Published in Hoppe Seylers Z Physiol Chem on June 01, 1975
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In vitro binding of plasma membrane-coated vesicle adaptors to the cytoplasmic domain of lysosomal acid phosphatase. J Biol Chem (1993) 1.72
The essential tyrosine of the internalization signal in lysosomal acid phosphatase is part of a beta turn. Cell (1991) 1.72
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Juvenile and adult metachromatic leukodystrophy: partial restoration of arylsulfatase A (cerebroside sulfatase) activity by inhibitors of thiol proteinases. Proc Natl Acad Sci U S A (1983) 1.71
Phylogenetic conservation of arylsulfatases. cDNA cloning and expression of human arylsulfatase B. J Biol Chem (1990) 1.69
Subcellular location of two enzymes involved in the synthesis of phosphorylated recognition markers in lysosomal enzymes. J Biol Chem (1981) 1.68
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Isolation and characterization of phosphorylated oligosaccharides from alpha-N-acetylglucosaminidase that are recognized by cell-surface receptors. Eur J Biochem (1979) 1.67
Early embryonic death of mice deficient in gamma-adaptin. J Biol Chem (1999) 1.64
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The cytoplasmic tail of lysosomal acid phosphatase contains overlapping but distinct signals for basolateral sorting and rapid internalization in polarized MDCK cells. EMBO J (1993) 1.57
High residual arylsulfatase A (ARSA) activity in a patient with late-infantile metachromatic leukodystrophy. Am J Hum Genet (1993) 1.55
Is movement of mannose 6-phosphate-specific receptor triggered by binding of lysosomal enzymes? J Cell Biol (1987) 1.54
Carbohydrate-free carboxypeptidase Y is transferred into the lysosome-like yeast vacuole. Biochem Biophys Res Commun (1982) 1.49
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Crystal structure of human arylsulfatase A: the aldehyde function and the metal ion at the active site suggest a novel mechanism for sulfate ester hydrolysis. Biochemistry (1998) 1.48
Lysosomal enzyme precursors in human fibroblasts. Activation of cathepsin D precursor in vitro and activity of beta-hexosaminidase A precursor towards ganglioside GM2. Eur J Biochem (1982) 1.48
Internalization of blocking antibodies against mannose-6-phosphate specific receptors. EMBO J (1985) 1.48
The iron sulfur protein AtsB is required for posttranslational formation of formylglycine in the Klebsiella sulfatase. J Biol Chem (1999) 1.46
Decorin-type I collagen interaction. Presence of separate core protein-binding domains. J Biol Chem (1995) 1.45
Small proteoglycans in human diabetic nephropathy: discrepancy between glomerular expression and protein accumulation of decorin, biglycan, lumican, and fibromodulin. FASEB J (2001) 1.45
Identification of N-sulphated disaccharide units in heparin-like polysaccharides. Biochem J (1979) 1.44
Enhanced breakdown of arylsulfatase A in multiple sulfatase deficiency. Eur J Biochem (1982) 1.44
Synthesis and processing of arylsulfatase A in human skin fibroblasts. Hoppe Seylers Z Physiol Chem (1982) 1.44
Phenotype of arylsulfatase A-deficient mice: relationship to human metachromatic leukodystrophy. Proc Natl Acad Sci U S A (1996) 1.44
The Sanfilippo A corrective factor. Purification and mode of action. J Biol Chem (1972) 1.41
Normal lysosomal morphology and function in LAMP-1-deficient mice. J Biol Chem (1999) 1.41
Sanfilippo A disease in the fetus. J Med Genet (1974) 1.40
Biosynthesis and maturation of arylsulfatase B in normal and mutant cultured human fibroblasts. J Biol Chem (1983) 1.40
The two mannose 6-phosphate receptors transport distinct complements of lysosomal proteins. J Biol Chem (1995) 1.39
Late-onset metachromatic leukodystrophy: molecular pathology in two siblings. Ann Neurol (1992) 1.38
Cloning and expression of a proteoglycan UDP-galactose:beta-xylose beta1,4-galactosyltransferase I. A seventh member of the human beta4-galactosyltransferase gene family. J Biol Chem (1999) 1.37
UDP-N-acetylglucosamine:lysosomal enzyme precursor N-acetylglucosamine-1-phosphotransferase. Partial purification and characterization of the rat liver Golgi enzyme. J Biol Chem (1982) 1.37
Neither type of mannose 6-phosphate receptor is sufficient for targeting of lysosomal enzymes along intracellular routes. J Cell Biol (1996) 1.36
A genetic defect in the biosynthesis of dermatan sulfate proteoglycan: galactosyltransferase I deficiency in fibroblasts from a patient with a progeroid syndrome. Proc Natl Acad Sci U S A (1990) 1.34
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Quantitation of Mr 46000 and Mr 300000 mannose 6-phosphate receptors in human cells and tissues. Biochem Int (1991) 1.33
Metabolism of sulfated glycosaminoglycans in cultured endothelial cells and smooth muscle cells from bovine aorta. Biochim Biophys Acta (1978) 1.33
Sanfilippo disease type D: deficiency of N-acetylglucosamine-6-sulfate sulfatase required for heparan sulfate degradation. Proc Natl Acad Sci U S A (1980) 1.33
Targeted disruption of the M(r) 46,000 mannose 6-phosphate receptor gene in mice results in misrouting of lysosomal proteins. EMBO J (1993) 1.31
Effects of brefeldin A on the endocytic route. Redistribution of mannose 6-phosphate/insulin-like growth factor II receptors to the cell surface. J Biol Chem (1991) 1.31
Guanidinoacetate methyltransferase deficiency: the first inborn error of creatine metabolism in man. Am J Hum Genet (1996) 1.31
Sequence determinants directing conversion of cysteine to formylglycine in eukaryotic sulfatases. EMBO J (1999) 1.31
The 46-kDa mannose 6-phosphate receptor contains multiple binding sites for clathrin adaptors. J Biol Chem (1997) 1.31
Sanfilippo syndrome type C: deficiency of acetyl-CoA:alpha-glucosaminide N-acetyltransferase in skin fibroblasts. Proc Natl Acad Sci U S A (1978) 1.30
Mannose 6-phosphate-specific receptor is a transmembrane protein with a C-terminal extension oriented towards the cytosol. Biochem J (1985) 1.29
Processing of human cathepsin D in lysosomes in vitro. J Biol Chem (1985) 1.29
Mannose 6-phosphate receptor dependent secretion of lysosomal enzymes. EMBO J (1990) 1.27
Processing of the phosphorylated recognition marker in lysosomal enzymes. Characterization and partial purification of a microsomal alpha-N-acetylglucosaminyl phosphodiesterase. J Biol Chem (1981) 1.26
The leucine-based sorting motifs in the cytoplasmic domain of the invariant chain are recognized by the clathrin adaptors AP1 and AP2 and their medium chains. J Biol Chem (1999) 1.26
Disease model: LAMP-2 enlightens Danon disease. Trends Mol Med (2001) 1.25
The sanfilippo B corrective factor: a N-acetyl-alpha-D-glucosamindiase. Biochem Biophys Res Commun (1972) 1.25
Inhibition by cyanate of the processing of lysosomal enzymes. Biochem J (1983) 1.25
Structure, biosynthesis and functions of glycoprotein glycans. Experientia (1982) 1.24
Carbohydrate-deficient glycoprotein syndrome type V: deficiency of dolichyl-P-Glc:Man9GlcNAc2-PP-dolichyl glucosyltransferase. Proc Natl Acad Sci U S A (1998) 1.24
Liberation of N-acetylglucosamine-6-sulfate by human beta-N-acetylhexosaminidase A. J Biol Chem (1981) 1.23
Metabolism of sulfated glycosaminoglycans in cultivated bovine arterial cells. I. Characterization of different pools of sulfated glycosaminoglycans. Hoppe Seylers Z Physiol Chem (1975) 1.23
Chemical changes of human knee joint menisci in various stages of degeneration. Ann Rheum Dis (1984) 1.21
Mu 1A deficiency induces a profound increase in MPR300/IGF-II receptor internalization rate. J Cell Sci (2001) 1.20
The two mannose 6-phosphate receptors have almost identical subcellular distributions in U937 monocytes. Eur J Cell Biol (1988) 1.20
Synthesis and processing of alpha-galactosidase A in human fibroblasts. Evidence for different mutations in Fabry disease. J Biol Chem (1987) 1.19
Cathepsin D and beta-hexosaminidase synthesized in the presence of 1-deoxynojirimycin accumulate in the endoplasmic reticulum. J Biol Chem (1984) 1.19