PubRank

James M Ervasti

Author PubWeight™ 46.81‹?›

Top papers

Rank Title Journal Year PubWeight™‹?›
1 Multi-isotope imaging mass spectrometry reveals slow protein turnover in hair-cell stereocilia. Nature 2012 2.52
2 Gamma-actin is required for cytoskeletal maintenance but not development. Proc Natl Acad Sci U S A 2009 1.74
3 Cytoplasmic gamma-actin contributes to a compensatory remodeling response in dystrophin-deficient muscle. Proc Natl Acad Sci U S A 2006 1.68
4 Enhanced laminin binding by alpha-dystroglycan after enzymatic deglycosylation. Biochem J 2005 1.56
5 β-Actin specifically controls cell growth, migration, and the G-actin pool. Mol Biol Cell 2011 1.46
6 Utrophin binds laterally along actin filaments and can couple costameric actin with sarcolemma when overexpressed in dystrophin-deficient muscle. Mol Biol Cell 2002 1.44
7 Cytoplasmic gamma-actin is not required for skeletal muscle development but its absence leads to a progressive myopathy. Dev Cell 2006 1.43
8 Site mapping and characterization of O-glycan structures on alpha-dystroglycan isolated from rabbit skeletal muscle. J Biol Chem 2010 1.43
9 The actin gene family: function follows isoform. Cytoskeleton (Hoboken) 2010 1.39
10 Dystrophin is a microtubule-associated protein. J Cell Biol 2009 1.38
11 Dystrophin and utrophin bind actin through distinct modes of contact. J Biol Chem 2006 1.36
12 Functional substitution by TAT-utrophin in dystrophin-deficient mice. PLoS Med 2009 1.30
13 β-actin and γ-actin are each dispensable for auditory hair cell development but required for Stereocilia maintenance. PLoS Genet 2010 1.30
14 Contributions of the LG modules and furin processing to laminin-2 functions. J Biol Chem 2002 1.28
15 Crystal structure and cell surface anchorage sites of laminin alpha1LG4-5. J Biol Chem 2007 1.27
16 Molecular dissection of the alpha-dystroglycan- and integrin-binding sites within the globular domain of human laminin-10. J Biol Chem 2003 1.26
17 An ex vivo gene therapy approach to treat muscular dystrophy using inducible pluripotent stem cells. Nat Commun 2013 1.17
18 The utrophin actin-binding domain binds F-actin in two different modes: implications for the spectrin superfamily of proteins. J Cell Biol 2002 1.12
19 Delayed embryonic development and impaired cell growth and survival in Actg1 null mice. Cytoskeleton (Hoboken) 2010 1.11
20 Expression of Dp260 in muscle tethers the actin cytoskeleton to the dystrophin-glycoprotein complex and partially prevents dystrophy. Hum Mol Genet 2002 1.10
21 Disease-causing missense mutations in actin binding domain 1 of dystrophin induce thermodynamic instability and protein aggregation. Proc Natl Acad Sci U S A 2010 1.04
22 Identification of spectrin-like repeats required for high affinity utrophin-actin interaction. J Biol Chem 2005 1.01
23 Axonal regeneration and neuronal function are preserved in motor neurons lacking ß-actin in vivo. PLoS One 2011 1.01
24 Internal deletion compromises the stability of dystrophin. Hum Mol Genet 2011 1.00
25 Context-dependent functional substitution of alpha-skeletal actin by gamma-cytoplasmic actin. FASEB J 2009 0.99
26 β-Actin and fascin-2 cooperate to maintain stereocilia length. J Neurosci 2013 0.99
27 Microtubule binding distinguishes dystrophin from utrophin. Proc Natl Acad Sci U S A 2014 0.98
28 Dystrophin and utrophin have distinct effects on the structural dynamics of actin. Proc Natl Acad Sci U S A 2009 0.98
29 Core 1 glycans on alpha-dystroglycan mediate laminin-induced acetylcholine receptor clustering but not laminin binding. J Biol Chem 2003 0.91
30 Skeletal muscle-specific ablation of gamma(cyto)-actin does not exacerbate the mdx phenotype. PLoS One 2008 0.90
31 Restricted morphological and behavioral abnormalities following ablation of β-actin in the brain. PLoS One 2012 0.90
32 TAT-μUtrophin mitigates the pathophysiology of dystrophin and utrophin double-knockout mice. J Appl Physiol (1985) 2011 0.87
33 Brain alpha-dystroglycan displays unique glycoepitopes and preferential binding to laminin-10/11. FEBS Lett 2006 0.86
34 Actin isoforms in neuronal development and function. Int Rev Cell Mol Biol 2013 0.85
35 The carboxy-terminal third of dystrophin enhances actin binding activity. J Mol Biol 2011 0.85
36 Quadriceps myopathy caused by skeletal muscle-specific ablation of β(cyto)-actin. J Cell Sci 2011 0.85
37 Cytoplasmic gamma-actin expression in diverse animal models of muscular dystrophy. Neuromuscul Disord 2007 0.85
38 Destabilization of the dystrophin-glycoprotein complex without functional deficits in alpha-dystrobrevin null muscle. PLoS One 2008 0.84
39 Impacts of dystrophin and utrophin domains on actin structural dynamics: implications for therapeutic design. J Mol Biol 2012 0.84
40 Transgenic overexpression of γ-cytoplasmic actin protects against eccentric contraction-induced force loss in mdx mice. Skelet Muscle 2011 0.82
41 Structural and functional properties of the actin gene family. Crit Rev Eukaryot Gene Expr 2011 0.80