Published in Gut on September 01, 1980
Non-invasive assessment of intraluminal lipolysis using a 13CO2 breath test. Arch Dis Child (1990) 1.16
Cystic fibrosis--a gastroenterological cornucopia. Gut (1987) 1.11
Treatment of Gastrointestinal Problems in Cystic Fibrosis. Curr Treat Options Gastroenterol (2003) 1.06
Enzyme replacement therapy for pancreatic insufficiency: present and future. Clin Exp Gastroenterol (2011) 0.94
Lingual lipase in cystic fibrosis. Quantitation of enzyme activity in the upper small intestine of patients with exocrine pancreatic insufficiency. J Clin Invest (1984) 0.85
Omeprazole, a proton pump inhibitor, improves residual steatorrhoea in cystic fibrosis patients treated with high dose pancreatic enzymes. Eur J Pediatr (2003) 0.85
Gastrointestinal tract and nutrition in cystic fibrosis: pathophysiology. J R Soc Med (1986) 0.84
Optimising the therapy of exocrine pancreatic insufficiency by the association of a proton pump inhibitor to enteric coated pancreatic extracts. Gut (2006) 0.83
Rationale of modern dietary recommendations in cystic fibrosis. J R Soc Med (1987) 0.82
Acid resistant lipase as replacement therapy in chronic pancreatic exocrine insufficiency: a study in dogs. Gut (1989) 0.81
Practical management of nutrition and gastrointestinal tract in cystic fibrosis. J R Soc Med (1986) 0.79
Uses and abuses of enzyme therapy in cystic fibrosis. J R Soc Med (1998) 0.78
Gastrointestinal symptoms before and after total pancreatectomy with islet autotransplantation: the role of pancreatic enzyme dosing and adherence. Pancreas (2015) 0.76
Effect of taurine supplementation on fat and energy absorption in cystic fibrosis. Arch Dis Child (1992) 0.76
Pancreatic enzyme replacement therapy for pancreatic exocrine insufficiency in the 21(st) century. World J Gastroenterol (2014) 0.76
Thymopentin treatment in severe atopic dermatitis--clinical and immunological evaluations. Arch Dis Child (1992) 0.75
Non-ulcer users of cimetidine. Br Med J (Clin Res Ed) (1981) 0.75
Effect of cimetidine in pancreatic steatorrhoea. Gut (1986) 0.75
Pathogenesis and physiopathology of cystic fibrosis of the pancreas. Fibrocystic disease of the pancreas (Mucoviscidosis). N Engl J Med (1967) 2.15
Comparative effects of antacids, cimetidine and enteric coating on the therapeutic response to oral enzymes in severe pancreatic insufficiency. N Engl J Med (1977) 1.85
Fate of orally ingested enzymes in pancreatic insufficiency. Comparison of two dosage schedules. N Engl J Med (1977) 1.84
Malabsorption of bile acids in children with cystic fibrosis. N Engl J Med (1973) 1.63
Fibrocystic disease of the pancreas with normal or partial pancreatic function; current views on pathogenesis and diagnosis. Pediatrics (1955) 1.49
Steatorrhea and azotorrhea and their relation to growth and nutrition in adolescents and young adults with cystic fibrosis. J Pediatr (1974) 1.46
The effect of cimetidine on maldigestion in cystic fibrosis. J Pediatr (1979) 1.43
Effect of sodium bicarbonate and pancreatin on the absorption of vitamin B12 and fat in pancreatic insufficiency. N Engl J Med (1962) 1.42
Abnormal biliary lipid composition in cystic fibrosis. Effect of pancreatic enzymes. N Engl J Med (1977) 1.23
Fat absorption studies in the diagnosis and treatment of pancreatic fibrosis. Arch Dis Child (1955) 1.21
Cystic fibrosis of the pancreas with varying degrees of pancreatic insufficiency. AMA J Dis Child (1956) 1.19
"Break-through in cystic fibrosis". Pediatrics (1961) 1.08
Comparative nitrogen balance study between young and aged adults using three levels of protein intake from a combination wheat-soy-milk mixture. Am J Clin Nutr (1978) 1.07
Enzyme replacement therapy of exocrine pancreatic insufficiency in man. Relations between in vitro enzyme activities and in vivo potency in commercial pancreatic extracts. N Engl J Med (1977) 1.02
Protein absorption and ammonia production: the effects of dietary protein and removal of the colon. Br J Nutr (1976) 0.95
Pancreatic extracts in the treatment of pancreatic exocrine insufficiency. Gut (1975) 0.91
Cystic fibrosis of the pancreas: intestinal absorption of fat and fatty acid labeled with I 131. Pediatrics (1958) 0.88
Comparative trial of pancrex V forte and nutrizym in treatment of malabsorption in cystic fibrosis. Br Med J (1974) 0.84
Clive Maine McCay (1898-1967)--a biographical sketch. J Nutr (1973) 0.83
Development of a computerized system for calculating nutrient intakes. J Can Diet Assoc (1979) 0.81
The STE4 and STE18 genes of yeast encode potential beta and gamma subunits of the mating factor receptor-coupled G protein. Cell (1989) 5.07
Rat intestinal microvillus membranes. Purification and biochemical characterization. Biochem J (1968) 3.66
General practice audit of asthma in childhood. Br Med J (Clin Res Ed) (1984) 2.98
Neuropsychology of first-episode schizophrenia: initial characterization and clinical correlates. Am J Psychiatry (2000) 2.93
Sex lethal controls dosage compensation in Drosophila by a non-splicing mechanism. Nature (1997) 2.52
The molecular cloning and characterisation of cDNA coding for the alpha subunit of the acetylcholine receptor. Nucleic Acids Res (1982) 1.80
Occurrence of crossed strand-exchange forms in yeast DNA during meiosis. Proc Natl Acad Sci U S A (1979) 1.78
Microvillus inclusion disease: an inherited defect of brush-border assembly and differentiation. N Engl J Med (1989) 1.77
Correlation of sweat chloride concentration with classes of the cystic fibrosis transmembrane conductance regulator gene mutations. J Pediatr (1995) 1.70
DNA marker haplotype association with pancreatic sufficiency in cystic fibrosis. Am J Hum Genet (1989) 1.66
Separation of branched from linear DNA by two-dimensional gel electrophoresis. Anal Biochem (1983) 1.59
A randomized, controlled trial of the efficacy of a heparin and vancomycin solution in preventing central venous catheter infections in children. J Pediatr (1995) 1.59
(1-14C)glucosamine incorporation by subcellular fractions of small intestinal mucosa. Identification by precursor labeling of three functionally distinct glycoprotein classes. J Biol Chem (1970) 1.57
Goblet cell mucin of rat small intestine. Chemical and physical characterization. Can J Biochem (1973) 1.55
High-dose pancreatic-enzyme supplements and fibrosing colonopathy in children with cystic fibrosis. N Engl J Med (1997) 1.51
Acute pancreatitis in childhood. J Pediatr (1988) 1.49
Antigenic and structural features of goblet-cell mucin of human small intestine. Biochem J (1984) 1.48
Shwachman syndrome: phenotypic manifestations of sibling sets and isolated cases in a large patient cohort are similar. J Pediatr (1999) 1.47
A position paper of the North American Society for Pediatric Gastroenterology and Nutrition. Pediatric gastroenterology Workforce Survey and future supply and demand. J Pediatr Gastroenterol Nutr (1998) 1.45
Bile acid secretion in cystic fibrosis: evidence for a defect unrelated to fat malabsorption. Gut (1986) 1.44
Release of intestinal surface-membrane glycoproteins associated with enzyme activity by brief digestion with papain. Biochem J (1971) 1.42
Heterogeneity of rat goblet-cell mucin before and after reduction. Biochem J (1983) 1.42
Biochemical characterization of the component parts of intestinal mucin from patients with cystic fibrosis. Biochem J (1984) 1.40
Lipid composition of the isolated rat intestinal microvillus membrane. Biochem J (1968) 1.40
Rickets due to calcium deficiency. N Engl J Med (1977) 1.37
Age-related alterations of immunoreactive pancreatic cationic trypsinogen in sera from cystic fibrosis patients with and without pancreatic insufficiency. Pediatr Res (1986) 1.34
Spatiotemporal segregation of endothelial cell integrin and nonintegrin extracellular matrix-binding proteins during adhesion events. J Cell Biol (1990) 1.32
Effects of long-term nutritional rehabilitation on body composition and clinical status in malnourished children and adolescents with cystic fibrosis. J Pediatr (1985) 1.30
Recommendations for management of liver and biliary tract disease in cystic fibrosis. Cystic Fibrosis Foundation Hepatobiliary Disease Consensus Group. J Pediatr Gastroenterol Nutr (1999) 1.28
Endothelial cell behavior after denudation injury is modulated by transforming growth factor-beta1 and fibronectin. Lab Invest (1989) 1.28
Treatment of distal intestinal obstruction syndrome in cystic fibrosis with a balanced intestinal lavage solution. Lancet (1986) 1.28
cDNA for the carboxyl-terminal region of a rat intestinal mucin-like peptide. J Biol Chem (1992) 1.28
Pathology of pancreatic and intestinal disorders in cystic fibrosis. J R Soc Med (1998) 1.28
Skeletal phenotype in patients with Shwachman-Diamond syndrome and mutations in SBDS. Clin Genet (2004) 1.27
Evidence for a primary defect of pancreatic HCO3-secretion in cystic fibrosis. Pediatr Res (1982) 1.26
Uncertainty in the diagnosis of cystic fibrosis: possible role of in vivo nasal potential difference measurements. J Pediatr (1998) 1.26
Shwachman syndrome: exocrine pancreatic dysfunction and variable phenotypic expression. Gastroenterology (1996) 1.25
Radioimmunoassay of human intestinal goblet cell mucin. Investigation of mucus from different organs and species. J Clin Invest (1979) 1.24
Synthesis of intestinal glycoprotein. Incorporation of (I- 14 C) glucosamine in vitro. Biochim Biophys Acta (1971) 1.23
Shwachman-Diamond syndrome with exocrine pancreatic dysfunction and bone marrow failure maps to the centromeric region of chromosome 7. Am J Hum Genet (2001) 1.21
Characterization and localization of the putative 'link' component in rat small-intestinal mucin. Biochem J (1987) 1.20
Modulation of vascular cell behavior by transforming growth factors beta. Mol Reprod Dev (1992) 1.19
Treatment of nongonococcal urethritis with ciprofloxacin. Am J Med (1987) 1.18
Colipase and lipase secretion in childhood-onset pancreatic insufficiency. Delineation of patients with steatorrhea secondary to relative colipase deficiency. Gastroenterology (1984) 1.17
Use of pancreatic enzyme supplements for patients with cystic fibrosis in the context of fibrosing colonopathy. Consensus Committee. J Pediatr (1995) 1.16
Phenotypic abnormalities in long-term surviving cystic fibrosis mice. Pediatr Res (1996) 1.16
Enhancement of the viscosity of mucin by serum albumin. Biochem J (1978) 1.14
Dietary intakes of young children with cystic fibrosis: is there a difference? J Pediatr Gastroenterol Nutr (1996) 1.12
Late gastrointestinal bleeding and protein loss after distal small-bowel resection in infancy. J Pediatr Gastroenterol Nutr (1989) 1.11
The T84 human colonic adenocarcinoma cell line produces mucin in culture and releases it in response to various secretagogues. Biochem J (1990) 1.08
Pathogenesis of mucosal injury in the blind loop syndrome. Brush border enzyme activity and glycoprotein degradation. J Clin Invest (1977) 1.06
The role of disulphide bonds in human intestinal mucin. Biochem J (1979) 1.05
Asynchronous development of the rat colon. Anat Embryol (Berl) (1991) 1.05
Leptospirosis in meat inspectors: preliminary results of a serological survey. N Z Med J (1979) 1.05
Fecal clearance of alpha 1-antitrypsin: a reliable measure of enteric protein loss in children. J Pediatr (1981) 1.04
Pathophysiology of the exocrine pancreas in cystic fibrosis. J R Soc Med (1989) 1.04
Contraceptive knowledge and practice among undergraduates at a Canadian university. Am J Obstet Gynecol (1976) 1.04
Iatrogenic hyperuricemia in children with cystic fibrosis. J Pediatr (1978) 1.04
Malnutrition: a cause of elevated sweat chloride concentration. Acta Paediatr Scand (1986) 1.03
Meconium ileus in the absence of cystic fibrosis. Arch Dis Child (1992) 1.03
Lavage treatment of distal intestinal obstruction syndrome in children with cystic fibrosis. Pediatrics (1989) 1.02
Effects of calcium on intestinal mucin: implications for cystic fibrosis. Pediatr Res (1976) 1.01
Synthesis and secretion of mucin by the human colonic tumour cell line LS180. Biochem J (1994) 1.01
Skeletal findings in children recently initiating glucocorticoids for the treatment of nephrotic syndrome. Osteoporos Int (2011) 1.00
The association of cystic fibrosis, gastroesophageal reflux, and reduced pulmonary function. Can Assoc Radiol J (1988) 1.00
Effects of soluble factors and extracellular matrix components on vascular cell behavior in vitro and in vivo: models of de-endothelialization and repair. J Cell Biochem (1991) 1.00
Soluble neutral and acid maltases in the suckling-rat intestine. The effect of cortisol and development. Biochem J (1974) 0.99
Plasma membrane and mucosal glycosphingolipids in the rat intestine. Biochim Biophys Acta (1973) 0.99
Pathogenesis of malnutrition in cystic fibrosis, and its treatment. Clin Nutr (2000) 0.98
Cholera toxin stimulates secretion of immunoreactive intestinal mucin. Am J Physiol (1981) 0.98
Isolation of microvillus plasma membranes from suckling-rat intestine. The influence of premature induction of digestive enzymes by injection of cortisol acetate. Biochem J (1974) 0.97
Peptic ulcer disease in children: etiology, clinical findings, and clinical course. Pediatrics (1988) 0.96
Calcium binding to intestinal goblet cell mucin. Biochim Biophys Acta (1975) 0.96
Radioimmunoassay of intestinal goblet cell mucin. Anal Biochem (1977) 0.95
Colipase and maximally activated pancreatic lipase in normal subjects and patients with steatorrhea. J Clin Invest (1982) 0.93
A scanning and transmission electron microscopical study of the morphogenesis of human colonic villi. Anat Embryol (Berl) (1982) 0.93
Anterior hippocampal volume reductions predict frontal lobe dysfunction in first episode schizophrenia. Schizophr Res (1995) 0.93
Surface sugar in the intestine. Am J Med Sci (1969) 0.93
Growth during maintenance hemodialysis: impact of enhanced nutrition and clearance. J Pediatr (1999) 0.92
Treatment of vitamin K deficiency in cystic fibrosis: Effectiveness of a daily fat-soluble vitamin combination. J Pediatr (2001) 0.92
Malabsorption of medium-chain triglycerides in infants with cystic fibrosis: correction with pancreatic enzyme supplement. J Pediatr (1980) 0.92
Isolated congenital lipase-colipase deficiency. Gastroenterology (1984) 0.92
NF-kappaB transcription factors are involved in normal erythropoiesis. Blood (1998) 0.91
Congenital fistulas of the lower lip. A family case report. Oral Surg Oral Med Oral Pathol (1966) 0.91
Accumulation of eosinophils in intestine-draining mesenteric lymph nodes occurs after Trichuris muris infection. Parasite Immunol (2011) 0.91
The carboxyl-terminal sequence of rat intestinal mucin RMuc3 contains a putative transmembrane region and two EGF-like motifs. Biochim Biophys Acta (1997) 0.91
Synthesis of intestinal clycoproteins. Inhibition of (I- 14 C)glucosamine incorporation by sodium salicylate in vitro. Biochim Biophys Acta (1972) 0.91