Published in Am J Dis Child on December 01, 1982
Improved survival at low lung function in cystic fibrosis: cohort study from 1990 to 2007. BMJ (2011) 1.74
Energy content of stools in normal healthy controls and patients with cystic fibrosis. Arch Dis Child (1991) 1.71
Comparison of four pancreatic extracts in cystic fibrosis. Arch Dis Child (1987) 1.38
Enteric coated microspheres of pancreatin in the treatment of cystic fibrosis: comparison with a standard enteric coated preparation. Thorax (1987) 1.15
Cystic fibrosis--a gastroenterological cornucopia. Gut (1987) 1.11
Two enteric coated microspheres in cystic fibrosis. Arch Dis Child (1990) 0.77
Pancreatic enzyme replacement therapy for pancreatic exocrine insufficiency in the 21(st) century. World J Gastroenterol (2014) 0.76
Influence of antacid and formulation on effectiveness of pancreatic enzyme supplementation in cystic fibrosis. Arch Dis Child (1987) 0.75
Hyaline membrane disease. Am Rev Respir Dis (1975) 3.20
Nutritional benefits of neonatal screening for cystic fibrosis. Wisconsin Cystic Fibrosis Neonatal Screening Study Group. N Engl J Med (1997) 2.91
Acceleration of lung disease in children with cystic fibrosis after Pseudomonas aeruginosa acquisition. Pediatr Pulmonol (2001) 2.59
Nutritional assessment and management in cystic fibrosis: a consensus report. The Consensus Committee. Am J Clin Nutr (1992) 2.36
Comprehensive analysis of risk factors for acquisition of Pseudomonas aeruginosa in young children with cystic fibrosis. Pediatr Pulmonol (1998) 2.22
Newborn screening for cystic fibrosis is complicated by age-related decline in immunoreactive trypsinogen levels. Pediatrics (1990) 2.19
Risk of persistent growth impairment after alternate-day prednisone treatment in children with cystic fibrosis. N Engl J Med (2000) 1.78
Nutritional status of infants with cystic fibrosis associated with early diagnosis and intervention. Am J Clin Nutr (1991) 1.66
Genetic counseling and neonatal screening for cystic fibrosis: an assessment of the communication process. Pediatrics (2001) 1.58
Growth status in children with cystic fibrosis based on the National Cystic Fibrosis Patient Registry data: evaluation of various criteria used to identify malnutrition. J Pediatr (1998) 1.57
Brain damage induced by prenatal exposure to dexamethasone in fetal rhesus macaques. I. Hippocampus. Brain Res Dev Brain Res (1990) 1.51
Physiologic jaundice: the enterohepatic circulation of bilirubin. N Engl J Med (1971) 1.51
Parents' knowledge of neonatal screening and response to false-positive cystic fibrosis testing. J Dev Behav Pediatr (1992) 1.47
Plasma tocopherol levels and tocopherol-lipid relationships in a normal population of children as compared to healthy adults. Am J Clin Nutr (1978) 1.36
Cystic fibrosis newborn screening: impact on reproductive behavior and implications for genetic counseling. Pediatrics (1998) 1.32
Tracheal mucociliary transport in patients with cystic fibrosis and its stimulation by terbutaline. Am Rev Respir Dis (1975) 1.28
The occurrence and effects of human vitamin E deficiency. A study in patients with cystic fibrosis. J Clin Invest (1977) 1.25
Clinical and roentgenographic scoring systems for assessing bronchopulmonary dysplasia. Am J Dis Child (1984) 1.24
The magnitude and challenge of false-positive newborn screening test results. Arch Pediatr Adolesc Med (2000) 1.23
Acquisition of Pseudomonas aeruginosa in children with cystic fibrosis. Pediatrics (1997) 1.23
Newborn screening for cystic fibrosis in Wisconsin: comparison of biochemical and molecular methods. Pediatrics (1997) 1.22
Application of DNA analysis in a population-screening program for neonatal diagnosis of cystic fibrosis (CF): comparison of screening protocols. Am J Hum Genet (1993) 1.19
Epidemiology of hyaline membrane disease in the United States: analysis of national mortality statistics. Pediatrics (1976) 1.18
Analysis of United States neonatal mortality statistics from 1968 to 1974, with specific reference to changing trends in major causalities. Am J Obstet Gynecol (1977) 1.15
A case report and literature review of "primary" pulmonary histiocytosis X of childhood. Med Pediatr Oncol (1986) 1.14
A prospective randomized trial of early diagnosis and treatment of cystic fibrosis: a unique ethical dilemma. Clin Res (1989) 1.14
Wisconsin cystic fibrosis chest radiograph scoring system. Pediatrics (1993) 1.14
Familial nonhemolytic jaundice with late onset of neurological damage. Pediatrics (1968) 1.13
Wisconsin cystic fibrosis chest radiograph scoring system: validation and standardization for application to longitudinal studies. Pediatr Pulmonol (2000) 1.12
The incidence of cystic fibrosis. Stat Med (1996) 1.11
Induction of choline phosphotransferase and lecithin synthesis in the fetal lung by corticosteroids. Science (1973) 1.10
Appendiceal abscess in cystic fibrosis. A diagnostic challenge. Gastroenterology (1984) 1.08
Newborn screening for cystic fibrosis. The Cystic Fibrosis Neonatal Screening Study Group. Adv Pediatr (1992) 1.06
Immunoreactive trypsinogen screening for cystic fibrosis: characterization of infants with a false-positive screening test. Pediatr Pulmonol (1989) 1.06
Early immune response to the components of the type III system of Pseudomonas aeruginosa in children with cystic fibrosis. J Clin Microbiol (2005) 1.04
Analysis of causes of neonatal death in the United States with specific emphasis on fatal hyaline membrane disease. Pediatrics (1982) 1.04
Discordance between male and female deaths due to the respiratory distress syndrome. Pediatrics (1986) 1.04
Influence of binding on the toxicity of bilirubin. Ann N Y Acad Sci (1973) 1.03
Mortality risk of exchange transfusion. Pediatrics (1968) 1.03
Bilirubin nephropathy in the Gunn strain of rat. Am J Physiol (1967) 1.02
Hemin: levels in experimental subarachnoid hematoma and effects on dissociated vascular smooth-muscle cells. J Neurosurg (1993) 1.02
Fatty acid abnormalities in cystic fibrosis. Pediatr Res (1985) 1.01
Nutritional status of patients with cystic fibrosis with meconium ileus: a comparison with patients without meconium ileus and diagnosed early through neonatal screening. Pediatrics (2000) 1.00
Studies in kernicterus. 3. The saturation of serum proteins with bilirubin during neonatal life and its relationship to brain damage at five years. J Pediatr (1970) 1.00
Demineralization in cystic fibrosis detected by direct photon absorptiometry. Am J Dis Child (1979) 1.00
Comparison of growth status of patients with cystic fibrosis between the United States and Canada. Am J Clin Nutr (1999) 1.00
"Physiologic" hyperbilirubinemia in the neonatal period. N Engl J Med (1967) 0.98
Measurement of free choline concentrations in maternal and neonatal blood by micropyrolysis gas chromatography. Clin Chim Acta (1985) 0.96
Newborn screening: principles and practice. Adv Pediatr (1996) 0.95
Diminished pulmonary lecithin synthesis in acidosis: experimental findings as related to the respiratory distress syndrome. Pediatrics (1976) 0.93
Studies in kernicterus. II. The determination of the saturation of serum albumin with bilirubin. J Pediatr (1969) 0.92
Utilization of glycogen for phospholipid synthesis in fetal rat lung. Biochim Biophys Acta (1982) 0.92
Maternal betamethasone and fetal growth and development in the monkey. Am J Obstet Gynecol (1977) 0.92
Predigested formula for infants with cystic fibrosis. J Am Diet Assoc (1987) 0.91
Psychological impact of false-positive results when screening for cystic fibrosis. Pediatr Pulmonol Suppl (1991) 0.90
Distribution of spermidine and spermine in blood from cystic fibrosis patients and control subjects. Blood (1976) 0.90
The choline incorporation pathway: primary mechanism for de novo lecithin synthesis in fetal primate lung. Pediatr Res (1975) 0.90
CFTR mutation analysis and haplotype associations in CF patients. Mol Genet Metab (2011) 0.89
State-to-state variations in newborn screening policies. Arch Pediatr Adolesc Med (1997) 0.89
Fetal lung development and the influence of glucocorticoids on pulmonary surfactant. J Steroid Biochem (1977) 0.89
The influence of bicarbonate administration on blood pH in a "closed system": clinical implications. J Pediatr (1972) 0.88
Cortisol-dihydrotachysterol antagonism in a patient with hypoparathyroidism and adrenal insufficiency: apparent inhibition of bone resorption. J Clin Endocrinol Metab (1976) 0.87
Current issues in neonatal screening for cystic fibrosis and implications of the CF gene discovery. Pediatr Pulmonol Suppl (1991) 0.86
The "bronze" baby syndrome: a complication of phototherapy. J Pediatr (1972) 0.86
Pseudomonas serology: confusion, controversy, and challenges. Thorax (2006) 0.86
Bilirubin in the liver and kidney in jaundiced rats. Am J Dis Child (1966) 0.86
The effect of bilirubin on the function of hamster small intestine. Pediatr Res (1981) 0.86
The stability of phospholipids in amniotic fluid. Am J Obstet Gynecol (1981) 0.85
Complications of pregnancy and fetal development. Diabetes (1982) 0.85
Granulocyte chemiluminescence in adolescent patients with cystic fibrosis. Am Rev Respir Dis (1982) 0.85
Effect of linoleic acid intake on growth of infants with cystic fibrosis. Am J Clin Nutr (1996) 0.85
Pseudomonas aeruginosa serological analysis in young children with cystic fibrosis diagnosed through newborn screening. Pediatr Pulmonol (2010) 0.84
Early diagnosis of cystic fibrosis: to screen or not to screen--an important question. Pediatrics (1984) 0.84
Perspectives on fetal lung development. Lung (1981) 0.84
25-Hydroxycholecalciferol levels in patients with cystic fibrosis. J Pediatr (1979) 0.83
Hypocalcemia associated with phototherapy in newborn rats: light source dependence. Photochem Photobiol (1983) 0.82
The influence of fatty acids on the binding of bilirubin to albumin. J Lab Clin Med (1977) 0.82
Vitamin E deficiency in premature infants. J Pediatr (1979) 0.82
The photodynamic action of bilirubin on erythrocytes. J Pediatr (1972) 0.82
Use of the hand refractometer in determining total serum proteins of infants and children. J Pediatr (1967) 0.82
Nutritional assessment of infants with cystic fibrosis diagnosed through screening. Pediatr Pulmonol Suppl (1991) 0.81
Severe hemolytic anemia associated with vitamin E deficiency in infants with cystic fibrosis. Implications for neonatal screening. Clin Pediatr (Phila) (1994) 0.81
The biochemistry of fetal lung development. Clin Perinatol (1978) 0.81
Comparison of plasma creatine phosphokinase changes in nutritional and genetic muscular dystrophy in the chicken. Ann N Y Acad Sci (1966) 0.81
Changes in food intake during menstrual cycles and pregnancy of normal and diabetic rhesus monkeys. Diabetologia (1984) 0.81
Correction of linoleic acid deficiency in cystic fibrosis. Pediatr Res (1986) 0.81
A rapid accurate assay for choline kinase. Anal Biochem (1977) 0.81
Fluctuations of unbound whole blood polyamine levels during the menstrual cycle. Proc Soc Exp Biol Med (1976) 0.81
Biochemical maturation of fetal rat lung: a comprehensive study including surfactant determination. Biol Neonate (1987) 0.81
Identification of an N-acetylated microsomal glutathione S-transferase by mass spectrometry. Biochem Pharmacol (1995) 0.80
The distribution and toxicity of bilirubin. E. Mead Johnson address 1969. Pediatrics (1970) 0.80