Published in J Neuropathol Exp Neurol on May 01, 2012
Autophagy in axonal and dendritic degeneration. Trends Neurosci (2013) 1.08
Prion Disease Induces Alzheimer Disease-Like Neuropathologic Changes. J Neuropathol Exp Neurol (2015) 0.91
Convection-enhanced delivery of AAV2-PrPshRNA in prion-infected mice. PLoS One (2014) 0.81
Levels of the Mahogunin Ring Finger 1 E3 ubiquitin ligase do not influence prion disease. PLoS One (2013) 0.79
White matter involvement in sporadic Creutzfeldt-Jakob disease. Brain (2014) 0.77
Brain Aggregates: An Effective In Vitro Cell Culture System Modeling Neurodegenerative Diseases. J Neuropathol Exp Neurol (2016) 0.75
Synthetic mammalian prions. Science (2004) 7.35
A change in the conformation of prions accompanies the emergence of a new prion strain. Neuron (2002) 3.36
Challenging the clinical utility of the 14-3-3 protein for the diagnosis of sporadic Creutzfeldt-Jakob disease. Arch Neurol (2003) 3.20
Age-dependent neurofibrillary tangle formation, neuron loss, and memory impairment in a mouse model of human tauopathy (P301L). J Neurosci (2005) 3.20
Continuum of prion protein structures enciphers a multitude of prion isolate-specified phenotypes. Proc Natl Acad Sci U S A (2006) 2.69
Design and construction of diverse mammalian prion strains. Proc Natl Acad Sci U S A (2009) 2.41
Purified and synthetic Alzheimer's amyloid beta (Aβ) prions. Proc Natl Acad Sci U S A (2012) 2.36
Nox2-derived radicals contribute to neurovascular and behavioral dysfunction in mice overexpressing the amyloid precursor protein. Proc Natl Acad Sci U S A (2008) 2.27
Transmission of multiple system atrophy prions to transgenic mice. Proc Natl Acad Sci U S A (2013) 2.19
Protease-sensitive synthetic prions. PLoS Pathog (2010) 2.14
Asymptomatic deer excrete infectious prions in faeces. Nature (2009) 2.10
Mutant PrPSc conformers induced by a synthetic peptide and several prion strains. J Virol (2004) 2.07
Transmission of elk and deer prions to transgenic mice. J Virol (2006) 2.03
Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene. Proc Natl Acad Sci U S A (2003) 2.01
Clinicopathological correlations in corticobasal degeneration. Ann Neurol (2011) 1.86
Prion clearance in bigenic mice. J Gen Virol (2005) 1.79
Conformational transformation and selection of synthetic prion strains. J Mol Biol (2011) 1.66
Dominant-negative inhibition of prion replication in transgenic mice. Proc Natl Acad Sci U S A (2002) 1.65
Time-controlled transcardiac perfusion cross-linking for the study of protein interactions in complex tissues. Nat Biotechnol (2004) 1.63
Measuring prions by bioluminescence imaging. Proc Natl Acad Sci U S A (2009) 1.59
Continuous quinacrine treatment results in the formation of drug-resistant prions. PLoS Pathog (2009) 1.58
A novel leucine zipper targets AKAP15 and cyclic AMP-dependent protein kinase to the C terminus of the skeletal muscle Ca2+ channel and modulates its function. J Biol Chem (2001) 1.57
Trafficking of prion proteins through a caveolae-mediated endosomal pathway. J Cell Biol (2003) 1.51
Prions in skeletal muscle. Proc Natl Acad Sci U S A (2002) 1.48
Bioluminescence imaging of Abeta deposition in bigenic mouse models of Alzheimer's disease. Proc Natl Acad Sci U S A (2011) 1.39
Cytosolic prion protein in neurons. J Neurosci (2003) 1.34
Selective frontoinsular von Economo neuron and fork cell loss in early behavioral variant frontotemporal dementia. Cereb Cortex (2011) 1.24
The influence of ferucarbotran on the chondrogenesis of human mesenchymal stem cells. Contrast Media Mol Imaging (2009) 1.24
Notch-1 activation and dendritic atrophy in prion disease. Proc Natl Acad Sci U S A (2005) 1.17
Transmission of scrapie and sheep-passaged bovine spongiform encephalopathy prions to transgenic mice expressing elk prion protein. J Gen Virol (2009) 1.15
The neurodegeneration sequence in prion diseases: evidence from functional, morphological and ultrastructural studies of the GABAergic system. J Neuropathol Exp Neurol (2004) 1.14
Resistance of bovine spongiform encephalopathy (BSE) prions to inactivation. PLoS Pathog (2008) 1.14
Correlating DWI MRI with pathologic and other features of Jakob-Creutzfeldt disease. Alzheimer Dis Assoc Disord (2009) 1.13
Cryo-immunogold electron microscopy for prions: toward identification of a conversion site. J Neurosci (2008) 1.12
Drug resistance confounding prion therapeutics. Proc Natl Acad Sci U S A (2013) 1.10
Spontaneous generation of anchorless prions in transgenic mice. Proc Natl Acad Sci U S A (2011) 1.08
Solution and crystallographic studies of branched multivalent ligands that inhibit the receptor-binding of cholera toxin. J Am Chem Soc (2002) 1.08
Distinct roles of Bazooka and Stardust in the specification of Drosophila photoreceptor membrane architecture. Proc Natl Acad Sci U S A (2003) 1.07
Human prion strain selection in transgenic mice. Ann Neurol (2010) 1.06
Spontaneous generation of rapidly transmissible prions in transgenic mice expressing wild-type bank vole prion protein. Proc Natl Acad Sci U S A (2012) 1.03
Principal network analysis: identification of subnetworks representing major dynamics using gene expression data. Bioinformatics (2010) 1.03
Disruption of Fnip1 reveals a metabolic checkpoint controlling B lymphocyte development. Immunity (2012) 1.02
Salivary prions in sheep and deer. Prion (2012) 1.02
Prion infection of mouse neurospheres. Proc Natl Acad Sci U S A (2006) 1.01
Conformation-dependent high-affinity monoclonal antibodies to prion proteins. J Immunol (2010) 1.00
A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP. J Neurosci (2009) 1.00
Characterization and crystal structure of a high-affinity pentavalent receptor-binding inhibitor for cholera toxin and E. coli heat-labile enterotoxin. J Am Chem Soc (2002) 1.00
New variants in the Enpp1 and Ptpn6 genes cause low BMD, crystal-related arthropathy, and vascular calcification. J Bone Miner Res (2009) 0.99
Differential diagnosis of Jakob-Creutzfeldt disease. Arch Neurol (2012) 0.98
Convergent replication of mouse synthetic prion strains. Am J Pathol (2013) 0.98
Sites and molecular mechanisms of modulation of Na(v)1.2 channels by Fyn tyrosine kinase. J Neurosci (2007) 0.98
Developmental expression of PrP in the post-implantation embryo. Brain Res (2006) 0.97
Chemical induction of misfolded prion protein conformers in cell culture. J Biol Chem (2009) 0.97
Sporadic corticobasal syndrome due to FTLD-TDP. Acta Neuropathol (2009) 0.95
Systems biology and the discovery of diagnostic biomarkers. Dis Markers (2010) 0.95
Seizures, enhanced excitation, and increased vesicle number in Lis1 mutant mice. Ann Neurol (2009) 0.95
Brain and circulating levels of Aβ1-40 differentially contribute to vasomotor dysfunction in the mouse brain. Stroke (2012) 0.91
Prion Disease Induces Alzheimer Disease-Like Neuropathologic Changes. J Neuropathol Exp Neurol (2015) 0.91
Neurotoxicity of intra-arterial papaverine preserved with chlorobutanol used for the treatment of cerebral vasospasm after aneurysmal subarachnoid hemorrhage. Stroke (2004) 0.90
Somatic differentiation and MR imaging of magnetically labeled human embryonic stem cells. Cell Transplant (2012) 0.89
A mutation in Ampd2 is associated with nephrotic syndrome and hypercholesterolemia in mice. Lipids Health Dis (2014) 0.89
A point mutation in the murine Hem1 gene reveals an essential role for Hematopoietic protein 1 in lymphopoiesis and innate immunity. J Exp Med (2008) 0.89
Identification of I137M and other mutations that modulate incubation periods for two human prion strains. J Virol (2012) 0.86
Chimeric elk/mouse prion proteins in transgenic mice. J Gen Virol (2012) 0.85
Behavioral variant frontotemporal dementia with corticobasal degeneration pathology: phenotypic comparison to bvFTD with Pick's disease. J Mol Neurosci (2011) 0.83
Prion and doppel proteins bind to granule cells of the cerebellum. Proc Natl Acad Sci U S A (2002) 0.82
Anchor-based design of improved cholera toxin and E. coli heat-labile enterotoxin receptor binding antagonists that display multiple binding modes. Chem Biol (2002) 0.82
Generation of antisera to purified prions in lipid rafts. Prion (2010) 0.82
Sciatic nerve transection triggers release and intercellular transfer of a genetically expressed macromolecular tracer in dorsal root ganglia. J Comp Neurol (2011) 0.80
Pathologic evidence that the T188R mutation in PRNP is associated with prion disease. J Neuropathol Exp Neurol (2010) 0.80
Sporadic Jakob-Creutzfeldt disease presenting as primary progressive aphasia. JAMA Neurol (2013) 0.79
Levels of the Mahogunin Ring Finger 1 E3 ubiquitin ligase do not influence prion disease. PLoS One (2013) 0.79
Human growth hormone-related iatrogenic Creutzfeldt-Jakob disease with abnormal imaging. Arch Neurol (2006) 0.78
Corticotropin-releasing factor receptor 2 mediates sex-specific cellular stress responses. Mol Med (2013) 0.78
Pharmacokinetics of quinacrine efflux from mouse brain via the P-glycoprotein efflux transporter. PLoS One (2012) 0.77
Generation and characterization of a rabbit monoclonal antibody site-specific for tau O-GlcNAcylated at serine 400. FEBS Lett (2013) 0.76
Changes in neuropeptide expression in mice infected with prions. Neurobiol Aging (2006) 0.76
Disrupted SOX10 function causes spongiform neurodegeneration in gray tremor mice. Mamm Genome (2014) 0.75
Seizures in corticobasal degeneration: a case report. Neurocase (2009) 0.75
Autobiography Series: From Sleep-Wake Mechanisms to Prion Diseases. J Neuropathol Exp Neurol (2017) 0.75