Published in J Lab Clin Med on June 01, 1982
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The large scale isolation of mouse beta-glucuronidase and comparison of allozymes. J Biol Chem (1978) 1.00
A regulatory locus for mouse beta-glucuronidase induction, Gur, controls messenger RNA activity. Science (1979) 0.99
Evidence for liver disease preceding amino acid abnormalities in hereditary tyrosinemia. N Engl J Med (1983) 0.99
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Characterization of two missense mutations in human galactose-1-phosphate uridyltransferase: different molecular mechanisms for galactosemia. Genomics (1992) 0.99
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Coordinated development of -glucuronidase and -galactosidase in mouse organs. Science (1972) 0.98
Bilateral lucency of the globus pallidus complicating methylmalonic acidemia. Ann Neurol (1986) 0.98
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Necessity of complete intake of phenylalanine-free amino acid mixture for metabolic control of phenylketonuria. J Am Diet Assoc (1999) 0.94
Characterization of a novel biochemical abnormality in galactosemia: deficiency of glycolipids containing galactose or N-acetylgalactosamine and accumulation of precursors in brain and lymphocytes. Biochem Med Metab Biol (1991) 0.94
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Regulation of the rate of beta-galactosidase synthese by the Bgs and Bgt loci in the mouse. J Biol Chem (1978) 0.91
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Histidase and histidinemia. Clinical and molecular considerations. Mol Biol Med (1991) 0.90
Molecular characterization of two galactosemia mutations and one polymorphism: implications for structure-function analysis of human galactose-1-phosphate uridyltransferase. Biochemistry (1992) 0.90
The effect of amino acids on host-controlled restriction of lambda phage. Virology (1968) 0.90