Published in Chest on April 01, 1999
Effect of Fasting on the Size of Abdominal Lymphatic Tumors in Women | NCT00552955
Mutations in the tuberous sclerosis complex gene TSC2 are a cause of sporadic pulmonary lymphangioleiomyomatosis. Proc Natl Acad Sci U S A (2000) 4.30
The NHLBI lymphangioleiomyomatosis registry: characteristics of 230 patients at enrollment. Am J Respir Crit Care Med (2005) 4.15
Lymphangioleiomyomatosis: calling it what it is: a low-grade, destructive, metastasizing neoplasm. Am J Respir Crit Care Med (2012) 3.42
Molecular and genetic analysis of disseminated neoplastic cells in lymphangioleiomyomatosis. Proc Natl Acad Sci U S A (2004) 2.27
Clinical experience of lymphangioleiomyomatosis in the UK. Thorax (2000) 1.80
Lymphangioleiomyomatosis: what do we know and what are we looking for? Eur Respir Rev (2011) 1.73
Pneumothorax after air travel in lymphangioleiomyomatosis, idiopathic pulmonary fibrosis, and sarcoidosis. Chest (2009) 1.64
Emerging clinical picture of lymphangioleiomyomatosis. Thorax (2005) 1.49
A Novel Quantitative Computed Tomographic Analysis Suggests How Sirolimus Stabilizes Progressive Air Trapping in Lymphangioleiomyomatosis. Ann Am Thorac Soc (2016) 1.40
Survival and disease progression in UK patients with lymphangioleiomyomatosis. Thorax (2004) 1.32
Sporadic lymphangioleiomyomatosis and tuberous sclerosis complex with lymphangioleiomyomatosis: comparison of CT features. Radiology (2006) 1.32
The natural history of lymphangioleiomyomatosis: markers of severity, rate of progression and prognosis. Lymphat Res Biol (2010) 1.27
Challenges in pulmonary fibrosis. 3: Cystic lung disease. Thorax (2007) 1.05
Automated quantification of high-resolution CT scan findings in individuals at risk for pulmonary fibrosis. Chest (2011) 1.03
CT of sclerotic bone lesions: imaging features differentiating tuberous sclerosis complex with lymphangioleiomyomatosis from sporadic lymphangioleiomymatosis. Radiology (2010) 1.00
Lymphangiomyomatosis arising in the pelvic cavity: a case report. J Korean Med Sci (2005) 0.98
Vascular endothelial growth factors C and D induces proliferation of lymphangioleiomyomatosis cells through autocrine crosstalk with endothelium. Am J Pathol (2009) 0.96
Lymphangioleiomyomatosis. MedGenMed (2006) 0.93
Frequency of undiagnosed cystic lung disease in patients with sporadic renal angiomyolipomas. Chest (2011) 0.92
Lymphangioleiomyomatosis (LAM): molecular insights lead to targeted therapies. Respir Med (2010) 0.92
Pulmonary artery pressure in lymphangioleiomyomatosis: an echocardiographic study. Chest (2007) 0.92
Unusual causes of pneumothorax. J Thorac Dis (2014) 0.91
Lymphatics in lymphangioleiomyomatosis and idiopathic pulmonary fibrosis. Eur Respir Rev (2012) 0.90
Effusion cytology: an effective method for the diagnosis of pulmonary lymphangioleiomyomatosis. J Thorac Dis (2014) 0.89
Doxycycline use in patients with lymphangioleiomyomatosis: biomarkers and pulmonary function response. J Bras Pneumol (2013) 0.88
Lymphatic involvement in lymphangioleiomyomatosis. Ann N Y Acad Sci (2008) 0.85
Involvement of lymphatics in lymphangioleiomyomatosis. Lymphat Res Biol (2009) 0.85
Sex-specific lung diseases: effect of oestrogen on cultured cells and in animal models. Eur Respir Rev (2013) 0.85
Reversible airflow obstruction in lymphangioleiomyomatosis. Chest (2009) 0.84
A case of lymphangioleiomyomatosis originated in the pelvic cavity. J Gynecol Oncol (2008) 0.83
Lymphangioleiomyomatosis: a case-control study of perinatal and early life events. Thorax (2003) 0.82
The neural crest lineage as a driver of disease heterogeneity in Tuberous Sclerosis Complex and Lymphangioleiomyomatosis. Front Cell Dev Biol (2014) 0.82
Rare lung diseases I--Lymphangioleiomyomatosis. Can Respir J (2006) 0.80
Desaturation - distance ratio: a new concept for a functional assessment of interstitial lung diseases. Clinics (Sao Paulo) (2010) 0.80
Lymphangioleiomyomatosis Biomarkers Linked to Lung Metastatic Potential and Cell Stemness. PLoS One (2015) 0.79
Perivascular epitheloid cell tumour (PEComa) of the retroperitoneum - a rare tumor with uncertain malignant behaviour: a case report. J Med Case Rep (2009) 0.78
A nationwide survey of lymphangioleiomyomatosis in Korea: recent increase in newly diagnosed patients. J Korean Med Sci (2010) 0.78
Pulmonary hypertension in parenchymal lung disease. Pulm Med (2012) 0.77
Imaging features of lymphangioleiomyomatosis: diagnostic pitfalls. AJR Am J Roentgenol (2011) 0.76
Risk of spontaneous pneumothorax due to air travel and diving in patients with Birt-Hogg-Dubé syndrome. Springerplus (2016) 0.76
Lymphangioleiomyomatosis. Atlas Genet Cytogenet Oncol Haematol (2015) 0.75
Management of refractory chylothorax in pulmonary lymphangioleiomyomatosis. Respirol Case Rep (2015) 0.75
Pulmonary lymphangioleiomyomatosis: unusual manifestations of multiple large pulmonary nodules with retroperitoneal lymph node involvement mimicking metastatic malignancy. BMJ Case Rep (2009) 0.75
Tuberous sclerosis complex presenting as pulmonary lymphangioleiomyomatosis--a clinicoradiological diagnosis. Pan Afr Med J (2015) 0.75
Incidental Nodal Lymphangioleiomyomatosis Is Not a Harbinger of Pulmonary Lymphangioleiomyomatosis: A Study of 19 Cases With Evaluation of Diagnostic Immunohistochemistry. Am J Surg Pathol (2015) 0.75
Sporadic lymphangioleiomyomatosis with bloody sputum as an initial symptom: A case report and review of the literature. Exp Ther Med (2015) 0.75
Primary abdominal lymphangioleiomyomatosis: report of a case. World J Surg Oncol (2015) 0.75
Recurrent pneumothorax in a young female with pulmonary lymphangiomyomatosis: a case report and overview of literature. J Family Med Prim Care (2014) 0.75
Acute constrictive pericarditis after lung transplantation for lymphangioleiomyomatosis. J Heart Lung Transplant (2008) 0.75
A National Heart, Lung, and Blood Institute history and perspective on lymphangioleiomyomatosis. Lymphat Res Biol (2010) 0.75
A case of lymphangioleiomyomatosis with membranous nephropathy and likely systemic lupus. Clin Exp Nephrol (2008) 0.75
Wegener granulomatosis: an analysis of 158 patients. Ann Intern Med (1992) 13.29
Requirement for generation of H2O2 for platelet-derived growth factor signal transduction. Science (1995) 8.17
The new World Health Organization classification of lung tumours. Eur Respir J (2001) 6.91
Age, thymopoiesis, and CD4+ T-lymphocyte regeneration after intensive chemotherapy. N Engl J Med (1995) 6.77
Inflammatory and immune processes in the human lung in health and disease: evaluation by bronchoalveolar lavage. Am J Pathol (1979) 5.94
Isolation of a brefeldin A-inhibited guanine nucleotide-exchange protein for ADP ribosylation factor (ARF) 1 and ARF3 that contains a Sec7-like domain. Proc Natl Acad Sci U S A (1996) 5.84
Herbal medicines and perioperative care. JAMA (2001) 5.05
NIH conference. The idiopathic hypereosinophilic syndrome. Clinical, pathophysiologic, and therapeutic considerations. Ann Intern Med (1982) 4.70
Ras proteins induce senescence by altering the intracellular levels of reactive oxygen species. J Biol Chem (1999) 4.38
Sarcoidosis of the heart. A clinicopathologic study of 35 necropsy patients (group 1) and review of 78 previously described necropsy patients (group 11). Am J Med (1977) 4.34
Histopathologic variability in usual and nonspecific interstitial pneumonias. Am J Respir Crit Care Med (2001) 4.01
A model of angiogenesis in the mouse cornea. Invest Ophthalmol Vis Sci (1996) 3.49
Activation of adenylate cyclase by choleragen. Annu Rev Biochem (1979) 3.16
Interstitial lung disease: current concepts of pathogenesis, staging and therapy. Am J Med (1981) 3.08
Hydrolysis of nicotinamide adenine dinucleotide by choleragen and its A protomer: possible role in the activation of adenylate cyclase. Proc Natl Acad Sci U S A (1976) 2.98
Mechanism of action of choleragen. Evidence for ADP-ribosyltransferase activity with arginine as an acceptor. J Biol Chem (1977) 2.76
Fisp12/mouse connective tissue growth factor mediates endothelial cell adhesion and migration through integrin alphavbeta3, promotes endothelial cell survival, and induces angiogenesis in vivo. Mol Cell Biol (1999) 2.67
Pertussis toxin-catalyzed ADP-ribosylation of transducin. Cysteine 347 is the ADP-ribose acceptor site. J Biol Chem (1985) 2.64
Radiological versus histological diagnosis in UIP and NSIP: survival implications. Thorax (2003) 2.54
Somatostatin receptor scintigraphy: its sensitivity compared with that of other imaging methods in detecting primary and metastatic gastrinomas. A prospective study. Ann Intern Med (1996) 2.51
Myocardial ultrastructure in idiopathic hypertrophic subaortic stenosis. A study of operatively excised left ventricular outflow tract muscle in 14 patients. Circulation (1972) 2.49
The biotin-dependent enzymes. Adv Enzymol Relat Areas Mol Biol (1971) 2.45
Dendritic cells with antigen-presenting capability reside in airway epithelium, lung parenchyma, and visceral pleura. J Exp Med (1986) 2.45
Pleomorphic (spindle/giant cell) carcinoma of the lung. A clinicopathologic correlation of 78 cases. Cancer (1994) 2.43
Mesenchymal precursor cells in the blood of normal individuals. Arthritis Res (2000) 2.37
Nonmuscle myosin II-B is required for normal development of the mouse heart. Proc Natl Acad Sci U S A (1997) 2.35
A clinicopathologic study of 100 cases of pulmonary sclerosing hemangioma with immunohistochemical studies: TTF-1 is expressed in both round and surface cells, suggesting an origin from primitive respiratory epithelium. Am J Surg Pathol (2000) 2.35
Cellular and molecular basis of the asbestos-related diseases. Am Rev Respir Dis (1991) 2.34
Regulation of reactive-oxygen-species generation in fibroblasts by Rac1. Biochem J (1996) 2.31
Prevalence and clinical characteristics of lymphangioleiomyomatosis (LAM) in patients with tuberous sclerosis complex. Am J Respir Crit Care Med (2001) 2.31
Role for mitochondrial oxidants as regulators of cellular metabolism. Mol Cell Biol (2000) 2.22
Intracellular processing of endothelial nitric oxide synthase isoforms associated with differences in severity of cardiopulmonary diseases: cleavage of proteins with aspartate vs. glutamate at position 298. Proc Natl Acad Sci U S A (2000) 2.21
Reactive oxygen species are downstream mediators of p53-dependent apoptosis. Proc Natl Acad Sci U S A (1996) 2.19
Clinical significance of histological classification of idiopathic interstitial pneumonia. Eur Respir J (2002) 2.19
A citation analysis of the Bulletin of the Medical Library Association. Bull Med Libr Assoc (1977) 2.18
Accurate quantification of cells recovered by bronchoalveolar lavage. Am Rev Respir Dis (1984) 2.17
Metastatic mature teratoma in lung following testicular embryonal carcinoma and teratocarcinoma. Arch Pathol Lab Med (1993) 2.16
Long-term in vivo survival of receptor-modified syngeneic T cells in patients with human immunodeficiency virus infection. Blood (2000) 2.15
Functional incorporation of ganglioside into intact cells: induction of choleragen responsiveness. Proc Natl Acad Sci U S A (1976) 2.14
Expression of the cystic fibrosis transmembrane conductance regulator gene in the respiratory tract of normal individuals and individuals with cystic fibrosis. Proc Natl Acad Sci U S A (1991) 2.12
Intraluminal fibrosis in interstitial lung disorders. Am J Pathol (1986) 2.10
Magnetic resonance imaging of cerebral hemiatrophy. J Formos Med Assoc (1993) 2.10
Rapid, reliable ligation-independent cloning of PCR products using modified plasmid vectors. Biotechniques (1992) 2.09
beta2-Adrenergic receptor regulation by GIT1, a G protein-coupled receptor kinase-associated ADP ribosylation factor GTPase-activating protein. Proc Natl Acad Sci U S A (1998) 2.08
New ultrathin-walled endotracheal tube with a novel laryngeal seal design. Long-term evaluation in sheep. Anesthesiology (1996) 2.08
Maintenance of granuloma formation in pulmonary sarcoidosis by T lymphocytes within the lung. N Engl J Med (1980) 2.07
Idiopathic nonspecific interstitial pneumonia: prognostic significance of cellular and fibrosing patterns: survival comparison with usual interstitial pneumonia and desquamative interstitial pneumonia. Am J Surg Pathol (2000) 2.07
Visceral adipose tissue differences in black and white women. Am J Clin Nutr (1995) 2.07
Activation of adenylate cyclase by heat-labile Escherichia coli enterotoxin. Evidence for ADP-ribosyltransferase activity similar to that of choleragen. J Clin Invest (1978) 2.07
Predicting the arrhythmogenic foci of atrial fibrillation before atrial transseptal procedure: implication for catheter ablation. J Cardiovasc Electrophysiol (2000) 2.06
A model for melanosome biogenesis based on the purification and analysis of early melanosomes. Proc Natl Acad Sci U S A (2001) 2.06
A randomized phase II trial of thalidomide, an angiogenesis inhibitor, in patients with androgen-independent prostate cancer. Clin Cancer Res (2001) 2.05
Endothelial nuclear patterns in the canine arterial tree with particular reference to hemodynamic events. Circ Res (1972) 2.03
The association between Internet addiction and psychiatric disorder: a review of the literature. Eur Psychiatry (2011) 2.02
Current status of biomedical book reviewing. II. Time lag in biomedical book reviewing. Bull Med Libr Assoc (1974) 2.00
Molecular identification of ADP-ribosylation factor mRNAs and their expression in mammalian cells. J Biol Chem (1991) 1.99
Solitary pulmonary papillomas in adults: a clinicopathologic and in situ hybridization study of 14 cases combined with 27 cases in the literature. Am J Surg Pathol (1998) 1.99
Acetyl coenzyme A carboxylase system of Escherichia coli. Purification and properties of the biotin carboxylase, carboxyltransferase, and carboxyl carrier protein components. J Biol Chem (1974) 1.99
Mortality variation across Australia: descriptive data for states and territories, and statistical divisions. Aust N Z J Public Health (2000) 1.98
Ultrastructure of pulmonary mast cells in patients with fibrotic lung disorders. Lab Invest (1979) 1.94
Acetyl coenzyme A carboxylase. Curr Top Cell Regul (1974) 1.94
Role of surgery in the treatment of primary carcinoma of the liver: a 31-year experience. Br J Surg (1987) 1.93
Extrapulmonary lymphangioleiomyomatosis (LAM): clinicopathologic features in 22 cases. Hum Pathol (2000) 1.93
New malignant diseases after allogeneic marrow transplantation for childhood acute leukemia. J Clin Oncol (2000) 1.92
Specificity of somatostatin receptor scintigraphy: a prospective study and effects of false-positive localizations on management in patients with gastrinomas. J Nucl Med (1999) 1.92
Characterization of mononuclear phagocyte subpopulations in the human lung by using monoclonal antibodies: changes in alveolar macrophage phenotype associated with pulmonary sarcoidosis. J Immunol (1985) 1.92
Pulmonary function and high-resolution CT findings in patients with an inherited form of pulmonary fibrosis, Hermansky-Pudlak syndrome, due to mutations in HPS-1. Chest (2000) 1.90
Structural features of cardiac myxomas. Histology, histochemistry, and electron microscopy. Hum Pathol (1973) 1.90
Cyr61 and Fisp12 are both ECM-associated signaling molecules: activities, metabolism, and localization during development. Exp Cell Res (1997) 1.88
rac1 regulates a cytokine-stimulated, redox-dependent pathway necessary for NF-kappaB activation. Mol Cell Biol (1996) 1.86
Differences in distribution of myocardial abnormalities in patients with obstructive and nonobstructive asymmetric septal hypertrophy (ASH). Light and electron microscopic findings. Circulation (1974) 1.85
Oxidation of either methionine 351 or methionine 358 in alpha 1-antitrypsin causes loss of anti-neutrophil elastase activity. J Biol Chem (2000) 1.82
Identification of antigens and antibodies specific for Pneumocystis carinii. J Immunol (1988) 1.81
Nitric oxide synthase, cyclooxygenase 2, and vascular endothelial growth factor in the angiogenesis of non-small cell lung carcinoma. Clin Cancer Res (2000) 1.81
Cytokine-mediated transcriptional induction of the human inducible nitric oxide synthase gene requires both activator protein 1 and nuclear factor kappaB-binding sites. J Biol Chem (1998) 1.81
Pathologic anatomy of the cardiomyopathies. Idiopathic dilated and hypertrophic types, infiltrative types, and endomyocardial disease with and without eosinophilia. Hum Pathol (1975) 1.80
Pediatric AIDS-associated lymphocytic interstitial pneumonia and pulmonary arterio-occlusive disease: role of VCAM-1/VLA-4 adhesion pathway and human herpesviruses. Am J Pathol (1999) 1.78
Purification and cloning of a brefeldin A-inhibited guanine nucleotide-exchange protein for ADP-ribosylation factors. J Biol Chem (1999) 1.78
Predictors of mortality in patients with pyogenic liver abscess. Neth J Med (2008) 1.77
Treatment of non-parasitic cystic disease of the liver: a new approach to therapy with polycystic liver. Ann Surg (1968) 1.77
Metabolic function and regeneration of cirrhotic and non-cirrhotic livers after hepatic lobectomy in man. Ann Surg (1965) 1.77
Bronchiolitis obliterans syndrome in popcorn production plant workers. Eur Respir J (2004) 1.75
Activation of rat brain phospholipase D by ADP-ribosylation factors 1,5, and 6: separation of ADP-ribosylation factor-dependent and oleate-dependent enzymes. Proc Natl Acad Sci U S A (1994) 1.74
Intraperitoneal once-daily dose of cefazolin and gentamicin for treating CAPD peritonitis. Perit Dial Int (1997) 1.74
Activation by thiol of the latent NAD glycohydrolase and ADP-ribosyltransferase activities of Bordetella pertussis toxin (islet-activating protein). J Biol Chem (1983) 1.74
Distinctions between CD8+ and CD4+ T-cell regenerative pathways result in prolonged T-cell subset imbalance after intensive chemotherapy. Blood (1997) 1.73
Lymphangioleiomyomatosis: what do we know and what are we looking for? Eur Respir Rev (2011) 1.73
Prophylaxis against ampicillin-associated diarrhea with a lactobacillus preparation. Am J Hosp Pharm (1979) 1.72
Mucinous cystadenoma of the lung. A report of two cases with immunohistochemical and ultrastructural analysis. Arch Pathol Lab Med (1990) 1.71
Identification of MEN1 gene mutations in sporadic carcinoid tumors of the lung. Hum Mol Genet (1997) 1.70
A role for reactive oxygen species in endothelial cell anoikis. Circ Res (1999) 1.69
Psychosocial and psychiatric risk factors for suicide. Case-control psychological autopsy study. Br J Psychiatry (2000) 1.69
Lack of utility of (111)In-pentetreotide scintigraphy in localizing ectopic ACTH producing tumors: follow-up of 18 patients. J Clin Endocrinol Metab (1999) 1.68
Alveolar macrophage replication. One mechanism for the expansion of the mononuclear phagocyte population in the chronically inflamed lung. J Clin Invest (1984) 1.68
Lymphangioleiomyomatosis: CT of diurnal variation of lymphangioleiomyomas. Radiology (2001) 1.67
Stimulation of choleragen enzymatic activities by GTP and two soluble proteins purified from bovine brain. J Biol Chem (1988) 1.67