasmacytoma with myeloma protein in the cerebrospinal fluid. Neurology (1966) 1.46
Glioneurofibroma: renaming the pediatric "gliofibroma": a neoplasm composed of Schwann cells and astrocytes. Mod Pathol (1991) 1.46
Low-stage medulloblastoma: final analysis of trial comparing standard-dose with reduced-dose neuraxis irradiation. J Clin Oncol (2000) 1.44
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Transient neonatal galactosaemia. Arch Dis Child (1988) 1.38
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Central neurofibromatosis with bilateral acoustic neuroma. Adv Neurol (1981) 1.34
The association of posterior capsular lens opacities with bilateral acoustic neuromas in patients with neurofibromatosis type 2. Arch Ophthalmol (1989) 1.34
Familial motor neuron disease. Evidence for at least three different types. Neurology (1976) 1.34
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A possible biochemical explanation for the insensitivity of the rat to cardiac glycosides. J Pharmacol Exp Ther (1969) 1.26
Migration of brain tumor cells on extracellular matrix proteins in vitro correlates with tumor type and grade and involves alphaV and beta1 integrins. Cancer Res (1996) 1.26
High-dose carboplatin, thiotepa, and etoposide with autologous stem-cell rescue for patients with recurrent medulloblastoma. Children's Cancer Group. J Clin Oncol (1998) 1.24
Central nervous system gangliogliomas. Part 2: Clinical outcome. J Neurosurg (1993) 1.22
Neoadjuvant chemotherapy for newly diagnosed germ-cell tumors of the central nervous system. J Neurosurg (1987) 1.22
Eye findings in bilateral acoustic (central) neurofibromatosis: association with presenile lens opacities and cataracts but absence of Lisch nodules. N Engl J Med (1986) 1.21
Foreign body reaction to hemostatic materials mimicking recurrent brain tumor. Report of three cases. J Neurosurg (2001) 1.21
Inhibition of host protein synthesis during infection of Escherichi coli by bacteriophage T4. 3. Inhibition by ghosts. J Virol (1970) 1.20
Survival and prognostic factors following radiation and/or chemotherapy for primitive neuroectodermal tumors of the pineal region in infants and children: a report of the Childrens Cancer Group. J Clin Oncol (1995) 1.20
Novel mtDNA mutations and oxidative phosphorylation dysfunction in Russian LHON families. Hum Genet (2001) 1.19
Survival of infants with primitive neuroectodermal tumors or malignant ependymomas of the CNS treated with eight drugs in 1 day: a report from the Childrens Cancer Group. J Clin Oncol (1994) 1.19
Environmental-occupational risk factors and familial associations in multiple system atrophy: a preliminary investigation. Clin Auton Res (1991) 1.19
Practical application of the European Field Guide in screening for diabetic retinopathy by using ophthalmoscopy and 35 mm retinal slides. Diabetologia (1998) 1.19
The low concordance rate for Parkinson's disease in twins: a possible explanation. Neurology (1984) 1.18
Mutational analysis of patients with neurofibromatosis 2. Am J Hum Genet (1994) 1.17
Antibodies against gamma-globulin after repeated blood transfusions in man. J Clin Invest (1966) 1.17
Improved prognosis of intracranial non-germinoma germ cell tumors with multimodality therapy. J Neurooncol (1997) 1.17
Mutations of the INI1 rhabdoid tumor suppressor gene in medulloblastomas and primitive neuroectodermal tumors of the central nervous system. Clin Cancer Res (2000) 1.15
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Gilles de la Tourette syndrome: clinical and genetic studies in a midwestern city. Neurology (1978) 1.12
Ouabain-induced signaling and vascular smooth muscle cell proliferation. J Biol Chem (2001) 1.12
Identification of a thymic inhibitor ('chalone') of lymphocyte transformation as a spermine complex. Nature (1977) 1.12
Genetics, geography and intelligence in the torsion dystonias. Birth Defects Orig Artic Ser (1971) 1.11
Primary intracranial rhabdomyosarcoma: case report and review of the literature. J Neurooncol (1987) 1.11
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Alphafetoprotein and human chorionic gonadotropin determination in cerebrospinal fluid. An aid to the diagnosis and management of intracranial germ-cell tumors. J Neurosurg (1979) 1.10
Elevated plasma dopamine- -hydroxylase activity in autosomal dominant torsion dystonia. N Engl J Med (1973) 1.10
Cisplatin in the treatment of recurrent childhood primary brain tumors. J Clin Oncol (1988) 1.09
Familial multiple sclerosis: clinical, histocompatibility, and viral serological studies. Ann Neurol (1978) 1.09
A family with histologically confirmed Alzheimer's disease. Arch Neurol (1983) 1.08
Phase I trial of pegylated interferon-alpha-2b in young patients with plexiform neurofibromas. Neurology (2011) 1.08
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A baculovirus homolog of a Cu/Zn superoxide dismutase gene. Virology (1991) 1.07
Isolation and characterization of the antigen of Neisseria gonorrhoeae. Infect Immun (1973) 1.07
Neurofibromatosis type 2 appears to be a genetically homogeneous disease. Am J Hum Genet (1992) 1.07
Analysis of glycosaminoglycans in urine by using acridine orange fluorescence. Biochem J (1978) 1.07
The development of the black blow fly, Phormia regina (Meigen). Forensic Sci Int (2001) 1.06
Clinical, genetic, and biochemical characterization of a Leber hereditary optic neuropathy family containing both the 11778 and 14484 primary mutations. Am J Med Genet (2001) 1.06
Some serum protein and cellular constituents of inflammatory lesions. Collection of exudates in a chamber adhered over skin wounds of rabbits. Johns Hopkins Med J (1967) 1.06
Screening tests for glycosaminoglycans in urine: experience from regional interlaboratory surveys. J Clin Pathol (1988) 1.05
Correlation between the inotropic action of ouabain and its effects on subcellular enzyme systems from canine myocardium. J Pharmacol Exp Ther (1970) 1.05
Dementia of the Alzheimer type: clinical and family study of 22 twin pairs. Neurology (1987) 1.04
Comparison of cefamandole, cephalothin, ampicillin, and chloramphenicol in experimental Escherichia coli meningitis. Antimicrob Agents Chemother (1980) 1.04
Visual impairment in patients with neurofibromatosis 2. Neurology (1993) 1.03
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Intractable facial pain associated with a ganglioglioma of the cervicomedullary junction: report of a case. Neurosurgery (1982) 1.03
Sympathetic ophthalmia, a disappearing disease. JAMA (1969) 1.03
Leukoencephalopathy following high-dose iv methotrexate chemotherapy with leucovorin rescue. Cancer Treat Rep (1980) 1.02
"Baltic" myoclonus epilepsy: hereditary disorder of childhood made worse by phenytoin. Lancet (1983) 1.02
Activation of neurotrophin-3 receptor TrkC induces apoptosis in medulloblastomas. Cancer Res (1999) 1.02