S G Priori

Author PubWeight™ 68.23‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Genotype-phenotype correlation in the long-QT syndrome: gene-specific triggers for life-threatening arrhythmias. Circulation 2001 7.47
2 Effectiveness and limitations of beta-blocker therapy in congenital long-QT syndrome. Circulation 2000 5.09
3 Long QT syndrome patients with mutations of the SCN5A and HERG genes have differential responses to Na+ channel blockade and to increases in heart rate. Implications for gene-specific therapy. Circulation 1995 4.48
4 Influence of genotype on the clinical course of the long-QT syndrome. International Long-QT Syndrome Registry Research Group. N Engl J Med 1998 3.41
5 Proposed diagnostic criteria for the Brugada syndrome. Eur Heart J 2002 3.01
6 Spectrum of ST-T-wave patterns and repolarization parameters in congenital long-QT syndrome: ECG findings identify genotypes. Circulation 2000 2.95
7 Age- and sex-related differences in clinical manifestations in patients with congenital long-QT syndrome: findings from the International LQTS Registry. Circulation 1998 2.53
8 Cardiac sodium channel mutations in patients with long QT syndrome, an inherited cardiac arrhythmia. Hum Mol Genet 1995 2.30
9 A common polymorphism associated with antibiotic-induced cardiac arrhythmia. Proc Natl Acad Sci U S A 2000 2.26
10 Gene-specific response of dynamic ventricular repolarization to sympathetic stimulation in LQT1, LQT2 and LQT3 forms of congenital long QT syndrome. Eur Heart J 2002 2.17
11 A molecular link between the sudden infant death syndrome and the long-QT syndrome. N Engl J Med 2000 2.02
12 Inherited Brugada and long QT-3 syndrome mutations of a single residue of the cardiac sodium channel confer distinct channel and clinical phenotypes. J Biol Chem 2001 1.78
13 Evidence for a cardiac ion channel mutation underlying drug-induced QT prolongation and life-threatening arrhythmias. J Cardiovasc Electrophysiol 2000 1.74
14 Novel arrhythmogenic mechanism revealed by a long-QT syndrome mutation in the cardiac Na(+) channel. Circ Res 2001 1.72
15 Electrocardiographic prediction of abnormal genotype in congenital long QT syndrome: experience in 101 related family members. J Cardiovasc Electrophysiol 2001 1.71
16 Molecular diagnosis in a child with sudden infant death syndrome. Lancet 2001 1.66
17 Gene-specific differences in the circadian variation of ventricular repolarization in the long QT syndrome: a key to sudden death during sleep? Ital Heart J 2000 1.59
18 New mutations in the KVLQT1 potassium channel that cause long-QT syndrome. Circulation 1998 1.53
19 Inferior vena cava loop of the implantable cardioverter defibrillator endocardial lead: a possible solution of the growth problem in pediatric implantation. Pacing Clin Electrophysiol 2000 1.48
20 Cellular dysfunction of LQT5-minK mutants: abnormalities of IKs, IKr and trafficking in long QT syndrome. Hum Mol Genet 1999 1.43
21 Brugada syndrome and sudden cardiac death in children. Lancet 2000 1.40
22 Comparison of clinical and genetic variables of cardiac events associated with loud noise versus swimming among subjects with the long QT syndrome. Am J Cardiol 1999 1.25
23 Mechanisms of I(Ks) suppression in LQT1 mutants. Am J Physiol Heart Circ Physiol 2000 1.24
24 Protective effect of vagal stimulation on reperfusion arrhythmias in cats. Circ Res 1987 1.20
25 Sympathetic stimulation produces a greater increase in both transmural and spatial dispersion of repolarization in LQT1 than LQT2 forms of congenital long QT syndrome. J Am Coll Cardiol 2001 1.12
26 CaMKII inhibition rectifies arrhythmic phenotype in a patient-specific model of catecholaminergic polymorphic ventricular tachycardia. Cell Death Dis 2013 1.01
27 Torsade de pointes. Mechanisms and management. Drugs 1994 1.01
28 Novel characteristics of a misprocessed mutant HERG channel linked to hereditary long QT syndrome. Am J Physiol Heart Circ Physiol 2000 1.00
29 Exploring the hidden danger of noncardiac drugs. J Cardiovasc Electrophysiol 1998 0.85
30 Sympathetic activation, ventricular repolarization and Ikr blockade: implications for the antifibrillatory efficacy of potassium channel blocking agents. J Am Coll Cardiol 1995 0.83
31 Homozygous deletion in KVLQT1 associated with Jervell and Lange-Nielsen syndrome. Circulation 1999 0.80
32 Clinical profile and genetic basis of Brugada syndrome in the Chinese population. Hong Kong Med J 2004 0.80
33 Brugada syndrome and sudden death. Eur Heart J 2000 0.78
34 [Long QT syndrome and Brugada syndrome: 2 aspects of the same disease?]. Ital Heart J Suppl 2001 0.77
35 Foretelling the future in Brugada syndrome: do we have the crystal ball? J Cardiovasc Electrophysiol 2001 0.76
36 Cardiovascular safety of second-generation antihistamines. Am J Rhinol 1999 0.76
37 Efficacy of diltiazem in two experimental feline models of sudden cardiac death. J Am Coll Cardiol 1986 0.76
38 From catheters to vectors: the dawn of molecular electrophysiology. Nat Med 2000 0.76
39 Is long QT syndrome entering the era of molecular diagnosis? Heart 1997 0.75
40 Multiple comparison of several antiarrhythmic agents by acute oral drug testing in patients with chronic ventricular arrhythmias. Eur Heart J 1988 0.75
41 Efficacy and safety of flecainide in low-risk patients with chronic ventricular arrhythmias: a two-year follow-up. Am Heart J 1989 0.75
42 [Electrophysiologic features of the modulation of ATP-dependent potassium channels]. Cardiologia 1995 0.75
43 [Genetic basis of sudden cardiac death]. Recenti Prog Med 2000 0.75
44 Delineation of the influence of propionylcarnitine on the accumulation of long-chain acylcarnitines and electrophysiologic derangements evoked by hypoxia in canine myocardium. Cardiovasc Drugs Ther 1991 0.75
45 Left cardiac sympathetic denervation in long QT syndrome patients. J Interv Cardiol 1995 0.75
46 Significance of QT dispersion in the long QT syndrome. Prog Cardiovasc Dis 2000 0.75