PubRank

Glenn E Morris

Author PubWeight™ 48.43‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Functional amounts of dystrophin produced by skipping the mutated exon in the mdx dystrophic mouse. Nat Med 2003 4.03
2 Neuronal SMN expression corrects spinal muscular atrophy in severe SMA mice while muscle-specific SMN expression has no phenotypic effect. Hum Mol Genet 2008 2.35
3 Indoprofen upregulates the survival motor neuron protein through a cyclooxygenase-independent mechanism. Chem Biol 2004 1.45
4 Effect of pathogenic mis-sense mutations in lamin A on its interaction with emerin in vivo. J Cell Sci 2003 1.44
5 Primary laminopathy fibroblasts display altered genome organization and apoptosis. Aging Cell 2007 1.43
6 Long-term persistence of donor nuclei in a Duchenne muscular dystrophy patient receiving bone marrow transplantation. J Clin Invest 2002 1.41
7 A role for complexes of survival of motor neurons (SMN) protein with gemins and profilin in neurite-like cytoplasmic extensions of cultured nerve cells. Exp Cell Res 2005 1.29
8 MSH2 ATPase domain mutation affects CTG*CAG repeat instability in transgenic mice. PLoS Genet 2009 1.22
9 A direct interaction between the survival motor neuron protein and p53 and its relationship to spinal muscular atrophy. J Biol Chem 2001 1.20
10 Muscleblind-like proteins: similarities and differences in normal and myotonic dystrophy muscle. Am J Pathol 2008 1.17
11 Defective mRNA in myotonic dystrophy accumulates at the periphery of nuclear splicing speckles. Genes Cells 2007 1.16
12 Matrix metalloproteinase-1 associates with intracellular organelles and confers resistance to lamin A/C degradation during apoptosis. Am J Pathol 2005 1.14
13 Nesprins, but not sun proteins, switch isoforms at the nuclear envelope during muscle development. Dev Dyn 2010 1.13
14 Emerin interacts in vitro with the splicing-associated factor, YT521-B. Eur J Biochem 2003 1.12
15 Specific nuclear envelope transmembrane proteins can promote the location of chromosomes to and from the nuclear periphery. Genome Biol 2013 1.11
16 Dysregulation of ubiquitin homeostasis and β-catenin signaling promote spinal muscular atrophy. J Clin Invest 2014 1.08
17 Molecular interaction between fukutin and POMGnT1 in the glycosylation pathway of alpha-dystroglycan. Biochem Biophys Res Commun 2006 1.03
18 Cytoplasmic CUG RNA foci are insufficient to elicit key DM1 features. PLoS One 2008 1.01
19 Phase I study of dystrophin plasmid-based gene therapy in Duchenne/Becker muscular dystrophy. Hum Gene Ther 2004 1.01
20 Strand bias in oligonucleotide-mediated dystrophin gene editing. Hum Mol Genet 2004 1.00
21 Absence of gemin5 from SMN complexes in nuclear Cajal bodies. BMC Cell Biol 2007 0.98
22 The apparent absence of lamin B1 and emerin in many tissue nuclei is due to epitope masking. J Mol Histol 2005 0.97
23 Expanded CUG repeats Dysregulate RNA splicing by altering the stoichiometry of the muscleblind 1 complex. J Biol Chem 2011 0.97
24 Analysis of exonic regions involved in nuclear localization, splicing activity, and dimerization of Muscleblind-like-1 isoforms. J Biol Chem 2011 0.94
25 ApoE isoform-specific regulation of regeneration in the peripheral nervous system. Hum Mol Genet 2011 0.93
26 The SMN interactome includes Myb-binding protein 1a. J Proteome Res 2010 0.88
27 Tissue-specific mismatch repair protein expression: MSH3 is higher than MSH6 in multiple mouse tissues. DNA Repair (Amst) 2012 0.86
28 Valproate and bone loss: iTRAQ proteomics show that valproate reduces collagens and osteonectin in SMA cells. J Proteome Res 2010 0.86
29 Characterization of MSH2 variants by endogenous gene modification in mouse embryonic stem cells. Hum Mutat 2011 0.86
30 High-content screening identifies small molecules that remove nuclear foci, affect MBNL distribution and CELF1 protein levels via a PKC-independent pathway in myotonic dystrophy cell lines. Hum Mol Genet 2013 0.86
31 Changes in myotonic dystrophy protein kinase levels and muscle development in congenital myotonic dystrophy. Am J Pathol 2003 0.84
32 A lamin A/C beta-strand containing the site of lipodystrophy mutations is a major surface epitope for a new panel of monoclonal antibodies. Biochim Biophys Acta 2004 0.84
33 82nd ENMC international workshop, 5th international Emery-Dreifuss muscular dystrophy (EDMD) workshop, 1st Workshop of the MYO-CLUSTER project EUROMEN (European muscle envelope nucleopathies), 15-16 September 2000, Naarden, The Netherlands. Neuromuscul Disord 2002 0.84
34 The mouse mismatch repair protein, MSH3, is a nucleoplasmic protein that aggregates into denser nuclear bodies under conditions of stress. J Cell Biochem 2011 0.81
35 Cell models for McArdle disease and aminoglycoside-induced read-through of a premature termination codon. Neuromuscul Disord 2012 0.81
36 Characterisation of the transcription factor, SIX5, using a new panel of monoclonal antibodies. J Cell Biochem 2005 0.81
37 Current research on SMN protein and treatment strategies for spinal muscular atrophy. Neuromuscul Disord 2011 0.79
38 Nesprin-2 epsilon: a novel nesprin isoform expressed in human ovary and Ntera-2 cells. Biochem Biophys Res Commun 2011 0.79
39 Lamin A/C assembly defects in Emery-Dreifuss muscular dystrophy can be regulated by culture medium composition. Neuromuscul Disord 2006 0.78
40 Monitoring of recombinant survival motor neuron protein using fiber-optic surface plasmon resonance. Analyst 2004 0.78
41 Detection of the dystroglycanopathy protein, fukutin, using a new panel of site-specific monoclonal antibodies. Biochem Biophys Res Commun 2012 0.77
42 Endosomal location of dopamine receptors in neuronal cell cytoplasm. J Mol Histol 2007 0.76
43 A rapid immunohistochemical test to distinguish congenital myotonic dystrophy from X-linked myotubular myopathy. Neuromuscul Disord 2011 0.76
44 The gemin2-binding site on SMN protein: accessibility to antibody. Biochem Biophys Res Commun 2013 0.75
45 Valproate reduces collagen and osteonectin in cultured bone cells. Epilepsy Res 2013 0.75
46 Naturally occurring plant polyphenols as potential therapies for inherited neuromuscular diseases. Future Med Chem 2013 0.75
47 Workshop on the nuclear envelope and Emery-Dreifuss muscular dystrophy 29th March 2006, Oswestry, UK. Neuromuscul Disord 2006 0.75