Published in Brain Pathol on January 01, 2002
Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt-Jakob disease: its effect on the phenotype and prion-type characteristics. Brain (2009) 2.12
Aβ oligomer-induced synapse degeneration in Alzheimer's disease. Cell Mol Neurobiol (2011) 1.33
Incidence and spectrum of sporadic Creutzfeldt-Jakob disease variants with mixed phenotype and co-occurrence of PrPSc types: an updated classification. Acta Neuropathol (2009) 1.32
Protease-sensitive conformers in broad spectrum of distinct PrPSc structures in sporadic Creutzfeldt-Jakob disease are indicator of progression rate. PLoS Pathog (2011) 1.11
Subcellular localization of disease-associated prion protein in the human brain. Am J Pathol (2005) 1.11
Prion diseases: from protein to cell pathology. Am J Pathol (2008) 1.01
First case of feline spongiform encephalopathy in a captive cheetah born in France: PrP(sc) analysis in various tissues revealed unexpected targeting of kidney and adrenal gland. Histochem Cell Biol (2003) 1.00
Human prion diseases in the Netherlands (1998-2009): clinical, genetic and molecular aspects. PLoS One (2012) 0.98
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Coexistence of protease sensitive and resistant prion protein in 129VV homozygous sporadic Creutzfeldt-Jakob disease: a case report. J Med Case Rep (2012) 0.86
Molecular pathogenesis of sporadic prion diseases in man. Prion (2012) 0.85
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Advances on the understanding of the origins of synaptic pathology in AD. Curr Genomics (2007) 0.83
Disease-associated prion protein in vessel walls. Am J Pathol (2002) 0.83
Lack of association between PRNP 1368 polymorphism and Alzheimer's disease or vascular dementia. BMC Med Genet (2009) 0.81
Prion protein-specific antibodies that detect multiple TSE agents with high sensitivity. PLoS One (2014) 0.81
Atypical and classical forms of the disease-associated state of the prion protein exhibit distinct neuronal tropism, deposition patterns, and lesion profiles. Am J Pathol (2013) 0.79
Variably protease-sensitive prionopathy, a unique prion variant with inefficient transmission properties. Emerg Infect Dis (2014) 0.78
Rapidly progressive corticobasal degeneration syndrome. Case Rep Neurol (2011) 0.77
Membrane toxicity of abnormal prion protein in adrenal chromaffin cells of scrapie infected sheep. PLoS One (2013) 0.77
Rapidly progressive dementia with thalamic degeneration and peculiar cortical prion protein immunoreactivity, but absence of proteinase K resistant PrP: a new disease entity? Acta Neuropathol Commun (2013) 0.76
Characterization of four new monoclonal antibodies against the distal N-terminal region of PrP(c). PeerJ (2015) 0.75
MGMT gene silencing and benefit from temozolomide in glioblastoma. N Engl J Med (2005) 29.65
Guidelines for the use and interpretation of assays for monitoring autophagy. Autophagy (2012) 20.08
Stem cell-related "self-renewal" signature and high epidermal growth factor receptor expression associated with resistance to concomitant chemoradiotherapy in glioblastoma. J Clin Oncol (2008) 6.41
Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient. Lancet (2004) 4.59
Recombinant prion protein induces a new transmissible prion disease in wild-type animals. Acta Neuropathol (2010) 3.19
Prevalent abnormal prion protein in human appendixes after bovine spongiform encephalopathy epizootic: large scale survey. BMJ (2013) 2.74
Genetic prion disease: the EUROCJD experience. Hum Genet (2005) 2.64
Angiocentric glioma: report of clinico-pathologic and genetic findings in 8 cases. Am J Surg Pathol (2007) 2.48
Prevalence of lymphoreticular prion protein accumulation in UK tissue samples. J Pathol (2004) 2.47
Prion protein heterogeneity in sporadic but not variant Creutzfeldt-Jakob disease: UK cases 1991-2002. Ann Neurol (2004) 2.44
Molecular classification of sporadic Creutzfeldt-Jakob disease. Brain (2003) 2.42
Delta-like 4 Notch ligand regulates tumor angiogenesis, improves tumor vascular function, and promotes tumor growth in vivo. Cancer Res (2007) 2.31
Mutations of the prion protein gene phenotypic spectrum. J Neurol (2002) 2.20
Real time quaking-induced conversion analysis of cerebrospinal fluid in sporadic Creutzfeldt-Jakob disease. Ann Neurol (2012) 2.18
Fibulin-5 mutations link inherited neuropathies, age-related macular degeneration and hyperelastic skin. Brain (2011) 2.15
Validation of diagnostic criteria for variant Creutzfeldt-Jakob disease. Ann Neurol (2010) 2.09
Diagnosing variant Creutzfeldt-Jakob disease with the pulvinar sign: MR imaging findings in 86 neuropathologically confirmed cases. AJNR Am J Neuroradiol (2003) 2.05
Rosette-forming glioneuronal tumor of the fourth ventricle. Acta Neuropathol (2003) 1.95
TARDBP variation associated with frontotemporal dementia, supranuclear gaze palsy, and chorea. Mov Disord (2009) 1.95
Detection of type 1 prion protein in variant Creutzfeldt-Jakob disease. Am J Pathol (2006) 1.80
Prevalence of disease related prion protein in anonymous tonsil specimens in Britain: cross sectional opportunistic survey. BMJ (2009) 1.75
Anti-O6-methylguanine-methyltransferase (MGMT) immunohistochemistry in glioblastoma multiforme: observer variability and lack of association with patient survival impede its use as clinical biomarker. Brain Pathol (2008) 1.74
Characterization of renal interstitial fibroblast-specific protein 1/S100A4-positive cells in healthy and inflamed rodent kidneys. Histochem Cell Biol (2005) 1.69
Severe depletion of mitochondrial DNA in spinal muscular atrophy. Acta Neuropathol (2002) 1.60
A peculiar constellation of tau pathology defines a subset of dementia in the elderly. Acta Neuropathol (2011) 1.60
Nodule formation and desmoplasia in medulloblastomas-defining the nodular/desmoplastic variant and its biological behavior. Brain Pathol (2007) 1.59
Interlaboratory comparison of assessments of Alzheimer disease-related lesions: a study of the BrainNet Europe Consortium. J Neuropathol Exp Neurol (2006) 1.56
Peripheral tissue involvement in sporadic, iatrogenic, and variant Creutzfeldt-Jakob disease: an immunohistochemical, quantitative, and biochemical study. Am J Pathol (2004) 1.56
Genesis of mammalian prions: from non-infectious amyloid fibrils to a transmissible prion disease. PLoS Pathog (2011) 1.53
Prion protein accumulation and neuroprotection in hypoxic brain damage. Am J Pathol (2004) 1.52
Management of a twenty-first century brain bank: experience in the BrainNet Europe consortium. Acta Neuropathol (2008) 1.51
Endoplasmic reticulum stress features are prominent in Alzheimer disease but not in prion diseases in vivo. J Neuropathol Exp Neurol (2006) 1.49
A multivariate analysis of factors determining tumor progression in childhood low-grade glioma: a population-based cohort study (CCLG CNS9702). Neuro Oncol (2010) 1.46
Inherited prion disease with 4-octapeptide repeat insertion: disease requires the interaction of multiple genetic risk factors. Brain (2011) 1.45
Accumulation of prion protein in tonsil and appendix: review of tissue samples. BMJ (2002) 1.44
Global democratic consensus on neuropathological disease criteria. Lancet Neurol (2002) 1.44
Prion protein accumulation in eyes of patients with sporadic and variant Creutzfeldt-Jakob disease. Invest Ophthalmol Vis Sci (2003) 1.42
Value and limitations of immunohistochemistry and gene sequencing for detection of the IDH1-R132H mutation in diffuse glioma biopsy specimens. J Neuropathol Exp Neurol (2011) 1.42
Sensitive and specific detection of sporadic Creutzfeldt-Jakob disease brain prion protein using real-time quaking-induced conversion. J Gen Virol (2011) 1.40
Transplantation of ocular tissue from a donor with sporadic Creutzfeldt-Jakob disease. Clin Experiment Ophthalmol (2006) 1.39
Tetracyclines affect prion infectivity. Proc Natl Acad Sci U S A (2002) 1.39
Immunohistochemical analysis of INI1 protein in malignant pediatric CNS tumors: Lack of INI1 in atypical teratoid/rhabdoid tumors and in a fraction of primitive neuroectodermal tumors without rhabdoid phenotype. Am J Surg Pathol (2006) 1.39
Brain protein preservation largely depends on the postmortem storage temperature: implications for study of proteins in human neurologic diseases and management of brain banks: a BrainNet Europe Study. J Neuropathol Exp Neurol (2007) 1.38
Effects of formalin fixation, paraffin embedding, and time of storage on DNA preservation in brain tissue: a BrainNet Europe study. Brain Pathol (2007) 1.36
D18G transthyretin is monomeric, aggregation prone, and not detectable in plasma and cerebrospinal fluid: a prescription for central nervous system amyloidosis? Biochemistry (2003) 1.36
5-Aminolevulinic acid is a promising marker for detection of anaplastic foci in diffusely infiltrating gliomas with nonsignificant contrast enhancement. Cancer (2010) 1.35
Non-Alzheimer neurodegenerative pathologies and their combinations are more frequent than commonly believed in the elderly brain: a community-based autopsy series. Acta Neuropathol (2013) 1.35
Phenotypic heterogeneity in inherited prion disease (P102L) is associated with differential propagation of protease-resistant wild-type and mutant prion protein. Brain (2006) 1.34
An antibody with high reactivity for disease-associated α-synuclein reveals extensive brain pathology. Acta Neuropathol (2012) 1.33
Overexpression of hypoxia-inducible factor 1alpha indicates diminished response to radiotherapy and unfavorable prognosis in patients receiving radical radiotherapy for cervical cancer. Clin Cancer Res (2003) 1.30
Consensus classification of human prion disease histotypes allows reliable identification of molecular subtypes: an inter-rater study among surveillance centres in Europe and USA. Acta Neuropathol (2012) 1.29
JC virus granule cell neuronopathy and GCN-IRIS under natalizumab treatment. Ann Neurol (2013) 1.29
Assessment of beta-amyloid deposits in human brain: a study of the BrainNet Europe Consortium. Acta Neuropathol (2009) 1.27
Detection and localization of PrPSc in the skeletal muscle of patients with variant, iatrogenic, and sporadic forms of Creutzfeldt-Jakob disease. Am J Pathol (2006) 1.26
A new mechanism for transmissible prion diseases. J Neurosci (2012) 1.25
Stabilization of a progressive hemangioblastoma under treatment with thalidomide. J Neurooncol (2004) 1.23
High frequency of t(14;18)-translocation breakpoints outside of major breakpoint and minor cluster regions in follicular lymphomas: improved polymerase chain reaction protocols for their detection. Am J Pathol (2002) 1.23
White matter tauopathy with globular glial inclusions: a distinct sporadic frontotemporal lobar degeneration. J Neuropathol Exp Neurol (2008) 1.21
Excretion of transmissible spongiform encephalopathy infectivity in urine. Emerg Infect Dis (2008) 1.21
Visualization of Central European tick-borne encephalitis infection in fatal human cases. J Neuropathol Exp Neurol (2005) 1.20
PRNP contains both intronic and upstream regulatory regions that may influence susceptibility to Creutzfeldt-Jakob Disease. Gene (2002) 1.17
Neuropathology of white matter disease in Leber's hereditary optic neuropathy. Brain (2004) 1.17
Mixed brain pathologies in dementia: the BrainNet Europe consortium experience. Dement Geriatr Cogn Disord (2008) 1.17
Staging/typing of Lewy body related alpha-synuclein pathology: a study of the BrainNet Europe Consortium. Acta Neuropathol (2009) 1.17
Humanized knock-in mice expressing chimeric prion protein showed varied susceptibility to different human prions. Am J Pathol (2003) 1.16
Beyond PrP res type 1/type 2 dichotomy in Creutzfeldt-Jakob disease. PLoS Pathog (2008) 1.14
Tumor lymphangiogenesis and metastasis to lymph nodes induced by cancer cell expression of podoplanin. Am J Pathol (2010) 1.13
Inter-laboratory comparison of neuropathological assessments of beta-amyloid protein: a study of the BrainNet Europe consortium. Acta Neuropathol (2008) 1.13
Stabilization of a prion strain of synthetic origin requires multiple serial passages. J Biol Chem (2012) 1.13
Incidence of atypical teratoid/rhabdoid tumors in children: a population-based study by the Austrian Brain Tumor Registry, 1996-2006. Cancer (2010) 1.13
Vascular patterns in glioblastoma influence clinical outcome and associate with variable expression of angiogenic proteins: evidence for distinct angiogenic subtypes. Brain Pathol (2003) 1.11
Subcellular localization of disease-associated prion protein in the human brain. Am J Pathol (2005) 1.11
14-3-3 proteins in Lewy bodies in Parkinson disease and diffuse Lewy body disease brains. J Neuropathol Exp Neurol (2002) 1.11
Ki-67 immunolabeling index is an accurate predictor of outcome in patients with intracranial ependymoma. Am J Surg Pathol (2004) 1.10
Genetic Creutzfeldt-Jakob disease associated with the E200K mutation: characterization of a complex proteinopathy. Acta Neuropathol (2010) 1.10
Assessment of alpha-synuclein pathology: a study of the BrainNet Europe Consortium. J Neuropathol Exp Neurol (2008) 1.08
Variant Creutzfeldt-Jakob disease in France and the United Kingdom: Evidence for the same agent strain. Ann Neurol (2009) 1.07