Rank |
Title |
Journal |
Year |
PubWeight™‹?› |
1
|
Hippo signaling is a potent in vivo growth and tumor suppressor pathway in the mammalian liver.
|
Proc Natl Acad Sci U S A
|
2010
|
4.95
|
2
|
In vitro expansion of single Lgr5+ liver stem cells induced by Wnt-driven regeneration.
|
Nature
|
2013
|
4.94
|
3
|
Epithelial cancer in Fanconi anemia complementation group D2 (Fancd2) knockout mice.
|
Genes Dev
|
2003
|
3.58
|
4
|
The ploidy conveyor of mature hepatocytes as a source of genetic variation.
|
Nature
|
2010
|
3.27
|
5
|
Nomenclature of the finer branches of the biliary tree: canals, ductules, and ductular reactions in human livers.
|
Hepatology
|
2004
|
3.00
|
6
|
Influence of gender, race, and ethnicity on suspected fatty liver in obese adolescents.
|
Pediatrics
|
2005
|
2.55
|
7
|
Prospective isolation of a bipotential clonogenic liver progenitor cell in adult mice.
|
Genes Dev
|
2011
|
2.17
|
8
|
Treatment of solid organ transplant recipients with autologous Epstein Barr virus-specific cytotoxic T lymphocytes (CTLs).
|
Blood
|
2006
|
1.75
|
9
|
Patients with biliary atresia have elevated direct/conjugated bilirubin levels shortly after birth.
|
Pediatrics
|
2011
|
1.75
|
10
|
Amifostine does not prevent platinum-induced hearing loss associated with the treatment of children with hepatoblastoma: a report of the Intergroup Hepatoblastoma Study P9645 as a part of the Children's Oncology Group.
|
Cancer
|
2009
|
1.62
|
11
|
GLP-2 receptor localizes to enteric neurons and endocrine cells expressing vasoactive peptides and mediates increased blood flow.
|
Gastroenterology
|
2006
|
1.55
|
12
|
Pseudo-hydrodynamic delivery of helper-dependent adenoviral vectors into non-human primates for liver-directed gene therapy.
|
Mol Ther
|
2007
|
1.50
|
13
|
Consequences of copper accumulation in the livers of the Atp7b-/- (Wilson disease gene) knockout mice.
|
Am J Pathol
|
2006
|
1.47
|
14
|
Rotavirus viremia and extraintestinal viral infection in the neonatal rat model.
|
J Virol
|
2006
|
1.43
|
15
|
Adeno-associated virus gene repair corrects a mouse model of hereditary tyrosinemia in vivo.
|
Hepatology
|
2010
|
1.41
|
16
|
Efficient, long-term hepatic gene transfer using clinically relevant HDAd doses by balloon occlusion catheter delivery in nonhuman primates.
|
Mol Ther
|
2008
|
1.40
|
17
|
Severe dysplasia in children with familial adenomatous polyposis: rare or simply overlooked?
|
J Pediatr Surg
|
2006
|
1.38
|
18
|
Lifelong elimination of hyperbilirubinemia in the Gunn rat with a single injection of helper-dependent adenoviral vector.
|
Proc Natl Acad Sci U S A
|
2005
|
1.36
|
19
|
Clonal tracing of Sox9+ liver progenitors in mouse oval cell injury.
|
Hepatology
|
2014
|
1.32
|
20
|
Ploidy reductions in murine fusion-derived hepatocytes.
|
PLoS Genet
|
2009
|
1.28
|
21
|
Small cell undifferentiated variant of hepatoblastoma: adverse clinical and molecular features similar to rhabdoid tumors.
|
Pediatr Blood Cancer
|
2009
|
1.28
|
22
|
Rosiglitazone attenuates age- and diet-associated nonalcoholic steatohepatitis in male low-density lipoprotein receptor knockout mice.
|
Hepatology
|
2010
|
1.27
|
23
|
Fibrolamellar hepatocellular carcinoma in children and adolescents.
|
Cancer
|
2003
|
1.25
|
24
|
Aneuploidy as a mechanism for stress-induced liver adaptation.
|
J Clin Invest
|
2012
|
1.23
|
25
|
Complete surgical resection is curative for children with hepatoblastoma with pure fetal histology: a report from the Children's Oncology Group.
|
J Clin Oncol
|
2011
|
1.19
|
26
|
Improved hepatic transduction, reduced systemic vector dissemination, and long-term transgene expression by delivering helper-dependent adenoviral vectors into the surgically isolated liver of nonhuman primates.
|
Hum Gene Ther
|
2006
|
1.18
|
27
|
Combined deletion of Fxr and Shp in mice induces Cyp17a1 and results in juvenile onset cholestasis.
|
J Clin Invest
|
2010
|
1.17
|
28
|
aP2-Cre-mediated inactivation of acetyl-CoA carboxylase 1 causes growth retardation and reduced lipid accumulation in adipose tissues.
|
Proc Natl Acad Sci U S A
|
2009
|
1.13
|
29
|
Toll-like receptor 4-dependent Kupffer cell activation and liver injury in a novel mouse model of parenteral nutrition and intestinal injury.
|
Hepatology
|
2012
|
1.13
|
30
|
Cellular immunity to Epstein-Barr virus in liver transplant recipients treated with rituximab for post-transplant lymphoproliferative disease.
|
Am J Transplant
|
2005
|
1.13
|
31
|
ATXN1 protein family and CIC regulate extracellular matrix remodeling and lung alveolarization.
|
Dev Cell
|
2011
|
1.12
|
32
|
Probiotics stimulate enterocyte migration and microbial diversity in the neonatal mouse intestine.
|
FASEB J
|
2012
|
1.10
|
33
|
Group A rotavirus infection and age-dependent diarrheal disease in rats: a new animal model to study the pathophysiology of rotavirus infection.
|
J Virol
|
2002
|
1.10
|
34
|
Gene expression in Barrett's esophagus: laser capture versus whole tissue.
|
Scand J Gastroenterol
|
2009
|
1.09
|
35
|
Histologic subtypes of hepatoblastoma are characterized by differential canonical Wnt and Notch pathway activation in DLK+ precursors.
|
Hum Pathol
|
2009
|
1.09
|
36
|
Treatment of unresectable and metastatic hepatoblastoma: a pediatric oncology group phase II study.
|
J Clin Oncol
|
2002
|
1.08
|
37
|
Further evidence for EpCAM as the gene for congenital tufting enteropathy.
|
Am J Med Genet A
|
2010
|
1.03
|
38
|
Increased liver pathology in hepatitis C virus transgenic mice expressing the hepatitis B virus X protein.
|
Virology
|
2006
|
1.02
|
39
|
Hep G2 is a hepatoblastoma-derived cell line.
|
Hum Pathol
|
2009
|
1.00
|
40
|
A novel role of nucleostemin in maintaining the genome integrity of dividing hepatocytes during mouse liver development and regeneration.
|
Hepatology
|
2013
|
1.00
|
41
|
Efficient production of Fah-null heterozygote pigs by chimeric adeno-associated virus-mediated gene knockout and somatic cell nuclear transfer.
|
Hepatology
|
2011
|
0.97
|
42
|
Reduced inflammation and improved airway expression using helper-dependent adenoviral vectors with a K18 promoter.
|
Mol Ther
|
2003
|
0.96
|
43
|
Altered DNA mutation spectrum in aflatoxin b1-treated transgenic mice that express the hepatitis B virus x protein.
|
J Virol
|
2002
|
0.95
|
44
|
Accelerated transition from the double-positive to single-positive thymocytes in G alpha i2-deficient mice.
|
Int Immunol
|
2005
|
0.94
|
45
|
AAV vectors containing rDNA homology display increased chromosomal integration and transgene persistence.
|
Mol Ther
|
2012
|
0.93
|
46
|
Host response to probiotics determined by nutritional status of rotavirus-infected neonatal mice.
|
J Pediatr Gastroenterol Nutr
|
2012
|
0.93
|
47
|
Hepatocellular carcinoma in children and adolescents: results from the Pediatric Oncology Group and the Children's Cancer Group intergroup study.
|
J Clin Oncol
|
2002
|
0.92
|
48
|
Development of T-cell lymphomas in Emu-IEX-1 mice.
|
Oncogene
|
2003
|
0.92
|
49
|
Gene expression profiling reveals signatures characterizing histologic subtypes of hepatoblastoma and global deregulation in cell growth and survival pathways.
|
Hum Pathol
|
2009
|
0.90
|
50
|
AAV-mediated gene targeting is significantly enhanced by transient inhibition of nonhomologous end joining or the proteasome in vivo.
|
Hum Gene Ther
|
2012
|
0.90
|
51
|
Diverse patterns of cell-specific gene expression in response to glucocorticoid in the developing small intestine.
|
Am J Physiol Gastrointest Liver Physiol
|
2006
|
0.89
|
52
|
Liver neoplasia in children.
|
Clin Liver Dis
|
2011
|
0.89
|
53
|
Developmental expression and function of aldehyde reductase in proximal tubules of the kidney.
|
Am J Physiol Renal Physiol
|
2005
|
0.88
|
54
|
Undifferentiated Embryonal Sarcoma of the Liver (UESL): A Single-Center Experience and Review of the Literature.
|
J Pediatr Hematol Oncol
|
2016
|
0.88
|
55
|
Impaired TGF-beta responses in peripheral T cells of G alpha i2-/- mice.
|
J Immunol
|
2005
|
0.87
|
56
|
Progressive familial intrahepatic cholestasis type 3: overlapping presentation with Wilson disease.
|
Clin Pediatr (Phila)
|
2012
|
0.86
|
57
|
Inactivation of CBF/NF-Y in postnatal liver causes hepatocellular degeneration, lipid deposition, and endoplasmic reticulum stress.
|
Sci Rep
|
2011
|
0.86
|
58
|
Hepatic stress in hereditary tyrosinemia type 1 (HT1) activates the AKT survival pathway in the fah-/- knockout mice model.
|
J Hepatol
|
2007
|
0.86
|
59
|
Osteopontin upregulation in rotavirus-induced murine biliary atresia requires replicating virus but is not necessary for development of biliary atresia.
|
Virology
|
2011
|
0.86
|
60
|
Recurrent nested stromal epithelial tumor of the liver with extrahepatic metastasis: case report and review of literature.
|
Pediatr Dev Pathol
|
2008
|
0.85
|
61
|
Nested stromal epithelial tumor of the liver: six cases of a distinctive pediatric neoplasm with frequent calcifications and association with cushing syndrome.
|
Am J Surg Pathol
|
2005
|
0.84
|
62
|
Morphologic findings in progressive familial intrahepatic cholestasis 2 (PFIC2): correlation with genetic and immunohistochemical studies.
|
Am J Surg Pathol
|
2011
|
0.84
|
63
|
Generation of a novel mouse model that recapitulates early and adult onset glycogenosis type IV.
|
Hum Mol Genet
|
2011
|
0.84
|
64
|
Development of the fetal intestine in mice lacking the glucocorticoid receptor (GR).
|
J Cell Physiol
|
2003
|
0.82
|
65
|
Vasoactive intestinal peptide increases hepatic transduction and reduces innate immune response following administration of helper-dependent Ad.
|
Mol Ther
|
2010
|
0.82
|
66
|
Absent smooth muscle actin immunoreactivity of the small bowel muscularis propria circular layer in association with chromosome 15q11 deletion in megacystis-microcolon-intestinal hypoperistalsis syndrome.
|
Pediatr Dev Pathol
|
2010
|
0.82
|
67
|
Elevated copper impairs hepatic nuclear receptor function in Wilson's disease.
|
J Clin Invest
|
2015
|
0.81
|
68
|
Wilson disease: histopathological correlations with treatment on follow-up liver biopsies.
|
World J Gastroenterol
|
2010
|
0.81
|
69
|
In vivo selection of transplanted hepatocytes by pharmacological inhibition of fumarylacetoacetate hydrolase in wild-type mice.
|
Mol Ther
|
2012
|
0.81
|
70
|
Distinct patterns of p27/KIP 1 gene expression in hepatoblastoma and prognostic implications with correlation before and after chemotherapy.
|
Hum Pathol
|
2002
|
0.81
|
71
|
Cytogenetic evaluation of a large series of hepatoblastomas: numerical abnormalities with recurring aberrations involving 1q12-q21.
|
Genes Chromosomes Cancer
|
2005
|
0.81
|
72
|
Diagnostic and therapeutic role of endoscopic retrograde cholangiopancreatography in biliary rhabdomyosarcoma.
|
World J Gastroenterol
|
2008
|
0.81
|
73
|
Rhabdoid tumors of the liver: rare, aggressive, and poorly responsive to standard cytotoxic chemotherapy.
|
Pediatr Blood Cancer
|
2010
|
0.80
|
74
|
Hepatic neoplasia and metabolic diseases in children.
|
Clin Liver Dis
|
2010
|
0.80
|
75
|
Diffuse reticuloendothelial system involvement in type IV glycogen storage disease with a novel GBE1 mutation: a case report and review.
|
Hum Pathol
|
2012
|
0.80
|
76
|
SMAD4 haploinsufficiency associates with augmented colonic inflammation in select humans and mice.
|
Ann Clin Lab Sci
|
2012
|
0.79
|
77
|
Successful management of rhabdoid tumor of the liver.
|
J Pediatr Hematol Oncol
|
2007
|
0.79
|
78
|
Does short bowel syndrome increase the risk of food allergy and eosinophilic gastrointestinal disease? Observations in Shah-Waardenburg syndrome.
|
J Allergy Clin Immunol
|
2012
|
0.79
|
79
|
TGF-β/β2-spectrin/CTCF-regulated tumor suppression in human stem cell disorder Beckwith-Wiedemann syndrome.
|
J Clin Invest
|
2016
|
0.78
|
80
|
Newborn Direct or Conjugated Bilirubin Measurements As a Potential Screen for Biliary Atresia.
|
J Pediatr Gastroenterol Nutr
|
2016
|
0.78
|
81
|
Opioid growth factor (OGF) for hepatoblastoma: a novel non-toxic treatment.
|
Invest New Drugs
|
2012
|
0.77
|
82
|
Rescue from neonatal death in the murine model of hereditary tyrosinemia by glutathione monoethylester and vitamin C treatment.
|
Mol Genet Metab
|
2007
|
0.75
|
83
|
Key Histopathologic Features of Liver Biopsies That Distinguish Biliary Atresia From Other Causes of Infantile Cholestasis and Their Correlation With Outcome: A Multicenter Study.
|
Am J Surg Pathol
|
2016
|
0.75
|
84
|
Discordant presentation of biliary atresia in premature monozygotic twins.
|
J Pediatr Gastroenterol Nutr
|
2013
|
0.75
|
85
|
Hepatoblastoma Arising in a Pigmented β-catenin-activated Hepatocellular Adenoma: Case Report and Review of the Literature.
|
Am J Surg Pathol
|
2016
|
0.75
|
86
|
Hepatitis C viral recurrence in a pediatric patient following liver transplantation.
|
Pediatr Transplant
|
2006
|
0.75
|
87
|
Peri-appendiceal inflammation in an 8-year-old child with chronic ulcerative colitis.
|
Ann Clin Lab Sci
|
2011
|
0.75
|
88
|
Mutations of PTCH1, MLL2, and MLL3 are not frequent events in hepatoblastoma.
|
Pediatr Blood Cancer
|
2011
|
0.75
|
89
|
CT, MRI, and 18F-FDG PET/CT in a patient with nested stromal epithelial tumor of the liver.
|
Clin Nucl Med
|
2015
|
0.75
|
90
|
A Rare Phenotype of Alpha-1-Antitrypsin Deficiency due to PI*IS in a Newborn With Liver Disease.
|
J Pediatr Gastroenterol Nutr
|
2017
|
0.75
|