Published in Am J Respir Crit Care Med on December 18, 2003
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Open-label, follow-on study of azithromycin in pediatric patients with CF uninfected with Pseudomonas aeruginosa. Pediatr Pulmonol (2012) 2.08
Pseudomonas aeruginosa microevolution during cystic fibrosis lung infection establishes clones with adapted virulence. Am J Respir Crit Care Med (2009) 2.08
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Maternal smoking in pregnancy and asthma in preschool children: a pooled analysis of eight birth cohorts. Am J Respir Crit Care Med (2012) 1.98
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Endothelial nitric oxide synthase variants in cystic fibrosis lung disease. Am J Respir Crit Care Med (2002) 1.87
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Stenotrophomonas maltophilia in cystic fibrosis: serologic response and effect on lung disease. Am J Respir Crit Care Med (2010) 1.82
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Hospital-based surveillance to estimate the burden of rotavirus gastroenteritis among European children younger than 5 years of age. Pediatrics (2009) 1.76
Lung clearance index as an outcome measure for clinical trials in young children with cystic fibrosis. A pilot study using inhaled hypertonic saline. Am J Respir Crit Care Med (2013) 1.76
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Molecular architecture of the regulatory Locus sae of Staphylococcus aureus and its impact on expression of virulence factors. J Bacteriol (2003) 1.67
Sputum induction in routine clinical care of children with cystic fibrosis. J Pediatr (2010) 1.67
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Nonmucoid Pseudomonas aeruginosa expresses alginate in the lungs of patients with cystic fibrosis and in a mouse model. J Infect Dis (2005) 1.62
Intestinal current measurement for diagnostic classification of patients with questionable cystic fibrosis: validation and reference data. Thorax (2010) 1.61
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The effect of chronic infection with Aspergillus fumigatus on lung function and hospitalization in patients with cystic fibrosis. Chest (2009) 1.56
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DYX1C1 is required for axonemal dynein assembly and ciliary motility. Nat Genet (2013) 1.44
An official American Thoracic Society research statement: noninfectious lung injury after hematopoietic stem cell transplantation: idiopathic pneumonia syndrome. Am J Respir Crit Care Med (2011) 1.40
Does pet ownership in infancy lead to asthma or allergy at school age? Pooled analysis of individual participant data from 11 European birth cohorts. PLoS One (2012) 1.39
Mutation of SFTPC in infantile pulmonary alveolar proteinosis with or without fibrosing lung disease. Am J Med Genet A (2004) 1.39
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Pulmonary T(H)2 response in Pseudomonas aeruginosa-infected patients with cystic fibrosis. J Allergy Clin Immunol (2005) 1.37
A Th17- and Th2-skewed cytokine profile in cystic fibrosis lungs represents a potential risk factor for Pseudomonas aeruginosa infection. Am J Respir Crit Care Med (2013) 1.36
Ultrastructural characterization of cystic fibrosis sputum using atomic force and scanning electron microscopy. J Cyst Fibros (2011) 1.36
Unifying candidate gene and GWAS Approaches in Asthma. PLoS One (2010) 1.36
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Life-threatening vallecular cyst in a 3-month-old infant: case report and literature review. Clin Pediatr (Phila) (2004) 1.34
The revised German Cystic Fibrosis Questionnaire: validation of a disease-specific health-related quality of life instrument. Qual Life Res (2003) 1.31
Effect of pulmonary exacerbations on long-term lung function decline in cystic fibrosis. Eur Respir J (2011) 1.31
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Alteration of the pulmonary surfactant system in full-term infants with hereditary ABCA3 deficiency. Am J Respir Crit Care Med (2006) 1.30
Beta-defensins and LL-37 in bronchoalveolar lavage fluid of patients with cystic fibrosis. J Cyst Fibros (2004) 1.29
Some ABCA3 mutations elevate ER stress and initiate apoptosis of lung epithelial cells. Respir Res (2011) 1.28
Genes that determine immunology and inflammation modify the basic defect of impaired ion conductance in cystic fibrosis epithelia. J Med Genet (2010) 1.26
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Inhaled hypertonic saline in infants and children younger than 6 years with cystic fibrosis: the ISIS randomized controlled trial. JAMA (2012) 1.25
Prenatal stress enhances susceptibility of murine adult offspring toward airway inflammation. J Immunol (2006) 1.24
Dietary prevention of allergic diseases in infants and small children. Pediatr Allergy Immunol (2008) 1.24
Increased arginase activity in cystic fibrosis airways. Am J Respir Crit Care Med (2005) 1.21
Colistin-tobramycin combinations are superior to monotherapy concerning the killing of biofilm Pseudomonas aeruginosa. J Infect Dis (2010) 1.21
Variants in a novel epidermal collagen gene (COL29A1) are associated with atopic dermatitis. PLoS Biol (2007) 1.21
Sequence diversity of the mucABD locus in Pseudomonas aeruginosa isolates from patients with cystic fibrosis. Microbiology (2006) 1.20
Associations between total serum IgE levels and the 6 potentially functional variants within the genes IL4, IL13, and IL4RA in German children: the German Multicenter Atopy Study. J Allergy Clin Immunol (2003) 1.20
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Plastic bronchitis as an unusual cause of mucus plugging in cystic fibrosis. Pediatr Pulmonol (2009) 1.19
An interaction between filaggrin mutations and early food sensitization improves the prediction of childhood asthma. J Allergy Clin Immunol (2009) 1.19
Mutations in SPAG1 cause primary ciliary dyskinesia associated with defective outer and inner dynein arms. Am J Hum Genet (2013) 1.19
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Restoring airway surface liquid in cystic fibrosis. N Engl J Med (2006) 1.14
Allergic rhinitis as a predictor for wheezing onset in school-aged children. J Allergy Clin Immunol (2010) 1.14