Published in Curr Med Res Opin on January 01, 1980
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A deficiency of both subunits of pyruvate dehydrogenase which is not expressed in fibroblasts. Pediatr Res (1988) 0.91
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Identification of two missense mutations in a dihydrolipoamide dehydrogenase-deficient patient. Proc Natl Acad Sci U S A (1993) 0.89
Characterization of two site-specifically mutated human dihydrolipoamide dehydrogenases (His-452----Gln and Glu-457----Gln). J Biol Chem (1992) 0.89
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Deficiency of dihydrolipoamide dehydrogenase due to two mutant alleles (E340K and G101del). Analysis of a family and prenatal testing. Biochim Biophys Acta (1997) 0.88
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Identification of a common mutation (Gly194Cys) in both Arab Moslem and Ashkenazi Jewish patients with dihydrolipoamide dehydrogenase (E3) deficiency: possible beneficial effect of vitamin therapy. J Inherit Metab Dis (2003) 0.86
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Mutations of the E1beta subunit gene (PDHB) in four families with pyruvate dehydrogenase deficiency. Mol Genet Metab (2008) 0.85
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Chronic hypoxia impairs the differentiation of 3T3-L1 fibroblast in culture: role of sustained protein kinase C activation. J Cell Physiol (1994) 0.84
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Spectroscopic studies of the characterization of recombinant human dihydrolipoamide dehydrogenase and its site-directed mutants. J Biol Chem (1995) 0.84
Experience with the pectoralis major myocutaneous flap for head and neck reconstruction in a general surgical unit. J Postgrad Med (1993) 0.84
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Surgical reversal of vasectomy by vas anastomosis. J Reprod Fertil (1974) 0.83
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Long-term effects of feeding high carbohydrate diet in pre-weaning period by gastrostomy: a new rat model for obesity. Int J Obes Relat Metab Disord (1993) 0.83
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Characterization of the mouse dihydrolipoamide dehydrogenase (Dld) gene: genomic structure, promoter sequence, and chromosomal localization. Genomics (1997) 0.83
Cloning and cDNA sequence of the beta-subunit component of human pyruvate dehydrogenase complex. Gene (1990) 0.83
Wandering spleen. J Postgrad Med (1981) 0.82
Expression of cDNA sequences encoding mature and precursor forms of human dihydrolipoamide dehydrogenase in Escherichia coli. Differences in kinetic mechanisms. J Biol Chem (1991) 0.82
Pentalogy of Fallot with total anomalous pulmonary venous drainage (a case report). J Postgrad Med (1987) 0.82
Diagnosis of venous disorders using impedance plethysmography. J Postgrad Med (1990) 0.82
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Severe combined immunodeficiency--the experience of the Royal Children's Hospital, Melbourne, 1969-1979. Aust Paediatr J (1982) 0.82
Overexpression and characterization of human tetrameric pyruvate dehydrogenase and its individual subunits. Protein Expr Purif (1995) 0.82
Multiple protein-binding domains and functional cis-elements in the 5'-flanking region of the human pyruvate dehydrogenase alpha-subunit gene. Biochemistry (1993) 0.81
Prevention and cure? Or: is an ounce of prevention worth a pound of cure? J Health Econ (1983) 0.81
A long-term high-carbohydrate diet causes an altered ontogeny of pancreatic islets of Langerhans in the neonatal rat. Pediatr Res (2001) 0.81
An investment appraisal of alternative technologies for the treatment of stones in the kidney and ureter. Community Med (1986) 0.81
Induction of dihydrolipoamide dehydrogenase in 3T3-L1 cells during differentiation. Biochem J (1988) 0.81
Homologous canine heart transplantation: a preliminary report of 100 experiments. Indian J Med Res (1965) 0.81
Characterization of the transcriptional regulatory region of the human dihydrolipoamide dehydrogenase gene. Proc Natl Acad Sci U S A (1992) 0.80
A structural model for human dihydrolipoamide dehydrogenase. Proteins (1992) 0.80