PubRank

Manfred Ballmann

Author PubWeight™ 32.01‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the F508del-CFTR mutation. Thorax 2011 2.84
2 Inhalation treatment with glutathione in patients with cystic fibrosis. A randomized clinical trial. Am J Respir Crit Care Med 2013 2.07
3 European best practice guidelines for cystic fibrosis neonatal screening. J Cyst Fibros 2009 1.75
4 Intestinal current measurement for diagnostic classification of patients with questionable cystic fibrosis: validation and reference data. Thorax 2010 1.61
5 Alteration of the pulmonary surfactant system in full-term infants with hereditary ABCA3 deficiency. Am J Respir Crit Care Med 2006 1.30
6 Genes that determine immunology and inflammation modify the basic defect of impaired ion conductance in cystic fibrosis epithelia. J Med Genet 2010 1.26
7 Effect of treatment with dornase alpha on airway inflammation in patients with cystic fibrosis. Am J Respir Crit Care Med 2003 1.24
8 Ex vivo CF diagnosis by intestinal current measurements (ICM) in small aperture, circulating Ussing chambers. J Cyst Fibros 2004 1.05
9 Basic protocol for transepithelial nasal potential difference measurements. J Cyst Fibros 2004 1.01
10 Pulmonary surfactant, lung function, and endobronchial inflammation in cystic fibrosis. Am J Respir Crit Care Med 2004 0.99
11 The risk, prevention, and outcome of cytomegalovirus after pediatric lung transplantation. Transplantation 2009 0.94
12 Functional analysis of F508del CFTR in native human colon. Biochim Biophys Acta 2010 0.92
13 Ex vivo transcriptional profiling reveals a common set of genes important for the adaptation of Pseudomonas aeruginosa to chronically infected host sites. Environ Microbiol 2012 0.91
14 Increased mortality after pulmonary fungal infection within the first year after pediatric lung transplantation. J Heart Lung Transplant 2008 0.87
15 Lung and heart-lung transplantation in children and adolescents: a long-term single-center experience. J Heart Lung Transplant 2009 0.86
16 Applying clinical outcome variables to appropriate aerosolized antibiotics for the treatment of patients with cystic fibrosis. Respir Med 2011 0.84
17 Calculation of the capnographic index based on expiratory molar mass-volume-curves--a suitable tool to screen for cystic fibrosis lung disease. J Cyst Fibros 2012 0.84
18 Quality of life is associated with physical activity and fitness in cystic fibrosis. BMC Pulm Med 2014 0.84
19 Effect of supervised training on FEV1 in cystic fibrosis: a randomised controlled trial. J Cyst Fibros 2013 0.84
20 Cystic fibrosis transmembrane conductance regulator (CFTR)-mediated residual chloride secretion does not protect against early chronic Pseudomonas aeruginosa infection in F508del homozygous cystic fibrosis patients. Pediatr Res 2003 0.83
21 Short-term effect of physiotherapy on variability of the lung clearance index in children with cystic fibrosis. Pediatr Pulmonol 2010 0.83
22 Cytomegalovirus immunoglobulin decreases the risk of cytomegalovirus infection but not disease after pediatric lung transplantation. J Heart Lung Transplant 2009 0.82
23 Pulmonary retransplantation in paediatric patients: a justified therapeutic option? A single-centre experience. Eur J Cardiothorac Surg 2010 0.81
24 Sequential analysis of surfactant, lung function and inflammation in cystic fibrosis patients. Respir Res 2005 0.81
25 Prognostic relevance of hypoglycemia following an oral glucose challenge for cystic fibrosis-related diabetes. Diabetes Care 2011 0.80
26 Diabetes in cystic fibrosis: multicenter screening results based on current guidelines. PLoS One 2013 0.79
27 Ex vivo biochemical analysis of CFTR in human rectal biopsies. Biochim Biophys Acta 2006 0.78
28 Heart-lung transplantation in a 14-year-old boy with Alström syndrome. J Heart Lung Transplant 2007 0.78
29 Size reduction of donor organs in pediatric lung transplantation. Pediatr Transplant 2009 0.77
30 Surfactant protein a in cystic fibrosis: supratrimeric structure and pulmonary outcome. PLoS One 2012 0.75
31 Minimal acute rejection in pediatric lung transplantation--does it matter? Pediatr Transplant 2010 0.75
32 Cystic fibrosis disease-specific centiles in 2000 and 2005. Am J Respir Crit Care Med 2006 0.75
33 Immunochemical analysis of mutant CFTR in lung explants. Cell Physiol Biochem 2012 0.75
34 CFTR protein analysis of splice site mutation 2789+5 G-A. J Cyst Fibros 2007 0.75