|
1
|
Biased incorporation of ribonucleotides on the mitochondrial L-strand accounts for apparent strand-asymmetric DNA replication.
|
Cell
|
2002
|
2.32
|
|
2
|
The mitochondrial fission protein hFis1 requires the endoplasmic reticulum gateway to induce apoptosis.
|
Mol Biol Cell
|
2006
|
1.58
|
|
3
|
Human skeletal muscle atrophy in amyotrophic lateral sclerosis reveals a reduction in Akt and an increase in atrogin-1.
|
FASEB J
|
2006
|
1.31
|
|
4
|
Inhibition of mitochondrial fission favours mutant over wild-type mitochondrial DNA.
|
Hum Mol Genet
|
2009
|
1.21
|
|
5
|
A novel deletion in the GTPase domain of OPA1 causes defects in mitochondrial morphology and distribution, but not in function.
|
Hum Mol Genet
|
2008
|
1.20
|
|
6
|
Spinal and bulbar muscular atrophy: skeletal muscle pathology in male patients and heterozygous females.
|
J Neurol Sci
|
2007
|
1.20
|
|
7
|
Overexpression of microRNA-206 in the skeletal muscle from myotonic dystrophy type 1 patients.
|
J Transl Med
|
2010
|
1.13
|
|
8
|
Respiratory function in cybrid cell lines carrying European mtDNA haplogroups: implications for Leber's hereditary optic neuropathy.
|
Biochim Biophys Acta
|
2002
|
0.93
|
|
9
|
Androgen-dependent impairment of myogenesis in spinal and bulbar muscular atrophy.
|
Acta Neuropathol
|
2013
|
0.89
|
|
10
|
Biosynthesis of flavin cofactors in man: implications in health and disease.
|
Curr Pharm Des
|
2013
|
0.87
|
|
11
|
A pilot trial with clenbuterol in amyotrophic lateral sclerosis.
|
Amyotroph Lateral Scler
|
2006
|
0.81
|
|
12
|
Coordinated and reversible reduction of enzymes involved in terminal oxidative metabolism in skeletal muscle mitochondria from a riboflavin-responsive, multiple acyl-CoA dehydrogenase deficiency patient.
|
Electrophoresis
|
2006
|
0.80
|
|
13
|
Decreased fatty acid beta-oxidation in riboflavin-responsive, multiple acylcoenzyme A dehydrogenase-deficient patients is associated with an increase in uncoupling protein-3.
|
J Clin Endocrinol Metab
|
2003
|
0.78
|
|
14
|
Energy matters: mitochondrial proteomics for biomedicine.
|
Proteomics
|
2011
|
0.76
|
|
15
|
Development and characterization of polyspecific anti-mitochondrion antibodies for proteomics studies on in toto tissue homogenates.
|
Electrophoresis
|
2009
|
0.76
|
|
16
|
IPG with electrodic plateaus (and other unusual procedures for 2-DE).
|
Electrophoresis
|
2007
|
0.75
|