Published in Pediatrics on July 24, 2006
Developmental and pathogenic mechanisms of basement membrane assembly. Curr Pharm Des (2009) 1.80
Mutations in the human laminin beta2 (LAMB2) gene and the associated phenotypic spectrum. Hum Mutat (2010) 1.67
Variable phenotype of Pierson syndrome. Pediatr Nephrol (2008) 1.04
A milder variant of Pierson syndrome. Pediatr Nephrol (2007) 1.02
A novel mutation of LAMB2 in a multigenerational mennonite family reveals a new phenotypic variant of Pierson syndrome. Ophthalmology (2011) 0.94
Forced expression of laminin beta1 in podocytes prevents nephrotic syndrome in mice lacking laminin beta2, a model for Pierson syndrome. Proc Natl Acad Sci U S A (2011) 0.87
Urinary neutrophil gelatinase-associated lipocalin as a biomarker of nephritis in childhood-onset systemic lupus erythematosus. Arthritis Rheum (2006) 2.27
Identification of S664 TSC2 phosphorylation as a marker for extracellular signal-regulated kinase mediated mTOR activation in tuberous sclerosis and human cancer. Cancer Res (2007) 1.94
Plexiform and dermal neurofibromas and pigmentation are caused by Nf1 loss in desert hedgehog-expressing cells. Cancer Cell (2008) 1.86
Viable mouse models of acid beta-glucosidase deficiency: the defect in Gaucher disease. Am J Pathol (2003) 1.81
System for integrated adherence monitoring: real-time non-adherence risk assessment in pediatric kidney transplantation. Pediatr Transplant (2012) 1.74
Mutations in the human laminin beta2 (LAMB2) gene and the associated phenotypic spectrum. Hum Mutat (2010) 1.67
Cdc42 coordinates proliferation, polarity, migration, and differentiation of small intestinal epithelial cells in mice. Gastroenterology (2013) 1.62
BK viremia precedes hemorrhagic cystitis in children undergoing allogeneic hematopoietic stem cell transplantation. Biol Blood Marrow Transplant (2013) 1.62
Small vessels, big trouble in the kidneys and beyond: hematopoietic stem cell transplantation-associated thrombotic microangiopathy. Blood (2011) 1.43
The impact of sirolimus on sex hormones in male adolescent kidney recipients. Pediatr Transplant (2012) 1.40
Cost-effectiveness of latent tuberculosis screening before steroid therapy for idiopathic nephrotic syndrome in children. Am J Kidney Dis (2012) 1.40
Association of noninvasively measured renal protein biomarkers with histologic features of lupus nephritis. Arthritis Rheum (2012) 1.32
Effect of rotavirus strain on the murine model of biliary atresia. J Virol (2006) 1.31
Cdc42 GTPase-activating protein deficiency promotes genomic instability and premature aging-like phenotypes. Proc Natl Acad Sci U S A (2007) 1.25
Abnormalities in the alternative pathway of complement in children with hematopoietic stem cell transplant-associated thrombotic microangiopathy. Blood (2013) 1.22
Comparison of adolescent and young adult self-collected and clinician-collected samples for human papillomavirus. Obstet Gynecol (2004) 1.18
SLC26A9 is expressed in gastric surface epithelial cells, mediates Cl-/HCO3- exchange, and is inhibited by NH4+. Am J Physiol Cell Physiol (2005) 1.15
Interferon-gamma:interleukin 4 ratios and associated type 1 cytokine expression in juvenile rheumatoid arthritis synovial tissue. J Rheumatol (2002) 1.14
Rac1 is essential for intraembryonic hematopoiesis and for the initial seeding of fetal liver with definitive hematopoietic progenitor cells. Blood (2007) 1.10
Neurodevelopmental deficits in Pierson (microcoria-congenital nephrosis) syndrome. Am J Med Genet A (2007) 1.09
The Allocation of Treatment Responsibility scale: a novel tool for assessing patient and caregiver management of pediatric medical treatment regimens. Pediatr Transplant (2010) 1.08
MHC class I-specific antibody binding to nonhematopoietic cells drives complement activation to induce transfusion-related acute lung injury in mice. J Exp Med (2011) 1.06
Blood, and not urine, BK viral load predicts renal outcome in children with hemorrhagic cystitis following hematopoietic stem cell transplantation. Biol Blood Marrow Transplant (2011) 1.04
Dyslipidemia in children with chronic kidney disease. Kidney Int (2010) 0.99
The evolution of population pharmacokinetic models to describe the enterohepatic recycling of mycophenolic acid in solid organ transplantation and autoimmune disease. Clin Pharmacokinet (2011) 0.97
Pulmonary arterial hypertension in pediatric patients with hematopoietic stem cell transplant-associated thrombotic microangiopathy. Biol Blood Marrow Transplant (2012) 0.97
Gaining the PROMIS perspective from children with nephrotic syndrome: a Midwest pediatric nephrology consortium study. Health Qual Life Outcomes (2013) 0.96
Inosine monophosphate dehydrogenase (IMPDH) activity as a pharmacodynamic biomarker of mycophenolic acid effects in pediatric kidney transplant recipients. J Clin Pharmacol (2010) 0.96
Gaining the Patient Reported Outcomes Measurement Information System (PROMIS) perspective in chronic kidney disease: a Midwest Pediatric Nephrology Consortium study. Pediatr Nephrol (2014) 0.94
Renal arteriolar C4d deposition: a novel characteristic of hematopoietic stem cell transplantation-associated thrombotic microangiopathy. Transplantation (2013) 0.94
Does early initiation of therapeutic plasma exchange improve outcome in pediatric stem cell transplant-associated thrombotic microangiopathy? Transfusion (2012) 0.94
Importance of murine study design for testing toxicity of retroviral vectors in support of phase I trials. Mol Ther (2007) 0.94
Lipid rafts in cytokine signaling. Cytokine Growth Factor Rev (2004) 0.93
Dependence of reversibility and progression of mouse neuronopathic Gaucher disease on acid beta-glucosidase residual activity levels. Mol Genet Metab (2008) 0.91
Cerebellar and posterior fossa malformations in patients with autism-associated chromosome 22q13 terminal deletion. Am J Med Genet A (2012) 0.90
UGT1A9, UGT2B7, and MRP2 genotypes can predict mycophenolic acid pharmacokinetic variability in pediatric kidney transplant recipients. Ther Drug Monit (2012) 0.90
Novel fibrillin 1 mutation in a case of neonatal Marfan syndrome: the increasing importance of early recognition. Congenit Heart Dis (2008) 0.89
Midgestational lethality in mice lacking the parathyroid hormone (PTH)/PTH-related peptide receptor is associated with abrupt cardiomyocyte death. Endocrinology (2003) 0.89
Rotavirus replication in the cholangiocyte mediates the temporal dependence of murine biliary atresia. PLoS One (2013) 0.88
Successful early intervention for hyperacute transplant-associated thrombotic microangiopathy following pediatric hematopoietic stem cell transplantation. Pediatr Transplant (2010) 0.88
Cystatin C-estimated glomerular filtration rate in pediatric autologous hematopoietic stem cell transplantation. Biol Blood Marrow Transplant (2012) 0.87
Acute Rejection Clinically Defined Phenotypes Correlate With Long-term Renal Allograft Survival. Transplantation (2015) 0.87
Pediatric aspects of therapeutic drug monitoring of mycophenolic acid in renal transplantation. Transplant Rev (Orlando) (2011) 0.87
The proximal convoluted tubule is a target for the uroguanylin-regulated natriuretic response. J Pediatr Gastroenterol Nutr (2006) 0.86
Calpain II colocalizes with detergent-insoluble rafts on human and Jurkat T-cells. Biochem Biophys Res Commun (2002) 0.86
The physicians quality reporting initiative: measure development, implementation and current procedural terminology coding. Adv Anat Pathol (2010) 0.83
Psychosocial Assessment Tool 2.0_General: validity of a psychosocial risk screener in a pediatric kidney transplant sample. Pediatr Transplant (2011) 0.83
The peptidoglycan-associated lipoprotein OprL helps protect a Pseudomonas aeruginosa mutant devoid of the transactivator OxyR from hydrogen peroxide-mediated killing during planktonic and biofilm culture. J Bacteriol (2008) 0.82
Tacrolimus-based immunosuppression with steroid withdrawal in pediatric kidney transplantation--4-year experience at a moderate-volume center. Pediatr Transplant (2003) 0.82
Increasing incidence of post-kidney transplant anemia in children. Am J Transplant (2005) 0.82
Risk of tacrolimus toxicity in CYP3A5 nonexpressors treated with intravenous nicardipine after kidney transplantation. Transplantation (2012) 0.81
Reliable individualized monitoring improves cholesterol control in kidney transplant recipients. Pediatrics (2013) 0.81
Subacute Propionibacterium acnes osteomyelitis of the spine in an adolescent. J Pediatr Orthop B (2003) 0.80
Clinically "silent" weight loss associated with mycophenolate mofetil in pediatric renal transplant recipients. Pediatr Transplant (2008) 0.79
An artificial tendon with durable muscle interface. J Orthop Res (2010) 0.79
Transitioning cognitively impaired young patients with special health needs to adult-oriented care: collaboration between medical providers and pediatric psychologists. Curr Opin Pediatr (2010) 0.79
Family strategies for achieving medication adherence in pediatric kidney transplantation. Nurs Res (2011) 0.79
The impact of disease duration on quality of life in children with nephrotic syndrome: a Midwest Pediatric Nephrology Consortium study. Pediatr Nephrol (2015) 0.79
Protective immunity and use of bortezomib for antibody-mediated rejection in a pediatric kidney transplant recipient. Pediatr Transplant (2014) 0.79
Fibrinogen deficiency, but not plasminogen deficiency, increases mortality synergistically in combination with sickle hemoglobin SAD in transgenic mice. Am J Hematol (2007) 0.79
Thrombocytopenia and proteinuria. Nonmuscle myosin heavy-chain-9-related disease ( MYH9 RD) or Epstein syndrome (ES). Pediatr Nephrol (2008) 0.78
A Banff Component Scoring-based Histologic Assessment of Bortezomib-based Antibody-mediated Rejection Therapy. Transplantation (2015) 0.78
Preparing for transition? The allocation of oral medication regimen tasks in adolescents with renal transplants. Pediatr Transplant (2010) 0.78
Endogenously expressed multimeric self-cleaving hammerhead ribozymes ablate mutant collagen in cellulo. Mol Ther (2005) 0.78
Intensive hemodialysis for cardiomyopathy associated with end-stage renal disease. Pediatr Nephrol (2011) 0.77
BK virus nephropathy in a pediatric autologous stem-cell transplant recipient. Pediatr Blood Cancer (2010) 0.77
Effects of unbound mycophenolic acid on inosine monophosphate dehydrogenase inhibition in pediatric kidney transplant patients. Ther Drug Monit (2014) 0.77
HIFU lesion volume as a function of sonication time, as determined by MRI, histology, and computations. J Biomech Eng (2010) 0.77
Population pharmacokinetic-pharmacodynamic modelling of mycophenolic acid in paediatric renal transplant recipients in the early post-transplant period. Br J Clin Pharmacol (2014) 0.76
Detection of SYT-SSX rearrangements in synovial sarcomas by real-time one-step RT-PCR. Pediatr Dev Pathol (2005) 0.76
Papillary urothelial neoplasm of low malignant potential in a pediatric renal transplant recipient (PUNLMP): a case report. Pediatr Transplant (2007) 0.76
The Noninvasive Urinary Polyomavirus Haufen Test Predicts BK Virus Nephropathy in Children After Hematopoietic Cell Transplantation: A Pilot Study. Transplantation (2016) 0.75
Erratum: IgG1 protects against renal disease in a mouse model of cryoglobulinaemia. Nature (2015) 0.75
Prevalence and predictors of aortic dilation as a novel cardiovascular complication in children with end-stage renal disease. Clin Nephrol (2015) 0.75
Should recipients with obstructive uropathy undergo close surveillance for BK virus infection post-transplant? Pediatr Transplant (2012) 0.75
Creating a monster: non-adherence underlying late transplant rejection. Pediatr Transplant (2012) 0.75
Granular cell astrocytoma of the cerebellum: report of the first case. Am J Clin Pathol (2006) 0.75
Interaction between tacrolimus and intravenous nicardipine in the treatment of post-kidney transplant hypertension at pediatric hospitals. Pediatr Transplant (2010) 0.75
A fetus with hypoplastic left heart syndrome and tricuspid stenosis with evolving hydrops fetalis. Pediatr Cardiol (2012) 0.75
End stage renal disease and kidney transplant in patients with anorectal malformation: is there an alternative route? Pediatr Surg Int (2015) 0.75
Structure-activity relationships of non-imidazole H(3) receptor ligands. Part 3: 5-Substituted 3-phenyl-1,2,4-oxadiazoles as potent antagonists. Bioorg Med Chem Lett (2004) 0.75
Fetal cervical teratoma: What is the role of fetal MRI in predicting pulmonary hypoplasia? Fetal Diagn Ther (2013) 0.75
Daclizumab therapy in kidney transplantation-different mechanisms of action in- versus ex-vivo? Transpl Immunol (2005) 0.75