Published in Pediatrics on May 01, 1989
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The nature of malnutrition in children with end-stage liver disease awaiting orthotopic liver transplantation. Am J Clin Nutr (1992) 0.93
Comparison of the Cosmed K4 b(2) and the Deltatrac II metabolic cart in measuring resting energy expenditure in adults. Clin Nutr (2002) 0.93
Colipase and maximally activated pancreatic lipase in normal subjects and patients with steatorrhea. J Clin Invest (1982) 0.93
Malabsorption of medium-chain triglycerides in infants with cystic fibrosis: correction with pancreatic enzyme supplement. J Pediatr (1980) 0.92
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The effects of weight loss strategies on gastric emptying and appetite control. Obes Rev (2011) 0.90
Childhood diaphragmatic hernias presenting after the neonatal period. Clin Radiol (1988) 0.89
Pancreatic function testing in cystic fibrosis. J Pediatr Gastroenterol Nutr (1984) 0.89
Steatorrhea and pancreatic insufficiency in Shwachman syndrome. Gastroenterology (1982) 0.89
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Pathophysiology of the pancreatic defect in Johanson-Blizzard syndrome: a disorder of acinar development. J Pediatr (1994) 0.89
Pathophysiology of the ciliary motility syndromes. Eur J Respir Dis Suppl (1983) 0.88
Serum immunoreactive cationic trypsinogen: a useful indicator of severe exocrine dysfunction in the paediatric patient without cystic fibrosis. Gut (1986) 0.87
Impact of ethnicity upon body composition assessment in Sri Lankan Australian children. J Paediatr Child Health (2005) 0.87
Survival, growth and quality of life in children after orthotopic liver transplantation: a 5 year experience. J Paediatr Child Health (1991) 0.86
The immotile cilia syndrome: radiological manifestations. Radiology (1985) 0.86
Bentiromide test for assessing pancreatic dysfunction using analysis of para-aminobenzoic acid in plasma and urine. Studies in cystic fibrosis and Shwachman's syndrome. Gastroenterology (1985) 0.86
Prepubertal ovarian cyst formation: 5 years' experience. Obstet Gynecol (1993) 0.86
Pre-operative nutritional support in children with end-stage liver disease accepted for liver transplantation: an approach to management. J Gastroenterol Hepatol (1991) 0.85
Longitudinal evaluation of serum trypsinogen measurement in pancreatic-insufficient and pancreatic-sufficient patients with cystic fibrosis. J Pediatr (1995) 0.85
Pediatric case of the day. Orbital hydatid cyst. Radiographics (1995) 0.85
Cytomegalovirus infection after liver transplantation in children. J Gastroenterol Hepatol (1994) 0.85
Management of fibrosing pancreatitis in children presenting with obstructive jaundice. Gut (1998) 0.85
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Nutritional rehabilitation in cystic fibrosis: a 5 year follow-up study. J Pediatr Gastroenterol Nutr (1992) 0.84
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Does the Macroduct collection system reliably define sweat chloride concentration in subjects with intermediate results? Clin Biochem (2009) 0.84
Cystic fibrosis modifier genes related to Pseudomonas aeruginosa infection. Genes Immun (2011) 0.84
Appendicitis in cystic fibrosis. Arch Dis Child (1991) 0.83
Diagnosis of Legionella lung abscess by percutaneous needle aspiration. Can Assoc Radiol J (1989) 0.83
Transplantation in children with biliary atresia. Transplant Proc (1992) 0.83
Treatment failure in celiac disease due to coexistent exocrine pancreatic insufficiency. Pediatrics (1987) 0.83
Validity of currently used cutoff values of body mass index as a measure of obesity in Sri Lankan children. Ceylon Med J (2009) 0.83
Recurrent tracheo-esophageal fistula: a protocol for investigation. Radiology (1984) 0.83
Effects of cisapride in patients with cystic fibrosis and distal intestinal obstruction syndrome. J Pediatr (1990) 0.82
Pediatric case of the day. Infected fourth branchial pouch sinus with an extensive complicating cervical and mediastinal abscess and left-sided empyema. Radiographics (1995) 0.82
The sleep patterns of infants and young children with gastro-oesophageal reflux. J Paediatr Child Health (1998) 0.82
Comparison of aortography, renal vein renin sampling, radionuclide scans, ultrasound and the IVU in the investigation of childhood renovascular hypertension. Br J Radiol (1984) 0.82
Airway cellularity, lipid laden macrophages and microbiology of gastric juice and airways in children with reflux oesophagitis. Respir Res (2005) 0.82
Academic potential and cognitive functioning of long-term survivors after childhood liver transplantation. Pediatr Transplant (2014) 0.81
Assessment of body composition in Sri Lankan children: validation of a bioelectrical impedance prediction equation. Eur J Clin Nutr (2007) 0.81
Pancreatitis and mutations of the cystic fibrosis gene. N Engl J Med (1998) 0.81
Exclusion of linkage of Shwachman-Diamond syndrome to chromosome regions 6q and 12q implicated by a de novo translocation. Am J Med Genet (1999) 0.81
Elevated serum immunoreactive pancreatic cationic trypsinogen in acute malnutrition: evidence of pancreatic damage. J Pediatr (1985) 0.81
Gruntzig angioplasty dilatation of an esophageal stricture in an infant. Pediatr Radiol (1985) 0.81
Skin irritation: Reference chemicals data bank. Toxicol In Vitro (1996) 0.81
Pathology considerations for, and subsequent risk assessment of, chemicals identified as immunosuppressive in routine toxicology. Food Chem Toxicol (1995) 0.80