Published in Biochemistry on March 23, 1999
Multi-system neurological disease is common in patients with OPA1 mutations. Brain (2010) 5.37
PROTHROMBIN DEFICIENCY AND THE EFFECTS OF VITAMIN K IN OBSTRUCTIVE JAUNDICE AND BILIARY FISTULA. Ann Surg (1939) 3.88
Autoantibodies to ganglionic acetylcholine receptors in autoimmune autonomic neuropathies. N Engl J Med (2000) 3.57
Management of Massively Bleeding Peptic Ulcer. Ann Surg (1948) 3.53
SACRO-COCCYGEAL CHORDOMA. Ann Surg (1927) 3.37
Amino acid control of asparagine synthetase: relation to asparaginase resistance in human leukemia cells. Am J Physiol (1997) 2.05
CLINICAL SIGNIFICANCE OF PROTHROMBIN DEFICIENCY AND ITS TREATMENT. Ann Surg (1941) 2.01
Evaluation of the HCFA model for the analysis of mortality following hospitalization. Health Serv Res (1992) 1.99
Screening for carriers of Tay-Sachs disease among Ashkenazi Jews. A comparison of DNA-based and enzyme-based tests. N Engl J Med (1990) 1.78
New insight into the catalytic mechanism of chorismate mutases from structural studies. Chem Biol (1995) 1.68
Nucleotide sequence of Escherichia coli asnB and deduced amino acid sequence of asparagine synthetase B. J Biol Chem (1990) 1.67
Characterization of the human HEXB gene encoding lysosomal beta-hexosaminidase. Genomics (1988) 1.60
Three-dimensional structure of Escherichia coli asparagine synthetase B: a short journey from substrate to product. Biochemistry (1999) 1.56
Activation of the human asparagine synthetase gene by the amino acid response and the endoplasmic reticulum stress response pathways occurs by common genomic elements. J Biol Chem (2000) 1.51
Serotonin Release Following Instillation of Hypertonic Glucose into the Proximal Intestine. Ann Surg (1962) 1.38
The clinical, histochemical, and molecular spectrum of PEO1 (Twinkle)-linked adPEO. Neurology (2010) 1.36
Transfer of monoclonal antibodies into mammalian cells by electroporation. J Biol Chem (1989) 1.25
Analysis of expressed sequence tags from Plasmodium falciparum. Mol Biochem Parasitol (1994) 1.23
Mechanistic issues in asparagine synthetase catalysis. Adv Enzymol Relat Areas Mol Biol (1998) 1.21
Cloning and characterization of subunit genes of ribonucleotide reductase, a cell-cycle-regulated enzyme, from Plasmodium falciparum. Proc Natl Acad Sci U S A (1993) 1.20
Expression of human asparagine synthetase in Escherichia coli. J Biol Chem (1989) 1.16
A relationship between asparagine synthetase A and aspartyl tRNA synthetase. J Biol Chem (1992) 1.13
Transcriptional regulation of the human asparagine synthetase gene by carbohydrate availability. Biochem J (1999) 1.13
Activation of the unfolded protein response pathway induces human asparagine synthetase gene expression. J Biol Chem (1999) 1.12
Observations on the Severely Wounded in Forward Field Hospitals: With Special Reference to Wound Shock. Ann Surg (1945) 1.12
A syndrome of asymmetric limb weakness with motor conduction block. Neurology (1990) 1.08
Current status of the Plasmodium falciparum genome project. Mol Biochem Parasitol (1996) 1.08
Glutamine-dependent nitrogen transfer in Escherichia coli asparagine synthetase B. Searching for the catalytic triad. J Biol Chem (1994) 1.08
Isolation and Antigenic Characterization of Corn Mitochondrial F(1)-ATPase. Plant Physiol (1985) 1.04
CONTROL OF POSTOPERATIVE BLEEDING IN OBSTRUCTIVE JAUNDICE. Ann Surg (1939) 1.03
Sciatic neuropathies. Br Med J (Clin Res Ed) (1983) 1.01
Gene sequence tags from Plasmodium falciparum genomic DNA fragments prepared by the "genease" activity of mung bean nuclease. Proc Natl Acad Sci U S A (1993) 0.99
Kinetic studies on rat liver and beef heart mitochondrial ATPase. Evidence for nucleotide binding at separate regulatory and catalytic sites. J Biol Chem (1975) 0.98
Exogenous mycoplasmal p37 protein alters gene expression, growth and morphology of prostate cancer cells. Cytogenet Genome Res (2007) 0.98
Lower motor neuron syndrome following radiotherapy. Can J Neurol Sci (1983) 0.96
OPA1 increases the risk of normal but not high tension glaucoma. J Med Genet (2009) 0.95
Tinel's sign and the carpal tunnel syndrome. Br Med J (1978) 0.95
Essential arginyl residues in mitochondrial adenosine triphosphatase. J Biol Chem (1976) 0.95
Normal distributions of thermal and vibration sensory thresholds. Muscle Nerve (1998) 0.95
The N-terminal cysteine of human asparagine synthetase is essential for glutamine-dependent activity. J Biol Chem (1989) 0.94
Characterization of inhibitors acting at the synthetase site of Escherichia coli asparagine synthetase B. Biochemistry (2001) 0.94
Structural basis for amide hydrolysis catalyzed by the 43C9 antibody. J Mol Biol (1999) 0.92
Venom Collection from Honey Bees. Science (1963) 0.90
Arginine 30 and asparagine 74 have functional roles in the glutamine dependent activities of Escherichia coli asparagine synthetase B. J Biol Chem (1994) 0.90
Rat liver 4-hydroxy-2-ketoglutarate aldolase: purification and kinetic characterization. Arch Biochem Biophys (1985) 0.90
The regulation of pyruvate dehydrogenase in isolated beef heart mitochondria. The role of calcium, magnesium, and permeant anions. J Biol Chem (1974) 0.89
Monoclonal antibodies specific for bovine pancreatic asparagine synthetase. Production and use in structural studies. J Biol Chem (1986) 0.89
Kinetic mechanism of Escherichia coli asparagine synthetase B. Biochemistry (1998) 0.89
Periodic alternating gaze. Neurology (1979) 0.89
Monoclonal antibodies specific for mercuric ions. Proc Natl Acad Sci U S A (1992) 0.88
Novel agouti-related-protein-based melanocortin-1 receptor antagonist. J Med Chem (2001) 0.88
Studies on the kinetic mechanism of oxidative phosphorylation. J Biol Chem (1977) 0.88
Studies on the regulation of pyruvate dehydrogenase in isolated beef heart mitochondria. Arch Biochem Biophys (1975) 0.87
Neurospora crassa mutants deficient in asparagine synthetase. J Bacteriol (1983) 0.87
Kinetic Analysis of Corn Mitochondrial F(1)-ATPase. Plant Physiol (1985) 0.87
Mutagenesis and chemical rescue indicate residues involved in beta-aspartyl-AMP formation by Escherichia coli asparagine synthetase B. J Biol Chem (1997) 0.87
Antimalarial activities of polyhydroxyphenyl and hydroxamic acid derivatives. Antimicrob Agents Chemother (1998) 0.87
Occupational cadmium exposure in jig solderers. Br J Ind Med (1986) 0.86
Detection of a catalytic antibody species acylated at the active site by electrospray mass spectrometry. Biochemistry (1995) 0.86
Studies of the energy-dependent uptake of divalent metal ions by beef heart mitochondria. J Biol Chem (1974) 0.86
A novel neurodegenerative disease characterised by posterior column ataxia and pyramidal tract involvement maps to chromosome 8p12-8q12.1. J Med Genet (2004) 0.86
Magnitude estimates of rotational velocity during and following prolonged increasing, constant, and zero angular acceleration. J Exp Psychol (1968) 0.86
Control of oxidative stress by the Keap1-Nrf2 pathway. Arch Toxicol (2011) 0.85
Probing the mechanism of nitrogen transfer in Escherichia coli asparagine synthetase by using heavy atom isotope effects. Biochemistry (1996) 0.85
Detection and typing of the virulence determinants cagA and vacA of Helicobacter pylori directly from biopsy DNA: are in vitro strains representative of in vivo strains? Eur J Gastroenterol Hepatol (1998) 0.85
Synthesis, conformational properties, and antibody recognition of peptides containing beta-turn mimetics based on alpha-alkylproline derivatives. J Med Chem (1991) 0.85
Thresholds for the perception of angular acceleration about the three major body axes. Acta Otolaryngol (1970) 0.84
The variable clinical manifestations of ulnar neuropathies at the elbow. J Neurol Neurosurg Psychiatry (1987) 0.84
Metal dependence and thermodynamic characteristics of the beef heart mitochondrial adenosine triphosphatase. J Biol Chem (1984) 0.84
A new assay for L-asparagine synthetase. J Biochem Biophys Methods (1980) 0.84
Comparison of three methods to determine thresholds for perception of angular acceleration. Am J Psychol (1968) 0.84
Antibodies specific for (6-4) DNA photoproducts: cloning, antibody modeling and construction of a single-chain Fv derivative. Biochim Biophys Acta (1998) 0.84
Effect of antenatal exposure to paroxetine (paxil) on growth and physical maturation of mice offspring. J Matern Fetal Med (2000) 0.84
Effects of deuterium on the kinetics of beef heart mitochondrial ATPase. Arch Biochem Biophys (1984) 0.84
A specific quantitative colorimetric assay for L-asparagine. Anal Biochem (1993) 0.84
Recombinant bovine heart mitochondrial F1-ATPase inhibitor protein: overproduction in Escherichia coli, purification, and structural studies. Biochemistry (1993) 0.83
Glutamine inhibits the ammonia-dependent activities of two Cys-1 mutants of human asparagine synthetase through the formation of an abortive complex. J Biol Chem (1993) 0.83
High-level expression of human asparagine synthetase and production of monoclonal antibodies for enzyme purification. Protein Expr Purif (1992) 0.83
Variations of hepatitis B virus core gene sequence in Western patients with chronic hepatitis B virus infection. J Viral Hepat (1997) 0.83
An alternative mechanism for the nitrogen transfer reaction in asparagine synthetase. FEBS Lett (1992) 0.83
Hydrolysis of adenyl-5-yl imidodiphosphate by beef heart mitochondrial ATPase. J Biol Chem (1986) 0.83
Effect of prenatally administered hypericum (St John's wort) on growth and physical maturation of mouse offspring. Am J Obstet Gynecol (2001) 0.82
Acro-osteolysis in a polyvinyl chloride worker with an atypical industrial history. J Soc Occup Med (1975) 0.82
Immunoaffinity chromatography utilizing monoclonal antibodies. Factors which influence antigen-binding capacity. J Immunol Methods (1987) 0.82
Effect of citreoviridin and isocitreoviridin on beef heart mitochondrial ATPase. Arch Biochem Biophys (1989) 0.82
Asymmetric Baeyer-Villiger oxidations of 4-mono- and 4,4-disubstituted cyclohexanones by whole cells of engineered Escherichia coli. J Org Chem (2001) 0.82
Polymorphisms hit the headlines. Arch Toxicol (2012) 0.82
Energy-dependent release of magnesium from beef heart submitochondrial particles. J Biol Chem (1973) 0.82