Published in J Cyst Fibros on August 01, 2004
Relationship Between Fat-Soluble Vitamin Supplementation and Blood Concentrations in Adolescent and Adult Patients With Cystic Fibrosis. Nutr Clin Pract (2014) 0.81
Retinol binding protein status in relation to ocular surface changes in patients with cystic fibrosis treated with daily vitamin A supplements. Eur J Pediatr (2004) 0.80
Why bother to take vitamins? J R Soc Med (2011) 0.75
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. N Engl J Med (2011) 8.73
Importance of hepatic fibrosis in cystic fibrosis and the predictive value of liver biopsy. Hepatology (2010) 2.82
Indexes of insulin resistance and secretion in obese children and adolescents: a validation study. Diabetes Care (2004) 1.88
Genetic modifiers of liver disease in cystic fibrosis. JAMA (2009) 1.88
Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation. Am J Respir Crit Care Med (2013) 1.73
Chronic suppurative lung disease and bronchiectasis in children and adults in Australia and New Zealand. Med J Aust (2010) 1.66
Within-host evolution of Burkholderia pseudomallei over a twelve-year chronic carriage infection. MBio (2013) 1.66
Transcriptional basis for hepatic fibrosis in cystic fibrosis-associated liver disease. J Pediatr Gastroenterol Nutr (2012) 1.46
Comparison of DNA extraction methods for microbial community profiling with an application to pediatric bronchoalveolar lavage samples. PLoS One (2012) 1.44
Rapid genotyping of Pseudomonas aeruginosa isolates harboured by adult and paediatric patients with cystic fibrosis using repetitive-element-based PCR assays. J Med Microbiol (2004) 1.43
Prevention and treatment of infant and childhood vitamin D deficiency in Australia and New Zealand: a consensus statement. Med J Aust (2006) 1.34
Fibrogenesis in pediatric cholestatic liver disease: role of taurocholate and hepatocyte-derived monocyte chemotaxis protein-1 in hepatic stellate cell recruitment. Hepatology (2009) 1.31
Identification of an unusual Brucella strain (BO2) from a lung biopsy in a 52 year-old patient with chronic destructive pneumonia. BMC Microbiol (2010) 1.29
Identification of Pseudomonas aeruginosa by a duplex real-time polymerase chain reaction assay targeting the ecfX and the gyrB genes. Diagn Microbiol Infect Dis (2008) 1.21
Comparison of three molecular techniques for typing Pseudomonas aeruginosa isolates in sputum samples from patients with cystic fibrosis. J Clin Microbiol (2010) 1.21
Australian children and adolescents with type 1 diabetes have low vitamin D levels. Med J Aust (2007) 1.20
Pseudomonas aeruginosa exhibits frequent recombination, but only a limited association between genotype and ecological setting. PLoS One (2012) 1.17
Effect of temperature on cystic fibrosis lung disease and infections: a replicated cohort study. PLoS One (2011) 1.16
'Iron lung': distinctive bronchoscopic features of acute iron tablet aspiration. Respirology (2003) 1.11
Cardiac troponin may be released by ischemia alone, without necrosis. Clin Chim Acta (2009) 1.11
Gene-environmental interaction in asthma. Curr Opin Allergy Clin Immunol (2007) 1.08
Gaming console exercise and cycle or treadmill exercise provide similar cardiovascular demand in adults with cystic fibrosis: a randomised cross-over trial. J Physiother (2011) 1.08
Room ventilation and the risk of airborne infection transmission in 3 health care settings within a large teaching hospital. Am J Infect Control (2011) 1.05
Reconstitution of the latent T-lymphocyte response to Epstein-Barr virus is coincident with long-term recovery from posttransplant lymphoma after adoptive immunotherapy. Transplantation (2003) 1.05
The lifestyle of our kids (LOOK) project: outline of methods. J Sci Med Sport (2007) 1.00
Randomized trial of a decision aid for patients with cystic fibrosis considering lung transplantation. Am J Respir Crit Care Med (2009) 0.99
Value of B-type natriuretic peptide for identifying significantly elevated pulmonary artery wedge pressure in patients treated for established chronic heart failure secondary to ischemic or idiopathic dilated cardiomyopathy. Am J Cardiol (2005) 0.96
Nebulised dornase alpha: adherence in adults with cystic fibrosis. J Cyst Fibros (2002) 0.95
Over time, high-sensitivity TnT replaces NT-proBNP as the most powerful predictor of death in patients with dialysis-dependent chronic renal failure. Clin Chim Acta (2010) 0.95
Low rates of Pseudomonas aeruginosa misidentification in isolates from cystic fibrosis patients. J Clin Microbiol (2009) 0.95
Novel neutrophil-derived proteins in bronchoalveolar lavage fluid indicate an exaggerated inflammatory response in pediatric cystic fibrosis patients. Clin Chem (2007) 0.94
Establishment of pediatric reference intervals on a large cohort of healthy children. Clin Chim Acta (2010) 0.94
Sub-inhibitory concentrations of ceftazidime and tobramycin reduce the quorum sensing signals of Pseudomonas aeruginosa. Pathology (2004) 0.93
GH treatment in adults with chronic liver disease: a randomized, double-blind, placebo-controlled, cross-over study. J Clin Endocrinol Metab (2002) 0.93
Shared Pseudomonas aeruginosa genotypes are common in Australian cystic fibrosis centres. Eur Respir J (2012) 0.92
Intestinal mucosa remodeling by recombinant human epidermal growth factor(1-48) in neonates with severe necrotizing enterocolitis. J Pediatr Surg (2007) 0.92
Symptomatic and asymptomatic viral recrudescence in solid-organ transplant recipients and its relationship with the antigen-specific CD8(+) T-cell response. J Virol (2007) 0.92
The month of July: an early experience with pandemic influenza A (H1N1) in adults with cystic fibrosis. BMC Pulm Med (2010) 0.91
Neonatal complete generalized glucocorticoid resistance and growth hormone deficiency caused by a novel homozygous mutation in Helix 12 of the ligand binding domain of the glucocorticoid receptor gene (NR3C1). J Clin Endocrinol Metab (2009) 0.91
Effect of population selection on 99th percentile values for a high sensitivity cardiac troponin I and T assays. Clin Biochem (2013) 0.90
Endogenous ursodeoxycholic acid and cholic acid in liver disease due to cystic fibrosis. Hepatology (2004) 0.90
Pharmacokinetics of digoxin cross-reacting substances in patients with acute yellow Oleander (Thevetia peruviana) poisoning, including the effect of activated charcoal. Ther Drug Monit (2006) 0.90
Serum markers of hepatic fibrogenesis in cystic fibrosis liver disease. J Hepatol (2004) 0.90
Clozapine-related myocarditis and cardiomyopathy in an Australian metropolitan psychiatric service. Aust N Z J Psychiatry (2004) 0.90
A d-optimal designed population pharmacokinetic study of oral itraconazole in adult cystic fibrosis patients. Br J Clin Pharmacol (2006) 0.90
Clonal complex Pseudomonas aeruginosa in horses. Vet Microbiol (2010) 0.88
Beta-lactam allergy in adults with cystic fibrosis. J Cyst Fibros (2006) 0.88
Burkholderia cepacia complex epidemiology in persons with cystic fibrosis from Australia and New Zealand. Res Microbiol (2008) 0.88
Pleural fluid nucleic acid testing enhances pneumococcal surveillance in children. Respirology (2012) 0.88
Effects of changes in adiposity and physical activity on preadolescent insulin resistance: the Australian LOOK longitudinal study. PLoS One (2012) 0.87
Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR. N Engl J Med (2015) 0.87
Clinical outcomes of Queensland children with cystic fibrosis: a comparison between tertiary centre and outreach services. Med J Aust (2008) 0.87
Prospective evaluation of respiratory exacerbations in children with cystic fibrosis from newborn screening to 5 years of age. Thorax (2013) 0.87
Bacterial causes of empyema in children, Australia, 2007-2009. Emerg Infect Dis (2011) 0.87
Pediatric acute liver failure: etiology, outcomes, and the role of serial pediatric end-stage liver disease scores. Pediatr Transplant (2013) 0.87
Comparison of the US and Australian cystic fibrosis registries: the impact of newborn screening. Pediatrics (2012) 0.87
Bone health in children with inflammatory bowel disease: adjusting for bone age. J Pediatr Gastroenterol Nutr (2009) 0.86
Characterisation of a highly sensitive troponin I assay and its application to a cardio-healthy population. Clin Chem Lab Med (2012) 0.85
Antibiotic desensitization in adults with cystic fibrosis. Respirology (2003) 0.85
Value of serology in predicting Pseudomonas aeruginosa infection in young children with cystic fibrosis. Thorax (2010) 0.85
Circulating microRNAs as noninvasive diagnostic biomarkers of liver disease in children with cystic fibrosis. J Pediatr Gastroenterol Nutr (2015) 0.84
Serum vitamin D levels are lower in Australian children and adolescents with type 1 diabetes than in children without diabetes. Pediatr Diabetes (2012) 0.84
Paediatric cholestatic liver disease: Diagnosis, assessment of disease progression and mechanisms of fibrogenesis. World J Gastrointest Pathophysiol (2010) 0.82
Factors influencing acquisition of Burkholderia cepacia complex organisms in patients with cystic fibrosis. J Clin Microbiol (2013) 0.82
Comparison of ultrasound and biopsy findings in children with cystic fibrosis related liver disease. J Cyst Fibros (2007) 0.82
A comparison of two informative SNP-based strategies for typing Pseudomonas aeruginosa isolates from patients with cystic fibrosis. BMC Infect Dis (2014) 0.82
Geographical differences in first acquisition of Pseudomonas aeruginosa in cystic fibrosis. Ann Am Thorac Soc (2013) 0.81
Relationships between myocardial injury, all-cause mortality, vitamin D, PTH, and biochemical bone turnover markers in older patients with hip fractures. Ann Clin Lab Sci (2007) 0.81
The Eat Smart Study: a randomised controlled trial of a reduced carbohydrate versus a low fat diet for weight loss in obese adolescents. BMC Public Health (2010) 0.81
Contrasting longitudinal and cross-sectional relationships between insulin resistance and percentage of body fat, fitness, and physical activity in children-the LOOK study. Pediatr Diabetes (2009) 0.81
Whole-Genome Sequences of Five Burkholderia pseudomallei Isolates from Australian Cystic Fibrosis Patients. Genome Announc (2015) 0.81
Abnormalities of the PTH-vitamin D axis and bone turnover markers in children, adolescents and adults with cystic fibrosis: comparison with healthy controls. Osteoporos Int (2003) 0.80
Opportunistic pathology-based screening for diabetes. BMJ Open (2013) 0.80
Pharmacogenetic screening and therapeutic drugs. Clin Chim Acta (2002) 0.80
Cystic fibrosis: An update for clinicians. Part 1: Nutrition and gastrointestinal complications. J Gastroenterol Hepatol (2014) 0.80
Multi-centre research in Australia: analysis of a recent National Health and Medical Research Council-funded project. Respirology (2009) 0.80
Signals for Hepatic Figrogenesis in Pediatric Cholestatic Liver Disease: Review and Hypothesis. Comp Hepatol (2004) 0.80
Newer cardiac troponin I assays have similar performance to troponin T in patients with end-stage renal disease. Ann Clin Biochem (2007) 0.80
High-throughput single-nucleotide polymorphism-based typing of shared Pseudomonas aeruginosa strains in cystic fibrosis patients using the Sequenom iPLEX platform. J Med Microbiol (2013) 0.80
Antibiotics for bronchiectasis exacerbations in children: rationale and study protocol for a randomised placebo-controlled trial. Trials (2012) 0.79
Year-in-review 2010: asthma, COPD, cystic fibrosis and airway biology. Respirology (2011) 0.79
The feasibility of a home-based moderate-intensity physical activity intervention in obese children and adolescents. Br J Sports Med (2008) 0.79