Published in Biochim Biophys Acta on April 02, 1975
Inverted terminal repetitions of the two linear DNA associated with the killer character of the yeast Kluyveromyces lactis. Nucleic Acids Res (1983) 1.31
Complete sequence of the mitochondrial genome of Tetrahymena thermophila and comparative methods for identifying highly divergent genes. Nucleic Acids Res (2003) 0.93
The hepatitis delta (delta) virus possesses a circular RNA. Nature (1986) 4.00
Biochemistry of peroxisomes. Annu Rev Biochem (1992) 3.51
Excised group II introns in yeast mitochondria are lariats and can be formed by self-splicing in vitro. Cell (1986) 3.23
Subunits of the translation initiation factor eIF2B are mutant in leukoencephalopathy with vanishing white matter. Nat Genet (2001) 3.05
HeLa nuclear protein recognizing DNA termini and translocating on DNA forming a regular DNA-multimeric protein complex. J Mol Biol (1989) 2.73
An insert in the single gene for the large ribosomal RNA in yeast mitochondrial DNA. Nature (1978) 2.53
Identification of genes involved in DNA replication of the Autographa californica baculovirus. Proc Natl Acad Sci U S A (1994) 2.48
The organization of ribosomal RNA genes in the mitochondrial DNA of Tetrahymena pyriformis strain ST. Biochim Biophys Acta (1978) 2.42
The restriction fragment map of rat-liver mitochondrial DNA: a reconsideration. Biochim Biophys Acta (1977) 2.17
Electron microscopy of chromatin subunit particles. Biochem Biophys Res Commun (1974) 2.17
Peroxisomal disorders: a newly recognised group of genetic diseases. Eur J Pediatr (1986) 2.05
Human peroxisomal 3-oxoacyl-coenzyme A thiolase deficiency. Proc Natl Acad Sci U S A (1987) 1.98
Purification, morphometric analysis, and characterization of the glycosomes (microbodies) of the protozoan hemoflagellate Trypanosoma brucei. J Cell Biol (1984) 1.82
Activity of peroxisomal enzymes and intracellular distribution of catalase in Zellweger syndrome. Biochem Biophys Res Commun (1984) 1.77
Sequence and organization of the Spodoptera exigua multicapsid nucleopolyhedrovirus genome. J Gen Virol (1999) 1.74
Some yeast mitochondrial RNAs are circular. Cell (1980) 1.73
Role of insulin receptors in the changing metabolism of adipose tissue during pregnancy and lactation in the rat. Biochem J (1979) 1.73
Genetic heterogeneity in the cerebrohepatorenal (Zellweger) syndrome and other inherited disorders with a generalized impairment of peroxisomal functions. A study using complementation analysis. J Clin Invest (1988) 1.68
A new peroxisomal disorder with enlarged peroxisomes and a specific deficiency of acyl-CoA oxidase (pseudo-neonatal adrenoleukodystrophy). Am J Hum Genet (1988) 1.59
Identification and organization of carbon dioxide fixation genes in Xanthobacter flavus H4-14. Mol Gen Genet (1991) 1.56
Mutations of MLC1 (KIAA0027), encoding a putative membrane protein, cause megalencephalic leukoencephalopathy with subcortical cysts. Am J Hum Genet (2001) 1.56
Splicing of large ribosomal precursor RNA and processing of intron RNA in yeast mitochondria. Cell (1984) 1.52
Human dihydroxyacetonephosphate acyltransferase deficiency: a new peroxisomal disorder. J Inherit Metab Dis (1992) 1.50
A novel baculovirus envelope fusion protein with a proprotein convertase cleavage site. Virology (2000) 1.50
Rhizomelic chondrodysplasia punctata with isolated DHAP-AT deficiency. Arch Dis Child (1993) 1.47
Variation, transcription and circular RNAs of the mitochondrial gene for subunit I of cytochrome c oxidase. J Mol Biol (1983) 1.43
Purification and some properties of nitrate reductase (EC 1.7.99.4) from Escherichia coli K12. Biochem J (1976) 1.42
DNA rearrangements involving the genes for variant antigens in Trypanosoma brucei. Cold Spring Harb Symp Quant Biol (1981) 1.41
Delay in diagnosis of X-linked adrenoleukodystrophy. Clin Neurol Neurosurg (1993) 1.40
Peroxisomal disorders: a review. J Neuropathol Exp Neurol (1995) 1.37
Peroxisomal disorders in neurology. J Neurol Sci (1988) 1.36
Severe plasmalogen deficiency in tissues of infants without peroxisomes (Zellweger syndrome). Nature (1983) 1.35
Tomato spotted wilt virus Infection Improves Host Suitability for Its Vector Frankliniella occidentalis. Phytopathology (2004) 1.33
Location of two putative origins of DNA replication of Autographa californica nuclear polyhedrosis virus. Virology (1993) 1.33
Plasma placenta growth factor levels in midtrimester pregnancies. Obstet Gynecol (2001) 1.31
Biosynthesis and maturation of peroxisomal beta-oxidation enzymes in fibroblasts in relation to the Zellweger syndrome and infantile Refsum disease. Proc Natl Acad Sci U S A (1986) 1.31
Measurement of peroxisomal fatty acid beta-oxidation in cultured human skin fibroblasts. J Inherit Metab Dis (1995) 1.31
Non-haem iron and the dissociation of piericidin A sensitivity from site 1 energy conservation in mitochondria from Torulopsis utilis. Biochem J (1971) 1.30
The organization of genes in yeast mitochondrial DNA II. The physical map of EcoRI and HindII + III fragments. Mol Gen Genet (1975) 1.29
Comparison of in vivo and in vitro translation of cowpea mosaic virus RNAs. Biochem Biophys Res Commun (1981) 1.29
Deficiency of acyl-CoA: dihydroxyacetone phosphate acyltransferase in patients with Zellweger (cerebro-hepato-renal) syndrome. Biochem Biophys Res Commun (1984) 1.28
Peroxisomal beta-oxidation enzyme proteins in the Zellweger syndrome. Biochem Biophys Res Commun (1985) 1.28
Pharmacologic rescue of lethal seizures in mice deficient in succinate semialdehyde dehydrogenase. Nat Genet (2001) 1.28
Plasmalogen biosynthesis in peroxisomal disorders: fatty alcohol versus alkylglycerol precursors. J Lipid Res (1988) 1.27
Metabolism of sheep adipose tissue during pregnancy and lactation. Adaptation and regulation. Biochem J (1981) 1.26
Reexamination of functional subdivisions of the rodent prefrontal cortex. Exp Neurol (1983) 1.26
2-Methylbutyryl-coenzyme A dehydrogenase deficiency: a new inborn error of L-isoleucine metabolism. Pediatr Res (2000) 1.25
Isolation and characterization of genomic clones covering the chicken vitellogenin gene. Nucleic Acids Res (1981) 1.25
Prolactin and the regulation of adipose-tissue metabolism during lactation in rats. Mol Cell Endocrinol (1981) 1.24
The cowpea mosaic virus M RNA-encoded 48-kilodalton protein is responsible for induction of tubular structures in protoplasts. J Virol (1993) 1.23
The nonstructural NSm protein of tomato spotted wilt virus induces tubular structures in plant and insect cells. Virology (1995) 1.21
The segregation of kinetoplast DNA networks in Trypanosoma brucei. Plasmid (1980) 1.21
Acyl-CoA:dihydroxyacetone phosphate acyltransferase in human skin fibroblasts: study of its properties using a new assay method. Biochim Biophys Acta (1986) 1.20
Beta-ketothiolase deficiency in a family confirmed by in vitro enzymatic assays in fibroblasts. Eur J Pediatr (1982) 1.19
Three functionally diverged major structural proteins of white spot syndrome virus evolved by gene duplication. J Gen Virol (2000) 1.19
Identification of seven putative origins of Autographa californica multiple nucleocapsid nuclear polyhedrosis virus DNA replication. J Gen Virol (1993) 1.19
The structure of kinetoplast DNA. 1. The mini-circles of Crithidia lucilae are heterogeneous in base sequence. Eur J Biochem (1976) 1.18
Lipolysis in rat adipocytes during pregnancy and lactation. The response to noradrenaline. Biochem J (1982) 1.16
L-2-hydroxyglutaric acidemia: a novel inherited neurometabolic disease. Ann Neurol (1992) 1.16
The human thyroglobulin gene contains two 15-17 kb introns near its 3'-end. Nucleic Acids Res (1983) 1.15
Prenatal diagnosis of succinic semialdehyde dehydrogenase deficiency: increased accuracy employing DNA, enzyme, and metabolite analyses. Mol Genet Metab (2001) 1.14
Penetrating head injury in young adulthood exacerbates cognitive decline in later years. J Neurosci (1989) 1.14
Biochemical studies in the liver and muscle of patients with Zellweger syndrome. Pediatr Res (1983) 1.13
Presence of peroxisomal membrane proteins in liver and fibroblasts from patients with the Zellweger syndrome and related disorders: evidence for the existence of peroxisomal ghosts. Eur J Cell Biol (1989) 1.13
The structure of kinetoplast DNA. I. Properties of the intact multi-circular complex from Crithidia luciliae. Biochim Biophys Acta (1975) 1.13
X-linked cardioskeletal myopathy and neutropenia (Barth syndrome): respiratory-chain abnormalities in cultured fibroblasts. J Inherit Metab Dis (1996) 1.13
Distribution and localization of bean common mosaic virus and bean black root virus in stems of doubly infected bean plants. Arch Virol (1994) 1.13
Growth yields of Torulopsis utilis grown in continuous culture with glycerol or iron as the growth-limiting nutrient. Biochem J (1971) 1.13
Postnatal diagnosis of peroxisomal disorders: a biochemical approach. Biochimie (1993) 1.13
Electron-paramagnetic-resonance studies on the molybdenum of nitrate reductase from Escherichia coli K12. Biochem J (1976) 1.12
Functional mapping of regions of the Autographa californica nuclear polyhedrosis viral genome required for DNA replication. Virology (1994) 1.12
Interlocked RNA circle formation by a self-splicing yeast mitochondrial group I intron. Cell (1987) 1.11
Electron microscopic and biochemical characterization of fraction I protein. Science (1965) 1.11
The movement proteins of cowpea mosaic virus and cauliflower mosaic virus induce tubular structures in plant and insect cells. J Gen Virol (1996) 1.09
The structure of Tetrahymena pyriformis mitochondrial DNA. I. Strain differences and occurrence of inverted repetitions. Biochim Biophys Acta (1977) 1.09
Kinetics of the assembly of peroxisomes after fusion of complementary cell lines from patients with the cerebro-hepato-renal (Zellweger) syndrome and related disorders. Biochem Biophys Res Commun (1988) 1.08
Self-splicing of a group II intron in yeast mitochondria: dependence on 5' exon sequences. EMBO J (1987) 1.07
Leigh syndrome associated with a deficiency of the pyruvate dehydrogenase complex: results of treatment with a ketogenic diet. Neuropediatrics (1992) 1.07
Rhizomelic chondrodysplasia punctata: another peroxisomal disorder. N Engl J Med (1985) 1.05
Fine structure of the 21S ribosomal RNA region on yeast mitochondrial DNA. II. The organization of sequences in petite mitochondrial DNAs carrying genetic markers from the 21S region. Mol Gen Genet (1979) 1.05
Potato leafroll virus binds to the equatorial domain of the aphid endosymbiotic GroEL homolog. J Virol (1998) 1.05
Properties of mitochondrial DNA from Kluyveromyces lactis. Biochim Biophys Acta (1974) 1.05
Direct demonstration that the deficient oxidation of very long chain fatty acids in X-linked adrenoleukodystrophy is due to an impaired ability of peroxisomes to activate very long chain fatty acids. Biochem Biophys Res Commun (1988) 1.04
Spodoptera exigua multicapsid nucleopolyhedrovirus deletion mutants generated in cell culture lack virulence in vivo. J Gen Virol (1996) 1.04
Elevation of protein kinase A and protein kinase C activities in malignant as compared with normal human breast tissue. Eur J Cancer (1996) 1.03
Genes coding for the elongation factor EF-1 alpha in Artemia. Eur J Biochem (1986) 1.03
The localization of mitochondrial creatine kinase, and its use for the determination of the sidedness of submitochondrial particles. Biochim Biophys Acta (1973) 1.03
Human alkyldihydroxyacetonephosphate synthase deficiency: a new peroxisomal disorder. J Inherit Metab Dis (1994) 1.02
Cloning and sequencing of the peroxisomal amine oxidase gene from Hansenula polymorpha. Biochim Biophys Acta (1989) 1.02
Efficient reverse transcription of cowpea mosaic virus RNAs. Nucleic Acids Res (1978) 1.02
Evidence that glucagon-mediated inhibition of acetyl-CoA carboxylase in isolated adipocytes involves increased phosphorylation of the enzyme by cyclic AMP-dependent protein kinase. Biochem J (1985) 1.02
The gene for leukoencephalopathy with vanishing white matter is located on chromosome 3q27. Am J Hum Genet (1999) 1.01
Rhizomelic chondrodysplasia punctata. Deficiency of 3-oxoacyl-coenzyme A thiolase in peroxisomes and impaired processing of the enzyme. J Clin Invest (1990) 1.01
Regulation of acetyl-CoA carboxylase in rat mammary gland. Effects of incubation with Ca2+, Mg2+ and ATP on enzyme activity in tissue extracts. Biochem J (1981) 1.01
Clinical and magnetic resonance imaging features of L-2-hydroxyglutaric acidemia: report of three cases in comparison with Canavan disease. J Child Neurol (1996) 1.00