Published in Hum Mol Genet on July 18, 2012
How much dystrophin is enough: the physiological consequences of different levels of dystrophin in the mdx mouse. Hum Mol Genet (2015) 1.07
The evolution of the dystroglycan complex, a major mediator of muscle integrity. Biol Open (2015) 0.85
Absence of Dystrophin Disrupts Skeletal Muscle Signaling: Roles of Ca2+, Reactive Oxygen Species, and Nitric Oxide in the Development of Muscular Dystrophy. Physiol Rev (2016) 0.85
Nuclear targeting of dystroglycan promotes the expression of androgen regulated transcription factors in prostate cancer. Sci Rep (2013) 0.84
Identification of new dystroglycan complexes in skeletal muscle. PLoS One (2013) 0.82
Cell entry of Lassa virus induces tyrosine phosphorylation of dystroglycan. Cell Microbiol (2012) 0.78
Phosphorylation within the cysteine-rich region of dystrophin enhances its association with β-dystroglycan and identifies a potential novel therapeutic target for skeletal muscle wasting. Hum Mol Genet (2014) 0.77
Dasatinib as a treatment for Duchenne muscular dystrophy. Hum Mol Genet (2015) 0.76
γ-Secretase Dependent Nuclear Targeting of Dystroglycan. J Cell Biochem (2016) 0.75
Genetic Engineering of Dystroglycan in Animal Models of Muscular Dystrophy. Biomed Res Int (2015) 0.75
Can Human Pluripotent Stem Cell-Derived Cardiomyocytes Advance Understanding of Muscular Dystrophies? J Neuromuscul Dis (2016) 0.75
Myelination is delayed during postnatal brain development in the mdx mouse model of Duchenne muscular dystrophy. BMC Neurosci (2017) 0.75
Local restoration of dystrophin expression with the morpholino oligomer AVI-4658 in Duchenne muscular dystrophy: a single-blind, placebo-controlled, dose-escalation, proof-of-concept study. Lancet Neurol (2009) 5.35
Rationale for heating oxaliplatin for the intraperitoneal treatment of peritoneal carcinomatosis: a study of the effect of heat on intraperitoneal oxaliplatin using a murine model. Ann Surg (2011) 2.09
Appearances can be deceiving: phenotypes of knockout mice. Brief Funct Genomic Proteomic (2007) 1.73
Toddler: an embryonic signal that promotes cell movement via Apelin receptors. Science (2014) 1.66
Chronic systemic therapy with low-dose morpholino oligomers ameliorates the pathology and normalizes locomotor behavior in mdx mice. Mol Ther (2010) 1.48
Normalization of nomenclature for peptide motifs as ligands of modular protein domains. FEBS Lett (2002) 1.46
Safety assessment of the oral cavity probiotic Streptococcus salivarius K12. Appl Environ Microbiol (2006) 1.42
Disease recurrence after liver transplantation in Western Australia. J Gastroenterol Hepatol (2002) 1.41
Plectin 1f scaffolding at the sarcolemma of dystrophic (mdx) muscle fibers through multiple interactions with beta-dystroglycan. J Cell Biol (2007) 1.39
Production of the lantibiotic salivaricin A and its variants by oral streptococci and use of a specific induction assay to detect their presence in human saliva. Appl Environ Microbiol (2006) 1.37
Perforin mediated apoptosis of cerebral microvascular endothelial cells during experimental cerebral malaria. Int J Parasitol (2006) 1.35
Transgenic mouse proteomics identifies new 14-3-3-associated proteins involved in cytoskeletal rearrangements and cell signaling. Mol Cell Proteomics (2006) 1.32
Intestinal ischemia after laparoscopic cholecystectomy. JSLS (2006) 1.31
Synergistic effects of Pten loss and WNT/CTNNB1 signaling pathway activation in ovarian granulosa cell tumor development and progression. Carcinogenesis (2008) 1.26
The neuroprotective effects of heat shock protein 27 overexpression in transgenic animals against kainate-induced seizures and hippocampal cell death. J Biol Chem (2003) 1.24
Codon and mRNA sequence optimization of microdystrophin transgenes improves expression and physiological outcome in dystrophic mdx mice following AAV2/8 gene transfer. Mol Ther (2008) 1.24
Development and function of the mammalian spleen. Bioessays (2007) 1.23
Uncoupling antisense-mediated silencing and DNA methylation in the imprinted Gnas cluster. PLoS Genet (2011) 1.23
Muscular dystrophies due to glycosylation defects: diagnosis and therapeutic strategies. Curr Opin Neurol (2011) 1.21
Relocalization of neuronal nitric oxide synthase (nNOS) as a marker for complete restoration of the dystrophin associated protein complex in skeletal muscle. Neuromuscul Disord (2003) 1.20
Physiological characterization of muscle strength with variable levels of dystrophin restoration in mdx mice following local antisense therapy. Mol Ther (2010) 1.20
Interactions between the yeast SM22 homologue Scp1 and actin demonstrate the importance of actin bundling in endocytosis. J Biol Chem (2008) 1.16
Assessing personalized medicines in Australia: a national framework for reviewing codependent technologies. Med Decis Making (2012) 1.15
Chronic physical and mental health conditions among adults may increase vulnerability to household food insecurity. J Nutr (2013) 1.15
Expression of opsin genes early in ocular development of humans and mice. Exp Eye Res (2003) 1.14
Characterization of the role of gamma2 R531G mutation in AMP-activated protein kinase in cardiac hypertrophy and Wolff-Parkinson-White syndrome. Am J Physiol Heart Circ Physiol (2005) 1.14
Sparks, signals and shock absorbers: how dystrophin loss causes muscular dystrophy. Trends Cell Biol (2006) 1.14
A mutation in the mitochondrial fission gene Dnm1l leads to cardiomyopathy. PLoS Genet (2010) 1.13
Clinical and haemodynamic effects of sildenafil in pulmonary hypertension: acute and mid-term effects. Eur Heart J (2004) 1.13
Adeno-associated virus vector gene transfer and sarcolemmal expression of a 144 kDa micro-dystrophin effectively restores the dystrophin-associated protein complex and inhibits myofibre degeneration in nude/mdx mice. Hum Mol Genet (2002) 1.13
Dystrophin: more than just the sum of its parts. Biochim Biophys Acta (2010) 1.12
Zebrafish melanopsin: isolation, tissue localisation and phylogenetic position. Brain Res Mol Brain Res (2002) 1.12
Giving women the power to plan their families. Lancet (2012) 1.11
Dystroglycan versatility in cell adhesion: a tale of multiple motifs. Cell Commun Signal (2010) 1.11
Protective effects of heat shock protein 27 in a model of ALS occur in the early stages of disease progression. Neurobiol Dis (2007) 1.11
Extracellular release of the atheroprotective heat shock protein 27 is mediated by estrogen and competitively inhibits acLDL binding to scavenger receptor-A. Circ Res (2008) 1.08
In vivo fluorescence lifetime tomography of a FRET probe expressed in mouse. Biomed Opt Express (2011) 1.07
Heat shock protein 27 protects the heart against myocardial infarction. Basic Res Cardiol (2004) 1.06
Dystroglycan, Tks5 and Src mediated assembly of podosomes in myoblasts. PLoS One (2008) 1.05
Outcomes from combined chemoradiotherapy in unresectable and locally advanced resected cholangiocarcinoma. J Gastrointest Cancer (2012) 1.05
Down-regulation of intestinal drug transporters in chronic renal failure in rats. J Pharmacol Exp Ther (2006) 1.03
Hsp27 overexpression in the R6/2 mouse model of Huntington's disease: chronic neurodegeneration does not induce Hsp27 activation. Hum Mol Genet (2007) 1.03
Modulation of cell spreading and cell-substrate adhesion dynamics by dystroglycan. J Cell Sci (2010) 1.03
Translational and regulatory challenges for exon skipping therapies. Hum Gene Ther (2014) 1.02
The use of QALY weights for QALY calculations: a review of industry submissions requesting listing on the Australian Pharmaceutical Benefits Scheme 2002-4. Pharmacoeconomics (2008) 1.02
Heat shock protein 27 protects against atherogenesis via an estrogen-dependent mechanism: role of selective estrogen receptor beta modulation. Arterioscler Thromb Vasc Biol (2009) 1.02
Towards a global barcode library for Lymantria (Lepidoptera: Lymantriinae) tussock moths of biosecurity concern. PLoS One (2010) 1.02
Spectrum of ENU-induced mutations in phenotype-driven and gene-driven screens in the mouse. Environ Mol Mutagen (2007) 1.01
Blastic plasmacytoid dendritic cell neoplasms: clinico-immunohistochemical correlations in a series of 91 patients. Am J Surg Pathol (2014) 0.99
An ENU-induced mutation in the Ankrd11 gene results in an osteopenia-like phenotype in the mouse mutant Yoda. Physiol Genomics (2007) 0.99
Learning, odour preference and flower foraging in moths. J Exp Biol (2004) 0.98
Metformin treatment has no beneficial effect in a dose-response survival study in the SOD1(G93A) mouse model of ALS and is harmful in female mice. PLoS One (2011) 0.98
Insect odour perception: recognition of odour components by flower foraging moths. Proc Biol Sci (2006) 0.97
Recruitment of Dbl by ezrin and dystroglycan drives membrane proximal Cdc42 activation and filopodia formation. Cell Cycle (2007) 0.97
Transgenic overexpression of LARGE induces α-dystroglycan hyperglycosylation in skeletal and cardiac muscle. PLoS One (2010) 0.95
An IL-7 fusion protein that shows increased thymopoietic ability. J Immunol (2005) 0.94
Neoadjuvant chemotherapy in invasive breast cancer results in a lower axillary lymph node count. J Am Coll Surg (2008) 0.94
The WASP homologue Las17 activates the novel actin-regulatory activity of Ysc84 to promote endocytosis in yeast. Mol Biol Cell (2009) 0.93
Hyperthermic intraperitoneal chemotherapy with oxaliplatin for peritoneal carcinomatosis arising from appendix: preliminary results of a survival analysis. Ann Surg Oncol (2008) 0.93
Microbubble stability is a major determinant of the efficiency of ultrasound and microbubble mediated in vivo gene transfer. Ultrasound Med Biol (2009) 0.93
Overexpression of heat shock protein 27 reduces cortical damage after cerebral ischemia. J Cereb Blood Flow Metab (2009) 0.92
ZZ domain of dystrophin and utrophin: topology and mapping of a beta-dystroglycan interaction site. Biochem J (2007) 0.92
Capn5 is expressed in a subset of T cells and is dispensable for development. Mol Cell Biol (2004) 0.91
Surgical margins in breast-conservation operations for invasive carcinoma: does neoadjuvant chemotherapy have an impact? J Am Coll Surg (2008) 0.91
Novel aeration technique for necrotizing fasciitis of the chest wall. Ann Thorac Surg (2008) 0.91
Acute graft-versus-host disease after liver transplant: novel use of etanercept and the role of tumor necrosis factor alpha inhibitors. Liver Transpl (2009) 0.91
A randomized optical coherence tomography study of coronary stent strut coverage and luminal protrusion with rapamycin-eluting stents. JACC Cardiovasc Interv (2009) 0.90
Rectal motion can reduce CTV coverage and increase rectal dose during prostate radiotherapy: A daily cone-beam CT study. Radiother Oncol (2008) 0.89
Glycine receptor α2 subunit activation promotes cortical interneuron migration. Cell Rep (2013) 0.89
Structure and evolution of the teleost extraretinal rod-like opsin (errlo) and ocular rod opsin (rho) genes: is teleost rho a retrogene? J Exp Zool B Mol Dev Evol (2003) 0.88
The transgenic expression of LARGE exacerbates the muscle phenotype of dystroglycanopathy mice. Hum Mol Genet (2013) 0.88
Identification of a repressor in the first intron of the human alpha2(I) collagen gene (COL1A2). J Biol Chem (2005) 0.88
Role of a 5'-enhancer in the transcriptional regulation of the human endothelial cell protein C receptor gene. Blood (2006) 0.87
The human ClC-4 protein, a member of the CLC chloride channel/transporter family, is localized to the endoplasmic reticulum by its N-terminus. FASEB J (2006) 0.87
ENU mutagenesis reveals a novel phenotype of reduced limb strength in mice lacking fibrillin 2. PLoS One (2010) 0.87
Cooperativity between far upstream enhancer and proximal promoter elements of the human {alpha}2(I) collagen (COL1A2) gene instructs tissue specificity in transgenic mice. J Biol Chem (2004) 0.86
Prostate cancer cells preferentially home to osteoblast-rich areas in the early stages of bone metastasis: evidence from in vivo models. J Bone Miner Res (2014) 0.86
Electroporation for gene transfer to skeletal muscles: current status. BioDrugs (2004) 0.85
An active Src kinase-beta-actin association is linked to actin dynamics at the periphery of colon cancer cells. Exp Cell Res (2007) 0.85
A role for β-dystroglycan in the organization and structure of the nucleus in myoblasts. Biochim Biophys Acta (2012) 0.85
Heat shock protein 27 overexpression mitigates cytokine-induced islet apoptosis and streptozotocin-induced diabetes. Endocrinology (2009) 0.85
Menadione kills trophozoites and cysts of Giardia intestinalis. Microbiology (2004) 0.85
Disentangling dispersal, vicariance and adaptive radiation patterns: a case study using armyworms in the pest genus Spodoptera (Lepidoptera: Noctuidae). Mol Phylogenet Evol (2012) 0.84
Depletion of the actin bundling protein SM22/transgelin increases actin dynamics and enhances the tumourigenic phenotypes of cells. BMC Cell Biol (2012) 0.84
Total dysphagia after short course of systemic corticotherapy: herpes simplex virus esophagitis. World J Gastroenterol (2013) 0.84
The inside and out of dystroglycan post-translational modification. Neuromuscul Disord (2012) 0.84
The effect of ingestion of milk supplemented with salivaricin A-producing Streptococcus salivarius on the bacteriocin-like inhibitory activity of streptococcal populations on the tongue. FEMS Microbiol Ecol (2006) 0.83
In silico characterisation and chromosomal localisation of human RRH (peropsin)--implications for opsin evolution. BMC Genomics (2003) 0.83
Identification of the key regions within the mouse pro-alpha 2(I) collagen gene far-upstream enhancer. J Biol Chem (2001) 0.83
Stable micro-dystrophin gene transfer using an integrating adeno-retroviral hybrid vector ameliorates the dystrophic pathology in mdx mouse muscle. Hum Mol Genet (2002) 0.83
Laparoscopic donor nephrectomy. ANZ J Surg (2010) 0.82
A new twist to coiled coil. FEBS Lett (2012) 0.82
Fataluku medicinal ethnobotany and the East Timorese military resistance. J Ethnobiol Ethnomed (2007) 0.82
Improving the acceptability of the atrial defibrillator: patient-activated cardioversion versus automatic night cardioversion with and without sedation (ADSAS 2). Pacing Clin Electrophysiol (2004) 0.82
Surgical cytoreduction and intraperitoneal chemotherapy for peritoneal carcinomatosis arising from the appendix. Can J Surg (2009) 0.81
Is severe intestinal chronic graft-versus-host disease an indication for surgery? A report of two cases. Transplantation (2004) 0.81
Effect of albumin and dextrose concentration on ultrasound and microbubble mediated gene transfection in vivo. Ultrasound Med Biol (2012) 0.81