Published in Brain on July 20, 2005
Memantine (10mg BID) for the Frontal and Temporal Subtypes of Frontotemporal Dementia | NCT00545974
Classification of primary progressive aphasia and its variants. Neurology (2011) 11.82
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Abeta amyloid and glucose metabolism in three variants of primary progressive aphasia. Ann Neurol (2008) 4.15
Clinicopathological and imaging correlates of progressive aphasia and apraxia of speech. Brain (2006) 4.07
Alzheimer and frontotemporal pathology in subsets of primary progressive aphasia. Ann Neurol (2008) 3.99
Criteria for the diagnosis of corticobasal degeneration. Neurology (2013) 3.07
Concomitant TAR-DNA-binding protein 43 pathology is present in Alzheimer disease and corticobasal degeneration but not in other tauopathies. J Neuropathol Exp Neurol (2008) 2.96
Progressive aphasia secondary to Alzheimer disease vs FTLD pathology. Neurology (2008) 2.45
CSF biomarkers in frontotemporal lobar degeneration with known pathology. Neurology (2008) 2.43
Clinicopathologic differences among patients with behavioral variant frontotemporal dementia. Neurology (2013) 2.26
Primary progressive aphasia: clinicopathological correlations. Nat Rev Neurol (2010) 2.19
Neuropathological background of phenotypical variability in frontotemporal dementia. Acta Neuropathol (2011) 2.17
Clinical and neuroanatomical signatures of tissue pathology in frontotemporal lobar degeneration. Brain (2011) 2.13
Distinct MRI atrophy patterns in autopsy-proven Alzheimer's disease and frontotemporal lobar degeneration. Am J Alzheimers Dis Other Demen (2008) 2.00
Prominent phenotypic variability associated with mutations in Progranulin. Neurobiol Aging (2007) 2.00
A review of fragile X premutation disorders: expanding the psychiatric perspective. J Clin Psychiatry (2009) 1.98
Distinct anatomical subtypes of the behavioural variant of frontotemporal dementia: a cluster analysis study. Brain (2009) 1.93
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Development of methodology for conducting clinical trials in frontotemporal lobar degeneration. Brain (2008) 1.82
White matter damage in primary progressive aphasias: a diffusion tensor tractography study. Brain (2011) 1.73
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The molecular basis of the frontotemporal lobar degeneration-amyotrophic lateral sclerosis spectrum. Ann Med (2012) 1.66
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Amyotrophic lateral sclerosis and frontotemporal lobar degeneration: a spectrum of TDP-43 proteinopathies. Neuropathology (2010) 1.53
Longitudinal decline in autopsy-defined frontotemporal lobar degeneration. Neurology (2008) 1.48
Atrophy patterns in histologic vs clinical groupings of frontotemporal lobar degeneration. Neurology (2009) 1.42
Neuropsychological decline in frontotemporal lobar degeneration: a longitudinal analysis. Neuropsychology (2009) 1.35
The non-fluent/agrammatic variant of primary progressive aphasia. Lancet Neurol (2012) 1.33
In vivo amyloid imaging with PET in frontotemporal dementia. Eur J Nucl Med Mol Imaging (2007) 1.29
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Eating and hypothalamus changes in behavioral-variant frontotemporal dementia. Ann Neurol (2010) 1.24
Anterior insula degeneration in frontotemporal dementia. Brain Struct Funct (2010) 1.24
Characteristics of frontotemporal dementia patients with a Progranulin mutation. Ann Neurol (2006) 1.22
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Neuropathological features of corticobasal degeneration presenting as corticobasal syndrome or Richardson syndrome. Brain (2011) 1.18
Alzheimer's pathology in primary progressive aphasia. Neurobiol Aging (2010) 1.18
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Distinguishing Alzheimer's disease from other major forms of dementia. Expert Rev Neurother (2011) 1.12
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The epidemiology of frontotemporal dementia. Int Rev Psychiatry (2013) 1.09
MRI correlates of protein deposition and disease severity in postmortem frontotemporal lobar degeneration. Neurodegener Dis (2009) 1.08
Saccade abnormalities in autopsy-confirmed frontotemporal lobar degeneration and Alzheimer disease. Arch Neurol (2012) 1.07
How a neuropsychiatric brain bank should be run: a consensus paper of Brainnet Europe II. J Neural Transm (Vienna) (2006) 1.07
Positive effects of language treatment for the logopenic variant of primary progressive aphasia. J Mol Neurosci (2011) 1.05
Conceptual evolution in Alzheimer's disease: implications for understanding the clinical phenotype of progressive neurodegenerative disease. J Alzheimers Dis (2010) 1.02
Primary progressive aphasia and the evolving neurology of the language network. Nat Rev Neurol (2014) 1.02
Neuroimaging in frontotemporal lobar degeneration--predicting molecular pathology. Nat Rev Neurol (2012) 0.99
Amyloid imaging in dementias with atypical presentation. Alzheimers Dement (2012) 0.99
Patterns of MRI atrophy in tau positive and ubiquitin positive frontotemporal lobar degeneration. J Neurol Neurosurg Psychiatry (2007) 0.97
Reversal of neurofibrillary tangles and tau-associated phenotype in the rTgTauEC model of early Alzheimer's disease. J Neurosci (2013) 0.96
Longitudinal patterns of semantic and episodic memory in frontotemporal lobar degeneration and Alzheimer's disease. J Int Neuropsychol Soc (2009) 0.96
Clinicopathologic correlation in PGRN mutations. Neurology (2007) 0.95
Neuropsychiatric symptoms in behavioral variant frontotemporal dementia and primary progressive aphasia. J Geriatr Psychiatry Neurol (2008) 0.95
Cerebrospinal fluid biomarkers for differentiation of frontotemporal lobar degeneration from Alzheimer's disease. Front Aging Neurosci (2013) 0.94
Quantitative neurofibrillary tangle density and brain volumetric MRI analyses in Alzheimer's disease presenting as logopenic progressive aphasia. Brain Lang (2013) 0.94
Patterns of breakdown in spelling in primary progressive aphasia. Cortex (2009) 0.92
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Clinical trajectories and biological features of primary progressive aphasia (PPA). Curr Alzheimer Res (2009) 0.91
Biomarkers in frontotemporal lobar degenerations--progress and challenges. Prog Neurobiol (2011) 0.91
Frontotemporal lobar degeneration. Neurol Clin (2007) 0.90
Presenilin-1 adopts pathogenic conformation in normal aging and in sporadic Alzheimer's disease. Acta Neuropathol (2012) 0.89
Progressive supranuclear palsy syndrome presenting as progressive nonfluent aphasia: a neuropsychological and neuroimaging analysis. Mov Disord (2010) 0.88
Corticobasal syndrome: Five new things. Neurol Clin Pract (2014) 0.87
Clinico-pathological correlations of the most common neurodegenerative dementias. Front Neurol (2012) 0.86
Characteristics of progressive supranuclear palsy presenting with corticobasal syndrome: a cortical variant. Neuropathol Appl Neurobiol (2014) 0.86
Association of ideomotor apraxia with frontal gray matter volume loss in corticobasal syndrome. Arch Neurol (2009) 0.85
Myelin oligodendrocyte basic protein and prognosis in behavioral-variant frontotemporal dementia. Neurology (2014) 0.84
Computerized analysis of speech and language to identify psycholinguistic correlates of frontotemporal lobar degeneration. Cogn Behav Neurol (2010) 0.84
The nature of naming errors in primary progressive aphasia versus acute post-stroke aphasia. Neuropsychology (2010) 0.83
Language, executive function and social cognition in the diagnosis of frontotemporal dementia syndromes. Int Rev Psychiatry (2013) 0.83
Serotonin transporter and saitohin genes in risk of Alzheimer's disease and frontotemporal lobar dementia: preliminary findings. Neurol Sci (2010) 0.83
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Extrapyramidal signs in the primary progressive aphasias. Am J Alzheimers Dis Other Demen (2011) 0.82
Primary progressive aphasias and their contribution to the contemporary knowledge about the brain-language relationship. Neuropsychol Rev (2011) 0.81
Patterns of brain atrophy in clinical variants of frontotemporal lobar degeneration. Dement Geriatr Cogn Disord (2013) 0.81
Is brain banking of psychiatric cases valuable for neurobiological research? Clinics (Sao Paulo) (2008) 0.81
Prevalence of frontotemporal lobar degeneration in an isolated population: the Vallecamonica study. Neurol Sci (2011) 0.81
Logopenic syndrome in posterior cortical atrophy. J Neurol (2012) 0.80
Challenges and new opportunities in the investigation of new drug therapies to treat frontotemporal dementia. Expert Opin Ther Targets (2008) 0.80
A visual [18F]FDG-PET rating scale for the differential diagnosis of frontotemporal lobar degeneration. Eur Arch Psychiatry Clin Neurosci (2011) 0.80
The Language Profile of Behavioral Variant Frontotemporal Dementia. J Alzheimers Dis (2015) 0.80
Frontotemporal dementia: diagnosis, deficits and management. Neurodegener Dis Manag (2014) 0.79
Identification of misdiagnosed fronto-temporal dementia using APOE genotype and phenotype-genotype correlation analyses. Curr Alzheimer Res (2014) 0.79
Early onset frontotemporal dementia with psychiatric presentation due to the C9ORF72 hexanucleotide repeat expansion: a case report. BMC Neurol (2014) 0.79
Latent profile analysis in frontotemporal lobar degeneration and related disorders: clinical presentation and SPECT functional correlates. BMC Neurol (2007) 0.79
New perspective on parkinsonism in frontotemporal lobar degeneration. J Mov Disord (2013) 0.79
Features of Patients With Nonfluent/Agrammatic Primary Progressive Aphasia With Underlying Progressive Supranuclear Palsy Pathology or Corticobasal Degeneration. JAMA Neurol (2016) 0.78
Typical and atypical pathology in primary progressive aphasia variants. Ann Neurol (2017) 0.78
Cognitive deficits and reduced insight in primary progressive aphasia. Am J Alzheimers Dis Other Demen (2008) 0.78
Estimating severity of illness and disability in Frontotemporal Dementia: Preliminary analysis of the Dementia Disability Rating (DDR). Acta Neuropsychol (2011) 0.78
Impaired Recognition and Regulation of Disgust Is Associated with Distinct but Partially Overlapping Patterns of Decreased Gray Matter Volume in the Ventroanterior Insula. Biol Psychiatry (2015) 0.78
Prevalence, characteristics, and survival of frontotemporal lobar degeneration syndromes. Neurology (2016) 0.78
Neuropathologic diagnostic and nosologic criteria for frontotemporal lobar degeneration: consensus of the Consortium for Frontotemporal Lobar Degeneration. Acta Neuropathol (2007) 8.10
Common variants at 7p21 are associated with frontotemporal lobar degeneration with TDP-43 inclusions. Nat Genet (2010) 5.52
FUS pathology defines the majority of tau- and TDP-43-negative frontotemporal lobar degeneration. Acta Neuropathol (2010) 2.30
Neuropathological substrates of psychiatric symptoms in prospectively studied patients with autopsy-confirmed dementia with lewy bodies. Am J Psychiatry (2004) 1.82
FET proteins TAF15 and EWS are selective markers that distinguish FTLD with FUS pathology from amyotrophic lateral sclerosis with FUS mutations. Brain (2011) 1.76
Primary progressive aphasia: diagnosis, varieties, evolution. J Int Neuropsychol Soc (2003) 1.56
Diagnosis and treatment of dementia: 2. Diagnosis. CMAJ (2008) 1.55
Semantic dementia: demography, familial factors and survival in a consecutive series of 100 cases. Brain (2009) 1.31
Distinct pathological subtypes of FTLD-FUS. Acta Neuropathol (2010) 1.26
Neuropsychological testing and assessment for dementia. Alzheimers Dement (2007) 1.15
Behavior and cognition in corticobasal degeneration and progressive supranuclear palsy. J Neurol Sci (2009) 1.11
A longitudinal study of behavior in frontotemporal dementia and primary progressive aphasia. Cogn Behav Neurol (2004) 1.11
The diagnosis and course of frontotemporal dementia. Alzheimer Dis Assoc Disord (2007) 1.08
TMEM106B is a genetic modifier of frontotemporal lobar degeneration with C9orf72 hexanucleotide repeat expansions. Acta Neuropathol (2014) 1.08
Postmortem examination of vascular lesions in cognitive impairment: a survey among neuropathological services. Stroke (2006) 1.05
What is semantic dementia?: a cohort study of diagnostic features and clinical boundaries. Arch Neurol (2010) 1.02
Systematic review of primary intracranial glioblastoma multiforme with symptomatic spinal metastases, with two illustrative patients. J Clin Neurosci (2012) 1.01
Transportin 1 accumulates specifically with FET proteins but no other transportin cargos in FTLD-FUS and is absent in FUS inclusions in ALS with FUS mutations. Acta Neuropathol (2012) 0.97
Enteric alpha-synuclein expression is increased in Parkinson's disease but not Alzheimer's disease. Mov Disord (2013) 0.97
Alzheimer's disease with and without cerebral infarcts. J Neurol Sci (2004) 0.97
Corticobasal degeneration and progressive aphasia. Neurology (2006) 0.96
Primary progressive aphasia and Pick complex. J Neurol Sci (2003) 0.93
Behavioral quantitation is more sensitive than cognitive testing in frontotemporal dementia. Alzheimer Dis Assoc Disord (2003) 0.93
Primary progressive aphasia: a review of the neurobiology of a common presentation of Pick complex. Am J Alzheimers Dis Other Demen (2002) 0.92
Rates of cognitive decline in Alzheimer's disease and dementia with Lewy bodies. Dement Geriatr Cogn Disord (2003) 0.92
Alpha-synuclein in the appendiceal mucosa of neurologically intact subjects. Mov Disord (2013) 0.88
High-resolution whole-genome analysis of skull base chordomas implicates FHIT loss in chordoma pathogenesis. Neoplasia (2012) 0.87
Quantitative and qualitative analyses of clock drawing in frontotemporal dementia and Alzheimer's disease. J Int Neuropsychol Soc (2006) 0.87
Novel types of frontotemporal lobar degeneration: beyond tau and TDP-43. J Mol Neurosci (2011) 0.87
Validation of the seven-minute screen neurocognitive battery for the diagnosis of dementia in a Spanish population-based sample. Dement Geriatr Cogn Disord (2006) 0.86
Frontotemporal degeneration, Pick's disease, Pick complex, and Ravel. Ann Neurol (2003) 0.84
Extrapyramidal syndromes in frontotemporal degeneration. J Mol Neurosci (2011) 0.84
Frontotemporal dementia. Med Clin North Am (2002) 0.84
Longitudinal associations of need for cognition, cognitive activity, and depressive symptomatology with cognitive function in recent retirees. J Gerontol B Psychol Sci Soc Sci (2012) 0.83
Intranuclear rodlets in the substantia nigra: interactions with marinesco bodies, ubiquitin, and promyelocytic leukemia protein. J Neuropathol Exp Neurol (2004) 0.82
Sarcoidosis complicated by cirrhosis and hepatopulmonary syndrome. Can Respir J (2008) 0.81
Leukoaraiosis and ischemia: beyond the myth. Stroke (2006) 0.80
Comorbid rat model of ischemia and β-amyloid toxicity: striatal and cortical degeneration. Brain Pathol (2014) 0.80
Preferred terminology. Ann Neurol (2003) 0.80
Intranuclear rodlets in human pancreatic islet cells. Pancreas (2007) 0.79
Amusia as an early manifestation of frontotemporal dementia caused by a novel progranulin mutation. J Neurol (2010) 0.79
FUS mutations in sporadic juvenile ALS: another step toward understanding ALS pathogenesis. Neurology (2010) 0.79
Extended kindred with recessive late-onset Alzheimer disease maps to locus 8p22-p21.2: a genome-wide linkage analysis. Alzheimer Dis Assoc Disord (2012) 0.79
Sequential performance in young and older adults: evidence of chunking and inhibition. Neuropsychol Dev Cogn B Aging Neuropsychol Cogn (2010) 0.78
Immunohistochemical expression of PTTG in brain tumors. Anticancer Res (2013) 0.78
A multigenerational pedigree of late-onset Alzheimer's disease implies new genetic causes. Brain (2005) 0.78
Spinal lobular capillary hemangioma with an intramedullary component. Clin Neuropathol (2013) 0.77
Sox10 is superior to S100 in the diagnosis of meningioma. Appl Immunohistochem Mol Morphol (2015) 0.77
Clinical and immunologic features of an atypical intracranial mycobacterium avium complex (MAC) infection compared with those of pulmonary MAC infections. Clin Vaccine Immunol (2008) 0.77
Reduction of neuronal intranuclear rodlets immunoreactive for tubulin and glucocorticoid receptor in Alzheimer's disease. Brain Pathol (2002) 0.77
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Rosai-Dorfman disease involving the neurohypophysis. Pituitary (2010) 0.76
Intracranial caseating granulomas with no infectious organism detected. Can J Neurol Sci (2011) 0.76
Intention tremor, parkinsonism, and generalized brain atrophy in male carriers of fragile X. Neurology (2002) 0.76
Chordoid meningiomas: incidence and clinicopathological features of a case series over 18 years. Neuropathology (2014) 0.76
A 63 year old woman with white matter lesions and pachymeningeal inflammation. Brain Pathol (2013) 0.76
Neurosurgical management of a giant colloid cyst with atypical clinical and radiological presentation. J Neurosurg (2014) 0.75
Familial dementia with dentate atrophy and failure of neurogenesis. Ann Neurol (2003) 0.75
Primary cerebral angiitis associated with amyloid angiopathy. Arch Neurol (2011) 0.75
Hemorrhagic epidermoid cyst in a patient with generalized tonic clonic seizure. J Clin Neurosci (2013) 0.75
Adult-onset leukoencephalopathy with axonal spheroids and pigmented glia: report on a case with morphometric studies. Clin Neuropathol (2013) 0.75
Fanning the Flames in Anti-N-methyl-D-aspartate Receptor Encephalitis. Int J Gynecol Pathol (2015) 0.75
Plaque-like demyelination in acute disseminated encephalomyelitis (ADEM) - an autopsy case report. Clin Neuropathol (2013) 0.75
Comparison of infectious and noninfectious intracranial caseating granulomas. Brain Pathol (2012) 0.75