Published in J Neurol on December 08, 2008
An item response analysis of the motor and behavioral subscales of the unified Huntington's disease rating scale in huntington disease gene expansion carriers. Mov Disord (2011) 1.68
Longitudinal change in regional brain volumes in prodromal Huntington disease. J Neurol Neurosurg Psychiatry (2010) 1.53
Magnetic resonance spectroscopy biomarkers in premanifest and early Huntington disease. Neurology (2010) 1.07
Regionally selective atrophy of subcortical structures in prodromal HD as revealed by statistical shape analysis. Hum Brain Mapp (2012) 1.07
Early atrophy of pallidum and accumbens nucleus in Huntington's disease. J Neurol (2010) 1.04
Loss of corticostriatal and thalamostriatal synaptic terminals precedes striatal projection neuron pathology in heterozygous Q140 Huntington's disease mice. Neurobiol Dis (2013) 0.95
MRI T2 Hypointensities in basal ganglia of premanifest Huntington's disease. PLoS Curr (2010) 0.93
Early changes in the hypothalamic region in prodromal Huntington disease revealed by MRI analysis. Neurobiol Dis (2010) 0.91
Basal ganglia atrophy in prodromal Huntington's disease is detectable over one year using automated segmentation. Mov Disord (2011) 0.89
Seven-year clinical follow-up of premanifest carriers of Huntington's disease. PLoS Curr (2011) 0.88
Depression in the early stages of Huntington disease. Neurodegener Dis Manag (2011) 0.85
Neuroanatomical correlates of cognitive functioning in prodromal Huntington disease. Brain Behav (2013) 0.85
Ventral striatal volume is associated with cognitive decline in older people: a population based MR-study. Neurobiol Aging (2010) 0.83
Cognitive reserve and brain reserve in prodromal Huntington's disease. J Int Neuropsychol Soc (2013) 0.83
Regional atrophy associated with cognitive and motor function in prodromal Huntington disease. J Huntingtons Dis (2013) 0.81
Complex relationships between cerebral blood flow and brain atrophy in early Huntington's disease. Neuroimage (2011) 0.81
Striatal metabolism and psychomotor speed as predictors of motor onset in Huntington's disease. J Neurol (2014) 0.78
Interaction without intent: the shape of the social world in Huntington's disease. Soc Cogn Affect Neurosci (2015) 0.78
Neuropsychiatry and White Matter Microstructure in Huntington's Disease. J Huntingtons Dis (2015) 0.78
Magnetization transfer imaging in 'premanifest' Huntington's disease. J Neurol (2009) 0.77
Patients with schizophrenia show aberrant patterns of basal ganglia activation: Evidence from ALE meta-analysis. Neuroimage Clin (2017) 0.75
Clinical and genetic investigation of a Brazilian family with Huntington's disease. Funct Neurol (2016) 0.75
"Mini-mental state". A practical method for grading the cognitive state of patients for the clinician. J Psychiatr Res (1975) 301.74
Accurate, robust, and automated longitudinal and cross-sectional brain change analysis. Neuroimage (2002) 8.03
Unified Huntington's Disease Rating Scale: reliability and consistency. Huntington Study Group. Mov Disord (1996) 8.02
A new model for prediction of the age of onset and penetrance for Huntington's disease based on CAG length. Clin Genet (2004) 4.73
Preparing for preventive clinical trials: the Predict-HD study. Arch Neurol (2006) 3.57
The behavioural and motor consequences of focal lesions of the basal ganglia in man. Brain (1994) 3.54
Onset and rate of striatal atrophy in preclinical Huntington disease. Neurology (2004) 2.81
Evidence for more widespread cerebral pathology in early HD: an MRI-based morphometric analysis. Neurology (2003) 2.73
Open interconnected model of basal ganglia-thalamocortical circuitry and its relevance to the clinical syndrome of Huntington's disease. Mov Disord (2001) 2.40
The distribution of structural neuropathology in pre-clinical Huntington's disease. Brain (2002) 2.05
Brain structure in preclinical Huntington's disease. Biol Psychiatry (2005) 2.05
Regional cortical thinning in preclinical Huntington disease and its relationship to cognition. Neurology (2005) 1.95
Basal ganglia volume and proximity to onset in presymptomatic Huntington disease. Arch Neurol (1996) 1.74
Reduced basal ganglia volume associated with the gene for Huntington's disease in asymptomatic at-risk persons. Neurology (1994) 1.61
Reduced basal ganglia blood flow and volume in pre-symptomatic, gene-tested persons at-risk for Huntington's disease. Brain (1999) 1.56
Verbal episodic memory declines prior to diagnosis in Huntington's disease. Neuropsychologia (2007) 1.54
Psychomotor, executive, and memory function in preclinical Huntington's disease. J Clin Exp Neuropsychol (2002) 1.51
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Regional white matter change in pre-symptomatic Huntington's disease: a diffusion tensor imaging study. Psychiatry Res (2005) 1.43
Longitudinal cognitive and motor changes among presymptomatic Huntington disease gene carriers. Arch Neurol (1999) 1.41
Brain imaging and cognitive dysfunctions in Huntington's disease. J Psychiatry Neurosci (2006) 1.35
Profile of cognitive progression in early Huntington's disease. Neurology (2003) 1.35
Thalamic atrophy in Huntington's disease co-varies with cognitive performance: a morphometric MRI analysis. Cereb Cortex (2004) 1.32
Executive dysfunction in early stages of Huntington's disease is associated with striatal and insular atrophy: a neuropsychological and voxel-based morphometric study. J Neurol Sci (2005) 1.31
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Neuropsychological correlates of brain atrophy in Huntington's disease: a magnetic resonance imaging study. Neuroradiology (1992) 1.08
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A prospective evaluation of cognitive decline in early Huntington's disease: functional and radiographic correlates. Neurology (1995) 0.95
Neuropsychological and neuroradiological correlates in Huntington's disease. J Neurol Neurosurg Psychiatry (1988) 0.90
Single photon emission computed tomographic blood flow and magnetic resonance volume imaging of basal ganglia in Huntington's disease. Arch Neurol (1996) 0.89
Longitudinal personality changes among presymptomatic Huntington disease gene carriers. Neuropsychiatry Neuropsychol Behav Neurol (2002) 0.87
Behavioural complaints in participants who underwent predictive testing for Huntington's disease. J Med Genet (2002) 0.79
Probability of regaining dexterity in the flaccid upper limb: impact of severity of paresis and time since onset in acute stroke. Stroke (2003) 3.43
Potential endpoints for clinical trials in premanifest and early Huntington's disease in the TRACK-HD study: analysis of 24 month observational data. Lancet Neurol (2011) 2.99
Brain magnetic resonance imaging correlates of impaired cognition in patients with type 2 diabetes. Diabetes (2006) 2.77
Probabilistic segmentation of white matter lesions in MR imaging. Neuroimage (2004) 2.66
Structural brain changes in migraine. JAMA (2012) 2.47
Aberrant splicing of HTT generates the pathogenic exon 1 protein in Huntington disease. Proc Natl Acad Sci U S A (2013) 2.21
Magnetic resonance imaging for quantitative flow measurement in infants with hydrocephalus: a prospective study. J Neurosurg Pediatr (2008) 2.05
Prospective study of clinical phenotypes in neuropsychiatric systemic lupus erythematosus; multidisciplinary approach to diagnosis and therapy. J Rheumatol (2012) 2.04
The cerebral beta-amyloid angiopathies: hereditary and sporadic. Brain Pathol (2006) 1.91
Measuring the arterial input function with gradient echo sequences. Magn Reson Med (2003) 1.60
Childhood-onset growth hormone deficiency, cognitive function and brain N-acetylaspartate. Psychoneuroendocrinology (2005) 1.55
Effect of satiety on brain activation during chocolate tasting in men and women. Am J Clin Nutr (2006) 1.55
Small N-terminal mutant huntingtin fragments, but not wild type, are mainly present in monomeric form: Implications for pathogenesis. Exp Neurol (2005) 1.53
Anatomical variations in the circle of Willis and migraine susceptibility: is there an association? Headache (2009) 1.51
Descriptive analysis of the Boston criteria applied to a Dutch-type cerebral amyloid angiopathy population. Stroke (2009) 1.46
Flow territory mapping of the cerebral arteries with regional perfusion MRI. Stroke (2004) 1.41
Early changes in white matter pathways of the sensorimotor cortex in premanifest Huntington's disease. Hum Brain Mapp (2011) 1.39
Probabilistic segmentation of brain tissue in MR imaging. Neuroimage (2005) 1.36
Imaging the default mode network in aging and dementia. Biochim Biophys Acta (2011) 1.35
Orexin loss in Huntington's disease. Hum Mol Genet (2004) 1.33
Measurements of cerebral perfusion and arterial hemodynamics during visual stimulation using TURBO-TILT. Magn Reson Med (2003) 1.31
Functional magnetic resonance imaging of human hypothalamic responses to sweet taste and calories. Am J Clin Nutr (2005) 1.29
Functional MRI of human hypothalamic responses following glucose ingestion. Neuroimage (2005) 1.29
Internal carotid artery occlusion assessed at pulsed arterial spin-labeling perfusion MR imaging at multiple delay times. Radiology (2004) 1.27
Brain perfusion territory imaging: methods and clinical applications of selective arterial spin-labeling MR imaging. Radiology (2008) 1.27
Distribution of cerebral blood flow in the circle of Willis. Radiology (2005) 1.25
Automatic segmentation of different-sized white matter lesions by voxel probability estimation. Med Image Anal (2004) 1.25
Longitudinal evaluation of "presymptomatic" carriers of Huntington's disease. J Neuropsychiatry Clin Neurosci (2007) 1.18
Sleep and circadian rhythm alterations correlate with depression and cognitive impairment in Huntington's disease. Parkinsonism Relat Disord (2010) 1.18
Cholinergic neuronal defect without cell loss in Huntington's disease. Hum Mol Genet (2006) 1.17
Memory complaints in patients with normal cognition are associated with smaller hippocampal volumes. J Neurol (2004) 1.15
In vivo flow territory mapping of major brain feeding arteries. Neuroimage (2005) 1.15
Symptomatic carotid artery occlusion: flow territories of major brain-feeding arteries. Radiology (2007) 1.15
Cerebellar injury in preterm infants: incidence and findings on US and MR images. Radiology (2009) 1.13
Probabilistic brain tissue segmentation in neonatal magnetic resonance imaging. Pediatr Res (2008) 1.13
Cross-sectional study on prevalences of psychiatric disorders in mutation carriers of Huntington's disease compared with mutation-negative first-degree relatives. J Clin Psychiatry (2008) 1.11
Cerebral microbleeds are predictive of mortality in the elderly. Stroke (2011) 1.10
Accumulation of aberrant ubiquitin induces aggregate formation and cell death in polyglutamine diseases. Hum Mol Genet (2004) 1.10
Partial volume effects on arterial input functions: shape and amplitude distortions and their correction. J Magn Reson Imaging (2005) 1.10
Cerebral perfusion and aortic stiffness are independent predictors of white matter brain atrophy in type 1 diabetic patients assessed with magnetic resonance imaging. Diabetes Care (2011) 1.09
Postural instability in Parkinson's disease: the adrenergic hypothesis and the locus coeruleus. Expert Rev Neurother (2009) 1.08
Oral glucose intake inhibits hypothalamic neuronal activity more effectively than glucose infusion. Am J Physiol Endocrinol Metab (2007) 1.07
Glucose ingestion fails to inhibit hypothalamic neuronal activity in patients with type 2 diabetes. Diabetes (2007) 1.07
Clinical implications of MR imaging findings in the white matter in very preterm infants: a 2-year follow-up study. Radiology (2011) 1.06
Ubiquitin-conjugating enzyme E2-25K increases aggregate formation and cell death in polyglutamine diseases. Mol Cell Neurosci (2006) 1.06
Magnetization transfer imaging in normal aging, mild cognitive impairment, and Alzheimer's disease. Ann Neurol (2002) 1.05
Clinical impairment in premanifest and early Huntington's disease is associated with regionally specific atrophy. Hum Brain Mapp (2011) 1.05
Behavioural problems in Huntington's disease using the Problem Behaviours Assessment. Gen Hosp Psychiatry (2008) 1.05
Focusing on vigilance instead of sleepiness in the assessment of narcolepsy: high sensitivity of the Sustained Attention to Response Task (SART). Sleep (2006) 1.04
Early atrophy of pallidum and accumbens nucleus in Huntington's disease. J Neurol (2010) 1.04
Multiethnic genome-wide association study of cerebral white matter hyperintensities on MRI. Circ Cardiovasc Genet (2015) 1.03
Selective involvement of the amygdala in systemic lupus erythematosus. PLoS Med (2006) 1.03
Exploratory 7-Tesla magnetic resonance spectroscopy in Huntington's disease provides in vivo evidence for impaired energy metabolism. J Neurol (2011) 1.02
Association of aortic arch pulse wave velocity with left ventricular mass and lacunar brain infarcts in hypertensive patients: assessment with MR imaging. Radiology (2009) 1.02
Increased functional connectivity and brain atrophy in elderly with subjective memory complaints. Brain Connect (2013) 1.01
Lacunar infarcts are the main correlate with cognitive dysfunction in CADASIL. Stroke (2007) 1.00
Late-onset dementia: structural brain damage and total cerebral blood flow. Radiology (2005) 1.00
Sydenham's chorea: a practical overview of the current literature. Pediatr Neurol (2010) 1.00
Late-onset Huntington disease with intermediate CAG repeats: true or false? J Neurol Neurosurg Psychiatry (2010) 0.99
Short-term caloric restriction normalizes hypothalamic neuronal responsiveness to glucose ingestion in patients with type 2 diabetes. Diabetes (2012) 0.99
Increased hypothalamic-pituitary-adrenal axis activity in Huntington's disease. J Clin Endocrinol Metab (2009) 0.99
MMSE scores correlate with local ventricular enlargement in the spectrum from cognitively normal to Alzheimer disease. Neuroimage (2007) 0.98
Tract-based spatial statistics on diffusion tensor imaging in systemic lupus erythematosus reveals localized involvement of white matter tracts. Arthritis Rheum (2010) 0.97
Cognitive and motor functioning in gene carriers for Huntington's disease: a baseline study. J Neuropsychiatry Clin Neurosci (2003) 0.97
Phase-contrast magnetic resonance imaging measurements of cerebral autoregulation with a breath-hold challenge: a feasibility study. Stroke (2004) 0.96
Association of visit-to-visit variability in blood pressure with cognitive function in old age: prospective cohort study. BMJ (2013) 0.96
Autosomal dominant adult neuronal ceroid lipofuscinosis: parkinsonism due to both striatal and nigral dysfunction. Mov Disord (2002) 0.96
Early diffusion-weighted MRI and 1H-Magnetic Resonance Spectroscopy in asphyxiated full-term neonates. Biol Neonate (2005) 0.96
Diagnosing cerebral collateral flow patterns: accuracy of non-invasive testing. Cerebrovasc Dis (2008) 0.96
Increased prevalence of psychopathology and maladaptive personality traits after long-term cure of Cushing's disease. J Clin Endocrinol Metab (2010) 0.95
Subtle cognitive impairments in patients with long-term cure of Cushing's disease. J Clin Endocrinol Metab (2010) 0.95
MRI measures and progression of cognitive decline in nondemented elderly attending a memory clinic. Int J Geriatr Psychiatry (2005) 0.94
Brain imaging findings in very preterm infants throughout the neonatal period: part I. Incidences and evolution of lesions, comparison between ultrasound and MRI. Early Hum Dev (2009) 0.94
The influence of gender on phenotype and disease progression in patients with Huntington's disease. Parkinsonism Relat Disord (2012) 0.94
Autosomal dominant adult neuronal ceroid lipofuscinosis: a novel form of NCL with granular osmiophilic deposits without palmitoyl protein thioesterase 1 deficiency. Brain Pathol (2003) 0.94
Therapeutic options for Huntington's disease. Curr Opin Investig Drugs (2003) 0.94
MRI T2 Hypointensities in basal ganglia of premanifest Huntington's disease. PLoS Curr (2010) 0.93
Altered flow territories after extracranial-intracranial bypass surgery. Neurosurgery (2005) 0.93
Magnetic resonance imaging of the brain in newborn infants: practical aspects. Early Hum Dev (2009) 0.93
Elevated brain iron is independent from atrophy in Huntington's Disease. Neuroimage (2012) 0.93
Mutant huntingtin represses CBP, but not p300, by binding and protein degradation. Mol Cell Neurosci (2005) 0.93
Perception of emotional facial expressions at different intensities in early-symptomatic Huntington's disease. Eur Neurol (2006) 0.93
Effect of carotid endarterectomy on primary collateral blood flow in patients with severe carotid artery lesions. Stroke (2003) 0.92
Lenticulostriate arterial lumina are normal in cerebral autosomal-dominant arteriopathy with subcortical infarcts and leukoencephalopathy: a high-field in vivo MRI study. Stroke (2010) 0.92
Is sequential cranial ultrasound reliable for detection of white matter injury in very preterm infants? Neuroradiology (2010) 0.92
The structural correlates of functional deficits in early huntington's disease. Hum Brain Mapp (2012) 0.92
Nonlinguistic cognitive impairment in poststroke aphasia: a prospective study. Neurorehabil Neural Repair (2013) 0.91
Bone marrow stromal cell-mediated tissue sparing enhances functional repair after spinal cord contusion in adult rats. Cell Transplant (2012) 0.91
Delayed onset of the diurnal melatonin rise in patients with Huntington's disease. J Neurol (2009) 0.91
Pravastatin decreases wall shear stress and blood velocity in the internal carotid artery without affecting flow volume: results from the PROSPER MRI study. Stroke (2007) 0.91