Anaesthesia for the porphyric patient.

PubWeight™: 3.12‹?› | Rank: Top 1%

🔗 View Article (PMID 8292131)

Published in Anaesthesia on May 01, 1993

Authors

G G Harrison1, P N Meissner, R J Hift

Author Affiliations

1: Department of Medicine, University of Cape Town, Observatory, South Africa.

Articles by these authors

The acute porphyrias. Lancet (1997) 1.80

A R59W mutation in human protoporphyrinogen oxidase results in decreased enzyme activity and is prevalent in South Africans with variegate porphyria. Nat Genet (1996) 1.78

The prevention of hepatitis. S Afr Med J (1994) 1.67

Liver disease in erythropoietic protoporphyria: insights and implications for management. Gut (2007) 1.31

A structured assessment of newly qualified medical graduates. Med Educ (2005) 1.28

Porphyrias. Br J Anaesth (2000) 1.19

Purification of and kinetic studies on a cloned protoporphyrinogen oxidase from the aerobic bacterium Bacillus subtilis. Arch Biochem Biophys (1998) 0.95

Molecular characterization of erythropoietic protoporphyria in South Africa. Br J Dermatol (2008) 0.92

Protoporphyrinogen oxidase and porphobilinogen deaminase in variegate porphyria. Eur J Clin Invest (1986) 0.89

Homozygous variegate porphyria: an evolving clinical syndrome. Postgrad Med J (1993) 0.88

A systematic study of the clinical and biochemical expression of variegate porphyria in a large South African family. Br J Dermatol (2004) 0.87

Homozygous variegate porphyria in South Africa: genotypic analysis in two cases. Mol Genet Metab (2000) 0.86

Variegate porphyria. Semin Liver Dis (1998) 0.84

Liver disease in erythropoietic protoporphyria: insights and implications for management. Postgrad Med J (2007) 0.82

The effect of oral activated charcoal on the course of congenital erythropoietic porphyria. Br J Dermatol (1993) 0.82

Treatment of acute porphyria. Hosp Med (2001) 0.82

Hepatoerythropoietic porphyria precipitated by viral hepatitis. Gut (1993) 0.81

Identification of the first variegate porphyria mutation in an indigenous black South African and further evidence for heterogeneity in variegate porphyria. Mol Genet Metab (2001) 0.81

Propofol as an i.v. anaesthetic induction agent in variegate porphyria. Br J Anaesth (1991) 0.80

Inhibition of mammalian protoporphyrinogen oxidase by acifluorfen. Biochem Mol Biol Int (1994) 0.79

Drugs in the acute porphyrias--toxicogenetic diseases. Cell Mol Biol (Noisy-le-grand) (1997) 0.78

Variegate porphyria in South Africa, 1688-1996--new developments in an old disease. S Afr Med J (1997) 0.77

Safety and efficacy of interferon alpha-2b following prednisone withdrawal in the treatment of chronic viral hepatitis B. A case-controlled, randomised study. S Afr Med J (1992) 0.77

Porphyrinogenicity of etomidate and ketamine as continuous infusions. Screening in the DDC-primed rat model. Br J Anaesth (1985) 0.77

Detection of four mutations in six unrelated South African patients with acute intermittent porphyria. Mol Cell Probes (1996) 0.77

Purification of human erythrocyte porphobilinogen deaminase. S Afr Med J (1991) 0.77

Identification and characterisation of a deletion (537delAT) in the protoporphyrinogen oxidase gene in a South African variegate porphyria family. Hum Mutat (1998) 0.77

Acute intermittent porphyria: the in vitro expression of mutant hydroxymethylbilane synthase. Mol Cell Probes (1997) 0.76

Safety of vancomycin in acute porphyria. Br J Clin Pharmacol (1990) 0.75

A jaundiced look at the management of hepatitis? S Afr Med J (1997) 0.75

Porphyria cutanea tarda: the etiological importance of mutations in the HFE gene and viral infection is population-dependent. Cell Mol Biol (Noisy-le-grand) (2002) 0.75

Primary biliary cirrhosis. A retrospective survey at Groote Schuur Hospital, Cape Town. S Afr Med J (1990) 0.75

The expression of protoporphyrinogen oxidase in human tissues. Cell Mol Biol (Noisy-le-grand) (2009) 0.75

Identification of two novel mutations in the hydroxymethylbilane synthase gene in three patients from two unrelated families with acute intermittent porphyria. Hum Hered (1998) 0.75

Administration of oral activated charcoal in variegate porphyria results in a paradoxical clinical and biochemical deterioration. Br J Dermatol (2003) 0.75

Uroporphyrinogen decarboxylase and protoporphyrinogen oxidase in dual porphyria. S Afr Med J (1989) 0.75

Diagnosis of variegate porphyria at birth by demonstration of the R59W mutation. S Afr Med J (1997) 0.75

Primary pyogenic psoas abscess. A case report. S Afr J Surg (1986) 0.75

Acute intermittent porphyria--an underdiagnosed cause of abdominal pain. S Afr Med J (1989) 0.75

Mapping of the variegate porphyria (VP) gene: contradictory evidence for linkage between VP and microsatellite markers at chromosome 14q32. Hum Genet (1996) 0.75

Carbamazepine and haem biosynthesis. Lancet (1983) 0.75

Prophylaxis and treatment of malaria in people with the acute porphyrias. S Afr Med J (1988) 0.75

Acute liver failure. S Afr Med J (1992) 0.75

The clinical diagnosis, prevention and management of the hepatic porphyrias. Trop Gastroenterol (1997) 0.75