Baseline Analysis of a Young α-1-Antitrypsin Deficiency Liver Disease Cohort Reveals Frequent Portal Hypertension.

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Published in J Pediatr Gastroenterol Nutr on July 01, 2015

Authors

Jeffrey H Teckman1, Philip Rosenthal, Robert Abel, Lee M Bass, Sonia Michail, Karen F Murray, David A Rudnick, Daniel W Thomas, Cathie Spino, Ronen Arnon, Paula M Hertel, James Heubi, Binita M Kamath, Wikrom Karnsakul, Kathleen M Loomes, John C Magee, Jean P Molleston, Rene Romero, Benjamin L Shneider, Averell H Sherker, Ronald J Sokol, Childhood Liver Disease Research Network (ChiLDReN)

Author Affiliations

1: *Pediatrics and Biochemistry, Saint Louis University, Cardinal Glennon Children's Medical Center, St Louis, MO †Pediatrics and Surgery, University of California San Francisco, San Francisco ‡Biostatistics, University of Michigan, Ann Arbor, MI §Pediatrics, Northwestern University Feinberg School of Medicine, Chicago, IL ||Pediatric Gastroenterology, Hepatology and Nutrition, Children's Hospital Los Angeles, Los Angeles, CA ¶Pediatric Gastroenterology and Hepatology, Seattle Children's Hospital, Seattle, WA #Pediatrics, Washington University, St Louis, MO **Pediatrics, Mount Sinai School of Medicine, New York, NY ††Pediatrics, Baylor College of Medicine, Texas Children's Hospital, Houston ‡‡Pediatric Gastroenterology and Hepatology, Children's Hospital Medical Center, Cincinnati, OH §§Pediatric Gastroenterology, Hepatology and Nutrition, Hospital for Sick Children, Toronto, Canada ||||Pediatrics, Johns Hopkins University School of Medicine, Baltimore, MD ¶¶Pediatric Gastroenterology, Hepatology and Nutrition, Children's Hospital of Philadelphia, Philadelphia, PA ##Surgery, University of Michigan School of Medicine, Ann Arbor ***Pediatric Gastroenterology, Hepatology and Nutrition, James Whitcomb Riley Hospital for Children, Indianapolis, IN †††Pediatrics, Emory University, Children's Healthcare Atlanta, Atlanta, GA ‡‡‡Pediatrics, University of Pittsburgh, Pittsburgh, PA §§§National Institute of Diabetes, Digestive and Kidney Disease, National Institutes of Health, Baltimore, MD ||||||Pediatric Gastroenterology, University of Colorado, Children's Hospital Colorado, Aurora.

Associated clinical trials:

Evaluating the Genetic Causes and Progression of Cholestatic Liver Diseases (LOGIC) (LOGIC) | NCT00571272

FibroScan™ in Pediatric Cholestatic Liver Disease Study Protocol (FORCE) | NCT02922751

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