Published in Cell Metab on June 01, 2009
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The striatum is highly susceptible to mitochondrial oxidative phosphorylation dysfunctions. J Neurosci (2011) 1.14
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A chemical enucleation method for the transfer of mitochondrial DNA to rho(o) cells. Nucleic Acids Res (2003) 1.08
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Increased mitochondrial biogenesis in muscle improves aging phenotypes in the mtDNA mutator mouse. Hum Mol Genet (2012) 1.02
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A metabolic shift induced by a PPAR panagonist markedly reduces the effects of pathogenic mitochondrial tRNA mutations. J Cell Mol Med (2011) 0.86
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Progressive cavitating leukoencephalopathy associated with respiratory chain complex I deficiency and a novel mutation in NDUFS1. Neurogenetics (2011) 0.83
Bezafibrate improves mitochondrial function in the CNS of a mouse model of mitochondrial encephalopathy. Mitochondrion (2012) 0.82
Transient systemic mtDNA damage leads to muscle wasting by reducing the satellite cell pool. Hum Mol Genet (2013) 0.82
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