| Rank |
Title |
Journal |
Year |
PubWeight™‹?› |
|
1
|
PML in a patient treated with fumaric acid.
|
N Engl J Med
|
2013
|
3.87
|
|
2
|
Senataxin, the ortholog of a yeast RNA helicase, is mutant in ataxia-ocular apraxia 2.
|
Nat Genet
|
2004
|
2.75
|
|
3
|
Early outcome of carotid angioplasty and stenting with and without cerebral protection devices: a systematic review of the literature.
|
Stroke
|
2003
|
2.63
|
|
4
|
Knockdown of transactive response DNA-binding protein (TDP-43) downregulates histone deacetylase 6.
|
EMBO J
|
2009
|
2.37
|
|
5
|
Repetitive bilateral arm training and motor cortex activation in chronic stroke: a randomized controlled trial.
|
JAMA
|
2004
|
2.36
|
|
6
|
Loss of function mutations in the gene encoding Omi/HtrA2 in Parkinson's disease.
|
Hum Mol Genet
|
2005
|
2.28
|
|
7
|
Biological and clinical characteristics of individuals at risk for spinocerebellar ataxia types 1, 2, 3, and 6 in the longitudinal RISCA study: analysis of baseline data.
|
Lancet Neurol
|
2013
|
2.24
|
|
8
|
Neuroprotective role of the Reaper-related serine protease HtrA2/Omi revealed by targeted deletion in mice.
|
Mol Cell Biol
|
2004
|
2.15
|
|
9
|
Pre-fibrillar alpha-synuclein variants with impaired beta-structure increase neurotoxicity in Parkinson's disease models.
|
EMBO J
|
2009
|
2.09
|
|
10
|
Systematic review of early recurrent stenosis after carotid angioplasty and stenting.
|
Stroke
|
2004
|
2.04
|
|
11
|
Loss of pain perception in diabetes is dependent on a receptor of the immunoglobulin superfamily.
|
J Clin Invest
|
2004
|
1.92
|
|
12
|
Treatment with simvastatin in normocholesterolemic patients with Alzheimer's disease: A 26-week randomized, placebo-controlled, double-blind trial.
|
Ann Neurol
|
2002
|
1.79
|
|
13
|
Cellular pathology of Parkinson's disease: astrocytes, microglia and inflammation.
|
Cell Tissue Res
|
2004
|
1.76
|
|
14
|
Short and long-term motor skill learning in an accelerated rotarod training paradigm.
|
Neurobiol Learn Mem
|
2004
|
1.72
|
|
15
|
Neuroprotection by hypoxic preconditioning requires sequential activation of vascular endothelial growth factor receptor and Akt.
|
J Neurosci
|
2002
|
1.72
|
|
16
|
Efficient inhibition of the Alzheimer's disease beta-secretase by membrane targeting.
|
Science
|
2008
|
1.67
|
|
17
|
Transgenic rat model of Huntington's disease.
|
Hum Mol Genet
|
2003
|
1.66
|
|
18
|
Protection by pioglitazone in the MPTP model of Parkinson's disease correlates with I kappa B alpha induction and block of NF kappa B and iNOS activation.
|
J Neurochem
|
2004
|
1.61
|
|
19
|
TDP-43-mediated neuron loss in vivo requires RNA-binding activity.
|
PLoS One
|
2010
|
1.58
|
|
20
|
Clinical predictors of transient ischemic attack, stroke, or death within 30 days of carotid angioplasty and stenting.
|
Stroke
|
2005
|
1.53
|
|
21
|
The heart in Friedreich ataxia: definition of cardiomyopathy, disease severity, and correlation with neurological symptoms.
|
Circulation
|
2012
|
1.50
|
|
22
|
Deep brain stimulation.
|
Cell Tissue Res
|
2004
|
1.42
|
|
23
|
Two molecular pathways initiate mitochondria-dependent dopaminergic neurodegeneration in experimental Parkinson's disease.
|
Proc Natl Acad Sci U S A
|
2007
|
1.41
|
|
24
|
Penguins and hummingbirds: midbrain atrophy in progressive supranuclear palsy.
|
Neurology
|
2006
|
1.40
|
|
25
|
Motor skill learning depends on protein synthesis in motor cortex after training.
|
J Neurosci
|
2004
|
1.37
|
|
26
|
Mitochondrial protein quality control by the proteasome involves ubiquitination and the protease Omi.
|
J Biol Chem
|
2008
|
1.30
|
|
27
|
The multidrug resistance protein 1 (Mrp1), but not Mrp5, mediates export of glutathione and glutathione disulfide from brain astrocytes.
|
J Neurochem
|
2006
|
1.28
|
|
28
|
Neurodegeneration and motor dysfunction in a conditional model of Parkinson's disease.
|
J Neurosci
|
2008
|
1.28
|
|
29
|
Identification of CD70-mediated apoptosis of immune effector cells as a novel immune escape pathway of human glioblastoma.
|
Cancer Res
|
2002
|
1.23
|
|
30
|
Novel homozygous p.E64D mutation in DJ1 in early onset Parkinson disease (PARK7).
|
Hum Mutat
|
2004
|
1.22
|
|
31
|
Identification and functional characterization of a novel R621C mutation in the synphilin-1 gene in Parkinson's disease.
|
Hum Mol Genet
|
2003
|
1.22
|
|
32
|
Silencing of the Pink1 gene expression by conditional RNAi does not induce dopaminergic neuron death in mice.
|
Int J Biol Sci
|
2007
|
1.20
|
|
33
|
Granulocyte-colony stimulating factor is neuroprotective in a model of Parkinson's disease.
|
J Neurochem
|
2006
|
1.16
|
|
34
|
Depression comorbidity in spinocerebellar ataxia.
|
Mov Disord
|
2011
|
1.15
|
|
35
|
Prevention of irradiation-induced glioma cell invasion by temozolomide involves caspase 3 activity and cleavage of focal adhesion kinase.
|
Cancer Res
|
2002
|
1.15
|
|
36
|
Lesion location alters brain activation in chronically impaired stroke survivors.
|
Neuroimage
|
2004
|
1.14
|
|
37
|
Relation between regional functional MRI activation and vascular reactivity to carbon dioxide during normal aging.
|
J Cereb Blood Flow Metab
|
2003
|
1.14
|
|
38
|
Diagnostic hallmarks and pitfalls in late-onset progressive transthyretin-related amyloid-neuropathy.
|
J Neurol
|
2013
|
1.14
|
|
39
|
Feasibility of prehospital teleconsultation in acute stroke--a pilot study in clinical routine.
|
PLoS One
|
2012
|
1.12
|
|
40
|
RET signaling does not modulate MPTP toxicity but is required for regeneration of dopaminergic axon terminals.
|
Proc Natl Acad Sci U S A
|
2007
|
1.11
|
|
41
|
Magnetic resonance imaging-based volumetry differentiates progressive supranuclear palsy from corticobasal degeneration.
|
Neuroimage
|
2004
|
1.10
|
|
42
|
Efficient gene therapy for Parkinson's disease using astrocytes as hosts for localized neurotrophic factor delivery.
|
Mol Ther
|
2011
|
1.06
|
|
43
|
The mitochondrial chaperone protein TRAP1 mitigates α-Synuclein toxicity.
|
PLoS Genet
|
2012
|
1.06
|
|
44
|
Characterization of motor skill and instrumental learning time scales in a skilled reaching task in rat.
|
Behav Brain Res
|
2004
|
1.05
|
|
45
|
Glutathione release from cultured brain cells: multidrug resistance protein 1 mediates the release of GSH from rat astroglial cells.
|
J Neurosci Res
|
2002
|
1.05
|
|
46
|
Accumulation and clearance of alpha-synuclein aggregates demonstrated by time-lapse imaging.
|
J Neurochem
|
2008
|
1.05
|
|
47
|
Comparison of three clinical rating scales in Friedreich ataxia (FRDA).
|
Mov Disord
|
2009
|
1.04
|
|
48
|
Influence of SORL1 gene variants: association with CSF amyloid-beta products in probable Alzheimer's disease.
|
Neurosci Lett
|
2008
|
1.04
|
|
49
|
Diagnostic challenge and therapeutic dilemma in necrotizing myopathy.
|
Neurology
|
2013
|
1.01
|
|
50
|
Investigating function and connectivity of morphometric findings--exemplified on cerebellar atrophy in spinocerebellar ataxia 17 (SCA17).
|
Neuroimage
|
2012
|
1.01
|
|
51
|
Co-enzyme Q10 and idebenone use in Friedreich's ataxia.
|
J Neurochem
|
2013
|
1.01
|
|
52
|
Genotype-specific patterns of atrophy progression are more sensitive than clinical decline in SCA1, SCA3 and SCA6.
|
Brain
|
2013
|
1.00
|
|
53
|
Fas/CD95 regulatory protein Faim2 is neuroprotective after transient brain ischemia.
|
J Neurosci
|
2011
|
0.99
|
|
54
|
Blood-based neurochemical diagnosis of vascular dementia: a pilot study.
|
J Neurochem
|
2007
|
0.96
|
|
55
|
Parkinson's disease: one biochemical pathway to fit all genes?
|
Trends Mol Med
|
2002
|
0.96
|
|
56
|
The proteasomal subunit S6 ATPase is a novel synphilin-1 interacting protein--implications for Parkinson's disease.
|
FASEB J
|
2007
|
0.96
|
|
57
|
The cancer stem cell subtype determines immune infiltration of glioblastoma.
|
Stem Cells Dev
|
2012
|
0.95
|
|
58
|
Drosophila melanogaster as a model organism for Alzheimer's disease.
|
Mol Neurodegener
|
2013
|
0.95
|
|
59
|
Transient expression of Nxf, a bHLH-PAS transactivator induced by neuronal preconditioning, confers neuroprotection in cultured cells.
|
Brain Res
|
2007
|
0.95
|
|
60
|
Palmitoylation is a sorting determinant for transport to the myelin membrane.
|
J Cell Sci
|
2005
|
0.94
|
|
61
|
Alternate-form reliability of the Montreal cognitive assessment screening test in a clinical setting.
|
Dement Geriatr Cogn Disord
|
2012
|
0.94
|
|
62
|
TRAP1 rescues PINK1 loss-of-function phenotypes.
|
Hum Mol Genet
|
2013
|
0.93
|
|
63
|
Spinocerebellar ataxia types 1, 2, 3 and 6: the clinical spectrum of ataxia and morphometric brainstem and cerebellar findings.
|
Cerebellum
|
2012
|
0.93
|
|
64
|
Targeted ablation of oligodendrocytes triggers axonal damage.
|
PLoS One
|
2011
|
0.93
|
|
65
|
Altered resting-state connectivity in Huntington's disease.
|
Hum Brain Mapp
|
2013
|
0.92
|
|
66
|
FasL (CD95L/APO-1L) resistance of neurons mediated by phosphatidylinositol 3-kinase-Akt/protein kinase B-dependent expression of lifeguard/neuronal membrane protein 35.
|
J Neurosci
|
2005
|
0.92
|
|
67
|
Cortical stimulation mapping using epidurally implanted thin-film microelectrode arrays.
|
J Neurosci Methods
|
2006
|
0.91
|
|
68
|
Chemotherapy-induced cell death in primary cerebellar granule neurons but not in astrocytes: in vitro paradigm of differential neurotoxicity.
|
J Neurochem
|
2004
|
0.91
|
|
69
|
CD95/Fas in the brain--not just a killer.
|
Cell Stem Cell
|
2009
|
0.91
|
|
70
|
Diffusion-weighted MRI in patients with symptomatic internal carotid artery disease.
|
J Neurol
|
2002
|
0.91
|
|
71
|
Neuroanatomic changes and their association with cognitive decline in mild cognitive impairment: a meta-analysis.
|
Brain Struct Funct
|
2011
|
0.91
|
|
72
|
Visualization and quantification of disease progression in multiple system atrophy.
|
Mov Disord
|
2006
|
0.91
|
|
73
|
Death receptor Fas (CD95) signaling in the central nervous system: tuning neuroplasticity?
|
Trends Neurosci
|
2008
|
0.90
|
|
74
|
Tat-Hsp70 protects dopaminergic neurons in midbrain cultures and in the substantia nigra in models of Parkinson's disease.
|
J Neurochem
|
2007
|
0.90
|
|
75
|
Statin therapy at carotid angioplasty and stent placement: effect on procedure-related stroke, myocardial infarction, and death.
|
Radiology
|
2006
|
0.90
|
|
76
|
Apoptotic mechanisms and antiapoptotic therapy in the MPTP model of Parkinson's disease.
|
Toxicol Lett
|
2003
|
0.90
|
|
77
|
Drosophila as a screening tool to study human neurodegenerative diseases.
|
J Neurochem
|
2013
|
0.88
|
|
78
|
Aggregate formation and toxicity by wild-type and R621C synphilin-1 in the nigrostriatal system of mice using adenoviral vectors.
|
J Neurochem
|
2009
|
0.88
|
|
79
|
The yeast HtrA orthologue Ynm3 is a protease with chaperone activity that aids survival under heat stress.
|
Mol Biol Cell
|
2008
|
0.88
|
|
80
|
Cholesterol depletion reduces aggregation of amyloid-beta peptide in hippocampal neurons.
|
Neurobiol Dis
|
2006
|
0.87
|
|
81
|
A30P α-synuclein impairs dopaminergic fiber regeneration and interacts with L-DOPA replacement in MPTP-treated mice.
|
Neurobiol Dis
|
2011
|
0.86
|
|
82
|
Magnetic resonance imaging in spinocerebellar ataxias.
|
Cerebellum
|
2008
|
0.86
|
|
83
|
Potential synergistic protection of retinal ganglion cells from axotomy-induced apoptosis by adenoviral administration of glial cell line-derived neurotrophic factor and X-chromosome-linked inhibitor of apoptosis.
|
Neurobiol Dis
|
2002
|
0.86
|
|
84
|
Transgenic overexpression of the alpha-synuclein interacting protein synphilin-1 leads to behavioral and neuropathological alterations in mice.
|
Neurogenetics
|
2010
|
0.85
|
|
85
|
Large-scale screen for modifiers of ataxin-3-derived polyglutamine-induced toxicity in Drosophila.
|
PLoS One
|
2012
|
0.85
|
|
86
|
Monitoring progression in Friedreich ataxia (FRDA): the use of clinical scales.
|
J Neurochem
|
2013
|
0.85
|
|
87
|
Protein synthesis inhibition blocks consolidation of an acrobatic motor skill.
|
Learn Mem
|
2004
|
0.85
|
|
88
|
Clinical significance of post-interventional cerebral hyperdensities after endovascular mechanical thrombectomy in acute ischaemic stroke.
|
Neuroradiology
|
2013
|
0.85
|
|
89
|
Receptor for advanced glycation endproducts (RAGE) deficiency protects against MPTP toxicity.
|
Neurobiol Aging
|
2012
|
0.84
|
|
90
|
Parkinson's disease and dementia: a longitudinal study (DEMPARK).
|
Neuroepidemiology
|
2011
|
0.84
|
|
91
|
Impairment of the septal cholinergic neurons in MPTP-treated A30P α-synuclein mice.
|
Neurobiol Aging
|
2012
|
0.83
|
|
92
|
Self-rated health status in spinocerebellar ataxia--results from a European multicenter study.
|
Mov Disord
|
2010
|
0.83
|
|
93
|
Efficacy of clinically relevant temozolomide dosing schemes in glioblastoma cancer stem cell lines.
|
J Neurooncol
|
2012
|
0.82
|
|
94
|
New developments in diagnosis and treatment of Parkinson's disease--from basic science to clinical applications.
|
J Neurol
|
2004
|
0.82
|
|
95
|
Membrane-permeable Bcl-xL prevents MPTP-induced dopaminergic neuronal loss in the substantia nigra.
|
J Neurochem
|
2007
|
0.82
|
|
96
|
Adenoviral (full-length) Apo2L/TRAIL gene transfer is an ineffective treatment strategy for malignant glioma.
|
J Neurooncol
|
2003
|
0.82
|
|
97
|
Increased brain tissue sodium concentration in Huntington's Disease - a sodium imaging study at 4 T.
|
Neuroimage
|
2012
|
0.81
|
|
98
|
Comparison of angioplasty and stenting with cerebral protection versus endarterectomy for treatment of internal carotid artery stenosis in elderly patients.
|
J Vasc Surg
|
2004
|
0.81
|
|
99
|
Diminished activation of motor working-memory networks in Parkinson's disease.
|
PLoS One
|
2013
|
0.81
|
|
100
|
Novel FHL1 mutation in a family with reducing body myopathy.
|
Muscle Nerve
|
2012
|
0.81
|
|
101
|
Early outcome of carotid angioplasty and stenting versus carotid endarterectomy in a single academic center.
|
Cerebrovasc Dis
|
2003
|
0.80
|
|
102
|
Neural correlates of impaired emotion processing in manifest Huntington's disease.
|
Soc Cogn Affect Neurosci
|
2013
|
0.80
|
|
103
|
Specific and disease stage-dependent episodic memory-related brain activation patterns in Alzheimer's disease: a coordinate-based meta-analysis.
|
Brain Struct Funct
|
2014
|
0.80
|
|
104
|
Case reports of PML in patients treated for psoriasis.
|
N Engl J Med
|
2013
|
0.79
|
|
105
|
PKC links Gq-coupled receptors to DAT-mediated dopamine release.
|
J Neurochem
|
2010
|
0.79
|
|
106
|
Clinical data and characterization of the liver conditional mouse model exclude neoplasia as a non-neurological manifestation associated with Friedreich's ataxia.
|
Dis Model Mech
|
2012
|
0.79
|
|
107
|
Ergoline and non-ergoline derivatives in the treatment of Parkinson's disease.
|
J Neurol
|
2006
|
0.79
|
|
108
|
Effects of dopamine on the glutathione metabolism of cultured astroglial cells: implications for Parkinson's disease.
|
J Neurochem
|
2002
|
0.78
|
|
109
|
Morphological spectrum and clinical features of myopathies with tubular aggregates.
|
Histol Histopathol
|
2013
|
0.78
|
|
110
|
Modulation of hippocampal neuroplasticity by Fas/CD95 regulatory protein 2 (Faim2) in the course of bacterial meningitis.
|
J Neuropathol Exp Neurol
|
2014
|
0.78
|
|
111
|
Spectrum of phenotypes and genotypes in Parkinson's disease.
|
J Neurol
|
2002
|
0.78
|
|
112
|
BAG1 modulates huntingtin toxicity, aggregation, degradation, and subcellular distribution.
|
J Neurochem
|
2009
|
0.78
|
|
113
|
Extracellular domain splice variants of a transforming protein tyrosine phosphatase alpha mutant differentially activate Src-kinase dependent focus formation.
|
Genes Cells
|
2007
|
0.78
|
|
114
|
150 years of Friedreich ataxia: from its discovery to therapy.
|
J Neurochem
|
2013
|
0.77
|
|
115
|
Lewy body dementia and Parkinson's disease with dementia.
|
J Neurol
|
2008
|
0.76
|
|
116
|
Differential pattern of brain-specific CSF proteins tau and amyloid-β in Parkinsonian syndromes.
|
Mov Disord
|
2010
|
0.76
|
|
117
|
Adjuvant granulocyte colony-stimulating factor therapy results in improved spatial learning and stimulates hippocampal neurogenesis in a mouse model of pneumococcal meningitis.
|
J Neuropathol Exp Neurol
|
2015
|
0.76
|
|
118
|
CDK5 protects from caspase-induced Ataxin-3 cleavage and neurodegeneration.
|
J Neurochem
|
2014
|
0.76
|
|
119
|
Therapeutic strategies for Parkinson's disease based on data derived from genetic research.
|
J Neurol
|
2003
|
0.75
|
|
120
|
Gene dosage-dependent effects of bcl-2 expression on cellular survival and redox status.
|
Free Radic Biol Med
|
2003
|
0.75
|
|
121
|
The dopaminergic nigrostriatal system: development, physiology, disease.
|
Cell Tissue Res
|
2004
|
0.75
|
|
122
|
Consensus paper: radiological biomarkers of cerebellar diseases.
|
Cerebellum
|
2015
|
0.75
|
|
123
|
Teaching neuroimages: combined retinal and cerebral hyperperfusion syndrome after carotid thromboendarterectomy.
|
Neurology
|
2013
|
0.75
|
|
124
|
Cognitive effects of deep brain stimulation for essential tremor: evaluation at 1 and 6 years.
|
J Neural Transm (Vienna)
|
2013
|
0.75
|
|
125
|
Myopathy with lobulated fibers, cores, and rods caused by a mutation in collagen VI.
|
Neurology
|
2012
|
0.75
|
|
126
|
Posterior Cortical Atrophy: A Case Report of a 6-Year Natural Progression.
|
Alzheimer Dis Assoc Disord
|
2016
|
0.75
|
|
127
|
Yeast, fish, fly--models to study the pathogenesis of proteinopathies and screen for interventions.
|
J Neurochem
|
2013
|
0.75
|
|
128
|
Chronic Subdural Hematoma-Antithrombotics and Thrombotic Complications.
|
Dtsch Arztebl Int
|
2022
|
0.75
|
|
129
|
Molecular imaging and its applications: visualization beyond imagination.
|
J Neurochem
|
2013
|
0.75
|
|
130
|
Can We Close the Discussion on PFO-Closure?
|
Hellenic J Cardiol
|
2015
|
0.75
|