Predicting survival in idiopathic pulmonary fibrosis: scoring system and survival model.

A placebo-controlled randomized trial of warfarin in idiopathic pulmonary fibrosis. Am J Respir Crit Care Med (2012) 4.81

Aberrant Wnt/beta-catenin pathway activation in idiopathic pulmonary fibrosis. Am J Pathol (2003) 4.31

Clinical and pathologic features of familial interstitial pneumonia. Am J Respir Crit Care Med (2005) 4.25

Peripheral blood proteins predict mortality in idiopathic pulmonary fibrosis. Am J Respir Crit Care Med (2012) 3.42

MMP1 and MMP7 as potential peripheral blood biomarkers in idiopathic pulmonary fibrosis. PLoS Med (2008) 2.79

Classification and natural history of the idiopathic interstitial pneumonias. Proc Am Thorac Soc (2006) 2.40

Idiopathic pulmonary fibrosis: prognostic value of changes in physiology and six-minute-walk test. Am J Respir Crit Care Med (2006) 2.37

Fibroblast foci are not discrete sites of lung injury or repair: the fibroblast reticulum. Am J Respir Crit Care Med (2006) 2.34

Association between the MUC5B promoter polymorphism and survival in patients with idiopathic pulmonary fibrosis. JAMA (2013) 2.20

Incidence, prevalence, and clinical course of idiopathic pulmonary fibrosis: a population-based study. Chest (2009) 2.16

Insulin-like growth factor binding proteins 3 and 5 are overexpressed in idiopathic pulmonary fibrosis and contribute to extracellular matrix deposition. Am J Pathol (2005) 1.91

Early interstitial lung disease in familial pulmonary fibrosis. Am J Respir Crit Care Med (2007) 1.91

High resolution multidetector CT-aided tissue analysis and quantification of lung fibrosis. Acad Radiol (2007) 1.90

Cigarette smoking is associated with subclinical parenchymal lung disease: the Multi-Ethnic Study of Atherosclerosis (MESA)-lung study. Am J Respir Crit Care Med (2009) 1.89

Accelerated variant of idiopathic pulmonary fibrosis: clinical behavior and gene expression pattern. PLoS One (2007) 1.88

Palliative care and location of death in decedents with idiopathic pulmonary fibrosis. Chest (2015) 1.85

Peripheral blood mononuclear cell gene expression profiles predict poor outcome in idiopathic pulmonary fibrosis. Sci Transl Med (2013) 1.81

Six-minute-walk distance predicts waiting list survival in idiopathic pulmonary fibrosis. Am J Respir Crit Care Med (2006) 1.80

Identification of early interstitial lung disease in smokers from the COPDGene Study. Acad Radiol (2009) 1.63

Molecular phenotypes distinguish patients with relatively stable from progressive idiopathic pulmonary fibrosis (IPF). PLoS One (2009) 1.56

Serum surfactant protein-A is a strong predictor of early mortality in idiopathic pulmonary fibrosis. Chest (2009) 1.50

Fibroblasts in fibrosis: novel roles and mediators. Front Pharmacol (2014) 1.47

The 6 minute walk in idiopathic pulmonary fibrosis: longitudinal changes and minimum important difference. Thorax (2009) 1.46

Impact of pulmonary hypertension on exercise performance in patients with interstitial lung disease undergoing evaluation for lung transplantation. Respirology (2014) 1.41

British Thoracic Society Study on cryptogenic fibrosing alveolitis: Response to treatment and survival. Thorax (2006) 1.39

Lung function in idiopathic pulmonary fibrosis--extended analyses of the IFIGENIA trial. Respir Res (2009) 1.34

Heart rate recovery after six-minute walk test predicts pulmonary hypertension in patients with idiopathic pulmonary fibrosis. Respirology (2011) 1.32

Evaluation of a hand-held, computer-based intervention to promote early self-care behaviors after lung transplant. Clin Transplant (2009) 1.24

Novel therapeutic approaches for pulmonary fibrosis. Br J Pharmacol (2011) 1.24

A novel mechanism for CCR4 in the regulation of macrophage activation in bleomycin-induced pulmonary fibrosis. Am J Pathol (2008) 1.24

A review of current and novel therapies for idiopathic pulmonary fibrosis. J Thorac Dis (2013) 1.18

Determinants of initiation and progression of idiopathic pulmonary fibrosis. Respirology (2009) 1.16

Lung collagens perpetuate pulmonary fibrosis via CD204 and M2 macrophage activation. PLoS One (2013) 1.14

The pulmonary fibrosis-associated MUC5B promoter polymorphism does not influence the development of interstitial pneumonia in systemic sclerosis. Chest (2012) 1.10

Signaling pathways in the epithelial origins of pulmonary fibrosis. Cell Cycle (2010) 1.10

Delayed access and survival in idiopathic pulmonary fibrosis: a cohort study. Am J Respir Crit Care Med (2011) 1.09

Racial and ethnic disparities in idiopathic pulmonary fibrosis: A UNOS/OPTN database analysis. Am J Transplant (2006) 1.09

The peripheral blood transcriptome identifies the presence and extent of disease in idiopathic pulmonary fibrosis. PLoS One (2012) 1.07

Right ventricular systolic pressure by echocardiography as a predictor of pulmonary hypertension in idiopathic pulmonary fibrosis. Respir Med (2008) 1.07

MRC chronic Dyspnea Scale: Relationships with cardiopulmonary exercise testing and 6-minute walk test in idiopathic pulmonary fibrosis patients: a prospective study. BMC Pulm Med (2010) 1.06

The prognostic value of cardiopulmonary exercise testing in idiopathic pulmonary fibrosis. Am J Respir Crit Care Med (2008) 1.04

Relationship between histopathological features and the course of idiopathic pulmonary fibrosis/usual interstitial pneumonia. Thorax (2006) 1.04

Combined pulmonary fibrosis and emphysema alters physiology but has similar mortality to pulmonary fibrosis without emphysema. Lung (2010) 1.04

FAK-related nonkinase is a multifunctional negative regulator of pulmonary fibrosis. Am J Pathol (2013) 1.04

New insights into the pathogenesis and treatment of idiopathic pulmonary fibrosis. Drugs (2011) 1.03

Heart rate recovery after 6-min walk test predicts survival in patients with idiopathic pulmonary fibrosis. Chest (2009) 1.03

Allele-specific transactivation of matrix metalloproteinase 7 by FOXA2 and correlation with plasma levels in idiopathic pulmonary fibrosis. Am J Physiol Lung Cell Mol Physiol (2012) 1.01

Genetics and early detection in idiopathic pulmonary fibrosis. Am J Respir Crit Care Med (2014) 1.01

Pulmonary function testing in idiopathic interstitial pneumonias. Proc Am Thorac Soc (2006) 1.01

Sildenafil in the treatment of pulmonary hypertension. Vasc Health Risk Manag (2006) 0.99

Treatment of idiopathic pulmonary fibrosis with losartan: a pilot project. Lung (2012) 0.98

Prostaglandin E₂ protects murine lungs from bleomycin-induced pulmonary fibrosis and lung dysfunction. Am J Physiol Lung Cell Mol Physiol (2011) 0.97

Workshop on idiopathic pulmonary fibrosis in older adults. Chest (2010) 0.96

Compartmentalized expression of c-FLIP in lung tissues of patients with idiopathic pulmonary fibrosis. Am J Respir Cell Mol Biol (2009) 0.95

Challenges in pulmonary fibrosis . 4: smoking-induced diffuse interstitial lung diseases. Thorax (2007) 0.94

Pathogenesis, current treatments and future directions for idiopathic pulmonary fibrosis. Curr Opin Pharmacol (2013) 0.94

Smoking and pulmonary fibrosis: novel insights. Pulm Med (2011) 0.92

Update on diagnosis and treatment of idiopathic pulmonary fibrosis. J Bras Pneumol (2015) 0.92

Idiopathic pulmonary fibrosis : new concepts in pathogenesis and implications for drug therapy. Treat Respir Med (2006) 0.90

The six-minute walk test in patients with pulmonary sarcoidosis. Ann Thorac Med (2009) 0.89

Validation of the Cough Quality-of-Life Questionnaire in patients with idiopathic pulmonary fibrosis. Chest (2013) 0.89

Epigenomics of idiopathic pulmonary fibrosis. Epigenomics (2012) 0.88

Re-evaluation of diagnostic parameters is crucial for obtaining accurate data on idiopathic pulmonary fibrosis. BMC Pulm Med (2015) 0.88

Idiopathic pulmonary fibrosis: CT and risk of death. Radiology (2014) 0.87

Idiopathic Pulmonary Fibrosis: Gender-Age-Physiology Index Stage for Predicting Future Lung Function Decline. Chest (2016) 0.86

Pleural mesothelial cells in pleural and lung diseases. J Thorac Dis (2015) 0.86

Cartilage oligomeric matrix protein in idiopathic pulmonary fibrosis. PLoS One (2013) 0.85

The pleural mesothelium in development and disease. Front Physiol (2014) 0.85

Does current knowledge explain the pathogenesis of idiopathic pulmonary fibrosis? A perspective. Proc Am Thorac Soc (2007) 0.84

A panel of lung injury biomarkers enhances the definition of primary graft dysfunction (PGD) after lung transplantation. J Heart Lung Transplant (2012) 0.84

Smoking and idiopathic pulmonary fibrosis. Pulm Med (2012) 0.84

Personalized medicine: applying 'omics' to lung fibrosis. Biomark Med (2012) 0.84

High-resolution CT scoring system-based grading scale predicts the clinical outcomes in patients with idiopathic pulmonary fibrosis. Respir Res (2014) 0.84

Idiopathic Pulmonary Fibrosis: A Genetic Disease That Involves Mucociliary Dysfunction of the Peripheral Airways. Physiol Rev (2016) 0.84

Idiopathic interstitial pneumonias: progress in classification, diagnosis, pathogenesis and management. Trans Am Clin Climatol Assoc (2004) 0.84

Therapeutic use of stem cell transplantation for cell replacement or cytoprotective effect of microvesicle released from mesenchymal stem cell. Mol Cells (2014) 0.83

Epigenetics of idiopathic pulmonary fibrosis. Transl Res (2014) 0.83

Glycyrrhizic acid alleviates bleomycin-induced pulmonary fibrosis in rats. Front Pharmacol (2015) 0.83

The clinical and immunologic features of pulmonary fibrosis in sarcoidosis. Transl Res (2012) 0.83

Predictors of diagnosis and survival in idiopathic pulmonary fibrosis and connective tissue disease-related usual interstitial pneumonia. Respir Res (2014) 0.82

Idiopathic pulmonary fibrosis: early detection and referral. Respir Med (2014) 0.82

Imaging diagnosis of interstitial pneumonia with emphysema (combined pulmonary fibrosis and emphysema). Pulm Med (2012) 0.82

Mycobacterial pulmonary infections in patients with idiopathic pulmonary fibrosis. J Korean Med Sci (2012) 0.82

High-resolution CT of complications of idiopathic fibrotic lung disease. Br J Radiol (2011) 0.81

Desmoplakin Variants Are Associated with Idiopathic Pulmonary Fibrosis. Am J Respir Crit Care Med (2016) 0.81

Association Between the MUC5B Promoter Polymorphism rs35705950 and Idiopathic Pulmonary Fibrosis: A Meta-analysis and Trial Sequential Analysis in Caucasian and Asian Populations. Medicine (Baltimore) (2015) 0.81

Models of disease behavior in idiopathic pulmonary fibrosis. BMC Med (2015) 0.81

Clinical characteristics of idiopathic pulmonary fibrosis patients with gender, age, and physiology staging at Okinawa Chubu Hospital. J Thorac Dis (2015) 0.81

A comparison of visual and quantitative methods to identify interstitial lung abnormalities. BMC Pulm Med (2015) 0.80

Right ventricular ejection fraction during exercise as a predictor of mortality in patients awaiting lung transplantation: a cohort study. BMJ Open (2013) 0.80

Prevalence of pulmonary hypertension in patients with idiopathic pulmonary fibrosis: correlation with physiological parameters. Lung (2011) 0.80

ROCK and Rho: Promising therapeutic targets to ameliorate pulmonary fibrosis. Am J Pathol (2015) 0.79

Therapeutic efficacy of Cintredekin Besudotox (IL13-PE38QQR) in murine lung fibrosis is unaffected by immunity to Pseudomonas aeruginosa exotoxin A. PLoS One (2010) 0.79

Diagnosis of idiopathic pulmonary fibrosis: Current issues. Intractable Rare Dis Res (2015) 0.79

New perspectives on management of idiopathic pulmonary fibrosis. Ther Adv Chronic Dis (2016) 0.79

Evaluating the interstitial lung disease multidisciplinary meeting: a survey of expert centres. BMC Pulm Med (2016) 0.78

Iron deposition and increased alveolar septal capillary density in nonfibrotic lung tissue are associated with pulmonary hypertension in idiopathic pulmonary fibrosis. Respir Res (2010) 0.78

Oxygen desaturation in healthy subjects undergoing the incremental shuttle walk test. J Bras Pneumol (2013) 0.78

The Role of Cardiopulmonary Exercise Test in IPF Prognosis. Pulm Med (2013) 0.78

Targeting the isoprenoid pathway to abrogate progression of pulmonary fibrosis. Free Radic Biol Med (2015) 0.78

Idiopathic pulmonary fibrosis: relationship between histopathologic features and mortality. Am J Respir Crit Care Med (2001) 4.45

Circulating immune complexes in the idiopathic interstitial pneumonias. N Engl J Med (1978) 3.83

Management of chronic obstructive pulmonary disease. N Engl J Med (1993) 3.41

The effect of polymorphisms of the beta(2)-adrenergic receptor on the response to regular use of albuterol in asthma. Am J Respir Crit Care Med (2000) 3.08

Rehabilitation of patients with chronic obstructive pulmonary disease. Am Rev Respir Dis (1976) 2.99

Normal standards for ventilatory function using an automated wedge spirometer. Am Rev Respir Dis (1972) 2.55

The predictability of corneal flap thickness and tissue laser ablation in laser in situ keratomileusis. Ophthalmology (2000) 2.48

Pre-operative aspirin decreases platelet aggregation and increases post-operative blood loss--a prospective, randomised, placebo controlled, double-blind clinical trial in 100 patients with chronic stable angina. Eur J Cardiothorac Surg (1994) 2.28

Progressive telomere shortening in aplastic anemia. Blood (1998) 2.10

Bacteremic hemophilus influenzae pneumonia in adults. A report of 24 cases and a review of the literature. Am J Med (1977) 2.04

Diffuse alveolar hemorrhage and systemic lupus erythematosus. Clinical presentation, histology, survival, and outcome. Medicine (Baltimore) (1997) 1.81

Predicting worsening asthma control following the common cold. Eur Respir J (2008) 1.70

A clinical, radiographic, and physiologic scoring system for the longitudinal assessment of patients with idiopathic pulmonary fibrosis. Am Rev Respir Dis (1986) 1.65

Hypersensitivity reactions to grain dust. J Allergy Clin Immunol (1974) 1.64

Safety and reproducibility of sputum induction in asthmatic subjects in a multicenter study. Am J Respir Crit Care Med (2001) 1.58

Coexistence of primary biliary cirrhosis and sarcoidosis. West J Med (1990) 1.57

Pulmonary manifestations of systemic lupus erythematosus: review of twelve cases of acute lupus pneumonitis. Medicine (Baltimore) (1975) 1.54

Diffuse panbronchiolitis in the United States. Am J Respir Crit Care Med (1996) 1.53

Idiopathic pulmonary fibrosis. Pretreatment bronchoalveolar lavage cellular constituents and their relationships with lung histopathology and clinical response to therapy. Am Rev Respir Dis (1987) 1.52

Hard-rock mining exposures affect smokers and nonsmokers differently. Results of a community prevalence study. Am Rev Respir Dis (1989) 1.52

Review of adverse experiences and tolerability in the first 2,516 patients treated with imipenem/cilastatin. Am J Med (1985) 1.44

Home care of chronic respiratory disease. JAMA (1969) 1.41

Imipenem-cilastatin in pediatric patients: an overview of safety and efficacy in studies conducted in the United States. Pediatr Infect Dis J (1989) 1.40

North American blastomycosis in Central Canada. A review of 36 cases. Can Med Assoc J (1972) 1.39

Diffuse alveolar hemorrhage with underlying isolated, pauciimmune pulmonary capillaritis. Am J Respir Crit Care Med (1997) 1.38

Methotrexate pneumonitis: case report and review of the literature. Thorax (1972) 1.38

Board-invited review: St. Anthony's Fire in livestock: causes, mechanisms, and potential solutions. J Anim Sci (2011) 1.35

Defects in nuclear and cytoskeletal morphology and mitochondrial localization in spermatozoa of mice lacking nectin-2, a component of cell-cell adherens junctions. Mol Cell Biol (2000) 1.35

Efficacy and safety of imipenem/cilastatin: a review of worldwide clinical experience. Rev Infect Dis (1985) 1.29

Tropical diseases of importance to the traveler. Adv Intern Med (1984) 1.28

Interstitial lung disease in polymyositis and dermatomyositis: analysis of six cases and review of the literature. Medicine (Baltimore) (1976) 1.24

Intraindividual variability in maximal expiratory flow-volume and closing volume in asymptomatic subjects. Am Rev Respir Dis (1975) 1.20

Increased monocyte tissue factor expression in coronary disease. Br Heart J (1995) 1.19

Immunofluorescent patterns in the idiopathic interstitial pneumonias. J Lab Clin Med (1978) 1.19

NHLBI Workshop Summary. Pharmacological therapy for idiopathic pulmonary fibrosis. Past, present, and future. Am J Respir Crit Care Med (1999) 1.18

Acquired aplastic anemia and paroxysmal nocturnal hemoglobinuria: studies on clonality. Blood (1991) 1.18

Effect of polymorphism of the beta(2)-adrenergic receptor on response to regular use of albuterol in asthma. Int Arch Allergy Immunol (2001) 1.18

Obliterative bronchiolitis: varying presentations and clinicopathological correlation. Eur Respir J (2002) 1.16

Acute eosinophilic pneumonia: a hypersensitivity phenomenon? Am Rev Respir Dis (1989) 1.15

Steroid-responsive hypercalcemia in disseminated bone tuberculosis. Arch Intern Med (1973) 1.15

Hypoxemia explained 36 years later. Chest (2001) 1.14

Acute interstitial pneumonitis. Case series and review of the literature. Medicine (Baltimore) (2000) 1.13

Resistance to airflow in patients with diffuse interstitial lung disease. Am Rev Respir Dis (1973) 1.11

Correlation of structure and function in idiopathic pulmonary fibrosis. Am J Respir Crit Care Med (1995) 1.10

Acute nephritis and pulmonary alveolitis following pneumococcal pneumonia. Arch Intern Med (1978) 1.10

NHLBI Workshop summary. Current concepts in idiopathic pulmonary fibrosis: a road map for the future. Am Rev Respir Dis (1991) 1.09

Microwave quantum logic gates for trapped ions. Nature (2011) 1.09

Sarcoidosis: the significance of an acinar pattern on chest roentgenogram. Chest (1974) 1.08

Trapped-ion quantum logic gates based on oscillating magnetic fields. Phys Rev Lett (2008) 1.08

Respiratory abnormalities in workers exposed to grain dust. Arch Environ Health (1973) 1.07

Ventilatory cost of exercise in chronic obstructive pulmonary disease. J Appl Physiol (1968) 1.06

The mechanical properties of the lungs in intermediate deficiency of 1 -antitrypsin. Am Rev Respir Dis (1972) 1.06

The organization of the Asthma Clinical Research Network: a multicenter, multiprotocol clinical trials team. Control Clin Trials (2001) 1.06

Mycoplasma pneumoniae-associated bronchiolitis causing severe restrictive lung disease in adults: report of three cases and literature review. Chest (1999) 1.04

Massive pleural effusions from prostatic lymphangitic carcinomatosis: resolution with endocrine therapy. Arch Intern Med (1982) 1.04

Computer analysis of the single-breath nitrogen washout curve. Am Rev Respir Dis (1976) 1.03

Effect of modification of the smoking habit on lung function. Am Rev Respir Dis (1976) 1.02

Prevention of death from endotoxin with antisera. I. The risk of fatal anaphylaxis to endotoxin. J Immunol (1969) 1.01

The effect of topical ophthalmic instillation of timolol and betaxolol on lung function in asthmatic subjects. Am Rev Respir Dis (1986) 1.00

The safety profile of imipenem/cilastatin: worldwide clinical experience based on 3470 patients. J Antimicrob Chemother (1986) 1.00

The intensity of chronic lung inflammation and fibrosis after bleomycin is directly related to the severity of acute injury. Am Rev Respir Dis (1988) 0.99

Idiopathic pulmonary fibrosis. Quantitative assessment of lung pathology. Comparison of a semiquantitative and a morphometric histopathologic scoring system. Am Rev Respir Dis (1992) 0.99

Transcriptional targets of hepatocyte growth factor signaling and Ki-ras oncogene activation in colorectal cancer. Oncogene (2006) 0.99

Increased levels of bombesin-like peptides in the lower respiratory tract of asymptomatic cigarette smokers. J Clin Invest (1989) 0.98

Evidence for a sodium electrogenic pump in airway smooth muscle. J Appl Physiol Respir Environ Exerc Physiol (1981) 0.98

Free and membrane-bound forms of bacterial cytochrome c4. Biochem J (1988) 0.97

Safety and tolerance comparison of imipenem-cilastatin to cephalothin and cefazolin. J Antimicrob Chemother (1983) 0.97

Letter: Alpha-thalassemia in Britain. Br Med J (1973) 0.96

Pulmonary artery hypertension in chronic obstructive pulmonary disease: determination by chest radiography. Invest Radiol (1981) 0.95

Lymphoid interstitial pneumonia: clinical features, associations and prognosis. Eur Respir J (2006) 0.94

Pulmonary cavitation following pulmonary infarction. Medicine (Baltimore) (1985) 0.94

Respiratory abnormalities in employees of the hard rock mining industry. Am Rev Respir Dis (1982) 0.94

Constriction of bovine vasculature caused by endophyte-infected tall fescue seed extract is similar to pure ergovaline. J Anim Sci (2011) 0.93

Comparison of the sensitivity of the vaginal mucous membranes of the albino rabbit and laboratory rat to nonoxynol-9. Food Chem Toxicol (1985) 0.93

Hodgkin's disease of the lung. Am Rev Respir Dis (1972) 0.93

Mechanical properties of the lung in extrinsic allergic alveolitis. Thorax (1978) 0.92

Characterization of human umbilical vein endothelial cell lines produced by transfection with the early region of SV40. Exp Cell Res (1992) 0.92

Prolonged survival in lymphangitic carcinomatosis. Ann Intern Med (1969) 0.91

Diffuse alveolar hemorrhage and pulmonary capillaritis due to propylthiouracil. Chest (1999) 0.91

Complexity in the redox titration of the dihaem cytochrome c4. Biochim Biophys Acta (1985) 0.91

The effect of acute, intensive cigarette smoking on maximal expiratory flows and the single-breath nitrogen washout trace. Am Rev Respir Dis (1976) 0.90

Imaging of pulmonary histiocytosis X. Radiographics (1992) 0.90

Relationship between serum theophylline levels and pulmonary function before and after inhaled beta-agonist in "stable" asthmatics. Am Rev Respir Dis (1983) 0.90

Pulmonary capillaritis. The association with progressive irreversible airflow limitation and hyperinflation. Am Rev Respir Dis (1993) 0.90

Diffuse alveolar hemorrhage with underlying pulmonary capillaritis in the retinoic acid syndrome. Am J Respir Crit Care Med (1998) 0.90

Inflammatory cells and eicosanoid mediators in subjects with late asthmatic responses and increases in airway responsiveness. J Allergy Clin Immunol (1992) 0.89

N-RAS gene mutation in patients with aplastic anemia and aplastic anemia/ paroxysmal nocturnal hemoglobinuria during evolution to clonal disease. Blood (2000) 0.89

Computer assistance in the clinical investigation of pulmonary function studies. Methods Inf Med (1973) 0.88

Lack of clinical efficacy of rituximab in the treatment of autoimmune neutropenia and pure red cell aplasia: implications for their pathophysiology. Ann Hematol (2006) 0.88

Incomplete consolidation in pneumococcal lobar pneumonia complicating pulmonary emphysema. Ann Intern Med (1970) 0.88

The influence of the "chest wall" on respiratory rate and depth. Respir Physiol (1967) 0.87

Osteoinduction using bone morphogenic protein in irradiated tissue. Arch Otolaryngol Head Neck Surg (1998) 0.87

Comprehensive care of COPD. Clin Notes Respir Dis (1981) 0.87

The role of cytochrome c4 in bacterial respiration. Cellular location and selective removal from membranes. Biochem J (1989) 0.86