Published in Ann Neurol on April 01, 1982
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IgM deposits at nodes of Ranvier in a patient with amyotrophic lateral sclerosis, anti-GM1 antibodies, and multifocal motor conduction block. Ann Neurol (1990) 2.67
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Premorbid weight, body mass, and varsity athletics in ALS. Neurology (2002) 2.23
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Distant effects of local injection of botulinum toxin. Muscle Nerve (1987) 2.02
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Benign infantile mitochondrial myopathy due to reversible cytochrome c oxidase deficiency. Ann Neurol (1983) 1.82
Prevalence of depressive disorders and change over time in late-stage ALS. Neurology (2005) 1.80
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Respiratory distress as the initial manifestation of Werdnig-Hoffmann disease. Pediatrics (1974) 1.76
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Nevus of Ota and leptomeningeal melanocytic lesions. Neurology (1993) 1.66
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Quantitative objective markers for upper and lower motor neuron dysfunction in ALS. Neurology (2007) 1.63
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Muscular dystrophy in young girls. Neurology (1970) 1.60
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Increased expression of the pro-inflammatory enzyme cyclooxygenase-2 in amyotrophic lateral sclerosis. Ann Neurol (2001) 1.55
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Muscle phosphofructokinase deficiency. Arch Neurol (1967) 1.54
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A clinical and genetic study of chronic proximal spinal muscular atrophy. Brain (1975) 1.48
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Drugs, coma, and myoglobinuria. Arch Neurol (1972) 1.47
Autopsy-proven amyotrophic lateral sclerosis, Waldenström's macroglobulinemia, and antibodies to sulfated glucuronic acid paragloboside. Neurology (1995) 1.44
Emery-Dreifuss muscular dystrophy. Ann Neurol (1979) 1.42
The ALSFRSr predicts survival time in an ALS clinic population. Neurology (2005) 1.42
Progressive multifocal leukoencephalopathy in a male homosexual with T-cell immune deficiency. N Engl J Med (1982) 1.41
ALS defeats gabapentin: reflections on another failed treatment. Neurology (2001) 1.41
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Recruitment of the mitochondrial-dependent apoptotic pathway in amyotrophic lateral sclerosis. J Neurosci (2001) 1.35
Prognosis of ocular myasthenia. Ann Neurol (1983) 1.35
Biochemistry of muscle membranes in Duchenne muscular dystrophy. Muscle Nerve (1980) 1.34
Botulinum toxin (BOTOX) for the treatment of "spastic dysphonia" as part of a trial of toxin injections for the treatment of other cranial dystonias. Laryngoscope (1986) 1.33
Changes in carbohydrate substrates, amino acids and ammonia in the brain during insulin-induced hypoglycemia. J Neurochem (1974) 1.33
Möbius syndrome and facioscapulohumeral muscular dystrophy. Arch Neurol (1971) 1.32
Celiac neuropathy. Neurology (2003) 1.31
Specificity of mouse and human monoclonal antibodies to myelin-associated glycoprotein. Neurology (1984) 1.30
Controversies about the treatment of myasthenia gravis. J Neurol Neurosurg Psychiatry (1980) 1.30
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A rational approach to total thymectomy in the treatment of myasthenia gravis. Ann Thorac Surg (1977) 1.28
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Experimental conduction block induced by serum from a patient with anti-GM1 antibodies. Ann Neurol (1992) 1.23
Dystrophinopathy in isolated cases of myopathy in females. Neurology (1992) 1.23
Metastatic carcinoma to the pituitary gland. Br J Neurosurg (1989) 1.22
Cramps, spasms and muscle stiffness. Rev Neurol (Paris) (1985) 1.22
The prognosis of acute polyradiculoneuritis. Neurology (1968) 1.22
The sympathetic skin response: normal values, elucidation of afferent components and application limits. J Neurol Sci (1988) 1.22
Cerebral energy state in insulin-induced hypoglycemia, related to blood glucose and to EEG. J Neurochem (1974) 1.21
Familial aggregation of amyotrophic lateral sclerosis, dementia, and Parkinson's disease: evidence of shared genetic susceptibility. Neurology (1994) 1.20
Clinical syndromes associated with ragged red fibers. Rev Neurol (Paris) (1991) 1.20
Physical and kinetic properties of human phosphofructokinase from skeletal muscle and erythrocytes. J Biol Chem (1969) 1.19
Normal pressure hydrocephalus and hypertensive cerebrovascular disease. Arch Neurol (1974) 1.19