Transcriptional basis for hepatic fibrosis in cystic fibrosis-associated liver disease.

Cystic fibrosis-associated liver disease: when will the future be now? J Pediatr Gastroenterol Nutr (2012) 0.80

Liver disease in cystic fibrosis: an update. Hepat Mon (2013) 0.77

Aetiopathogenesis of liver changes in the course of cystic fibrosis, considering disturbances of the bile acid profile as well as genetic and immunological factors. Prz Gastroenterol (2013) 0.75

Disrupted hepcidin regulation in HFE-associated haemochromatosis and the liver as a regulator of body iron homoeostasis. Lancet (2003) 4.49

Acute liver failure in children: the first 348 patients in the pediatric acute liver failure study group. J Pediatr (2006) 3.03

Importance of hepatic fibrosis in cystic fibrosis and the predictive value of liver biopsy. Hepatology (2010) 2.82

Screening for hemochromatosis in asymptomatic subjects with or without a family history. Arch Intern Med (2006) 2.11

Biliary atresia: clinical profiles, risk factors, and outcomes of 755 patients listed for liver transplantation. J Pediatr (2005) 1.97

Screening and outcomes in biliary atresia: summary of a National Institutes of Health workshop. Hepatology (2007) 1.81

Prolonged neonatal jaundice and the diagnosis of biliary atresia: a single-center analysis of trends in age at diagnosis and outcomes. Pediatrics (2008) 1.70

Aldehydic products of lipid peroxidation do not directly activate rat hepatic stellate cells. J Gastroenterol Hepatol (2002) 1.47

Serum hyaluronic acid with serum ferritin accurately predicts cirrhosis and reduces the need for liver biopsy in C282Y hemochromatosis. Hepatology (2009) 1.47

Fibrogenesis in pediatric cholestatic liver disease: role of taurocholate and hepatocyte-derived monocyte chemotaxis protein-1 in hepatic stellate cell recruitment. Hepatology (2009) 1.31

A role for serotonin (5-HT) in hepatic stellate cell function and liver fibrosis. Am J Pathol (2006) 1.24

Australian children and adolescents with type 1 diabetes have low vitamin D levels. Med J Aust (2007) 1.20

Temporal expression of chemokines dictates the hepatic inflammatory infiltrate in a murine model of schistosomiasis. PLoS Negl Trop Dis (2010) 1.18

A contributory role for activated hepatic stellate cells in the dynamics of Schistosoma japonicum egg-induced fibrosis. Int J Parasitol (2006) 1.17

Ferritin functions as a proinflammatory cytokine via iron-independent protein kinase C zeta/nuclear factor kappaB-regulated signaling in rat hepatic stellate cells. Hepatology (2009) 1.15

Extrahepatic biliary atresia: a disease or a phenotype? Hepatology (2002) 1.12

The role of hepatic stellate cells and transforming growth factor-beta(1) in cystic fibrosis liver disease. Am J Pathol (2002) 1.11

Attenuated liver progenitor (oval) cell and fibrogenic responses to the choline deficient, ethionine supplemented diet in the BALB/c inbred strain of mice. J Hepatol (2006) 1.08

Functional analysis of a unique troponin c mutation, GLY159ASP, that causes familial dilated cardiomyopathy, studied in explanted heart muscle. Circ Heart Fail (2009) 1.06

Hepatic fibrosis and survival in biliary atresia. J Pediatr (2004) 1.05

The function of serotonin within the liver. J Hepatol (2008) 1.05

High parasite burdens cause liver damage in mice following Plasmodium berghei ANKA infection independently of CD8(+) T cell-mediated immune pathology. Infect Immun (2011) 1.03

Environmental and genetic modifiers of the progression to fibrosis and cirrhosis in hemochromatosis. Blood (2008) 1.02

Outcome after portoenterostomy in biliary atresia: pivotal role of degree of liver fibrosis and intensity of stellate cell activation. J Pediatr Gastroenterol Nutr (2006) 1.01

Lymphotoxin-beta receptor signaling regulates hepatic stellate cell function and wound healing in a murine model of chronic liver injury. Hepatology (2009) 0.97

Panoptic versus conventional ophthalmoscope. Clin Experiment Ophthalmol (2004) 0.97

The clinical relevance of compound heterozygosity for the C282Y and H63D substitutions in hemochromatosis. Clin Gastroenterol Hepatol (2006) 0.97

Assessment of hepatic steatosis: comparison of quantitative and semiquantitative methods in 108 liver biopsies. Liver Int (2008) 0.95

Management of periocular basal cell carcinoma with modified en face frozen section controlled excision. Ophthal Plast Reconstr Surg (2002) 0.95

Hepatic macrophages promote the neutrophil-dependent resolution of fibrosis in repairing cholestatic rat livers. Surgery (2008) 0.94

Periocular keratoacanthoma: clinical features, pathology, and management. Ophthalmology (2003) 0.93

Schistosomajaponicum Eggs Induce a Proinflammatory, Anti-Fibrogenic Phenotype in Hepatic Stellate Cells. PLoS One (2013) 0.93

Intestinal mucosa remodeling by recombinant human epidermal growth factor(1-48) in neonates with severe necrotizing enterocolitis. J Pediatr Surg (2007) 0.92

Spatial and temporal transcriptomics of Schistosoma japonicum-induced hepatic granuloma formation reveals novel roles for neutrophils. J Leukoc Biol (2013) 0.92

Body composition and components of energy expenditure in children with end-stage liver disease. J Pediatr Gastroenterol Nutr (2003) 0.91

Endogenous ursodeoxycholic acid and cholic acid in liver disease due to cystic fibrosis. Hepatology (2004) 0.90

Quantitative analysis of the expression of ACAT genes in human tissues by real-time PCR. J Lipid Res (2004) 0.90

Serum markers of hepatic fibrogenesis in cystic fibrosis liver disease. J Hepatol (2004) 0.90

Clonal complex Pseudomonas aeruginosa in horses. Vet Microbiol (2010) 0.88

Identification and characterization of the hepatic stellate cell transferrin receptor. Am J Pathol (2003) 0.88

Neutrophil depletion blocks early collagen degradation in repairing cholestatic rat livers. Am J Pathol (2010) 0.88

Hereditary hemochromatosis in the post-HFE era. Hepatology (2008) 0.87

Pediatric acute liver failure: etiology, outcomes, and the role of serial pediatric end-stage liver disease scores. Pediatr Transplant (2013) 0.87

Differential expression of chemokine and matrix re-modelling genes is associated with contrasting schistosome-induced hepatopathology in murine models. PLoS Negl Trop Dis (2011) 0.86

Bone health in children with inflammatory bowel disease: adjusting for bone age. J Pediatr Gastroenterol Nutr (2009) 0.86

Biliary strictures in pediatric liver transplant recipients - early diagnosis and treatment results in excellent graft outcomes. Pediatr Transplant (2009) 0.86

Role of resident liver cells in the pathogenesis of schistosomiasis. Trends Parasitol (2012) 0.86

A novel mutation in ferroportin implicated in iron overload. J Hepatol (2007) 0.85

Repair after cholestatic liver injury correlates with neutrophil infiltration and matrix metalloproteinase 8 activity. Surgery (2005) 0.85

Co-ordinated gene expression in the liver and spleen during Schistosoma japonicum infection regulates cell migration. PLoS Negl Trop Dis (2010) 0.85

Circulating microRNAs as noninvasive diagnostic biomarkers of liver disease in children with cystic fibrosis. J Pediatr Gastroenterol Nutr (2015) 0.84

How much iron is too much? Expert Rev Gastroenterol Hepatol (2008) 0.83

Enhanced length-dependent Ca2+ activation in fish cardiomyocytes permits a large operating range of sarcomere lengths. J Mol Cell Cardiol (2010) 0.83

Resting energy expenditure and body composition in children with myelomeningocele. Pediatr Rehabil (2003) 0.83

From genotype to phenotype: a longitudinal study of a patient with hypertrophic cardiomyopathy due to a mutation in the MYBPC3 gene. J Muscle Res Cell Motil (2009) 0.83

Iron and hepatic carcinogenesis. Crit Rev Oncog (2013) 0.83

Hemojuvelin (HJV)-associated hemochromatosis: analysis of HJV and HFE mutations and iron overload in three families. Haematologica (2005) 0.83

Paediatric cholestatic liver disease: Diagnosis, assessment of disease progression and mechanisms of fibrogenesis. World J Gastrointest Pathophysiol (2010) 0.82

The outcome in Australian children with hyperinsulinism of infancy: early extensive surgery in severe cases lowers risk of diabetes. Clin Endocrinol (Oxf) (2003) 0.82

Comparison of ultrasound and biopsy findings in children with cystic fibrosis related liver disease. J Cyst Fibros (2007) 0.82

Effect of phorbol ester and platelet-derived growth factor on protein kinase C in rat hepatic stellate cells. Liver Int (2007) 0.82

Hepatic iron deposition does not predict extrahepatic iron loading in mouse models of hereditary hemochromatosis. Am J Pathol (2012) 0.81

Test and teach. Incidentally discovered splenic vascular lesion. Littoral cell angioma of the spleen. Pathology (2002) 0.81

Co-circulation of four human coronaviruses (HCoVs) in Queensland children with acute respiratory tract illnesses in 2004. Viruses (2012) 0.80

Signals for Hepatic Figrogenesis in Pediatric Cholestatic Liver Disease: Review and Hypothesis. Comp Hepatol (2004) 0.80

Cystic fibrosis: An update for clinicians. Part 1: Nutrition and gastrointestinal complications. J Gastroenterol Hepatol (2014) 0.80

Lymphotoxin-beta production following bile duct ligation: possible role for Kupffer cells. J Gastroenterol Hepatol (2005) 0.80

Ductular reaction in hereditary hemochromatosis: the link between hepatocyte senescence and fibrosis progression. Hepatology (2014) 0.80

Evidence for a sub-morphological inflammatory process in the liver in haemochromatosis. J Hepatol (2003) 0.79

A membrane vesicle-based dual vaccine against melanoma and Lewis lung carcinoma. Biomaterials (2012) 0.79

Use of the electroretinogram in a paediatric hospital. Clin Experiment Ophthalmol (2011) 0.79

Role of TWEAK in coregulating liver progenitor cell and fibrogenic responses. Hepatology (2014) 0.78

Clinical cofactors and hepatic fibrosis in hereditary hemochromatosis: the role of diabetes mellitus. Hepatology (2012) 0.78

Liver transplantation and chemotherapy in children with unresectable primary hepatic malignancies: development of a management algorithm. J Pediatr Gastroenterol Nutr (2006) 0.78

Cough and reflux esophagitis in children: their co-existence and airway cellularity. BMC Pediatr (2006) 0.78

The association between ketoacidosis and 25(OH)-vitamin D levels at presentation in children with type 1 diabetes mellitus. Pediatr Diabetes (2008) 0.78

Newborn Direct or Conjugated Bilirubin Measurements As a Potential Screen for Biliary Atresia. J Pediatr Gastroenterol Nutr (2016) 0.78

Vitamin A levels in patients with CF are influenced by the inflammatory response. J Cyst Fibros (2004) 0.77

Ability of commonly used prediction equations to predict resting energy expenditure in children with inflammatory bowel disease. Inflamm Bowel Dis (2010) 0.76

Pubertal development and its influences on bone mineral density in Australian children and adolescents with cystic fibrosis. J Paediatr Child Health (2005) 0.76

Possible role of WT1 in a human fetus with evolving bronchial atresia, pulmonary malformation and renal agenesis. Pediatr Dev Pathol (2011) 0.76

Case Report: Fetal Bilateral Diaphragmatic Agenesis, Ectopic Liver and Abnormal Pancreas. Fetal Pediatr Pathol (2015) 0.76